Create issue ticket

146 Possible Causes for 5 aminopentanamide, L lysine, acetyl CoA, catabolic, process, to, via

Did you mean: 5 aminopentanamide, L lysine, acetyl CoA, catabolic, proteus, to, via

  • Biotin Deficiency

    […] developed in an 11-month-old Japanese infant who had been diagnosed as a neonate with cow milk and soy bean allergy and fed with an amino acid formula and hypoallergenic rice processed[ncbi.nlm.nih.gov] We conclude that anticonvulsant treatment led to increased biotin catabolism and probably to reduced biotin status.[ncbi.nlm.nih.gov] Am J Physiol 263:G81–G86 PubMed Google Scholar Said HM, Thuy LP, Sweetman L et al (1993) Transport of the biotin dietary derivative biocytin (N-biotinyl-L-lysine) in rat small[doi.org] For example, acetyl-CoA carboxylase catalyzes the rate-limiting step in fatty acid elongation.[ncbi.nlm.nih.gov] If you have access to journal via a society or associations, read the instructions below Members of _ can log in with their society credentials below Username (required) Password[doi.org] Also, try to avoid processed foods, since processing strips this and other vitamins out of the food you eat.[stop-being-tired.com] Therefore, biotin is essential for amino acid catabolism, gluconeogenesis, and fatty acid metabolism.[en.wikipedia.org]

    Missing: 5 aminopentanamide to
  • Cytosolic Acetoacetyl-CoA Thiolase Deficiency

    This process is experimental and the keywords may be updated as the learning algorithm improves. This is a preview of subscription content, log in to check access.[link.springer.com] Associations: Defects in ACAT1 are a cause of 3-ketothiolase deficiency (3KTD) [ MIM:203750 ], also known as alpha-methylacetoaceticaciduria. 3KTD is an inborn error of isoleucine catabolism[mitosciences.com] Deficiency of lyase Deficiency of lysine-tRNA ligase Deficiency of lysolecithin acylmutase Deficiency of lysophospholipase Deficiency of lysozyme Deficiency of malate dehydrogenase[icdlist.com] CoA Thiolase, Acetoacetyl; C- Acetyltransferase, Acetyl- CoA; Acetyltransferase, Acetyl- CoA; Acetyl CoA C Acetyltransferase; Acetyl CoA Acetyltransferase Substance CAS Registry[reference.md] To view the fulltext, please log in To view the pdf, please log in Buy FullText & PDF Unlimited re-access via MyKarger Unrestricted printing, no saving restrictions for personal[karger.com] Sequence processing i : The displayed sequence is further processed into a mature form. This entry describes 2 isoforms i produced by alternative splicing .[uniprot.org] Prenatal Diagnosis / Carrier Detection Research Abstract Beta-ketothiolase deficiency (3KTD) is an autosomal recessive metabolic disease of organic acids involving isoleucine catabolic[kaken.nii.ac.jp]

    Missing: 5 aminopentanamide to
  • Acetyl-CoA Carboxylase Deficiency

    Two colleagues were particularly helpful ledge of genetic defects, biochemical abnormalities, and provided us with essential and unpublished f- and cellular processes underlying[books.google.com] Provider 3- Methylcrotonyl - CoA Carboxylase Deficiency (3MMC or 3MCC) Description: 3- Methylcrotonyl - CoA Carboxylase Deficiency is an autosomal recessive disorder of leucine catabolism[yumpu.com] […] dipeptidase Deficiency of L-serine dehydratase Deficiency of lyase Deficiency of lysine racemase Deficiency of lysine-tRNA ligase Deficiency of lysolecithin acylmutase Deficiency[icd9data.com] An important gene associated with Acetyl-Coa Carboxylase Deficiency is ACACA (Acetyl-CoA Carboxylase Alpha).[malacards.org] For example, AMPK activation increases (a) glucose uptake (via recruiting to the cell membrane or activating glucose transporters GLUT4 and GLUT1), (b) glycolysis (via phosphorylation[www4.ilovetranslation.com] : vitamin metabolic process; acetyl-CoA metabolic process; positive regulation of cellular metabolic process; lipid homeostasis; triacylglycerol biosynthetic process; carnitine[mybiosource.com] Maintenance on a low-protein diet, to minimize the burden of leucine that must be catabolized, prevents the development of metabolic acidosis.[doctorabel.us]

