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3,653 Possible Causes for Endolymphatic Sac Tumor, Nystagmus, Sensorineural Hearing Loss Associated with ELSTs

  • Von Hippel-Lindau Disease

    […] body, including the brain, spine, eyes, kidneys, pancreas, adrenal glands, inner ears, reproductive tract, liver and lung: Brain/Spinal Hemangioblastoma Headaches, ataxia, nystagmus[rarediseases.org] ) hearing loss, sensorineural, associated with elsts Genitourinary Kidneys: multiple renal cysts renal hemangioblastoma renal cell carcinoma (e.g., ) Genitourinary Internal[malacards.org] KEYWORDS: endolymphatic sac tumor; prevalence; temporal bone MRI; von Hippel-Lindau[ncbi.nlm.nih.gov]

  • Hemangioblastoma

    In general, HBA may be associated with hydrocephalus and increased intracranial pressure that may provoke headaches, vomiting, distinct neurological symptoms and nystagmus[symptoma.com] […] in the central nervous system (CNS) and retina, renal carcinoma, pheochromocytomas, pancreatic serous cystadenoma, and endolymphatic sac tumors.[ncbi.nlm.nih.gov] Neurological examination was remarkable for papilledema, horizontal nystagmus on the right, left lateral gazes, absent gag reflex, dysphagia, ataxic gait, and motor incoordination[karger.com]

    Missing: Sensorineural Hearing Loss Associated with ELSTs
  • Meniere's Disease

    Periodic alternating nystagmus (PAN) is a spontaneous horizontal nystagmus that reverses direction periodically. PAN has been reported in acquired and congenital forms.[ncbi.nlm.nih.gov] sac tumor that was treated with surgical excision.[ncbi.nlm.nih.gov] Periodic alternating nystagmus is a rare central nervous system disorder in which the eyes undergo a horizontal jerk nystagmus that periodically reverses direction.[ncbi.nlm.nih.gov]

    Missing: Sensorineural Hearing Loss Associated with ELSTs
  • Cerebellar Hemangioblastoma

    This patient was very unsteady and had strong positional nystagmus due to removal of her cerebellar nodulus.[dizziness-and-balance.com] An incidental left endolymphatic-sac tumor is also depicted on this image ( arrowhead ). (5660/29.7; TI, 150) C, CT image shows further enlargement of the cyst 21 months after[ajnr.org] sac tumors pancreatic tumors Evaluation Genetic testing usually on lymphocytes of the peripheral blood Imaging techniques used to identify associated diseases e.g., MRI/CT[medbullets.com]

    Missing: Sensorineural Hearing Loss Associated with ELSTs
  • Cerebellar Neoplasm

    This patient was very unsteady and had strong positional nystagmus due to removal of her cerebellar nodulus.[dizziness-and-balance.com] CNS manifestations include endolymphatic sac tumors and multiple hemangioblastomas.[clinicalgate.com] , epididymis cysts, cystadenomas of the broad ligament and endolymphatic sac tumors of the middle ear.[neuropathology-web.org]

    Missing: Sensorineural Hearing Loss Associated with ELSTs
  • Cerebellopontine Angle Tumor

    CONCLUSIONS: The contribution of hyperventilation on vestibular nystagmus differs depending on the disease phase or underlying pathologies.[ncbi.nlm.nih.gov] Endolymphatic sac tumors (ELST) are rare papillary tumors of the temporal bone.[ncbi.nlm.nih.gov] Identifier Bruns_nystagmus Title Bruns nystagmus due to a cerebellopontine angle tumor Subject Jerk Nystagmus, Gaze Evoked Nystagmus, Vestibular Nystagmus Creator Daniel R[collections.lib.utah.edu]

    Missing: Sensorineural Hearing Loss Associated with ELSTs
  • Retinal Angioma

    Patients with a cerebellar hemangioblastoma may present with headache, nausea, broad based gait, ataxia, slurred speech, nystagmus or papilledema.[path.upmc.edu] Endolymphatic sac tumors occur in about 10% of patients. Cystic lesions are often associated with the tumors, especially in the pancreas.[disorders.eyes.arizona.edu] […] body, including the brain, spine, eyes, kidneys, pancreas, adrenal glands, inner ears, reproductive tract, liver and lung: Brain/Spinal Hemangioblastoma Headaches, ataxia, nystagmus[rarediseases.org]

    Missing: Sensorineural Hearing Loss Associated with ELSTs
  • Acoustic Neuroma

    Hyperventilation for 30 seconds provoked an ipsilateral beating nystagmus and reproduced the vertiginous sensation in both subjects.[ncbi.nlm.nih.gov] […] temporal bone Chondrosarcoma Chordoma Endolymphatic sac tumors Esthesioneuroblastomas Inflammatory pseudotumors of the skull base Metastatic disease Many others Diagnosis[brighamandwomens.org] […] neuroma (mainly intracanalicular type) were studied with a full audio-vestibular test battery (pure tone and speech audiometry, caloric bithermal test, vibration-induced nystagmus[ncbi.nlm.nih.gov]

    Missing: Sensorineural Hearing Loss Associated with ELSTs
  • Temporal Bone Fracture

    The nystagmus is easily seen by the naked eye.[emedicine.medscape.com] A small extension of the tumor into the middle ear is present EndoLymphatic Sac Tumor (ELST) ELST is a rare entity. These tumors originate from the endolymphatic sac.[radiologyassistant.nl] With repetition, the nystagmus is not reproducible at a point; contrarily, central positional vertigo is a changing-direction nystagmus that has no latency period, is nonfatiguing[emedicine.medscape.com]

    Missing: Sensorineural Hearing Loss Associated with ELSTs
  • Autosomal Recessive Spinocerebellar Ataxia 8

    Findings on examination include spastic and ataxic dysarthria, gaze-evoked nystagmus, limb and gait ataxia, limb spasticity, and diminished vibratory sensation.[ataxia.uchicago.edu] Endolymphatic sac tumors affect about 10% of cases, and VHL should be considered in persons with bilateral endolymphatic sac tumors.[tchain.com] Other features of ARCA1 include abnormal eye movements (nystagmus) and problems following the movements of objects with the eyes.[ghr.nlm.nih.gov]

    Missing: Sensorineural Hearing Loss Associated with ELSTs

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