Chromosomal disorder found in individuals of Hispanic descent with ancestry from the San Luis Valley in the Southwest of the United States. The association of mental retardation, congenital heart defects, seizures, a characteristic facial appearance, and urogenital anomalies characterizes the syndrome. San Luis[…]
[accessanesthesiology.mhmedical.com]
Medullary sponge kidney is a disorder in which dilated collecting tubules (1 to 7.5 mm in diameter) are found in one or more renal papillae. 1 In the absence of complications
[nejm.org]
MSP is a benign disorder which occurs when dilatations of the collecting tubules in one or more renal papillae appear.
[symptoma.com]
[…] urography suggested a diagnosis of polycystic renal disease (PRD); but the linear and cystic dilatation of collecting tubules, many of which contained numerous calculi, was
[ncbi.nlm.nih.gov]
collecting tubules filled with contrast.
[drdebasismaity.com]
Autosomal Recessive Polycystic Kidney Disease (ARPKD) ARPKD, a heritable condition, is characterized by cystic dilations of the renal collecting tubules.
[hawaii.edu]
Microscopically, the cysts are lined by flattened (undifferentiated) epithelium and represent fusiform dilation of collecting tubules that retain their connection to the afferent
[homeopathyworldcommunity.ning.com]
[…] and cystic collecting tubules.
[usmleforum.com]
The disease is characterized by dilatation of the collecting tubules. 5.
[urologyweb.com]
Autosomal Recessive Polycystic Kidney Disease (ARPKD) ARPKD, a heritable condition, is characterized by cystic dilations of the renal collecting tubules.
[hawaii.edu]
[…] of the collecting tubules.
[cags.org.ae]
There is cystic dilatation of the collecting tubules in one or both kidneys. Nephrocalcinosis and recurrent renal stones are usually seen.
[patient.info]
[…] urinary system Mode of Inheritance Autosomal dominant Gene Map Locus Multicystic renal dysplasia is a congenital dysplasia of the kidney characterized by large nonhomogeneous dilations
[cags.org.ae]
These corresponded pathologically to radially oriented, dilated collecting tubules. Autosomal recessive polycystic kidney disease (ARPKD).
[emedicine.com]
Image C Image D Histology: Cystic dilatation of terminal ends of ampullary collecting ducts, proximal convoluted tubules, and Bowman's capsule ( glomerular or tubular cysts
[auanet.org]
[b] In congenital hepatic fibrosis, dilatation of the collecting tubules is considered as the most common associated renal lesion (1). Multiple FULL TEXT
[annals.org]
A similar mechanism might explain the dilatation of the renal collecting tubules.
[kjim.org]
That is, an identical insult at different loci may result in choledochal cyst, dilatations of the major intrahepatic bile ducts (Caroli’s disease), congenital hepatic fibrosis
[kjim.org]
collecting tubules SKELETAL: Joint contractures; [Spine]; Scoliosis, progressive; [Hands]; Camptodactyly; Fifth finger clinodactyly; [Feet]; Deep plantar furrows SKIN, NAILS
[genome.jp]
[…] studies show a single ossification center in the sternum GENITOURINARY: Genitourinary anomalies (48%); [Internal genitalia, male]; Cryptorchidism; [Kidneys]; Hydronephrosis; Dilated
[genome.jp]
Medullary Sponge Kiney Ectatic dilatation of the distal collecting tubules confined to the renal pyramids Not exactly a true NC as the calcium deposition lies in the dilated
[slideshare.net]
The intraluminal deposits in such tubules appeared to be obstructing a number of the inner medullary collecting ducts, as evidenced by dilatation of these tubules at and proximal
[doi.org]
Many of these upstream dilated collecting ducts contained cast material and were lined by damaged cells.
[doi.org]
Unlike the adult polycystic kidney disease, there is no renal parenchyma, only dilated collecting tubules [27].
[intechopen.com]
The cysts can replace the parenchyma and are produced by the dilatation of the collecting tubules and other tubular segments of the nephrons.
[intechopen.com]
Multicystic kidney disease It is a congenital disorder characterized by cystic lesions that correspond primarily to dilated collecting tubules.
