Papillary necrosis is a common renal manifestation of vaso-occlusion, leading to isosthenuria (ie, inability to concentrate urine).
[emedicine.medscape.com]
Isosthenuria results in a large loss of water, further contributing to dehydration in these patients. Renal failure may ensue, usually preceded by proteinuria.
[emedicine.medscape.com]
Crossref PubMed Scopus (65) Google Scholar and (ii) a reduction or complete blunting of the osmotic gradient in the renal medulla, causing isosthenuria, i.e., an impaired
[kidney-international.org]
[…] are often large early in the disease, with variable echogenicity on ultrasound, but shrink with development of renal failure.
[radiopaedia.org]
[…] extent than is seen in sickle cell anemia. 2 Known renal manifestations of sickle cell trait include microscopic hematuria, renal papillary necrosis with gross hematuria, isosthenuria
[hematology.org]
Bilateral echogenic pyramids are frequently seen in sickle cell disease renal papillary necrosis renal vein thrombosis Gastrointestinal tract approximately 40% patient may
[radiopaedia.org]
We observed a 30-year-old woman in whom a large mass in the right lower quadrant and bilaterally enlarged cystic kidneys with markedly distorted collecting systems by excretory
[ncbi.nlm.nih.gov]
Figure 5: Note the small posterior cephalocele, the large abdominal distention due to the bilateral cystic kidneys and the postaxial polydactyly.
[thefetus.net]
Typical clinical features are chronic renal failure, anemia, polyuria, polydipsia, isosthenuria, and growth retardation.
[genecards.org]
MKS is characterized by central nervous system malformation (usually occipital encephalocele), bilateral large multicystic kidneys, fibrotic changes of the liver, and polydactyly
[nature.com]
Sonography shows bilateral small kidneys with loss of corticomedullary junction and multiple cysts only in the medulla.
[en.wikipedia.org]
Clinical features of familial juvenile nephronophthisis include anemia, polyuria, polydipsia, isosthenuria, and death in uremia.
[malacards.org]
[…] which there is progressive symmetrical destruction of the kidneys involving both the tubules and glomeruli, characteristically resulting in anemia, polyuria, polydipsia, isosthenuria
[medicinenet.com]
[…] recessive polycystic kidney disease Large kidneys with multiple bilateral cysts Hepatic fibrosis ESRD during childhood Bardet-Biedl syndrome Intellectual disability Retinopathy
[merckmanuals.com]
[…] which there is progressive symmetrical destruction of the kidneys involving both the tubules and glomeruli, characteristically resulting in anemia, polyuria, polydipsia, isosthenuria
[medicinenet.com]
[…] by 30years of age large kidneys without cysts in infants and children patients with no known risk bilateral renal enlargements and cysts in absence of indication for different
[en.wikibooks.org]
Posteriorly inclined and low-positioned ears Retrognathia Prominent and pointed nose Large anterior fontanelle Clindodactyly of 5th finger, bilateral Narrow thorax Short neck
[malformations.org]
[…] glomerulosclerosis, LAMA5 related LAMA5 FSH releasing protein deficiency INHBA Gilbert syndrome UGT1A1 Gitelman syndrome SLC12A3 Glomerulocystic kidney disease with hyperuricemia and isosthenuria
[centogene.com]
Narrow thorax Short neck Adrenal hypoplasia, fetal HSJ487 Lobulated, fused and horseshoe kidney Omphalocele Ureteral duplication, complete, unilateral Facial dysmorphism
[malformations.org]
Autopsy revealed bilateral large cystic dysplastic kidneys [Figure - 7] and occipital cephalocele [Figure - 8]. Urinary bladder and both ureters were identified.
