Interrupted Aortic Arch: Causes & Reasons

Possible Causes for Interrupted Aortic Arch

In our case, the 22q11.2 deletion likely played a major role in the etiology of the interrupted aortic arch. [ncbi.nlm.nih.gov]

aortic arch truncus arteriosus characteristic facies elongated face long philtrum facial asymmetry prominent nose hypernasal speech learning disabilities decreased immunity [radiopaedia.org]

We describe a neonate with DiGeorge syndrome undergoing diagnosis and successful repair of interrupted right aortic arch and origin of the left pulmonary artery from the aorta [ncbi.nlm.nih.gov]

Coarctation of the Aorta

Complete interruption of the aortic arch Complete interruption of the aorta, or interrupted aortic arch (IAA), is a fairly rare condition. [emedicine.medscape.com]

OBJECTIVES: The objectives of this review are to discuss the perioperative management of coarctation of the aorta, interrupted aortic arch, and the borderline left ventricle [ncbi.nlm.nih.gov]

Complications following reparative surgery for aortic coarctation or interrupted aortic arch. Surg Today. 1998. 28(9):889-94. [Medline]. [emedicine.medscape.com]

Bronchial Compression

Successful correction of bronchial compression and severe bronchomalacia complicating repair of interrupted aortic arch was achieved using transverse aortic arch extension [ncbi.nlm.nih.gov]

We report here a patient with interrupted aortic arch and a right descending aorta, in whom the surgical management was complicated by the development of right bronchus compression [ncbi.nlm.nih.gov]

Abstract Four cases of interruption of the aortic arch with the rare association of right ductus arteriosus and right descending aorta are described. [ncbi.nlm.nih.gov]

Congenital Absence of Ductus Arteriosus

What is interrupted aortic arch? [mottchildren.org]

aortic arch. [books.mcai.org.uk]

The aortic arch is interrupted (red double headed arrow) distal to the left subclavian artery ( LSA ) and proximal to the arterial duct. [ipccc.net]

Taussig Bing Anomaly

We report a case of staged repair of Type A Interrupted aortic arch with Taussig-Bing anomaly in a one month old male. [ajol.info]

aortic arch-type A Single-stage repair of Taussig-Bing anomaly and interrupted aortic arch-type A Source: Multimedia Manual of CT Surgery Published on 2016-07-14 Scimitar [ct-assist.com]

The results of a surgical program for interrupted aortic arch J Thorac Cardiovasc Surg 1988 96 864 877 [7] Reoperations for interrupted aortic arch. [ejcts.oxfordjournals.org]

Persistent Fifth Aortic Arch

[…] and Interrupted Fourth Aortic Arch Neonatal Repair of Persistent Fifth Aortic Arch Coarctation and Interrupted Fourth Aortic Arch Source: Annals of Thoracic Surgery Published [ct-assist.com]

We report a case of a neonate with type A interrupted aortic arch and severe coarctation of a persistent fifth aortic arch, which was discovered after repair of a left congenital [ncbi.nlm.nih.gov]

To detect persistent fifth aortic arch with interrupted aortic arch, the following methods were used: echocardiogram, angiocardiography, and magnetic resonance imaging. [ncbi.nlm.nih.gov]

Cervical Aortic Arch

Interrupted aortic arch is a rare congenital anomaly in newborns and infants and is commonly associated with other cardiovascular anomalies. [ncbi.nlm.nih.gov]

The angiographic diagnosis was interruption of the aortic arch type II, with aberrant right subclavian artery, a closed ductus arteriosus and retrograde vertebral-subclavian [ncbi.nlm.nih.gov]

Interruption of aortic arch 7. [slideshare.net]

Anomalies of Great Veins, Congenital

[…] type A aortic arch interruption. [link.springer.com]

Other arch anomalies hypoplastic ascending aorta coarctation of the aorta interrupted aortic arch patent ductus arteriosus cervical aortic arch ductus diverticulum circumflex [radiopaedia.org]