    Missing: 5 aminopentanamide to
  • Isovaleric Acidemia

    We have reported elsewhere nine point mutations in the IVD gene in fibroblasts of patients with IVA, which lead to abnormalities in IVD protein processing and activity.[ncbi.nlm.nih.gov] In approximately one-fifth of catabolic episodes, no trigger was apparent. Triggering factors of catabolic episodes in symptomatic isovaleric acidemia (IVA) .[ncbi.nlm.nih.gov] L-Methionine, L- Cystine, L Valine, L-Phenylalanine, L- Alanine, L-Aspartic acid, L-Tyrosine, L-Glutamic Acid, Glutamine, Lysine) Tri calcium phosphate, Magnesium oxide, Ferric[pristineorganics.com] The Ki of isovaleryl-CoA dehydrogenase by (methylenecyclopropyl)acetyl-CoA was approximately 2 microM.[ncbi.nlm.nih.gov] This suggests that detoxification via glucuronide conjugation plays an important role when the glycine conjugation system is saturated.[ncbi.nlm.nih.gov] These data suggest that binding of the variant protein to mitochondrial membrane receptors per se is hindered, resulting in the inefficient mitochondrial processing.[ncbi.nlm.nih.gov] Its pathophysiological process is mainly via the competitive inhibition of N-acetylglutamate synthetase.[ncbi.nlm.nih.gov]

    Missing: 5 aminopentanamide to
  • Glutaric Aciduria

    Proton magnetic resonance spectroscopy in the parietal white matter revealed a markedly increased choline/creatine ratio, suggesting a demyelinating process.[ncbi.nlm.nih.gov] Glutaric aciduria type I (GA-I; synonym, glutaric acidemia type I) is a rare inherited metabolic disease caused by deficiency of glutaryl-CoA dehydrogenase located in the catabolic[ncbi.nlm.nih.gov] The primary defect is the deficiency of Glutaryl-CoA dehydrogenase (EC number 1.3.99.7) enzyme that is involved in the catabolic pathways of the amino acids l-lysine, l-hydroxylysine[ncbi.nlm.nih.gov] […] will then produce two molecules of acetyl-CoA and enter TCA Cycle 19 Lysine Degradation 20 Lysine Degradation 21 Tryptophan Degradation Eight mechanistic steps Eventually[powershow.com] In conclusion, our results indicate a low but specific efflux transport for GA, 3-OH-GA, and MMA across pBCEC, an in vitro model of the BBB, via OAT1 and OAT3 but not across[ncbi.nlm.nih.gov] This might indicate increased resynthesis of dendritic processes secondary to preceding metabolic crises.[ncbi.nlm.nih.gov] Glutaric aciduria type I is caused by inherited deficiency of glutaryl-CoA dehydrogenase which is involved in the catabolic pathways of L-lysine, L-hydroxylysine and L-tryptophan[ncbi.nlm.nih.gov]

    Missing: 5 aminopentanamide to
  • Pipecolic Acidemia

    Quickly grasp the fundamentals you need to know through a more precise, streamlined format, reorganized by systems and disease processes, as well as "Teaching Boxes" that[books.google.com] Packaging 1 g in glass bottle 100, 250 mg in glass insert Biochem/physiol Actions L-Pipecolic acid is a lysine metabolite; defect in its catabolism is involved in hyperpipecolic[sigmaaldrich.com] C01186 (3S,5S)-3,5-Diaminohexanoate C01211 Procollagen 5-hydroxy-L-lysine C01259 (3S)-3-Hydroxy-N6,N6,N6-trimethyl-L-lysine C01672 Cadaverine C02188 Protein lysine C02727[genome.jp] See also AASDHPPT PHYH References External links Definition in biology-online.org v t e Inborn error of amino acid metabolism ( E70–E72 , 270 ) K acetyl-CoA Lysine /straight[worldlibrary.org] ., July 31, via Qnebeo AlU. 25. witb iron to order. U. S. steam transpor... ... forces here.[newspaperslibrary.org] […] intake or from mammalian or intestinal bacterial enzyme metabolism Recent studies suggest that plasma pipecolic acid, particularly the D-isomer, originates mainly from the catabolism[metagene.de] Background: The essential amino acid lysine can be degraded via two pathways, the saccharopine pathway and the pipecolic acid (PA) pathway.[southtees.nhs.uk]

