Possible Causes for central nervous system involvement Blue Rubber Bleb Nevus Syndrome We report a rare case of blue rubber bleb nevus syndrome with gastrointestinal and central nervous system involvement. [ncbi.nlm.nih.gov] The central nervous system involvement is seldom reported, and neurological symptoms at onset in adulthood are extremely rare. [ncbi.nlm.nih.gov] Central nervous system involvement in BRBNS is not often reported, and most cases of BRBNS are sporadic. [ncbi.nlm.nih.gov] Malignant Angioendotheliomatosis Although the disease primarily involves the vasculature of the skin and central nervous system, vascular involvement of other organs may occur and may produce a variety of [ncbi.nlm.nih.gov] Multiple organ systems are involved and the clinical presentation resembles a systemic necrotizing vasculitis with skin and central nervous system most commonly involved. [ncbi.nlm.nih.gov] All patients presented with symptoms referable to central nervous system (CNS) involvement. In two patients, the diagnosis was made on brain biopsy specimens. [ncbi.nlm.nih.gov] Lupus Encephalitis Central nervous system (CNS) involvement has been emphasised as one of the major lupus manifestations since the first descriptions of the disease and is among the leading [lupusuk.org.uk] With severe central nervous system involvement, CSF levels of nitric oxide are found to be elevated and can help to monitor LC progression. [symptoma.com] Karassa FB, Ioannidis JP, Touloumi G, Boki KA, Moutsopoulos HM (2000) Risk factors for central nervous system involvement in systemic lupus erythematosus. [journals.plos.org] Bickerstaff Brainstem Encephalitis system involvement with cortical, subcortical and cerebellar lesions on brain magnetic resonance imaging (MRI), and was eventually diagnosed with BBE. [psasir.upm.edu.my] nervous system involvement in the Miller Fisher syndrome. [collections.lib.utah.edu] […] and peripheral nervous system involvement. [ncbi.nlm.nih.gov] Lymphomatoid Granulomatosis An extensive systemic work-up ruled out other site(s) of involvement. [ncbi.nlm.nih.gov] Because central nervous system (CNS) involvement of LYG has been known to show poor prognosis, the establishment of an effective treatment for CNS LYG with mild adverse effects [ncbi.nlm.nih.gov] The clinical features reflect systemic multi-organ disease with lung, skin, and central nervous system involvement. [secure.ssa.gov] Congenital Merosin-Positive Muscular Dystrophy nervous system involvement. [pubfacts.com] […] we describe a 3-year-old Mediterranean child with clinical and histopathological signs of CMD, normal expression of merosin, severe clinical and radiological evidence of central [ncbi.nlm.nih.gov] In general, central nervous system involvement is not present. There is also evidence for still unclassified forms. [ncbi.nlm.nih.gov] Malignant Atrophic Papulosis She died as a result of central nervous system involvement from Degos' disease. [ncbi.nlm.nih.gov] nervous system involvement in a child. [scholars.northwestern.edu] Malignant atrophic papulosis (Kohlmeier-Degos disease) is reported for the first time with pathologic verification of central nervous system involvement in a child. [ncbi.nlm.nih.gov] CINCA Syndrome Some patients present with the full early-onset pathognomonic clinical picture, with central nervous system involvement and early onset arthropathies. [orpha.net] nervous system involvement. [ncbi.nlm.nih.gov] Central nervous system involvement is revealed by chronic headaches due to chronic meningitis with granulocytes. In the severe forms, intellectual deficit can occur. [orpha.net] Systemic Lupus Erythematosus with Organ/System Involvement Only one patient had associated central nervous system involvement at that time. All patients were positive for IgM and IgG anticardiolipin antibodies. [ncbi.nlm.nih.gov] OBJECTIVE: To describe the psychiatric presentation, serologic findings, and neuroimaging patterns in children and adolescents with central nervous system involvement with [ncbi.nlm.nih.gov] Abstract Central nervous system involvement is a common but rarely reviewed feature of pediatric systemic lupus erythematosus (SLE). [ncbi.nlm.nih.gov] Orbital Burkitt's Lymphoma During chemotherapy regimen patient showed bradycardia and Babinski response, suggestive of central nervous system involvement. sBL associated with orbital involvement is [contempclindent.org] Fourteen (88%) of the patients had systemic involvement, of which the most common locations were central nervous system (6/16), lymphatics (6/16), bone marrow (6/16), and [ncbi.nlm.nih.gov] nervous system involvement Acute paraplegia, urinary and fecal incontinence are symptoms due to spinal cord compression. [explainmedicine.com] Hemangiomatosis Described here is a case of diffuse neonatal hemangiomatosis with predominant