Correction of the interrupted aortic arch carries a high risk of mortality. [ots1.narod.ru]

Aortopulmonary Septal Defect

Surgical repair of an aortopulmonary septal defect, interrupted aortic arch and the duct that coexists in this setting usually includes closure of the aortopulmonary septal [ncbi.nlm.nih.gov]

Thus, aortopulmonary septal defect with type B interrupted aortic arch was suspected. [eurekamag.com]

3 Shone’s complex 7 PAPVR 1 Interrupted aortic arch 1/11 (9%) Double aortic arch 1 [onlinejacc.org]

Persistent Truncus Arteriosus

Five patients had type A and 3 patients had type B aortic arch interruption. [ncbi.nlm.nih.gov]

[…] arteriosus with interrupted aortic arch in an 85-day-old infant. [ncbi.nlm.nih.gov]

We present a case of a 3-week-old boy with persistent truncus arteriosus associated with interrupted right aortic arch having an anomalous origin of the left vertebral artery [ncbi.nlm.nih.gov]

Congenital Pulmonary Veins Atresia or Stenosis

Syndrome Interrupted Aortic Arch Patent Ductus Arteriosus (PDA) Pulmonary Artery Sling Pulmonary Stenosis Tetralogy of Fallot Total Anomalous Pulmonary Venous Return Transposition [nemours.org]

aortic arch (IAA) Kawasaki disease Long QT syndrome Marfan syndrome Mitral stenosis Partial anomalous pulmonary venous connection (PAPVC) Patent ductus arteriosus (PDA) Patent [texaschildrens.org]

Pediatr Radiol 35(10):947–960 CrossRef PubMed Google Scholar Dillman JR, Yarram SG, D’Amico AR (2008) Interrupted aortic arch: spectrum of MRI findings. [link.springer.com]

Acyanotic Congenital Heart Disease

Causes: Presentation in Week 1 Transient Myocardial Ischemia Dysrhythmias Arteriovenous fistula Increased Pulse s Aortic Coarctation (Interrupted aortic arch) Asymmetric Pulse [fpnotebook.com]

Cardiac anomalies which predispose to this type of compression include ventricular septal defect, patent ductus arteriosus, interruption of the aortic arch, and tetralogy [experts.umn.edu]

Stenosis Aortic Coarctation Aortic atresia IV. [fpnotebook.com]

Discrete Fibromuscular Subaortic Stenosis

When present in infancy, associated left heart obstructive lesions, such as coarctation of the aorta or interrupted aortic arch may coexist. [chw.org]

Outcomes in patients with interrupted aortic arch and ventricular septal defect. J Thorac Cardiovasc Surg 1994;107:1099-1113 3. [slideshare.net]

Exceptions include patients with Shone complex and interrupted aortic arch, who can have SAS in early infancy. [emedicine.medscape.com]

Right Hemitruncus

arch type A4: presence of an associated interrupted aortic arch Associations right sided aortic arch interrupted aortic arch 8 persistence of primitive aortic arches DiGeorge [radiopaedia.org]

arch, descending aorta or right ventricle (previously known as hemitruncus) type A4: truncus with aortic isthmus stenosis or interrupted aortic arch. [dhzb.de]

Type A4 denotes truncus associated with an interrupted aortic arch. [musculoskeletalkey.com]

Left Ventricular Outflow Obstruction

Abstract Residual left ventricular outflow tract (LVOT) obstruction is a significant problem after repair of interrupted aortic arch (IAA) and ventricular septal defect. [ncbi.nlm.nih.gov]

Abstract This study looked at echocardiographic predictors of left ventricular outflow obstruction after primary neonatal repair of interrupted aortic arch and ventricular [ncbi.nlm.nih.gov]

The results of a surgical program for interrupted aortic arch. J Thorac Cardiovasc Surg 1988 ; 96 : 864 – 877. 20. [cambridge.org]

