Treatment of longQTsyndrome was initiated with oral propanolol. … Schroeder,T.G. di Sessa Coincidence of longQTsyndrome and propionic acidemia 2 E. … An Pediatr 2015;83:281-2 - Vol. 83 Num.4 DOI: 10.1016/j.anpede.2015.09.001 Scientific Letter Propionic acidemia and longQTsyndrome: A potentially serious combination Acidemia
If symptoms appear in childhood, genetic testing to confirm mutations characteristic for Brugada or longQTsyndromes is necessary. … QTsyndrome and Brugada syndrome, respectively. … Long QT and Brugada syndromes - Two ventricular arrhythmias induced by genetic events present usually in early life (mean onset of symptoms in longQTsyndrome is 12 years
A significant risk factor for this condition, however, is seen in patients with longQTsyndrome, renal disease, myasthenia gravis, optic neuritis and G6PD, suggesting that … To reduce the risk of cinchonism, quinine should never be administered to patients suffering from renal disease, cardiac abnormalities such as longQTsyndrome, myasthenia … To reduce the risk of cinchonism, quinine should be avoided in patients suffering from cardiac (most importantly longQTsyndrome) or renal disease, myasthenia gravis, optic
Genetic testing for Brugada and longQTsyndromes and catecholaminergic polymorphic VT is also useful. … When VT occurs in a patient with longQTsyndrome, this entity is called "torsade de pointes" and has a particular morphology.
LongQTsyndrome can result in VF, particularly in patients with a family history of sudden cardiac death (SCD; risk is also increased in acquired longQTsyndrome caused … PMID: 8339437  Scoring: 1 point low probability of longQTsyndrome 1 to 3 points intermediate probability of longQTsyndrome 3.5 points high probability of longQTsyndrome … Diagnostic criteria for the longQTsyndrome.
QTsyndrome Congenital coronary artery abnormalities Inherited longQTsyndromeLongQTsyndrome is characterized by QT interval prolongation, T-wave abnormalities and polymorphic … Together, those 5 genes are responsible for virtually 100% of cases of inherited longQTsyndrome. … In both acquired and congenital longQTsyndromes , prolonged repolarization predisposes to torsades de pointes , a reentrant rhythm with a constantly varying circuit. 
The most common channelopathy in Ireland is LongQTsyndrome (LQTS). … The term longQTsyndrome describes a particular pattern of the electrical activation in the heart. … Catecholaminergic polymorphic ventricular tachycardia (CPVT) is similar in many ways to longQTsyndrome.