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587 Possible Causes for Langerhans Cell Histiocytosis, Tuberous Sclerosis

  • Interstitial Lung Disease

    A 10-year-old boy with prolonged cough, and computed tomography of thorax with features suggestive of primary Langerhans's cell histiocytosis.[] sclerosis, LAM, glycogen storage disease (Gaucher’s), secondary pulmonary hypertension, and advanced stage sarcoidosis and others.[] cell histiocytosis.[]

  • Lymphangioleiomyomatosis

    Lymphangioleiomyomatosis (LAM) and pulmonary Langerhans cell histiocytosis (PLCH) are rare diseases that lead to progressive cystic destruction of the lungs.[] […] can develop in women without the tuberous sclerosis complex, owing to somatic mutations in tuberous sclerosis genes. 4 The cells comprising the lymphangioleiomyomatosis lesions[] Cystic fibrosis and Langerhans cell histiocytosis (eosinophilic granuloma) share this feature.[]

  • Cystic Lung Disease

    MATERIALS AND METHODS: The authors evaluated the size of cystic lesions, as seen on paired inspiratory and expiratory HRCT scans, in 54 patients with Langerhans cell histiocytosis[] RESULTS: Cystic lung disease (defined as 4 cysts) was seen in 11 of 29 men (38%) with tuberous sclerosis complex.[] cell histiocytosis.[]

  • Honeycomb Lung

    Langerhan cell histiocytosis 7. Interstitial lung diseases 8. Idiopathic interstitial fibrosis ( Fibrosing necrotizing alveolitis ) 9. Neurofibromatosis 10.[] Causes include: commonly, end-stage pulmonary fibrosis of any cause neurofibromatosis tuberous sclerosis Hand-Schuller-Christian disease eosinophilic granuloma There is a[] This combination of findings is typical for Langerhans cell histiocytosis.[]

  • Birt-Hogg-Dubé Syndrome

    cell histiocytosis and lymphangioleiomyomatosis (see below).[] Tuberous sclerosis complex 2 gene; Mechanistic target of rapamycin complex 1 Subscription required Not yet a registered user?[] cell histiocytosis, lymphangioleiomyomatosis, which can occur as an isolated finding or as part of tuberous sclerosis complex. 2 In case of respiratory manifestations, it[]

  • Secondary Pulmonary Interstitial Fibrosis

    cell histiocytosis (EG) – Langerhans cell histiocytosis (EG) – Respiratory bronchiolitis-ILD – Respiratory bronchiolitis-ILD Subacute hypersensitivity pneumonitis Subacute[] sclerosis, LAM, glycogen storage disease (Gaucher’s), secondary pulmonary hypertension, and advanced stage sarcoidosis and others.[] […] and or granulomas Predominantly bronchiolocentric distribution Features of other defined diseases such as: Langerhans cell histiocytosis Sarcoidosis Marked inflammation Marked[]

  • Lung Biopsy showing Centrilobular Emphysema

    Introduction Pulmonary Langerhans cell histiocytosis (PLCH) is an isolated form of Langerhans cell histiocytosis characterised by granulomatous infiltration of the distal[] Sclerosis LAM/Tuberous Sclerosis  Round cysts with thin walls  Round cysts with thin walls  Diffuse with basilar predominance  Diffuse with basilar predominance  Normal[] Keywords Pulmonary langerhans cell histiocytosis; Pulmonary hypertension; Langerhans cell histiocytosis; Obstructive and restrictive lung disease; Rare cause of dyspnea; Reticulonodular[]

  • Pulmonary Lymphangioleiomyomatosis

    Pulmonary Langerhans cell histiocytosis What is PLCH?[] […] with tuberous sclerosis.[] Imaging evaluation plays an important role in the assessment of patients with tuberous sclerosis complex.[]

  • Chronic Interstitial Lung Disease

    Irregular, thick- and thin-walled cysts and nodules in a patient with pulmonary Langerhans cell histiocytosis.[] . • Genetic markers for inherited interstitial lung diseases such as dyskeratosis congenita, tuberous sclerosis/LAM, and hyper-IgE syndrome.[] Examples include Hermansky-Pudlak syndrome and Tuberous Sclerosis Complex. The fourth category is called “idiopathic,” meaning the cause is unknown.[]

  • Diffuse Pulmonary Lymphangiomatosis

    cell histiocytosis on PETCT 204 Case 79 Talc pleurodesis on PETCT 206 Case 80 Esophagitis on PETCT 208 Case 81 Takayasus arteritis on PETCT 212 Case 82 Window and level settings[] Messer, R. : Lymphangiomyoma and tuberous sclerosis. Cancer, 19: 1118 – 1192 , 1972 . Google Scholar 28. Jelihovsky, T. Nicks, R.[] Key Facts Rare non-langerhans cell histiocytosis Pleural and perirenal soft tissue thickening Diffuse septal thickening Imaging Findings Chest radiograph Cardiomegaly, Kerley[]

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