Disproportionate Short Stature - Ptosis - Valvular Heart Lesions

Heterotaxy, atrial ventricular canal, and interrupted aortic arch may occur in tandem. [dermatologyadvisor.com]

In patients in whom a bicuspid aortic valve is observed in association with other types of left heart obstruction (coarctation or interrupted aortic arch), the bicuspid valve [chd-uk.co.uk]

Truncus arteriosus/interruption of the aortic arch 1. 22q11 deletion syndrome (see above) 2. Trisomy 8 3. Deletion 10p C. [circ.ahajournals.org]

Aortic Arch Interruption

[…] and Symptoms of Interrupted Aortic Arch Outlook for Interrupted Aortic Arch Last Updated: Feb 26, 2019 Written by Dr. [news-medical.net]

What Is Interrupted Aortic Arch (IAA)? [secondscount.org]

[…] and Treatment of Interrupted Aortic Arch Outlook for Interrupted Aortic Arch [news-medical.net]

Velocardiofacial Syndrome

The commonest cardiac defects in VFCS are interrupted aortic arch seen in up to 50% of cases, involvement of truncus arteriosus, and tetralogy of fallot. [symptoma.com]

B, a heart defect in which the aorta does not completely develop, thus resulting in an incomplete, or “interrupted” aortic arch • Ventricular septal defect, when the wall [rarediseases.org]

Aortic Arch - 15% Ventral Septal Defect - 13% Truncus Arteriosus - 7% Other Defect - 17% Palate Palatal Defects occur in 69% of patients Velopharyngeal incompetence (VPI) [en.wikibooks.org]

Abnormal Origin of the Pulmonary Artery

Aorto-pulmonary window, interrupted aortic arch and abnormal origin of the right pulmonary artery from the aorta, combined with patent ductus arteriosus and with intact ventricular [ncbi.nlm.nih.gov]

interrupted aortic arch distal to the brachiocephalic trunk. and isolated origin of the left carotid artery from the right pulmonary artery, hypoplastic right ventricle [ipccc.net]

Casteñeda. (1976) Interrupted aortic arch in infancy. J. Pediatr. 38:959-962. [anatomyatlases.org]

Congenital Heart Disease

Interrupted Aortic Arch. Interrupted Aortic Arch. Chest radiograph. Condition Description: Interrupted Aortic Arch. Endocardial fibroelastosis (Cardiomyopathy). [bcm.edu]

The patient was transported to the ED for evaluation, where a bedside echocardiogram revealed interrupted aortic arch (IAA), ventricular septal defect, minimal flow through [ncbi.nlm.nih.gov]

However, MCA-PI and Z score decreased in aortic stenosis but not in interrupted aortic arch or coarctation subgroups, whereas they increased in pulmonary atresia but not pulmonary [ncbi.nlm.nih.gov]

Aorto-Right Ventricular Tunnel

Furthermore, thorough evaluation of the arch is important to rule-out possible association of interrupted arch (commonly type A interrupted aortic arch) or presence of associated [pedecho.org]

Repair of hypoplastic or interrupted aortic arch using autogenous or prosthetic material; with cardiopulmonary bypass. [quizlet.com]

Epidemiology  Isolated /With extracardiac anomalies  Incidence:0.03 to 0.14 per 1000 live births  1% of all CHD  Association: coarctation, aortic arch hypoplasia, or interrupted [slideshare.net]

Subvalvular Aortic Stenosis

The most frequently encountered associated lesions were ventricular septal defect (n = 19) and coarctation of the aorta/interrupted aortic arch (n = 14). [ncbi.nlm.nih.gov]

coarctation of aorta, and interrupted aortic arch. [journals.lww.com]

Exceptions include patients with Shone complex and interrupted aortic arch, who can have SAS in early infancy. [emedicine.medscape.com]

22q11.2 Duplication Syndrome

aortic arch) Laitenberger 2007 reported one patient with transposition of the great arteries with Ebstein anomaly de la Rochebrochard 2006, reported a complex, non-conotruncal [c22c.org]

aortic arch 0011611 Microcephaly Abnormally small skull Decreased circumference of cranium Decreased size of skull Reduced head circumference Small head circumference [ more [rarediseases.info.nih.gov]