    Missing: to
  • Lactobacillus Bulgaricus

    KEYWORDS: Lactobacillus bulgaricus extract; freeze–thawing process; poly (vinyl alcohol); poly (vinyl alcohol)κ-Carrageenan[ncbi.nlm.nih.gov] These results suggest that lactose catabolism is not under catabolic repression by glucose in L. bulgaricus .[aem.asm.org] ATP-binding subunit ClpX ( clpX ), chromosomal replication initiation protein ( dnaA ), CTP synthetase ( pyrG ), chaperonin GroEL ( groEL ), UDP-N-acetylmuramoylalanyl-D-glutamate-L-lysine[nature.com] Acetyl-CoA may subsequently be used for the production of saturated fatty acids.[ncbi.nlm.nih.gov] . & Gerhardt P. 1981 Dialysis continuous process for ammonium-lactate fermentation: simulated and experimental dialysated-feed immobilized cell systems.[link.springer.com] Ardo Y (2006) Flavour formation by amino acid catabolism. Biotechnol Adv 24: 238–242. View Article Google Scholar 36.[journals.plos.org] During the freeze-drying process, the wall materials alone provided little protection against cell mortality.[zora.uzh.ch]

    Missing: 5 aminopentanamide to
  • Lactococcus Lactis

    Under these conditions, almost 10% of the 900 samples processed yielded viable phages.[doi.org] Changes in aroma profile resembled some of the biochemical changes occurring during cheese ripening and reflected amino acid catabolism, metabolism of fatty acids and conversion[ncbi.nlm.nih.gov] For the other genes, which play minor roles in the thermal tolerance, llmg_2477 and llmg_2541 encodes lysine specific permease and cation transporting ATPase, respectively[nature.com] Under aerobic conditions, the PDH complex is the only pathway leading to the formation of acetyl-CoA from pyruvate, and as acetyl-CoA is an essential metabolite in many processes[bmcmicrobiol.biomedcentral.com] The pH of culture was controlled at 6.0 for 6–24 h via the addition of NaOH (10 M).[nature.com] Pagina 241 - The work on peptidases and amino acid catabolism conducted in our laboratory was supported in part by the College of Agricultural and Life Sciences at the University[books.google.ro] […] selected for use in fermentations based on their metabolic stability, their resistance to bacteriophage, and their ability to produce unique compounds often from amino acid catabolism[uniprot.org]

    Missing: 5 aminopentanamide to
  • Propionic Acidemia

    This is one step in the process of converting certain amino acids and fats into sugar for energy.[en.wikipedia.org] Four acetyl CoA precursors increased during clinical episodes: glutaric acid, a catabolic intermediate of lysine; 3-hydroxyisovaleric acid and 3-methylglutaconic acid, catabolic[ncbi.nlm.nih.gov] Homocitrullinuria, presence of epsilon-N-acetyl-l-lysine in urine, and absence of saccharopine indicate deficiency of the saccharopine pathway of lysine degradation.[ncbi.nlm.nih.gov] Continuous venovenous hemodialysis was performed successfully for both infants via extracorporeal membrane oxygenation pump, and both rapidly improved.[ncbi.nlm.nih.gov] […] propionic acid, propionylcarnitine and methylcitrate on the KvLQT1/KCNE1 channel complex cause long QT syndrome in patients with propionic acidemia by inhibition of K flow via[ncbi.nlm.nih.gov] Propionic acidemia is an autosomal recessive metabolic disorder where the body is unable to process certain parts of proteins and lipids.[ncbi.nlm.nih.gov] Reversal of catabolism by stopping protein intake and administering non-protein calories in the form of intravenous fluids is the mainstay of treatment of a crisis.[orpha.net]

    Missing: 5 aminopentanamide to
  • Hyperammonemia

    Hyperammonemia in neuroendocrine tumor would represent a potentially reversible but ongoing process associated with an indolent malignancy.[ncbi.nlm.nih.gov] […] multifactorial including limited capacity of liver detoxification function due to congenital porto-caval shunt, liver ischemia, excessive protein intake and increased protein catabolic[ncbi.nlm.nih.gov] Increased urinary excretion of lysine is seen in LPI, whereas in HHH syndrome, plasma ornithine level is elevated along with increased urinary homocitrulline.[emedicine.medscape.com] KIC loading also increased levels of several leucine-related acyl-CoAs and reduced acetyl-CoA levels.[ncbi.nlm.nih.gov] The case represents the first report of a successful closure of splenorenal shunt via percutaneous embolization of the splenic vein with an amplatzer plug using a common femoral[ncbi.nlm.nih.gov] Abstract Ammonia is constantly produced as a metabolic waste from amino acid catabolism in mammals.[ncbi.nlm.nih.gov] SUMMARY: Signaling via myostatin and eIF2α phosphorylation causes decreases in protein synthesis and mTORC1 activity with a parallel mitochondrial dysfunction and increased[ncbi.nlm.nih.gov]

    Missing: 5 aminopentanamide to