Deafness: Causes & Reasons

Possible Causes for Deafness

Sometimes, it can present as sudden deafness with vertigo, without brainstem or cerebellar signs. [ncbi.nlm.nih.gov]

Initially, deafness maybe there only for low frequencies. [symptoma.com]

An anterior inferior cerebellar artery (AICA) stroke is characterized by vertigo, tinnitus, and deafness in addition to facial weakness, hemiataxia, and hypalgesia. [ncbi.nlm.nih.gov]

Presbycusis

Deafness is the complete inability to hear sound. Deafness and hearing loss have many causes and can occur at any age. [bodyandhealth.canada.com]

Age-related hearing loss, Presbyacusia, senile deafness, age related hearing loss, hard of hearing (presbyacusis), presbyacusis, senile presbyacusis, Presbycusis;senile, [fpnotebook.com]

Western Institute for the Deaf and Hard of Hearing WIDHH is a non-profit organization dedicated to creating a society in which people who are deaf, deafened, deafblind and [fraserhealth.ca]

Congenital Deafness

deafness and about 37% of sporadic cases. [dizziness-and-balance.com]

DbPre-lingual deafnessPost-lingual deafness 20. [slideshare.net]

The distinction between congenital and acquired deafness specifies only the time that the deafness appears. [medicinenet.com]

Susac Syndrome

It is clinically characterized by a typical triad of sensorineural deafness, encephalopathy, and visual defect, due to microangiopathy involving the brain, inner ear, and [ncbi.nlm.nih.gov]

Abstract Susac's syndrome is extremely rare and is characterized by the clinical triad of encephalopathy, retinal artery occlusion and deafness. [cambridge.org]

Susac Syndrome is a rare disease characterized by encephalopathy, branch retinal artery occlusion and sensorineural deafness. [clinicaltrials.gov]

Wolfram Syndrome

Several other features are observed in patients including deafness, ataxia, and peripheral neuropathy. [ncbi.nlm.nih.gov]

The Wolfram syndrome (MIM 222300) is a disease of unknown origin consisting of diabetes insipidus, diabetes mellitus, optic atrophy, and deafness. [ncbi.nlm.nih.gov]

DIDMOAD stands for Diabetes Insipidus, Diabetes Mellitus, Optic Atrophy, and Deafness (symptoms of Wolfram Syndrome) This definition appears somewhat frequently and is found [acronymfinder.com]

Cinchonism

[…] cinchonism [sin´ko-nizm] toxicity due to overdosage of cinchona alkaloids; symptoms are tinnitus and slight deafness, photophobia and other visual disturbances, mental dullness [medical-dictionary.thefreedictionary.com]

[…] cinchonism * * * cin·cho·nism 'siŋ-kə-.niz-əm, 'sin-chə- n a disorder due to excessive or prolonged use of cinchona or its alkaloids and marked by temporary deafness, ringing [medicine.academic.ru]

— Poisoning by cinchona, quinine, or quinidine; characterized by tinnitus, headache, deafness, and occasionally, anaphylactoid shock. [translate.academic.ru]

Sensorineural Hearing Impairment

[…] hearing disorder Alternative Titles: nerve deafness, sensorineural hearing loss, sensorineural impairment Learn about this topic in these articles: deaf-blindness In deaf-blindness [britannica.com]

Not all cases of sudden deafness are idiopathic. More than 50 different causes of sudden deafness have been described. [masseyeandear.org]

National Foundation for the Deaf website. Helpful resources. www.nfd.org.nz/helpfulresources. Accessed October 23, 2018. [nlm.nih.gov]

Otosclerosis

Profound deafness has received increasing attention in recent years, largely because of the availability of cochlear implants. [ncbi.nlm.nih.gov]

In the preliminary stages, the individuals suffer from partial hear loss which gets worse over time and results in complete deafness. [symptoma.com]

Deafness made him unable to hear his late compositions. [hear-it.org]

Herpes Zoster Oticus

This may occasionally be associated with tinnitus, vertigo, deafness, severe otalgia, and inflammation of the pinna. [profiles.umassmed.edu]

Last edited 03/2021 and last reviewed 10/2021 The Ramsay Hunt Syndrome is characterised by sensorineural deafness, vertigo and facial paralysis following Herpes Zoster infection [gpnotebook.com]

The 59 years old male patient referred to the clinic with diplopia, deafness, disphagia and hoarseness after herpes zoster oticus infection. [tjn.org.tr]

Lermoyez Syndrome

Lermoyez nasal punch Lermoyez syndrome - increasing deafness interrupted by a sudden attack of dizziness after which the hearing improves. [medical-dictionary.thefreedictionary.com]

A dictionary of medical eponyms Related people Marcel Emile Joseph Lermoyez A variant of Ménière’s syndrome characterised by attacks of tinnitus and diminished hearing/deafness [whonamedit.com]

MELAS Syndrome

Central deafness is only rarely reported. We report here an 11-year-old boy with MELAS syndrome who presented with subacute deafness after waking up from sleep. [ncbi.nlm.nih.gov]

