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12 Possible Causes for Cerebellar Sign, Myoclonic Jerking, Onset of Disease between 25 and 40 Years of Age

  • Acute Cerebellar Ataxia

    The age of onset may vary between 40 - 80 years and the mean duration of ataxia between 3 - 25 years.[neuroweb.us] Disorders of the blood vessels that supply blood to the cerebellum can also cause acute cerebellar ataxia. WHAT ARE SIGNS OF ACUTE CEREBELLAR ATAXIA?[medfriendly.com] Four weeks later he developed myoclonic jerks. Electroencephalogram showed characteristic periodic complexes time-locked with myoclonus.[ncbi.nlm.nih.gov]

  • Benign Adult Familial Myoclonic Epilepsy

    Celiac disease (or gluten sensitive enteropathy): The age of onset may vary between 40 - 80 years and the mean duration of ataxia between 3 to 25 years.[neuroweb.us] Table 2 SCA6 group, patient characteristics SCA Gender Age Age at onset Cerebellar symptoms Cerebellar atrophy Drug CAG repeats Ocular signs motor ocular (MRI) nys osc sac[academic.oup.com] By the jerk-locked averaging method, a positive spike time-locked to the myoclonic jerk was demonstrated in four patients before 15-20 msec of myoclonic jerk.[ci.nii.ac.jp]

  • Wilson Disease

    Onset is slow and begins between 11 and 25 years of age. Signs and Symptoms In about 40 to 50% of patients, the disease first affects the central nervous system (CNS).[diagnose-me.com] In Wilson disease, an abnormal striatum depicted on MR images correlated with pseudoparkinsonian signs, an abnormal dentatothalamic tract correlated with cerebellar signs,[pubs.rsna.org] jerking similar to that seen in progressive myoclonic syndrome.[web.archive.org]

  • Subacute Cerebellar Degeneration

    Other clinical signs include early falling and fine myoclonic jerks of the fingers /limb and can be elicited by tapping the limb.[neuroweb.us] Conclusion: The case highlights the challenge of the evaluation of patients who present with progressive cerebellar signs and the need to consider a paraneoplastic syndrome[karger.com] Syndromes of cerebellar degeneration typically manifest as subacute or chronic cerebellar neurological signs.[clinicaladvisor.com]

  • Adult-Onset Autosomal Recessive Cerebellar Ataxia

    […] to manage her frequent myoclonic jerking.[jnnp.bmj.com] The age of onset may vary between 40 - 80 years and the mean duration of ataxia between 3 - 25 years.[neuroweb.us] A relatively important one is sporadic Creutzfeldt-Jakob disease that can present with predominantly cerebellar signs [ 8 ].[patient.info]

  • Alcoholic Cerebellar Degeneration

    Other clinical signs include early falling and fine myoclonic jerks of the fingers /limb and can be elicited by tapping the limb.[neuroweb.us] Nine of the 14 patients (Group A) had clinical signs of alcoholic cerebellar degeneration, and the remaining 5 (Group B) did not have signs of alcoholic cerebellar degeneration[ncbi.nlm.nih.gov] Syndromes of cerebellar degeneration typically manifest as subacute or chronic cerebellar neurological signs.[clinicaladvisor.com]

  • Cerebellar Ataxia with Peripheral Neuropathy Type 2

    Other clinical signs include early falling and fine myoclonic jerks of the fingers /limb and can be elicited by tapping the limb.[neuroweb.us] Syndromes of cerebellar degeneration typically manifest as subacute or chronic cerebellar neurological signs.[clinicaladvisor.com] Males females, Scanning speech and nystagmus unusual, Gait ataxia and postural instability more evident than the other cerebellar signs seen with more lateral cerebellar disease[medexam.net]

  • Early-Onset Cerebellar Ataxia

    Other clinical signs include early falling and fine myoclonic jerks of the fingers /limb and can be elicited by tapping the limb.[neuroweb.us] Apart from cerebellar signs and brisk knee jerks in all, other important findings were abnormal ocular movements (mostly impaired saccades) in 92.8%, Babinski's sign (78.6%[ncbi.nlm.nih.gov] Autosomal dominant cerebellar ataxia type III produces relatively pure cerebellar signs.[medlink.com]

  • Spinocerebellar Ataxia with Rigidity and Peripheral Neuropathy

    Other clinical signs include early falling and fine myoclonic jerks of the fingers /limb and can be elicited by tapping the limb.[neuroweb.us] […] infarction in the territory of all three cerebellar arteries Isolated vertigo – mimics acute labyrinthitis Isolated cerebellar signs – variable cerebellar signs Posterior[lifeinthefastlane.com] Subacute necrotizing encephalopathy, also called Leigh disease, is a lethal disorder of infancy marked by psychomotor delay, myoclonic jerks, paralyses of eye movements, and[britannica.com]

  • Cognitive Impairment with or without Cerebellar Ataxia

    Other clinical signs include early falling and fine myoclonic jerks of the fingers /limb and can be elicited by tapping the limb.[neuroweb.us] signs present absent Fluctuations in attention or alertness present absent hallucinations present absent dysautonomia present absent Significant cognitive impairment or dementia[catalog.coriell.org] Radiologic features include atrophy of the pons, middle cerebellar peduncle, and putamen, with the hot cross bun sign being highly specific, though not pathognomonic.[amjmed.org]

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