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168 Possible Causes for Bilateral Congenital Profound Sensorineural Hearing Loss, T Wave Alternans

  • Long QT Syndrome

    The Jervell and Lange-Nielsen syndrome is an autosomal recessive form of LQTS and is characterized by congenital profound bilateral sensorineural hearing loss and long QT[medicinenet.com] […] case with type 3 congenital long QT syndrome, who exhibited a sudden paradoxical QT-interval prolongation during a progressive increase in heart rate, which exacerbated T-wave[ncbi.nlm.nih.gov] In some cases, LQTS may be associated with congenital profound bilateral sensorineural hearing loss, known as Jervell and Lange-Nielsen syndrome (JLNS).[mayomedicallaboratories.com]

  • Long QT Syndrome 6

    The Jervell and Lange-Nielsen syndrome is an autosomal recessive form of LQTS and is characterized by congenital profound bilateral sensorineural hearing loss and long QT[medicinenet.com] Macroscopic T wave alternans in long QT syndrome. Indian J Pediatr. 2006;73:539–40. PubMed CrossRef 14. Abass FA, Shahi M, Kumar N, Bhargava M, Gupta S, Puliyel JM.[springermedizin.de] In some cases, LQTS may be associated with congenital profound bilateral sensorineural hearing loss, known as Jervell and Lange-Nielsen syndrome (JLNS).[mayomedicallaboratories.com]

  • Long QT Syndrome 13

    The Jervell and Lange-Nielsen syndrome is an autosomal recessive form of LQTS and is characterized by congenital profound bilateral sensorineural hearing loss and long QT[medicinenet.com] alternans [1 point] Notched T wave in 3 leads [1 point] Low heart rate for age [0.5 point] Clinical history Syncope [2 points] With stress [1 point] Without stress [1 point[athletesheart.org] In some cases, LQTS may be associated with congenital profound bilateral sensorineural hearing loss, known as Jervell and Lange-Nielsen syndrome (JLNS).[mayomedicallaboratories.com]

  • Long QT Syndrome 10

    In some cases, LQTS may be associated with congenital profound bilateral sensorineural hearing loss, known as Jervell and Lange-Nielsen syndrome (JLNS).[mayomedicallaboratories.com] T-wave alternans and sinus pause corroborates this further.[ecgwaves.com] wave alternans - 1 point Notched T wave in at least 3 leads - 1 point Low heart rate for age (children) - 0.5 points Syncope (one cannot receive points both for syncope and[checkorphan.org]

  • Torsades De Pointes

    U wave was observed in 86 episodes (56.9%), among that in 69 episodes, the U/T wave ratio was 1. Macro T wave alternans was observed in 4 patients.[ncbi.nlm.nih.gov] […] reversed asymmetry (20.0% vs 0%, P .001), and T-wave alternans (35.0% vs 0%, P .001).[ncbi.nlm.nih.gov] T-wave alternans and sinus pause corroborates this further.[ecgwaves.com]

    Missing: Bilateral Congenital Profound Sensorineural Hearing Loss
  • Nonsustained Ventricular Tachycardia

    We examined whether T-wave alternans (TWA) level is correlated with nonsustained ventricular tachycardia (NSVT) incidence in association with PCI in patients with acute ST-segment[ncbi.nlm.nih.gov] OBJECTIVE: Microvolt T-wave Alternans (TWA) is associated with abnormal repolarization and predicts arrhythmic mortality in patients with previous myocardial infarction (MI[ncbi.nlm.nih.gov] Alternans T-wave alternans (TWA) is a test that is thought to reflect dispersion of repolarization and has been shown to predict VT inducibility and future arrhythmic events[clinicalgate.com]

    Missing: Bilateral Congenital Profound Sensorineural Hearing Loss
  • Ventricular Tachycardia

    Like T-wave alternans, the test is not widely used, with the exception of longitudinal evaluation of patients with suspected ARVC.[emedicine.com] Chow T, Kereiakes DJ, Bartone C, et al. Prognostic utility of microvolt T-wave alternans in risk stratification of patients with ischemic cardiomyopathy .[ncbi.nlm.nih.gov] Other noninvasive tests, such as T-wave alternans, signal-averaged ECG, and heart rate variability, do not provide diagnostic confirmation, but might be helpful in defining[revespcardiol.org]

    Missing: Bilateral Congenital Profound Sensorineural Hearing Loss
  • Ventricular Fibrillation

    RESULTS: Frequencies of history of syncope and spontaneous type 1 ECG, r-J interval in V1, QRS duration in V6, and LAS40, Tpeak-Tend dispersion, and max T-wave alternans were[ncbi.nlm.nih.gov] In this type of test, slight changes in your electrocardiogram’s T wave are monitored during gentle exercise.[healthline.com] wave alternans 1 Notched T waves in three leads 1 Low heart rate for age (resting rate below second percentile 0.5 Clinical History Syncope With stress 2 Without stress 1[emedicine.medscape.com]

    Missing: Bilateral Congenital Profound Sensorineural Hearing Loss
  • Ventricular Arrhythmia

    T wave alternans in idiopathic long QT syndrome. J Am Coll Cardiol. 1994;23(7):1541–6. PubMed CrossRef Google Scholar 50. Napolitano C, Priori SG, Schwartz PJ.[doi.org] […] morphology, 8 9 T-wave alternans, 10 an abnormal slope of the relation of QT interval to cycle length (QT/RR interval slope), 11 12 13 and an abnormal QRST isoarea distribution[doi.org] […] systolic blood pressure rises above 200 mm Hg, there is an increase in premature ventricular contractions or nonsustained ventricular tachycardia or polymorphic VT occurs, T-wave[doi.org]

    Missing: Bilateral Congenital Profound Sensorineural Hearing Loss
  • Paroxysmal Ventricular Tachycardia

    Paroxysmal ventricular tachycardia is a rhythm abnormality characterized by a series of ventricular contractions originating from one or more ventricular loci, at a rate greater than 100-120 beats/minute. The tachycardia is considered to be nonsustained if it lasts for less than 30 seconds, or sustained if the[…][symptoma.com]

    Missing: Bilateral Congenital Profound Sensorineural Hearing Loss

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