central nervous system involvement. [ncbi.nlm.nih.gov] One infant developed thrombocytopenia and bleeding while the other infant with more widely diffuse lesions succumbed to extensive central nervous system involvement. [pediatrics.aappublications.org] Diffuse hemangiomatosis with predominant central nervous system involvement. Pediatr Neurol 2009; 40 (1) 54-57 6 Liu X, Qu X, Zheng J, Zhang L. [thieme-connect.com] Familial Hemophagocytic Lymphohistiocytosis The presence of central nervous system involvement has a profound impact on the prognosis, treatment, and clinical outcome of the disease. [ncbi.nlm.nih.gov] Central nervous system involvement of HLH can cause catastrophic results. [ncbi.nlm.nih.gov] Conclusions: Physicians managing patients with HLH must be vigilant about the possibility of central nervous system involvement including stroke. [ingentaconnect.com] Xanthoma Disseminatum Ocular, liver, bone marrow, respiratory, skeletal, and central nervous system involvement may accompany the classic findings of the disease. [ncbi.nlm.nih.gov] We describe an illustrative case with extensive mucocutaneous, ocular, laryngeal, pituitary and central nervous system involvement, which responded to treatment with cyclophosphamide [ncbi.nlm.nih.gov] Central nervous system involvement is rare and usually occurs in the systemic variety. [ncbi.nlm.nih.gov] Whipple Disease Central nervous system involvement, including severe cognitive deterioration, may precede systemic manifestations, appear during the course of the disease, or even be the [ncbi.nlm.nih.gov] The central nervous system (CNS) is involved in 3 situations: CNS involvement in classic WD, CNS relapse in previously treated WD, and isolated CNS infection. [ncbi.nlm.nih.gov] A subset of patients with the disease may either initially have or eventually develop symptoms of central nervous system involvement. [ncbi.nlm.nih.gov] Leptomeningeal Metastasis Non-Hodgkin's lymphoma which occasionally involves the central nervous system, occurs more often in high-grade cases and implicates a poor prognosis. [ncbi.nlm.nih.gov] Central nervous system involvement is unusual and particularly the occurrence of leptomeningeal metastasis (LM) is extremely rare, with few cases described in the medical [ncbi.nlm.nih.gov] High-dose therapy with hematopoietic cell transplantation for patients with central nervous system involvement by non-Hodgkin's lymphoma. [link.springer.com] Miller-Fisher Syndrome However there are occasional reports of central nervous system involvement. [ncbi.nlm.nih.gov] nervous system involvement in the Miller Fisher syndrome. [ncbi.nlm.nih.gov] Of six patients with autopsy findings, four exhibited central nervous system lesions. [journals.lww.com] Malignant Meningeal Lymphoma PURPOSE: Non-Hodgkin's lymphoma which occasionally involves the central nervous system, occurs more often in high-grade cases and implicates a poor prognosis. [ncbi.nlm.nih.gov] Korsager S, Laursen B, Mortensen TM: Dementia and central nervous system involvement in chronic lymphocytic leukemia. [link.springer.com] nervous system lymphoma in a patient with orbital non-Hodgkin’s lymphoma is 5.9%,(12) and the most common form of central nervous system involvement in lymphoma is leptomeningeal [djo.harvard.edu] Neurologic Manifestation of Whipple Disease Central Nervous System involvement is not uncommon and it may precede other disease manifestations, appear after treatment and improvement of gastrointestinal signs or rarely [benthamopen.com] Lumbar puncture was done to look for central nervous system involvement, and PCR for Tropheryma whipplei in the CSF was positive. [shmabstracts.com] More than 70 leading experts provide comprehensive, current information on all infections—both neural-specific and systemic—that involve the central nervous system. [books.google.com] Rosai-Dorfman Disease Central nervous system (CNS) involvement is infrequent and typically manifests as an isolated lesion. [ncbi.nlm.nih.gov] Central nervous system involvement is extremely rare, particularly cases with multiple intracranial masses. [ncbi.nlm.nih.gov] Rosai-Dorfman disease with multiple lesions primarily involving the central nervous system is rare. [ncbi.nlm.nih.gov] Pulmonary Lymphomatoid Granulomatosis Many patients die as a result of pulmonary hemorrhage, central nervous system involvement, or transformation to an aggressive lymphoma. [synapse.koreamed.org] In some young patient with LYG were detected central nervous system involvement or skin involvement without pulmonary involvement. [siicsalud.com] Central nervous system (CNS) involvement was considered. Therefore, the patient received whole brain irradiation with a total dose of 30 Gy in 10 fractions. [spandidos-publications.com] Spinal Pachymeningitis nervous system involvement of AASV. [ncbi.nlm.nih.gov] Chan