[ijri.org]
[…] glomerulosclerosis, LAMA5 related LAMA5 FSH releasing protein deficiency INHBA Gilbert syndrome UGT1A1 Gitelman syndrome SLC12A3 Glomerulocystic kidney disease with hyperuricemia and isosthenuria
[centogene.com]
Post-mortem examination of the fetus revealed a large abdomen [Figure - 5], a small head with a boggy swelling over the occipital region, bilateral clubfeet and six digits
[ijri.org]
large kidneys with multifocal round lesions; unilateral enlargement may be the first manifestation of the disease Adult Polycystic Kidney Disease Multiple low attenuation
[learningradiology.com]
[…] glomerulosclerosis, LAMA5 related LAMA5 FSH releasing protein deficiency INHBA Gilbert syndrome UGT1A1 Gitelman syndrome SLC12A3 Glomerulocystic kidney disease with hyperuricemia and isosthenuria
[centogene.com]
[…] by 30years of age large kidneys without cysts in infants and children patients with no known risk bilateral renal enlargements and cysts in absence of indication for different
[en.wikibooks.org]
Ultrasound and CT scan reveal large, bilateral cysts in all regions of the kidney.
[medbullets.com]
Nephronophthisis, Asphyxiating thoracic dysplasia (ATD; Jeune) AR 23 63 UMOD Familial juvenile hyperuricemic nephropathy, Glomerulocystic kidney disease with hyperuricemia and isosthenuria
[blueprintgenetics.com]
[…] disease PKHD1 Polycystic kidney disease SIX5 Branchiootorenal syndrome UMOD Familial juvenile hyperuricemic nephropathy, Glomerulocystic kidney disease with hyperuricemia and isosthenuria
[genda.com.ar]
Knobby, bilaterally enlarged kidneys support a diagnosis of polycystic kidney disease, and a palpable bladder or large prostate suggests obstructive uropathy and is an indication
[meddean.luc.edu]
Common abnormalities in CKD are proteinuria, broad casts and isosthenuria.
[clinicaladvisor.com]
Histology Clear Cell Carcinoma - 75%, lipid/glycogen Chromphilic - Bilateral mulftifocal Chromophobic - Large polygonal Cells Oncocytoma - Rarely metastasize Collecting Tubules
[youtube.com]
These include 1) gross hematuria, 2) papillary necrosis, 3) nephrotic syndrome, 4) renal infarction, 5) isosthenuria, and 6) pyelonephritis.
[pediatrics.aappublications.org]
STAGING OF Renal Cell Carcinoma Stage 1 - Within the kidney and less than 7cm.
[youtube.com]
Vascular disease includes large vessel disease such as bilateral renal artery stenosis and small vessel disease such as ischemic nephropathy, hemolytic-uremic syndrome, and
[en.wikipedia.org]
Isosthenuria A physiologic hallmark of ATN is a failure to maximally dilute or concentrate urine (isosthenuria).
[emedicine.com]
Historically, kidney disease has been classified according to the part of the kidney anatomy involved.
[en.wikipedia.org]
It can be bilateral, unilateral or relate to a portion of the kidney.
[clinicalcasereportsint.com]
Hypomagnesemia-Hypokalemia, Primary Renotubular, With Hypocalciuria Potassium And Magnesium Depletion GS 263800 Genetic Test Registry Glomerulocystic Kidney Disease With Hyperuricemia And Isosthenuria
[ukgtn.nhs.uk]
[…] fetal adrenals for the absent kidneys.
[sonoworld.com]
Perisylvian + Muscular Dystrophy, Congenital, with Severe Central Nervous System Atrophy and Absence of Large Myelinated Fibers Stroke, Ischemic + + 601446 Right Pelvic Kidney
[studyres.com]
[…] dystrophy, crystalline, of Schnyder) UBR1 (Johanson-Blizzard syndrome) UGT1A1 (Crigler Najjar syndrome type I) UMOD (Glomerulocystic kidney disease with hyperuricemia and isosthenuria
[en.praenatal-medizin.de]
Syndrome + 278250 Wrinkly Skin Syndrome + + 300000 Xeroderma Pigmentosum, Complementation Group A Opitz Syndrome 300068 Androgen Insensitivity Syndrome 300388 Polymicrogyria, Bilateral
[studyres.com]