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83 Possible Causes for 'Eye of the Tiger' Sign on MRI, Focal Sharp-Waves or Spikes Occipital or Temporal, Jerk-Locked Premyoclonus Spikes

  • Benign Adult Familial Myoclonic Epilepsy

    T2 weighted brain MRI shows an ”eye of the tigersign corresponding to pallidal hypointensity with a high signal center.[neuroweb.us] […] cortical spikes detected by the jerk-locked back-averaging) ( Ikeda et al., 1990 ).[academic.oup.com] spikes detected by the jerk-locked back averaging (JLA) method), and a good response to antiepileptic drugs. 2 BAFME was first reported in 1990 in the Japanese population[nature.com]

  • Generalized Clonic or Tonic-Clonic Seizures

    premyoclonus spikes Hand tremor Neuronal loss in central nervous system Cutaneous photosensitivity Hyperreflexia Heterogeneous Weight loss Dystonia Splenomegaly Thrombocytopenia[mendelian.co] […] callosum Muscular hypotonia Infantile onset Intellectual disability, moderate Intention tremor Progressive neurologic deterioration Absence seizures Nevus EEG abnormality Jerk-locked[mendelian.co]

    Missing: 'Eye of the Tiger' Sign on MRI
  • Hallervorden-Spatz Syndrome

    Iron deposition in conjunction with destruction of the globus pallidus gives rise to the characteristic eye-of-the-tiger sign in MRI.[ncbi.nlm.nih.gov] […] of the tiger" sign.[ncbi.nlm.nih.gov] It has been postulated that pantothenate kinase 2 mutations underlying all cases of classic Hallervorden-Spatz syndrome are always associated with the eye-of-the-tiger sign[ncbi.nlm.nih.gov]

    Missing: Focal Sharp-Waves or Spikes Occipital or Temporal Jerk-Locked Premyoclonus Spikes
  • Epilepsy

    Focal cortical dysplasia is a common cause of medically refractory epilepsy in infancy and childhood. We report a neonate with seizures occurring within the first day of life. Continuous video-EEG monitoring led to detection of left motor seizures and a right frontal EEG seizure pattern. Brain MRI revealed a lesion[…][ncbi.nlm.nih.gov]

    Missing: 'Eye of the Tiger' Sign on MRI Jerk-Locked Premyoclonus Spikes
  • Juvenile Myoclonic Epilepsy

    Juvenile myoclonic epilepsy (JME) is a type of epilepsy that starts in in childhood or the teen years. People who have it wake up from sleep with quick, jerking movements of their arms and legs. These are called myoclonic jerks. Even if you don’t have epilepsy, you’ve probably had these jerks that jolt you awake,[…][webmd.com]

    Missing: 'Eye of the Tiger' Sign on MRI Jerk-Locked Premyoclonus Spikes
  • Vascular Dementia

    Many of the previous studies of vascular dementia using proton magnetic resonance (MR) spectroscopy had been carried out on white matter. However, no proton spectroscopic data of the subcortical gray matter are available in such disease. We report two cases suffering from vascular dementia, with an unilateral[…][ncbi.nlm.nih.gov]

    Missing: 'Eye of the Tiger' Sign on MRI Jerk-Locked Premyoclonus Spikes
  • West Syndrome

    2015 ICD-9-CM Diagnosis Code 345.6 Infantile spasms There are 2 ICD-9-CM codes below 345.6 that define this diagnosis in greater detail. Do not use this code on a reimbursement claim. Clinical Information A rare autosomal recessive inherited neurodegenerative disorder caused by mutations in the pla2g6 gene. It is[…][icd9data.com]

    Missing: 'Eye of the Tiger' Sign on MRI Jerk-Locked Premyoclonus Spikes
  • Idiopathic Generalized Epilepsy

    Tonic status epilepticus (TSE) in patients with idiopathic generalized epilepsy (IGE) is not well recognized. The objective of this study is to report episodes of TSE in patients with IGE. We retrospectively reviewed the clinical and EEG evaluation of three IGE patients who presented TSE. The three patients had mainly[…][ncbi.nlm.nih.gov]

    Missing: 'Eye of the Tiger' Sign on MRI Jerk-Locked Premyoclonus Spikes
  • Encephalopathy

    *Repetitive and fairly stereotyped waveforms appearing at regular intervals, sharps/spike waves or complex discharges.[slideshare.net] […] frontal lobe lesion *OIRDA --occipital dominant ,seen in children as in absence seizure *TIRDA– temporal lobe epilepsy 21.[slideshare.net] *Frontal dominance (FIRDA) --non specific ,diffuse encephalopathy, if focal ?[slideshare.net]

    Missing: 'Eye of the Tiger' Sign on MRI Jerk-Locked Premyoclonus Spikes
  • Encephalitis

    Rev Neurol (Paris). 2018 Apr;174(4):228-236. doi: 10.1016/j.neurol.2017.11.004. Epub 2018 Mar 31. Author information 1 Centre de référence maladies rares 'Syndromes neurologiques paranéoplasiques', hospices civils de Lyon, hôpital neurologique, neurologie B, 69677 Bron, France; INMG (NeuroMyoGene Institut), Inserm U1217/CNRS[…][ncbi.nlm.nih.gov]

    Missing: 'Eye of the Tiger' Sign on MRI Jerk-Locked Premyoclonus Spikes