Inner ear deafness is often the cause of sensorineural hearing loss associated with mitochondrial encephalomyopathy. However, retrocochlear deafness may also be a cause. [jstage.jst.go.jp]

Both have a maternally-inherited neurosensory deafness and insulin-dependent T2DM. A renal biopsy was performed in both patients. [ncbi.nlm.nih.gov]

Acoustic Neuritis

Gerlier disease - a paroxysmal attack of severe vertigo, not accompanied by deafness or tinnitus, due to unilateral vestibular dysfunction. [medical-dictionary.thefreedictionary.com]

Some ear disorders can result in hearing disorders and deafness. [icdlist.com]

Nail-patella syndrome Nails-only DDEB NAIT Naito-Oyanagi disease Najjar syndrome Nakagawa angioblastoma Nakajo-Nishimura syndrome Nakamura-Osame syndrome NALD NAM Nance deafness [orpha.net]

Suppurative Labyrinthitis

ACQUIRED MEASLES DEAFNESS -Rubeola virus causes measles -impt cause of acquired deafness. [ent.com.au]

Eight (57%) individuals became deaf, while six (43%) acquired mixed hearing loss. [ncbi.nlm.nih.gov]

Deafness may follow, but the condition usually clears up spontaneously within days or weeks. labyrinthitis inflammation of the inner ear resulting in disturbance of balance [medical-dictionary.thefreedictionary.com]

Impacted Cerumen

Impacted cerumen was seen causing the deafness. Removal of cerumen or ear wax was done using ear curette. [youtube.com]

The symptoms usually include sudden deafness. The wax is easily removed by a physician. [britannica.com]

Differential diagnosis Other causes of acute deafness - eg, Eustachian tube dysfunction, foreign body. Otitis externa. [patient.info]

Acoustic Trauma

Homepage Rare diseases Search Search for a rare disease Acute sensorineural hearing loss by acute acoustic trauma or sudden deafness or surgery induced acoustic trauma Summary [orpha.net]

Homepage Rare diseases Search Search for a rare disease Acute sensorineural hearing loss by acute acoustic trauma or sudden deafness or surgery induced acoustic trauma ORPHA [orpha.net]

Undersea Medical Center How to cite this article Author(s): Morihiko Oya, Yutaka Tadano, Yasuhiro Takihata, Fumitaka Ikomi, Tetsuji Tokunaga Key words: HBOT - sensorineural deafness [arquivosdeorl.org.br]

Diffuse Cerebral Sclerosis of Schilder

The clinical course tends to be progressive and includes dementia, cortical blindness, cortical deafness, spastic hemiplegia, and pseudobulbar palsy. [icd9data.com]

Signs and symptoms include dementia, cortical deafness and blindness, pseudobulbar palsy, and hemiplegia. (NCI Thesaurus) ALSO IN ENCYCLOPEDIA : [tititudorancea.com]

Signs and symptoms include dementia, cortical deafness and blindness, pseudobulbar palsy, and hemiplegia Applies To Balo's concentric sclerosis Encephalitis periaxialis: concentrica [icd9data.com]

Alport Syndrome

Epstein CJ, Sahud MA, Piel CF, Goodman JR, Bernfield MR, Kushner JH, Ablin AR (1972) Hereditary macrothrombocytopathia, nephritis and deafness. [link.springer.com]

A fourth kindred displaying the triad of hereditary nephritis, deafness and thrombocytopenia with giant platelets is described. [ncbi.nlm.nih.gov]

About 50% of male patients with X-linked Alport syndrome show sensorineural deafness by age 25 years, and about 90% are deaf by age 40 years. [emedicine.medscape.com]

Krabbe Disease

It affects infants and is characterized by intellectual disability, paralysis, blindness, deafness, and pseudobulbar palsy, progressing to death. [msdmanuals.com]

It can cause: Blindness Deafness Severe problems with muscle tone The disease is usually life-threatening. [nlm.nih.gov]

Krabbe disease is a sphingolipidosis, an inherited disorder of metabolism, that causes intellectual disability, paralysis, blindness, deafness, and pseudobulbar palsy, progressing [msdmanuals.com]

Acoustic Neuroma

The authors report a case of sudden deafness with unilateral tinnitus. [ncbi.nlm.nih.gov]

(National Institute on Deafness and Other Communication Disorders) Also in Spanish NIDCD Glossary (National Institute on Deafness and Other Communication Disorders) [medlineplus.gov]

One had normal hearing while the other already had a unilateral sensorineural deafness. [ncbi.nlm.nih.gov]

Labyrinthine Fistula

Surgically-induced deafness occurred in 3.3 per cent. All surgical groups showed similar hearing results, except for less conductive deafness in the CAT group. [ncbi.nlm.nih.gov]

Surgery that was performed against established rules caused deafness in three ears. [ncbi.nlm.nih.gov]

No patient presented with surgery-related deafness postoperatively. [ncbi.nlm.nih.gov]

