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431 Possible Causes for Bilateral Congenital Profound Sensorineural Hearing Loss, Prolongation of Corrected QT Interval, T Wave Alternans

  • Long QT Syndrome

    The Jervell and Lange-Nielsen syndrome is an autosomal recessive form of LQTS and is characterized by congenital profound bilateral sensorineural hearing loss and long QT[medicinenet.com] […] case with type 3 congenital long QT syndrome, who exhibited a sudden paradoxical QT-interval prolongation during a progressive increase in heart rate, which exacerbated T-wave[ncbi.nlm.nih.gov] Demographics included mechanism of presentation, corrected QT interval pretreatment, symptom history, medication compliance, and administration of QT-prolonging medications[ncbi.nlm.nih.gov]

  • Long QT Syndrome 10

    In some cases, LQTS may be associated with congenital profound bilateral sensorineural hearing loss, known as Jervell and Lange-Nielsen syndrome (JLNS).[mayomedicallaboratories.com] T-wave alternans and sinus pause corroborates this further.[ecgwaves.com] However, an electrocardiogram (ECG) showed a prolonged QTC (corrected QT interval) of 480 ms.[eplabdigest.com]

  • Long QT Syndrome 13

    The Jervell and Lange-Nielsen syndrome is an autosomal recessive form of LQTS and is characterized by congenital profound bilateral sensorineural hearing loss and long QT[medicinenet.com] alternans [1 point] Notched T wave in 3 leads [1 point] Low heart rate for age [0.5 point] Clinical history Syncope [2 points] With stress [1 point] Without stress [1 point[athletesheart.org] Long QT refers to the QT-interval measured on the electrocardiogram as being prolonged. The "corrected" QT-interval (QTc) is adjusted for heart rate.[briannabadger.com]

  • Long QT Syndrome 6

    The Jervell and Lange-Nielsen syndrome is an autosomal recessive form of LQTS and is characterized by congenital profound bilateral sensorineural hearing loss and long QT[medicinenet.com] Macroscopic T wave alternans in long QT syndrome. Indian J Pediatr. 2006;73:539–40. PubMed CrossRef 14. Abass FA, Shahi M, Kumar N, Bhargava M, Gupta S, Puliyel JM.[springermedizin.de] The ECG showed prolonged corrected QT interval suggestive of LQT1 (see Figure 4 ).[radcliffecardiology.com]

  • Torsades De Pointes

    U wave was observed in 86 episodes (56.9%), among that in 69 episodes, the U/T wave ratio was 1. Macro T wave alternans was observed in 4 patients.[ncbi.nlm.nih.gov] corrected QT interval during LT.[ncbi.nlm.nih.gov] […] reversed asymmetry (20.0% vs 0%, P .001), and T-wave alternans (35.0% vs 0%, P .001).[ncbi.nlm.nih.gov]

    Missing: Bilateral Congenital Profound Sensorineural Hearing Loss
  • Long QT Syndrome 8

    Jervell and Lange-Nielsen syndrome (JLNS) is characterized by congenital profound bilateral sensorineural hearing loss and LQTc usually greater than 500 msec.[ncbi.nlm.nih.gov] Abstract We report a family with congenital long QT syndrome, an inherited disorder of myocardial repolarization in which affected individuals have prolongation of corrected[ncbi.nlm.nih.gov] The severity of T-wave alternans tends to correlate with the risk of cardiac events. 10 View/Print Figure FIGURE 3. Electrocardiogram showing torsades de pointes.[aafp.org]

  • Long QT Syndrome 14

    […] individual. 5/14 patients with LQTS had pathological findings during ambulatory ECG monitoring (2 patients with episodes of torsade de pointes tachycardia, 2 patients with T-wave[karger.com] However, an electrocardiogram (ECG) showed a prolonged QTC (corrected QT interval) of 480 ms.[eplabdigest.com] Suspecting acquired long QT syndrome, the pediatrician obtained an ECG, which demonstrated a prolonged corrected QT interval (QTc 0.5 sec ½ ).[pedsinreview.aappublications.org]

    Missing: Bilateral Congenital Profound Sensorineural Hearing Loss
  • Ventricular Arrhythmia

    T wave alternans in idiopathic long QT syndrome. J Am Coll Cardiol. 1994;23(7):1541–6. PubMed CrossRef Google Scholar 50. Napolitano C, Priori SG, Schwartz PJ.[doi.org] […] for QT interval prolongation.[doi.org] […] morphology, 8 9 T-wave alternans, 10 an abnormal slope of the relation of QT interval to cycle length (QT/RR interval slope), 11 12 13 and an abnormal QRST isoarea distribution[doi.org]

    Missing: Bilateral Congenital Profound Sensorineural Hearing Loss
  • Nonsustained Ventricular Tachycardia

    We examined whether T-wave alternans (TWA) level is correlated with nonsustained ventricular tachycardia (NSVT) incidence in association with PCI in patients with acute ST-segment[ncbi.nlm.nih.gov] Efforts should be made to correct hypokalemia and to withdraw any long-term medications associated with QT-interval prolongation.[emedicine.medscape.com] OBJECTIVE: Microvolt T-wave Alternans (TWA) is associated with abnormal repolarization and predicts arrhythmic mortality in patients with previous myocardial infarction (MI[ncbi.nlm.nih.gov]

    Missing: Bilateral Congenital Profound Sensorineural Hearing Loss
  • Ventricular Tachycardia

    Removing offending drugs that prolong the QT interval and correcting potassium or calcium imbalances is crucial.[healio.com] Like T-wave alternans, the test is not widely used, with the exception of longitudinal evaluation of patients with suspected ARVC.[emedicine.com] […] of QT interval and pause-dependent, early afterdepolarization-mediated torsades de pointes most often is caused by medication and occasionally is caused by metabolic derangement[cogprints.org]

    Missing: Bilateral Congenital Profound Sensorineural Hearing Loss