[intechopen.com]
Medullary sponge kidney is a developmental anomaly characterized by cystic dilatation of the collecting tubules in one or more renal medullary pyramids.
[sonoworld.com]
Medullary Sponge Kiney Ectatic dilatation of the distal collecting tubules confined to the renal pyramids Not exactly a true NC as the calcium deposition lies in the dilated
[slideshare.net]
The intraluminal deposits in such tubules appeared to be obstructing a number of the inner medullary collecting ducts, as evidenced by dilatation of these tubules at and proximal
[doi.org]
collecting tubules -large cystic masses that measure up to 6 cm in size -usually unilateraly but can be bilat or segmental Potter syndrome Type III: Autosomal Dominant Polycystic
[flashcardbook.com]
Histology: Cysts are formed by dilated collecting tubules. 3.3.3.3.2 Renal dysplasia Etiology: Renal dysplasia is the result of complete obstruction at either renal pelvis
[atlases.muni.cz]
[…] normal -oligohydramnios Potter syndrome Type II: Multicystic Dysplastic Kidney (MCKD) Congenital renal disorder characterized by cystic lesions that correspond primarily to dilated
[flashcardbook.com]
Medullary sponge kidney (MSK) is a rare congenital disease characterized by diffuse ectasia or dilation of precalyceal collecting tubules.
[ncbi.nlm.nih.gov]
The myriad of 1-mm to 3-mm dilated collecting tubules are too small for ultrasound to detect as individual cysts, and the multiple interfaces encountered by the transmitted
[healio.com]
[…] renal collecting tubules (CT) in utero and loss of renal function in patients if they survive the perinatal period.
[ajpcell.physiology.org]
Autosomal recessive polycystic kidney disease (ARPKD) is associated with loss of function of PKHD1-encoded protein fibrocystin-1 and is characterized by cystic dilation of
[ajpcell.physiology.org]
[…] characterized cystic dilation of collecting tubules in 1 or more renal pyramids in 1 or both kidneys dilated or distended collecting system variant of extrarenal pelvis backed
[quizlet.com]
Obstructions at this level cause dilation of the collecting tubules of the kidney. This is called hydronephrosis.
[childrens.memorialhermann.org]
Uric acid crystals Pathologic findings consist of dilation of the collecting ducts and distal tubules and chronic tubular atrophy with little glomerular damage.
[msdmanuals.com]
Dilation takes 3 days from the onset of obstructive uropathy to develop; before then, the collecting system is relatively noncompliant and less likely to dilate.
[msdmanuals.com]
Autosomal Recessive Polycystic Kidney Disease (ARPKD) ARPKD, a heritable condition, is characterized by cystic dilations of the renal collecting tubules.
[hawaii.edu]
Microscopically, the cysts are lined by flattened (undifferentiated) epithelium and represent fusiform dilation of collecting tubules that retain their connection to the afferent
[homeopathyworldcommunity.ning.com]
Microscopic evaluation shows cystic dilatations in all segments of the nephron, with loss of connection to the tubule.
[homeopathyworldcommunity.ning.com]
This manifests as dilatation of the collecting renal tubules, renal tubular ectasia, adult recessive polycystic disease, and rarely adult dominant polycystic kidney disease
[healio.com]
A similar mechanism might explain the dilatation of the renal collecting tubules.
[kjim.org]
That is, an identical insult at different loci may result in choledochal cyst, dilatations of the major intrahepatic bile ducts (Caroli’s disease), congenital hepatic fibrosis
[kjim.org]
[…] medial to renal hilum Infantile Polycystic Disease Recessive-inherited, dilation of the renal collecting tubules in the renal cortex, prenatal-most do not survive long after
[quizlet.com]
[…] of the medullary and papillary portions of the collecting tubules; associated w/ Caroli's disease, young to middle-aged adults; renal function is usually normal, pyramids
[quizlet.com]
[…] develop bilateral cysts 90%; 1st 3 months of treatment the kidneys are normal, after 3 years the development of numerous cysts is common non-hereditary, dysplastic cystic dilation
[quizlet.com]
This observation could explain the dilated proximal tubules that are observed upon renal biopsy of ARF kidneys, even though GFR is less than 10% of normal.
