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14 Possible Causes for Decreased Number of Myelinated Fibers (Sural Nerve Biopsy), Shy Drager Syndrome

Did you mean: Decreased Number of Myelinated Fibers (Sural Nerve Biopsy, Shy Drager Syndrome

  • Autonomic Neuropathy

    Pathology Sural nerve biopsy reveals a marked reduction in nerve size and depletion of large and small myelinated fibers but only a slightly decreased number of unmyelinated[ojrd.biomedcentral.com] […] atrophy with autonomic failure (Shy-Drager syndrome) Parkinson’s syndrome with autonomic failure Secondary causes of autonomic neuropathy include: Amyloidosis (abnormal protein[my.clevelandclinic.org] Most people who are diagnosed with Shy-Drager syndrome die within seven to 10 years after symptoms begin.[rarediseasesnetwork.org]

  • Acute Intermittent Porphyria

    Open nerve and muscle biopsies showed significantly decreased numbers of myelinated fibers in the sural nerve and atrophy of type I and II fibers in the quadriceps muscle,[doi.org] Sensory nerve conduction velocities were absent in ulnar, sural, and plantar nerves, while peroneal motor conduction velocity was decreased (24 m/s; normal, 40 m/s), compatible[doi.org]

  • Familial Dysautonomia

    Pathology Sural nerve biopsy reveals a marked reduction in nerve size and depletion of large and small myelinated fibers but only a slightly decreased number of unmyelinated[doi.org] Dysautonomia may occur as the result of other diseases, such as diabetes mellitus, multiple system atrophy (Shy-Drager syndrome), Guillain-Barré syndrome and a number of other[internationalpain.org] Most people who are diagnosed with Shy-Drager syndrome die within seven to 10 years after symptoms begin.[rarediseasesnetwork.org]

  • Dysautonomia

    .: Sural nerve biopsy from a CMT1A case.[tankonyvtar.hu] Anesth Analg 2004; 98:40–5 Hutchinson RC, Sugden JC: Anaesthesia for Shy-Drager syndrome.[doi.org] To subscribe, click on the link below and follow: Shy-Drager Syndrome Electronic ListServer[vumc.org]

  • Autosomal Dominant Hereditary Sensory and Autonomic Neuropathy

    Pathologically, HSAN II demonstrates a virtual absence of myelinated fibers and a decreased number of unmyelinated fibers in sural nerve biopsies ( table 1 ).[anesthesiology.pubs.asahq.org] .: Sural nerve biopsy from a CMT1A case.[tankonyvtar.hu] Pathology Sural nerve biopsy reveals a marked reduction in nerve size and depletion of large and small myelinated fibers but only a slightly decreased number of unmyelinated[ojrd.biomedcentral.com]

  • GM2-Gangliosidosis Variant AB

    Muscle biopsy shows signs of neurogenic atrophy with type grouping and increased connective tissue. Sural nerve biopsy demonstrates decreased fiber density.[78stepshealth.us] It is effective in the treatment of acute cardiac failure, postmyocardial infarction low-output syndrome, shock, and reducing orthostatic hypotension in the Shy-Drager syndrome[healthdictionary.info] A histogram of counted nerve fibers shows a decrease in the number of large myelinated fibers and an increase in small myelinated fibers, indicating active regeneration.[78stepshealth.us]

  • Channelopathy-Associated Congenital Insensitivity to Pain

    Pathologically, HSAN II demonstrates a virtual absence of myelinated fibers and a decreased number of unmyelinated fibers in sural nerve biopsies ( table 1 ).[anesthesiology.pubs.asahq.org] Pathology Sural nerve biopsy reveals a marked reduction in nerve size and depletion of large and small myelinated fibers but only a slightly decreased number of unmyelinated[ojrd.biomedcentral.com] Pediatr Neurol 1994; 11:50–6Rosemberg, S Marie, SKN Kliemann, S Malan MD, Crago RR: Anaesthetic considerations in idiopathic orthostatic hypotension and the Shy-Drager syndrome[anesthesiology.pubs.asahq.org]

  • Peripheral Motor Neuropathy - Dysautonomia Syndrome

    Pathology Sural nerve biopsy reveals a marked reduction in nerve size and depletion of large and small myelinated fibers but only a slightly decreased number of unmyelinated[ojrd.biomedcentral.com] […] atrophy with autonomic failure (Shy-Drager syndrome) Parkinson’s syndrome with autonomic failure Secondary causes of autonomic neuropathy include: Amyloidosis (abnormal protein[my.clevelandclinic.org] Although the tendon reflexes are decreased or absent, there is no muscle atrophy or muscle weakness.[ojrd.biomedcentral.com]

  • Hereditary Sensory Radicular Neuropathy

    Pathology Sural nerve biopsy reveals a marked reduction in nerve size and depletion of large and small myelinated fibers but only a slightly decreased number of unmyelinated[ojrd.biomedcentral.com] - Multiple system atrophy ( Shy-Drager syndrome, Olivopontocerebellar atrophy )[wikidoc.org] Although the tendon reflexes are decreased or absent, there is no muscle atrophy or muscle weakness.[ojrd.biomedcentral.com]

  • Congenital Autosomal Dominant Indifference to Pain

    Pathologically, HSAN II demonstrates a virtual absence of myelinated fibers and a decreased number of unmyelinated fibers in sural nerve biopsies ( table 1 ).[anesthesiology.pubs.asahq.org] Pathology Sural nerve biopsy reveals a marked reduction in nerve size and depletion of large and small myelinated fibers but only a slightly decreased number of unmyelinated[ojrd.biomedcentral.com] Pediatr Neurol 1994; 11:50–6Rosemberg, S Marie, SKN Kliemann, S Malan MD, Crago RR: Anaesthetic considerations in idiopathic orthostatic hypotension and the Shy-Drager syndrome[anesthesiology.pubs.asahq.org]

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