Anomalous Origin of the Innominate Artery

[…] type B interrupted aortic arch. [quizlet.com]

Anomalous RSCA-Hunauld,1735 Double aortic arch-Hommel 1737 Right aortic arch –Fioratti,Aglieti-1763 Interrupted aortic arch-Steidele-1788 Bayford,1787-dysphagia by vascular [slideshare.net]

It can be embryologically explained using Edwards hypothetical double aortic arch model where the left aortic arch is interrupted proximal to the left common carotid artery [scmr.org]

Mitral Valve Atresia

We experienced that one patient from another series with an interrupted aortic arch, ventricular septal defect, and aortic root with a diameter of 64% of normal values showed [medical.med.tokushima-u.ac.jp]

aortic arch, pulmonary atresia with intact septum, single ventricle, total anomalous pulmonary venous connection, tetralogy of Fallot, tricuspid atresia, and truncus arteriosus [icdlist.com]

It is commonly associated with coarctation, interrupted aortic arch, VSD as well as defects of the mitral valve. This lesion is usually overlooked in infancy. [pedcard.rush.edu]

Congenital Pericardium Anomaly

Interrupted Aortic Arch. Interrupted Aortic Arch. Chest radiograph. Condition Description: Interrupted Aortic Arch. Endocardial fibroelastosis (Cardiomyopathy). [bcm.edu]

aortic arch and others. [cachnet.org]

Absence of a normal “V”-sign confluence of the arterial arches can be used to detect aortic arch abnormalities: right aortic arch, double aortic arch ( Figure 22 ) and interrupted [intechopen.com]

Left-to-Right Cardiac Shunt

Interrupted Aortic Arch. Interrupted Aortic Arch. Chest radiograph. Condition Description: Interrupted Aortic Arch. Endocardial fibroelastosis (Cardiomyopathy). [bcm.edu]

Syndrome Interrupted Aortic Arch Patent Ductus Arteriosus (PDA) Pulmonary Artery Sling Pulmonary Stenosis Tetralogy of Fallot Total Anomalous Pulmonary Venous Return Transposition [nemours.org]

Examples of left-sided ductus-dependent congenital heart disease include hypoplastic left heart syndrome, critical aortic stenosis, coarctation of aorta and interrupted aortic [patient.info]

Cyanotic Congenital Heart Disease

aortic arch Pulmonary atresia (PA) Pulmonary stenosis (critical) Eisenmenger syndrome (reversal of shunt due to pulmonary hypertension). [en.wikipedia.org]

The symmetry and amplitude of pulses should be routinely observed, in order not to miss associated abnormalities such as coarctation of the aorta or interrupted aortic arch [symptoma.com]

Double Aortic Arch

No reports on pulmonary atresia with ventricular septal defect with the combination of double aortic arch and interruption between left and right carotid arteries have been [ncbi.nlm.nih.gov]

aortic arch Hypoplasia of aorta Hypoplastic aorta syndrome Interrupted aortic arch Kommerell's diverticulum Kommerells diverticulum Overriding aorta Pseudocoarctation of [icd10data.com]

In literature, TA with a double aortic arch is observed as a very rare condition. [ncbi.nlm.nih.gov]

Thymic Aplasia

Common anomalies are: Interrupted aortic arch Patent truncus arteriosus Tetralogy of Fallot Ventricular septal defect Poor circulation of oxygenated blood results in: Palataldefects [lecturio.com]

arch, interrupted aortic arch, tetrology of Fallot, aberrant subclavian artery, right infundibular stenosis and ventricular septal defect. [ispub.com]

aortic arch, ventricular septal defect Immune deficiency (> 75%): thymic hypoplasia, rarely aplasia, with T cell lymphopenia Palatal anomalies (70%): velopharyngeal insufficiency [pathologyoutlines.com]