[jci.org]
In fact, microdissection of individual nephrons of kidneys from patients with ARF demonstrated obstructing casts in distal tubules and collecting ducts ( 42 ).
[jci.org]
[…] of collecting tubules resulting in multiple 1- to 2-mm cysts · Liver: periportal fibrosis often with abnormal proliferation + dilatation of bile ducts · Pancreas: pancreatic
[learningradiology.com]
[…] of renal tubules increase number of acoustic interfaces) · Increased renal through-transmission (high fluid content of cysts) · Loss of corticomedullary differentiation,
[learningradiology.com]
[…] images · Increasingly dense nephrogram · Poor visualization of collecting system · "Sunburst nephrogram" = striated nephrogram with persistent radiating opaque streaks (collecting
[learningradiology.com]
Micro: Cysts in the kidney have a uniform cuboidal lining w/ a cylindrical or saccular dilation of the collecting tubules.
[quizlet.com]
collecting tubules in one or more renal pyramids in one or both kidneys.
[quizlet.com]
Gross: superficially normal that reveal dilated papillary ducts and small cysts in the medulla in cut section giving it a sponge-like character Micro: Cystic dilation of the
[quizlet.com]
The collecting tubules are not dilated but are definitely shorter than normal, and they are oriented transversely rather than vertically from the corticomedullary junction
[urotoday.com]
tubules are not dilated but are definitely shorter than normal, and they are oriented transversely rather than vertically from the corticomedullary junction 26 Pathophysiology
[slideplayer.com]
[…] caliectesis) rather than rounded The medullary pyramids have a semilunar configuration, instead of the normal triangular or cone shape, and the tip of each papilla is flat The collecting
[slideplayer.com]
The collecting tubules dilate and the muscular walls of the pelvis and calices stretch, are replaced by fibrous tissue, and eventually form a large, fluid-filled, functionless
[medical-dictionary.thefreedictionary.com]
The collecting tubules dilate and the muscular walls of the renal pelvis and calices stretch, are replaced by fibrous tissue, and eventually form a large, fluid-filled, functionless
[medical-dictionary.thefreedictionary.com]
There is cystic dilatation of the collecting tubules in one or both kidneys. Nephrocalcinosis and recurrent renal stones are usually seen.
[patient.info]
[…] of collecting tubule origin and cuboidal epithelium Relatively common cystic disease in adults, often an incidental finding, normal renal function complications: calcification
[studyblue.com]
infection, stones See cystically dilated papillary ducts and cuboidal or transitional epithelial lining Sporadic (non-familial) -20% Familial juvenile nephronophthisis -
[studyblue.com]
[…] duct proliferation infantile and juvenile forms also have congenital hepatic fibrosis numerous small cysts in cortex and medulla Microscopically see saccular to cylindrical dilation
[studyblue.com]
[…] of the collecting tubules of the medullary portion of the renal pyramids give the organ a spongy, porous feeling and appearance.
[medical-dictionary.thefreedictionary.com]
[…] band of tissue as a result of fusion of the poles of the renal anlagen. medullary sponge kidney a usually asymptomatic congenital condition in which multiple small cystic dilatations
[medical-dictionary.thefreedictionary.com]
[…] of the collecting tubules. 10(p40) Patients are frequently asymptomatic, but may have microhematuria.
[appliedradiology.com]
Classically described as having a “paint brush” appearance, contrast opacifies the dilated tubules, resulting in dense striations extending from the papillary tips into the
[appliedradiology.com]
[…] more papillae, or caliceal-filling defects from sloughed papillae (Figure 1). 10(p89,p151),11(pt3,sec3,p46) Renal tubular ectasia is characterized by noncalcified cystic dilatation
[appliedradiology.com]
[…] proximal tubules with thinning or loss of PAS+ brush border; hyaline, granular and pigmented cases, particularly in distal and collecting ducts, eosinophilic hyaline casts
[pathologyoutlines.com]
Microscopic (histologic) description Ischemic ATN: Early: varies from cell swelling to focal tubular epithelial necrosis and apoptosis with desquamation of cells into lumen; dilated
[pathologyoutlines.com]
