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70 Possible Causes for Beaked Nose, Hypertension, Systemic Scleroderma

  • Systemic Scleroderma

    Renal crisis can be effectively managed when hypertension is aggressively controlled with angiotensin converting enzyme (ACE) inhibitors.[ncbi.nlm.nih.gov] Face Matt telangiectases on face, chest, palms Peri-oral furrowing (fat loss) Microstomia (limited oral aperture defined as interlabial distance 4.5 cm) Beaked nose Other[dermnetnz.org] Patients diagnosed with systemic scleroderma can be categorized under two wide categories: diffuse systemic sclerosis (dSSc) and limited cutaneous systemic sclerosis (lSSc[symptoma.com]

  • Diffuse Scleroderma

    Twelve patients (35% of the total cohort) had pulmonary hypertension defined as PAs of 30 mm Hg or greater.[ncbi.nlm.nih.gov] Face Matt telangiectases on face, chest, palms Peri-oral furrowing (fat loss) Microstomia (limited oral aperture defined as interlabial distance 4.5 cm) Beaked nose Other[dermnetnz.org] […] sclerosis or systemic scleroderma Progressive systemic sclerosis Scleroderma syndrome Scleroderma PSS Systemic Scleroderma Scleroderma, Diffuse SSc Scleroderma, Systemic[wikidata.org]

  • Limited Cutaneous Systemic Sclerosis

    Abstract A patient is described with a typical manifestation of pulmonary hypertension associated with limited cutaneous scleroderma, also known as CREST syndrome.[ncbi.nlm.nih.gov] […] like nose -Shiny skin -Taut lips -Salt and pepper hypo/hyperpigmentation Sclerodactyly in systemic scleroderma -The skin is very taut -Painful -Easy to get digital ulcers[quizlet.com] Scleroderma renal crisis in a patient with anticentromere antibody-positive limited cutaneous systemic sclerosis. Mod Rheumatol 2006;16(5):309-11. 61.[degruyter.com]

  • Scleroderma

    Abstract Fistulas between systemic and pulmonary arteries are associated with various underlying etiologies and cause pulmonary hypertension (PH).[ncbi.nlm.nih.gov] systemic scleroderma .[ghr.nlm.nih.gov] Face Matt telangiectases on face, chest, palms Peri-oral furrowing (fat loss) Microstomia (limited oral aperture defined as interlabial distance 4.5 cm) Beaked nose Other[dermnetnz.org]

  • Sclerodactyly

    Right heart catheterization with pulmonary hypertension. Disclosures None.[ahajournals.org] Systemic scleroderma often affects the hands. The initial stage is swelling (edema), which can last for weeks, months, or years.[doctorsgates.blogspot.com] Face Matt telangiectases on face, chest, palms Peri-oral furrowing (fat loss) Microstomia (limited oral aperture defined as interlabial distance 4.5 cm) Beaked nose Other[dermnetnz.org]

  • Werner Syndrome

    Heritable Pulmonary Arterial Hypertension Eric D Austin, James E Loyd, and John A Phillips, III. Initial Posting: July 18, 2002; Last Update: June 11, 2015.[ncbi.nlm.nih.gov] An excellent discussion of the distinguishing features that separate systemic scleroderma from WS is also presented.) Capell, BC, Tlougan, BE, Orlow, SJ.[dermatologyadvisor.com] Grating hair, scanty eyebrows, a pinched or beaked nose, protuberant eyes and the absence of eyelashes contribute to the presenile appearance.[whonamedit.com]

  • Sanjad-Sakati Syndrome

    1459 Pathophysiology of Hypertension 1485 Evaluation of Hypertension in Childhood Diseases 1519 Management of the Hypertensive Child 1541 Pathogenesis of Acute Renal Failure[books.google.com] DISCUSSION Intestinal pseudo obstruction encompasses a broad range of disorders and is classified as primary (idiopathic) or secondary to other diseases (scleroderma, systemic[ghrnet.org] The facial features included microcephaly, thin lips, beaked nose, low set ears, and a retrognathic mandible.[ncbi.nlm.nih.gov]

  • Progeria

    We report the first autopsied case of an incomplete type of Hunchinson-Gilford progeria associated with fatal pulmonary hypertension.[ncbi.nlm.nih.gov] […] wasting, skin atrophy, disseminated skeletal osteoporosis (documented for at least 25 years), especially in the vertebral column and metacarpal joints with short stature, beaked[ncbi.nlm.nih.gov] The child also presented scleroderma plaques on the abdomen.[ncbi.nlm.nih.gov]

  • Hallermann Syndrome

    A patient with the classic signs--plus a müllerian developmental anomaly, hypertension, glaucoma, and an extensive surgical history--was artificially inseminated, and a term[ncbi.nlm.nih.gov] The Hallermann-Streiff syndrome is characterized by bird-like face, micropthalmia, cataracts, micrognathia, beaked nose, abnormal dentition, hypotrichosis, cutaneous atrophy[ncbi.nlm.nih.gov] […] sclerosis, Skerodermie ICD 10: M34.0 Synonyme: Progressive systemic sclerosis, Scleroderma, CREST syndrome Spinale Muskelatrophie ( 1 Files ) Erkrankung: Spinale Muskelatrophie[orphananesthesia.eu]

  • Lipodystrophy

    Although BSCL is recessive, heterozygous carriers either show a reduced phenotype of partial lipodystrophy, pulmonary hypertension, or no phenotype.[ncbi.nlm.nih.gov] (Also see Linear Scleroderma ) Sjogren's Syndrome Lipoatrophy can be a common sequela of panniculitis in patients with connective tissue diseases (eg, systemic lupus erythematosus[sclero.org] Other clinical features include cutaneous atrophy with prominent superficial vasculature and mottled hyperpigmentation, thin beaked nose, hair loss, delayed dentition, crowded[clinicaladvisor.com]

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