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69 Possible Causes for Bilateral Congenital Profound Sensorineural Hearing Loss, Hearing Problem

  • Microtia

    problems.[ncbi.nlm.nih.gov] […] canals, and bilateral profound sensorineural hearing loss (HL).[ncbi.nlm.nih.gov] When accompanied by a missing ear canal it also can cause hearing problems and difficulty telling which direction a sound comes from.[my.clevelandclinic.org]

  • Congenital Deafness

    Infant/Toddler Hearing Checklist Parents are often the first people to sense that their child has a hearing problem.[pamf.org] hearing loss ranges from mild to profound hearing loss.[wvdhhr.org] Loss Sensorineural Hearing Loss Hearing Problems Fungal Ear Infections Outer Ear Infections Middle Ear Infections Tinnitus Can You Prevent Tinnitus Links Between Hearing[hiddenhearing.co.uk]

  • Deafness

    Websites Table Of Contents External Websites How Stuff Works - Healthguide - Hearing Loss and Deafness British Broadcasting Corporation - Deafness and Hearing Problems National[web.archive.org] Mumps (Epidemic parotitis) may result in profound sensorineural hearing loss (90 dB or more), unilateral (one ear) or bilateral (both ears). congenital rubella (also called[en.wikipedia.org] Do you feel handicapped by a hearing problem? Does a hearing problem cause you difficulty when visiting friends, relatives, or neighbors?[merckmanuals.com]

  • Usher Syndrome Type 1H

    These types are distinguished by the severity of hearing loss, the presence or absence of balance problems, and the age at which signs and symptoms appear.[ncbi.nlm.nih.gov] Usher syndrome type I is characterized by congenital, bilateral, profound sensorineural hearing loss, vestibular areflexia, and adolescent-onset retinitis pigmentosa.[ncbi.nlm.nih.gov] Degeneration of these sensory cells causes the hearing loss, balance problems, and vision loss that occur with Usher syndrome .[ghr.nlm.nih.gov]

  • AMACR Deficiency

    […] loss, diabetes mellitus, mental problems, and hypogonadism.[ncbi.nlm.nih.gov] , bilateral, profound sensorineural hearing loss, vestibular areflexia, and adolescent-onset retinitis pigmentosa.[refsumdisease.org] […] characterized by rod-cone dystrophy (retinitis pigmentosa), obesity, hand and foot abnormalities including polydactyly (mostly but not exclusively postaxial), sensorineural hearing[ncbi.nlm.nih.gov]

  • Tietz Syndrome

    Hearing loss is always bilateral, congenital, sensorineural, and profound, and affected subjects communicate manually.[dx.doi.org] From Wikidata Jump to navigation Jump to search monogenic disease that is characterized by congenital profound bilateral sensorineural hearing loss and generalized albino-like[wikidata.org] Hearing loss is always bilateral, congenital, sensorineural and profound. Psychomotor development is normal.[orpha.net]

  • Usher Syndrome Type 1K

    These types are distinguished by the severity of hearing loss, the presence or absence of balance problems, and the age at which signs and symptoms appear.[ncbi.nlm.nih.gov] Usher syndrome type I is characterized by congenital, bilateral, profound sensorineural hearing loss, vestibular areflexia, and adolescent-onset retinitis pigmentosa.[ncbi.nlm.nih.gov] Diagnostic methods Clinical diagnosis is based on findings of bilateral sensorineural hearing loss (symmetric, congenital and profound for type 1, and moderate to severe with[orpha.net]

  • Usher Syndrome Type 1

    Typically, students develop notable hearing problems by adolescence.[sess.ie] , profound sensorineural hearing loss, adolescent-onset retinitis pigmentosa and loss of vestibular function.[ltd.aruplab.com] Diagnostic methods Clinical diagnosis is based on findings of bilateral sensorineural hearing loss (symmetric, congenital and profound for type 1, and moderate to severe with[orpha.net]

  • Usher Syndrome Type 1J

    All newborn babies are screened for hearing problems. If a hearing problem is found in the newborn, the baby will have follow-up testing.[hopkinsmedicine.org] Diagnostic methods Clinical diagnosis is based on findings of bilateral sensorineural hearing loss (symmetric, congenital and profound for type 1, and moderate to severe with[orpha.net] Usher syndrome type I should be suspected in individuals with: Congenital (i.e., prelingual) profound bilateral sensorineural hearing loss No significant vestibular responses[centogene.com]

  • Usher Syndrome Type 1D

    Hearing problems are noticed by the teenage years and they become deaf by mid-to-late adulthood. Night blindness starts around puberty.[patient.info] Usher syndrome type I is characterized by congenital, bilateral, profound sensorineural hearing loss, vestibular areflexia, and adolescent-onset retinitis pigmentosa.[ncbi.nlm.nih.gov] Diagnostic methods Clinical diagnosis is based on findings of bilateral sensorineural hearing loss (symmetric, congenital and profound for type 1, and moderate to severe with[orpha.net]

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