Mucopolysaccharidosis Type 1 H

[…] glycosaminoglycans and is characterized by deformities of the skeleton and features, hepatosplenomegaly, restricted joint flexibility, clouding of the cornea, intellectual disability, deafness [merriam-webster.com]

It is clinically characterized by mental retardation, corneal clouding, deafness and cardiac disease, with death resulting in the first decade of life, often from cardiac [radiopaedia.org]

Bromate Poisoning

The spectrum of bromate (BrO3-) toxicity is different from bromide (Bγ) and includes the induction of ARF and deafness. [karger.com]

Cochlear Implantation after Bromate Intoxication-Induced Bilateral Deafness: A Case Report. J Int Adv Otol 2019; 15(3): 459-62. [advancedotology.org]

This report of potassium bromate poisoning and its resultant deafness and renal failure further emphasizes the curious relationship between these two organ systems. [ncbi.nlm.nih.gov]

Mumps

Good outcomes have been reported regarding the use of cochlear implants for mumps deafness. [ncbi.nlm.nih.gov]

The diagnosis was made according to the criteria for diagnosis of mumps deafness determined by the Acute Profound Deafness Committee set up by the Ministry of Health and Welfare [doi.org]

Deafness occurs in 0.5 to 5.0 per 100,000 cases. The Mayo Clinic reports that deafness can occur in one or both ears and is usually permanent. [livestrong.com]

Internal Auditory Artery Occlusion

He was first diagnosed with right-sided sudden deafness. [omicsonline.org]

Bilateral sudden deafness as a prodrome of anterior inferior cerebellar artery infarction. Arch Neurol 2001;58:1287-1289. 24. [j-stroke.org]

With conduction deafness, sound transmits best to the side of the deafness. [dartmouth.edu]

Paget Disease of the Bone

The usual features of Paget's disease of bone, e.g. large head, deafness due to involvement of the 8th cranial nerve and bowing of the legs are all well described in text [ncbi.nlm.nih.gov]

Abstract A fifty-four year old woman with Paget's disease of the skull had progressive deafness and tinnitus for eight years prior to the diagnosis and operative removal of [amjmed.com]

These disorders feature high bone turnover, deafness during early childhood, "idiopathic external lysis" of adult teeth, and sometimes focal lesions in appendicular bones [ncbi.nlm.nih.gov]

Alstrom Syndrome

Total blindness and deafness are likely to develop. Did you find this information useful? [patient.info]

Total blindness and deafness are likely to develop. [patient.info]

This disease can lead to blindness, deafness, diabetes, and obesity. Alström syndrome is inherited in an autosomal recessive manner. [medlineplus.gov]

Cockayne Syndrome

Synonyms Deafness-Dwarfism-Retinal Atrophy; Dwarfism with Renal Atrophy and Deafness; Neill-Dingwall Syndrome; Progeroid Nanism. [accessanesthesiology.mhmedical.com]

She was thin and frail; her neck, epiglottis and larynx were stiff; she was deaf and blind; and she could not speak, sit unaided, or perspire. [ncbi.nlm.nih.gov]

[…] and large hands and feet, kyphosis, cold blue extremities, beak-like nose giving the patient a prematurely old appearance, sparse hair, mental retardation, sensorineural deafness [whonamedit.com]

Salicylate Poisoning

GI: Nausea Vomiting Epigastric pain Hematemesis Pulmonary: Tachypnea Noncardiogenic pulmonary edema CNS: Tinnitus Deafness Delirium Seizures Coma In suspected overdose settings [5minuteconsult.com]

[…] toxicity: acid-base disturbance, uncoupling of oxidative phosphorylation, disordered glucose metabolism aspirin CLINICAL FEATURES nausea, vomiting, abdominal pain, tinnitus deafness [lifeinthefastlane.com]

(mg/kg) Serum Level (mg/dL) Estimated Severity Clinical Features Minimal GIT intolerance, bleeding Hypersensitivity Acute gout 150-300 40-110 Mild-to-moderate Tinnitus, deafness [emedsa.org.au]

Kearns-Sayre Syndrome

Hearing aids may be given to those with sensorineural deafness. Supplementation with coenzyme Q10 has been beneficial in some cases. [orpha.net]

Elevated CSF protein, sensorineural deafness, seizures, and pyramidal signs may also be present. Ragged-red fibers are found on muscle biopsy. [profiles.umassmed.edu]

To examine the evidence for a cochlear, retrocochlear, or central site of lesion for deafness in two cochlear implant recipients with Kearns-Sayre Syndrome (KSS). [ncbi.nlm.nih.gov]

Familial Paget Disease of Bone

Beethoven’s deafness. Journal of the American Medical Association 1970 ; 213: 434 – 437. Google Scholar | Crossref 31. Shearer, PD. [doi.org]

The most common neurological complication is deafness arising from involvement of the petrous temporal bone. [mja.com.au]

0304-324X (Print) eISSN: 1423-0003 (Online) For additional information: https://www.karger.com/GER Abstract The usual features of Paget’s disease of bone, e.g. large head, deafness [doi.org]