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2,152 Possible Causes for Bilateral Congenital Profound Sensorineural Hearing Loss, Long QT Syndrome, T Wave Alternans

  • Long QT Syndrome

    The Jervell and Lange-Nielsen syndrome is an autosomal recessive form of LQTS and is characterized by congenital profound bilateral sensorineural hearing loss and long QT[medicinenet.com] […] case with type 3 congenital long QT syndrome, who exhibited a sudden paradoxical QT-interval prolongation during a progressive increase in heart rate, which exacerbated T-wave[ncbi.nlm.nih.gov] Although Long QT syndrome is often a genetic condition, a prolonged QT interval associated with an increased risk of abnormal heart rhythms can also occur in people without[en.wikipedia.org]

  • Long QT Syndrome 6

    The Jervell and Lange-Nielsen syndrome is an autosomal recessive form of LQTS and is characterized by congenital profound bilateral sensorineural hearing loss and long QT[medicinenet.com] Macroscopic T wave alternans in long QT syndrome. Indian J Pediatr. 2006;73:539–40. PubMed CrossRef 14. Abass FA, Shahi M, Kumar N, Bhargava M, Gupta S, Puliyel JM.[springermedizin.de] […] interval with normal and prolonged QT intervals Diagnosing Long QT syndrome is challenging.[en.wikipedia.org]

  • Long QT Syndrome 13

    The Jervell and Lange-Nielsen syndrome is an autosomal recessive form of LQTS and is characterized by congenital profound bilateral sensorineural hearing loss and long QT[medicinenet.com] alternans [1 point] Notched T wave in 3 leads [1 point] Low heart rate for age [0.5 point] Clinical history Syncope [2 points] With stress [1 point] Without stress [1 point[athletesheart.org] QT-interval.[jtd.amegroups.com]

  • Long QT Syndrome 10

    In some cases, LQTS may be associated with congenital profound bilateral sensorineural hearing loss, known as Jervell and Lange-Nielsen syndrome (JLNS).[mayomedicallaboratories.com] T-wave alternans and sinus pause corroborates this further.[ecgwaves.com] The electrocardiogram of these patients has a prominent U wave and a normal or modestly prolonged QT interval.[geneticheartdisease.org]

  • Torsades De Pointes

    U wave was observed in 86 episodes (56.9%), among that in 69 episodes, the U/T wave ratio was 1. Macro T wave alternans was observed in 4 patients.[ncbi.nlm.nih.gov] Prolonged QT interval may be associated with torsades de pointes and lead to sudden cardiac death.[ncbi.nlm.nih.gov] […] reversed asymmetry (20.0% vs 0%, P .001), and T-wave alternans (35.0% vs 0%, P .001).[ncbi.nlm.nih.gov]

    Missing: Bilateral Congenital Profound Sensorineural Hearing Loss
  • Ventricular Tachycardia

    Like T-wave alternans, the test is not widely used, with the exception of longitudinal evaluation of patients with suspected ARVC.[emedicine.com] KEYWORDS: RYR2 mutation; bradycardia; catecholaminergic polymorphic ventricular tachycardia; long QT syndrome[ncbi.nlm.nih.gov] Females, who have long QT syndrome, are more prone to develop ventricular tachycardia.[symptoma.com]

    Missing: Bilateral Congenital Profound Sensorineural Hearing Loss
  • Ventricular Arrhythmia

    T wave alternans in idiopathic long QT syndrome. J Am Coll Cardiol. 1994;23(7):1541–6. PubMed CrossRef Google Scholar 50. Napolitano C, Priori SG, Schwartz PJ.[doi.org] Management of long QT syndrome Torsades de pointes (a severe manifestation of prolonged QT interval) is a medical emergency.[pharmaceutical-journal.com] […] morphology, 8 9 T-wave alternans, 10 an abnormal slope of the relation of QT interval to cycle length (QT/RR interval slope), 11 12 13 and an abnormal QRST isoarea distribution[doi.org]

    Missing: Bilateral Congenital Profound Sensorineural Hearing Loss
  • Ventricular Fibrillation

    RESULTS: Frequencies of history of syncope and spontaneous type 1 ECG, r-J interval in V1, QRS duration in V6, and LAS40, Tpeak-Tend dispersion, and max T-wave alternans were[ncbi.nlm.nih.gov] Congenital long QT syndrome (LQTS) is a potentially lethal but highly treatable channelopathy.[ncbi.nlm.nih.gov] In this type of test, slight changes in your electrocardiogram’s T wave are monitored during gentle exercise.[healthline.com]

    Missing: Bilateral Congenital Profound Sensorineural Hearing Loss
  • Long QT Syndrome 14

    […] individual. 5/14 patients with LQTS had pathological findings during ambulatory ECG monitoring (2 patients with episodes of torsade de pointes tachycardia, 2 patients with T-wave[karger.com] Format Definition A form of long QT syndrome, a heart disorder characterized by a prolonged QT interval on the ECG and polymorphic ventricular arrhythmias.[uniprot.org] QT-interval.[jtd.amegroups.com]

    Missing: Bilateral Congenital Profound Sensorineural Hearing Loss
  • Nonsustained Ventricular Tachycardia

    We examined whether T-wave alternans (TWA) level is correlated with nonsustained ventricular tachycardia (NSVT) incidence in association with PCI in patients with acute ST-segment[ncbi.nlm.nih.gov] The prognostic value of NSVT in conditions such as the long-QT syndromes, primary ventricular fibrillation, and Brugada syndrome, as well as in patients with hypertension[ncbi.nlm.nih.gov] OBJECTIVE: Microvolt T-wave Alternans (TWA) is associated with abnormal repolarization and predicts arrhythmic mortality in patients with previous myocardial infarction (MI[ncbi.nlm.nih.gov]

    Missing: Bilateral Congenital Profound Sensorineural Hearing Loss

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