West Syndrome
We report on a 3-year-old girl with West syndrome and with focal hypsarrhythmia.[ncbi.nlm.nih.gov]
[…] the corpus callosum is important in the generalization of hypsarrhythmia.[ncbi.nlm.nih.gov]
OBJECTIVE: Fast oscillations (FOs) were first explored from scalp electroencephalographic (EEG) data from hypsarrhythmia in West syndrome (infantile spasms) to investigate[ncbi.nlm.nih.gov]
Early Infantile Epileptic Encephalopathy Type 17
Over her lifetime, neither hypsarrhythmia nor diffuse slow spike-wave pattern were seen.[ncbi.nlm.nih.gov]
[…] at around age 3-6 months, and further from hypsarrhythmia to diffuse slow spike-waves at around age 1.[ncbi.nlm.nih.gov]
In 7 of the 9 patients with OS, EEG findings transitioned from suppression-burst pattern to hypsarrhythmia.[ncbi.nlm.nih.gov]
Myoclonic-Astatic Epilepsy
Infantile spasms (West syndrome) West syndrome usually occurs in the first year of life and consists of the triad of infantile spasms, developmental deterioration, and a hypsarrhythmia[emedicine.medscape.com]
The origin of hypsarrhythmia and tonic spasms in West syndrome: evidence from a case of porencephaly and hydrocephalus with focal hypsarrhythmia.[malattierare.regione.veneto.it]
West Syndrome is characterized by infantile spasms, developmental regression, and a specific pattern on electroencephalography (EEG) testing called hypsarrhythmia (chaotic[epilepsywarriors.org]
Hypothalamic Hamartoma
Results of electroencephalographic (EEG) study at the time of IS diagnosis showed hypsarrhythmia in two (33%).[ncbi.nlm.nih.gov]
We describe a male infant with Pallister-Hall syndrome who had a large HH presenting with infantile spasms without hypsarrhythmia. [(18)F]fluoro-deoxyglucose positron emission[ncbi.nlm.nih.gov]
These patients may have hypsarrhythmia on initial EEG, and may respond to ACTH treatment with improvement of IS.[ncbi.nlm.nih.gov]
Sturge-Weber Syndrome
In the presence of epileptic spasms or generalized seizure types, the background may show widespread slowing or hypsarrhythmia.[epilepsydiagnosis.org]
Hypsarrhythmia can be seen in those with epileptic spasms. Activation EEG abnormality is enhanced by sleep deprivation and in sleep.[epilepsydiagnosis.org]
Early Infantile Epileptic Encephalopathy Type 3
At five months, inter-ictal EEG revealed hypsarrhythmia, but his attacks were still only myoclonuses.[ncbi.nlm.nih.gov]
The course observation clarifies differences between both syndromes; SBs evolve to hypsarrhythmia around 3-4 months of age, and sometimes further to diffuse slow spike-waves[ncbi.nlm.nih.gov]
All three cases with NKH survived with increasing microcephaly, muscle tonicity; all developed infantile spasm with hypsarrhythmia on EEGs.[ncbi.nlm.nih.gov]
Lissencephaly
Approximately 80% have infantile spasms, although the EEG does not always show the typical hypsarrhythmia pattern.[ncbi.nlm.nih.gov]
Lennox-Gastaut Syndrome
There is also a tendency for psychosis to develop with time. 20% of all patients with Lennox-Gastaut syndrome have prior infantile spasms with hypsarrhythmia. [ 3 ] Although[patient.info]
[…] condition characterized by three features: Infantile spasms Developmental regression A pattern of erratic brain activity on electroencephalogram (EEG), which is known as hypsarrhythmia[verywellhealth.com]
Early Infantile Epileptic Encephalopathy Type 2
[…] at around age 3-6 months, and further from hypsarrhythmia to diffuse slow spike-waves at around age 1.[ncbi.nlm.nih.gov]
The seizures evolved to brief tonic spasms, and hypsarrhythmia on EEG was noticed at age of 5 months, indicating the transition to West syndrome.[ncbi.nlm.nih.gov]
VPA, ZNS, PB, and clonazepam were given, but his EEG at the age of 7 mo showed transformation to hypsarrhythmia.[ncbi.nlm.nih.gov]
Familial Infantile Myoclonic Epilepsy
Ongoing IS (and hypsarrhythmia) have the potential to adversely impact all aspects of brain development.[childneurologyfoundation.org]
Results: All six affected boys had myoclonic seizures and TCS; two had infantile spasms, but only one had hypsarrhythmia.[neurology.org]
: Infantile spasm, IS, X-linked infantile spasm syndrome, X-linked infantile spasms, West's syndrome, Tonic spasms with clustering, arrest of psychomotor development and hypsarrhythmia[rarediseases.info.nih.gov]