SK, Cheuk W, Chan KT, Chan JK (2009) IgG4-related sclerosing pachymeningitis: a previously unrecognized form of central nervous system involvement in IgG4-related sclerosing [springermedizin.de] […] corticosteroid, cyclophosphamide, and azathioprine) was initiated and brought control of the disease during the subsequent 6 months of follow-up.HSP is a relatively rare form of central [ncbi.nlm.nih.gov] Juvenile Xanthogranuloma Solitary lesions in the spinal column are an especially rare presentation of this disease, and central nervous system involvement can portend a poor prognosis. [ncbi.nlm.nih.gov] Central nervous system involvement is a poor prognostic factor. [ncbi.nlm.nih.gov] Less commonly JXG may involve locations such as the lung, liver, adrenal gland, appendix, bones, bone marrow, pituitary gland, central nervous system, kidney, heart, small [histio.org] Facial Hemiatrophy system (CNS) involvement in both diseases and the possible coexistence of PFH with scleroderma in other body sites. [ncbi.nlm.nih.gov] nervous system (CNS) involvement in both diseases and the possible coexistence of PFH with scleroderma in other body sites. [jrheum.org] Clinical and radiological involvement of the central nervous system may be observed in PRS. [ncbi.nlm.nih.gov] Tuberculosis of Nervous System Do Not Do Recommendation For people with HIV (human immunodeficiency virus) and active TB (tuberculosis)without central nervous system involvement, do not routinely extend [nice.org.uk] Abstract The incidence of tuberculosis in the United States is increasing in all age groups; 5% of all of these patients have central nervous system involvement. [ncbi.nlm.nih.gov] Central nervous system involvement is one of the most serious forms of this infection, acting as a prominent cause of morbidity and mortality in developing countries. [journals.lww.com] Behçet Disease A rare combination of both cerebral venous thrombosis and parenchymal central nervous system involvement was identified by neuroimaging. [ncbi.nlm.nih.gov] Recurrent mucocutaneous lesions may be the only symptoms in mild cases, but articular, ocular, vascular, and/or gastrointestinal and central nervous system involvement may [ncbi.nlm.nih.gov] Brain Central nervous system involvement is one of the most dangerous manifestations of Behcet’s. [hopkinsvasculitis.org] Mitochondrial Complex 3 Deficiency Nuclear Type 1 OBJECTIVE To report a rare manifestation of CoQ(10) deficiency with isolated mitochondrial myopathy without central nervous system involvement. [unboundmedicine.com] Cancer and the Central Nervous System Involvement E-2292 134 Posttreatment Neurologic Sequelae of Pediatric Central Nervous System Tumors E-2297 135 Muscle and Nerve Development [books.google.com] OBJECTIVE: To report a rare manifestation of CoQ(10) deficiency with isolated mitochondrial myopathy without central nervous system involvement. [unboundmedicine.com] Neurosyphilis […] in central nervous system (CNS) disorders. [ncbi.nlm.nih.gov] Central nervous system involvement by this infection is referred to as neurosyphilis. [docneuro.com] nervous system involvement occurs in 5%-10% of those infected and in up to a third of cases progressing to advanced stages developing neurosyphilis.6 Currently, atypical [revistanefrologia.com] Kerosene Poisoning Others features noted were central nervous system involvement (14.5%), vomiting (20%), and fever 16 (29.1%). There were 3 deaths giving the mortality of 5.5%. [ncbi.nlm.nih.gov] […] kerosene on the central nervous system. [ncbi.nlm.nih.gov] All patients with central nervous system complications had severe pulmonary involvement, suggesting a close relationship between the severity of pulmonary involvement and [ncbi.nlm.nih.gov] Granulomatosis with Polyangiitis Abstract The aims of this study were to estimate the frequency of central nervous system (CNS) involvement in Greek patients with granulomatosis with polyangiitis (GPA) and [ncbi.nlm.nih.gov] However, central nervous system involvement is uncommon and frequently refractory to classical therapy. [ncbi.nlm.nih.gov] Central nervous system involvement is relatively uncommon with most cases being secondary to ischaemic infarctions. [ncbi.nlm.nih.gov] Cerebral Angiitis Central nervous system involvement in hepatitis C virus cryoglobulinemia vasculitis: a multicenter case-control study using magnetic resonance imaging and neuropsychological [frontiersin.org] licensee BioMed Central Ltd. 2012 Received: 7 February 2012 Accepted: 15 May 2012 Published: 13 September 2012 Abstract Introduction Central nervous system involvement [jmedicalcasereports.biomedcentral.com] References 1 An unusual central nervous system involvement in rheumatoid arthritis: combination of pachymeningitis and cerebral vasculitis, Rheumatol Int, 2009, vol. 29 (pg [academic.oup.com]
