Leptomeningeal-angiomatosis: Causes & Reasons

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Possible Causes for leptomeningeal angiomatosis

Sturge-Weber Syndrome

In SWS, especially in association with focal leptomeningeal angiomatosis, FCD may thus play a major role in epileptogenesis. [ncbi.nlm.nih.gov]

Neuroimaging studies show leptomeningeal angiomatosis, supporting diagnosis. [ncbi.nlm.nih.gov]

[…] angiomas Sturge-Weber-Krabbe angiomatosis Sturge-Weber Disease Meningeal capillary angiomatosis Leptomeningeal angiomatosis Encephalofacial angiomatosis Sturge-Weber-Dimitri [wikidata.org]

Infantile Choroidocerebral Calcification Syndrome

Sturge-Weber syndrome is a sporadic condition of mesodermal phakomatosis characterized by a portwine vascular nevus on the upper part of the face, leptomeningeal angiomatosis [synapse.koreamed.org]

Leptomeningeal Angiomatosis with infantile spasms. Ped Neuro 2004; 31(5): 353-6. (accessed 29 Mar 2012). Medlink neurology: clinical summary. Sturge-Weber syndrome. [physio-pedia.com]

angiomatosis, and astrogliosis in the brain. 18 The diagnosis of SWS is based on the presence of at least two of the three manifestations of the classic triad (leptomeningeal [dovepress.com]

Recessive Aplasia Cutis Congenita of Limbs

Pozzati E, Padovanie R, Frank F, Gaist G (1983) Leptomeningeal angiomatosis and aplasia congenita of the scalp: case report.J Neurosurg 58:937–940 Google Scholar 16. [link.springer.com]

angiomatosis, gastroschisis, congenital midline porencephaly, ectopia of ear, omphalocele Depends upon underlying condition 5 ACC with fetus papyraceus or placental infarcts [hindawi.com]

angiomatosis, cranial stenosis, spinal dysraphism, gastroschisis, and omphalocele variable 5 ACC associated with fetus papyraceous (results from the death of a twin fetus [ncbi.nlm.nih.gov]

Aplasia Cutis Congenita

Pozzati E, Padovanie R, Frank F, Gaist G (1983) Leptomeningeal angiomatosis and aplasia congenita of the scalp: case report.J Neurosurg 58:937–940 Google Scholar 16. [link.springer.com]

angiomatosis, cranial stenosis, spinal dysraphism, gastroschisis, and omphalocele variable 5 ACC associated with fetus papyraceous (results from the death of a twin fetus [ncbi.nlm.nih.gov]

[…] neurologic problems: (seizures, mental retardation, corneal opacities, and eyelid colobomas) sporadic 4 ACC with embryologic malformations: meningomyelocele, porencephaly, leptomeningeal [ncbi.nlm.nih.gov]

Non-Syndromic Aplasia Cutis Congenita

Pozzati E, Padovanie R, Frank F, Gaist G (1983) Leptomeningeal angiomatosis and aplasia congenita of the scalp: case report.J Neurosurg 58:937–940 Google Scholar 16. [link.springer.com]

angiomatosis, gastroschisis, congenital midline porencephaly, ectopia of ear, omphalocele Depends upon underlying condition 5 ACC with fetus papyraceus or placental infarcts [hindawi.com]

angiomatosis, cranial stenosis, spinal dysraphism, gastroschisis, and omphalocele variable 5 ACC associated with fetus papyraceous (results from the death of a twin fetus [ncbi.nlm.nih.gov]

Medial Sclerosis

Leptomeningeal enhancement Coronal MR-images of a patient with Sturge-Weber show leptomeningeal enhancement in the right posterior hemispere. Sturge-Weber angiomatosis. [radiologyassistant.nl]

angiomatosis. [radiologyassistant.nl]

The MR-images show leptomeningeal angiomatosis which is mainly localized in the occipital lobes. Venous stasis and calcifications are best seen on the SWI. [radiologyassistant.nl]

Mucocutaneous Venous Malformations

Sturge-Weber syndrome (SWS), also known as encephalotrigeminal angiomatosis, is characterized by leptomeningeal angiomatosis, facial port-wine stain (capillary malformation [unboundmedicine.com]

Neurofibromatosis Type 2

Leptomeningeal angiomatosis has not been described with this tumour predisposition syndrome. [ncbi.nlm.nih.gov]

This report documents an unusual association of leptomeningeal angiomatosis in a case of NF2. [ncbi.nlm.nih.gov]

Acute Exertional Rhabdomyolysis

Case presentation: A Chinese girl presented with extensive port-wine stains, congenital bilateral glaucoma, and leptomeningeal angiomatosis. [zdoc.site]

Our patient presented with extensive port-wine stains, congenital bilateral glaucoma, stroke-like episodes, epilepsy, slight leptomeningeal angiomatosis, and cortical atrophy [zdoc.site]

angiomatosis in right temporal-parietal areas (C); SWI shows vein hyperplasia in the atrophic cerebral sulcus (D). oil red O (ORO) stain (Figure 3A). [zdoc.site]

Choroid Hemangioma

angiomatosis）・てんかん発作・先天性緑内障（脈絡膜血管腫）・精神発達遅滞・片麻痺、半盲（stroke-like episode） Sturge-Weber syndrome Subtypes ・ type 1(“classic”type) : both facial and intracranial manifestations [trc-rad.jp]

The Sturge-Weber syndrome (encephalotrigeminal angiomatosis) is a neurocutaneous syndrome manifesting as facial and leptomeningeal angiomas, and ocular involvement manifesting [ijri.org]

[…] syndrome ・稀（1/50000）・ほとんどは散発性、稀に家族発生の報告・男女差、人種差なし・脳病変の原因は不明だが、脳表の静脈系の発生障害が想定されている・顔面のCapillary malformation （“port wine stain”）・同側軟膜のCapillary-venous malformation　（leptomeningeal [trc-rad.jp]

Temporal Lobe Epilepsy

Leptomeningeal enhancement Coronal MR-images of a patient with Sturge-Weber show leptomeningeal enhancement in the right posterior hemispere. Sturge-Weber angiomatosis. [radiologyassistant.nl]

angiomatosis. [radiologyassistant.nl]

The MR-images show leptomeningeal angiomatosis which is mainly localized in the occipital lobes. Venous stasis and calcifications are best seen on the SWI. [radiologyassistant.nl]

Migrainous Stroke

Other MA potentially associated conditions include leptomeningeal angiomatosis (Sturge Weber syndrome) and hereditary haemorrhagic teleangectasia. [ijponline.biomedcentral.com]

angiomatosis, Sneddon syndrome, Moyamoya syndrome, right-to-left shunts, antiphospholipid antibody syndrome, cardiac myxoma, essential thrombocythemia, and mitochondrial [ahajournals.org]

[…] have been linked with MA. 9 These include cerebral autosomal-dominant arteriopathy with subcortical infarcts and leukoencephalopathy (CADASIL), arteriovenous malformations, leptomeningeal [stroke.ahajournals.org]

Infratentorial Tumor

Angiomatosis Infratentorial Neoplasms Intracranial tumors originating in the region of the brain inferior to the tentorium cerebelli, which contains the cerebellum, fourth [rgd.mcw.edu]

Sarcoma Cerebral Ventricle Neoplasms Cerebroretinal Microangiopathy with Calcifications and Cysts Desmoplastic Cerebral Astrocytoma of Infancy Familial Capillaro-Venous Leptomeningeal [rgd.mcw.edu]

Classic Migraine

angiomatosis (Sturge Weber syndrome) 6.4. [curadeldolore.altervista.org]

(AVM) 6.3.3 Headache attributed to dural arteriovenous fistula (DAVF) 6.3.4 Headache attributed to cavernous angioma 6.3.5 Headache attributed to encephalotrigeminal or leptomeningeal [curadeldolore.altervista.org]

Diffuse Corticomeningeal Angiomatosis of Divry and Van Bogaert

Synonyms: familial type orthochromatic leukodystrophy with diffuse leptomeningeal angiomatosis, sudanophilic leuokodystrophy with meningeal angiomatosis, infantile form of [strokenotes.blogspot.com]

Post-mortem studies gave basically similar results: (1) diffuse capillaro-venous noncalcifying leptomeningeal angiomatosis increasing towards the occipital lobes; (2) focal [karger.com]

angiomatosis distal tapering of the carotid, cerebellar, and meningeal arteries prominent venous pattern Neurologic Behavioral Psychiatric Manifestations: emotional lability [malacards.org]

Retinal Angioma

[1] The disease spectrum includes leptomeningeal hemangioma, facial angiomatosis, and ocular pathological changes. [kjophthal.com]

The Sturge-Weber syndrome (encephalotrigeminal angiomatosis) is a neurocutaneous syndrome manifesting as facial and leptomeningeal angiomas, and ocular involvement manifesting [ijri.org]

angiomatosis, and astrogliosis. [kjophthal.com]

Lytic Bone Lesion

[…] encephalotrigeminal Angiomatosis leptomeningeal capillary - venous Angiomatosis systemic cystic Seip syndrome Angiomyomatous Hamartoma Angioneurotic edema hereditary due [statemaster.com]

Angiomatosis encephalotrigeminal[?] Angiomatosis leptomeningeal capillary - venous[?] Angiomatosis systemic cystic Seip syndrome[?] Angiomyomatous Hamartoma[?] [encyclopedia.kids.net.au]

Angiofollicular lymph hyperplasia Angioimmunoblastic with dysproteinemia lymphadenopathy Angiokeratoma mental retardation coarse face Angiolipoma Angioma hereditary neurocutaneous Angiomatosis [statemaster.com]

Phakomatosis Pigmentokeratotica

Dimitri Disease Encephalofacial Angiomatosis Encephalotrigeminal Angiomatosis Leptomeningeal Angiomatosis Meningeal Capillary Angiomatosis Sturge-Kalischer-Weber Syndrome [diki.pl]

[1] The disease spectrum includes leptomeningeal hemangioma, facial angiomatosis, and ocular pathological changes. [kjophthal.com]

[…] of the face, ipsilateral leptomeningeal angiomatosis, and ocular involvement [ 1, 2 ]. [karger.com]

Trigonocephaly

The cardinal features of Sturge-Weber syndrome are facial cutaneous capillary malformation (port-wine stain), leptomeningeal angiomatosis, and glaucoma. [ncbi.nlm.nih.gov]

Benign Adult Familial Myoclonic Epilepsy

enchephalotrigeminal angiomatosis, fourth phacomatosis, leptomeningeal angiomatosis, meningeal capillary angiomatosis, Sturge-Kalischer-Weber syndrome, SWS, SWS type 1-facial [orphananesthesia.eu]

[…] and leptomeningeal angiomas, SWS type 2 - facial angioma alone - no CNS involvement, SWS type 3 - isolated leptomeningeal angiomas TAR Syndrom ( 1 Files ) Erkrankung: Thrombocytopenia [orphananesthesia.eu]

Tako-Tsubo-Kardiomyopathie, Tako-Tsubo-Syndrom Sturge-Weber Syndrom ( 1 Files ) Erkrankung: Sturge-Weber Syndrom ICD 10: Q85.8 Synonyme: Dmitri disease, encephalofacial angiomatosis [orphananesthesia.eu]

Distal Spinal Muscular Atrophy Type 3

High-Output Heart Failure

Angiomatosis affecting the facial skin, eyes, and leptomeninges produces the characteristic features of the Sturge-Weber syndrome, which is characterized by capillary nevus [hawaii.edu]

Trigeminal Autonomic Cephalalgia

angiomatosis (Sturge Weber syndrome) 6.4. [curadeldolore.altervista.org]

Focal-Onset Impaired-Awareness Seizure

Leptomeningeal enhancement Coronal MR-images of a patient with Sturge-Weber show leptomeningeal enhancement in the right posterior hemispere. Sturge-Weber angiomatosis. [radiologyassistant.nl]

angiomatosis. [radiologyassistant.nl]

The MR-images show leptomeningeal angiomatosis which is mainly localized in the occipital lobes. Venous stasis and calcifications are best seen on the SWI. [radiologyassistant.nl]

Upper Limb Hypertrophy

A diagnosis of Overlap between SWS and KTS was made on the basis (according to association) of port-wine vascular nevus, hypertrophy of bone, leptomeningeal angiomatosis that [latunisiemedicale.com]

Distal Myopathy Type 3

[…] and leptomeningeal angiomas, SWS type 2 - facial angioma alone - no CNS involvement, SWS type 3 - isolated leptomeningeal angiomas TAR-syndrome ( 1 Files ) Disease name: [orphananesthesia.eu]

Hydronephrosis

angiomatosis. [ncbi.nlm.nih.gov]

CNS features in ECCL include intracranial and intraspinal lipomas, seen in 61% of patients, and less often cerebral asymmetry, arachnoid cysts, enlarged ventricles, and leptomeningeal [ncbi.nlm.nih.gov]

Klippel-Trenaunay-Weber Syndrome

He showed nevus flameus on the right leg and both part of the face and back, leptomeningeal angiomatosis on right hemisphere, hypertrophy of the right leg, hemiconvulsion [ncbi.nlm.nih.gov]

Lafora Disease

subcortical calcification of vessel walls, gliosis without leptomeningeal involvement, and large jagged microcalcifications. [academic.oup.com]

Pathological specimens of resected tissue demonstrate cortical vascular abnormality with patchy pial angiomatosis, venous haemangiomas in deep cortical layers, fibrosed veins [academic.oup.com]

Pleomorphic Xanthoastrocytoma

Leptomeningeal enhancement Coronal MR-images of a patient with Sturge-Weber show leptomeningeal enhancement in the right posterior hemispere. Sturge-Weber angiomatosis. [radiologyassistant.nl]

angiomatosis. [radiologyassistant.nl]

The MR-images show leptomeningeal angiomatosis which is mainly localized in the occipital lobes. Venous stasis and calcifications are best seen on the SWI. [radiologyassistant.nl]