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[wikiwand.com]
A muscle MRI demonstrated atrophy and fatty replacement most severely affecting the tensor fasciae latae, semitendinosus, sartorius, gracilis, gastrocnemius, soleus and peroneus
[frontiersin.org]
Later in the course of the disease proximal muscles are affected with mild to moderate fatty degeneration and atrophy of gluteus maximus, hamstring, vastus medialis and lateralis
[ncbi.nlm.nih.gov]
atrophy and fatty replacement of the tensor fasciae latae (A—red), semitendinosus (B—blue), sartorius (B—yellow), gracilis (B—green), gastrocnemius (C—orange), soleus (C—purple
[frontiersin.org]
Histologically, there is often dense fibrous tissue, fatty replacement, muscular atrophy, dysplastic veins and lymphoplasmacytic aggregates in the skeletal muscle.
[radiopaedia.org]
(Fig. 2-4) Furthermore, severe ipsilateral atrophy of the sternocleidomastoid and trapezius muscles and fatty replacement of the left hemi tongue was seen (Fig. 3 and 5-7)
[eurorad.org]
Neurologic examination revealed no limb weakness. magnetic resonance imaging studies showed atrophy and findings, suggesting fatty replacement of paraspinal muscles.
[mayoclinic.pure.elsevier.com]
MRI Diffuse isolated atrophy and fatty replacement of the paraspinal muscles, with high T1 and T2 signal which suppresses on fat-saturated sequences History and etymology
[radiopaedia.org]
Recent research suggests that - at least in Parkinson disease - the problem originates centrally in the brain, and not at the level of the muscles themselves.
[radiopaedia.org]
[…] of muscle Fatty replacement of skeletal muscle Increased variability in muscle fiber diameter Infantile muscular hypotonia ... ...
[familydiagnosis.com]
Muscle biopsy showed dystrophic changes, substantial fatty replacement, and fiber size variation.
[link.springer.com]
replacement of skeletal muscle ; Increased variability in muscle fiber diameter ; Infantile muscular hypotonia ; Infantile onset ; Intellectual disability ; Motor delay ;
[mousephenotype.org]
In myopathic sarcoid myopathy, there are nonspecific findings of symmetric proximal muscle atrophy with fatty replacement and increased signal intensity of involved muscle
[en.wikibooks.org]
MRI may be helpful in delineating the extent of fatty replacement and indicating an optimal location for muscle biopsy.
[en.wikibooks.org]
Corticosteroid therapy may be a confounding factor in evaluating potential sarcoid muscle atrophy with the differentation based on clinical findings.
[en.wikibooks.org]
Although endomysial fibrosis, which reflects muscle fiber loss and replacement by connective tissue, is a better indicator of muscle function loss than fatty tissue infiltration
[practicalneurology.com]
The T1-weighted images can be used to assess muscle anatomy; detect fatty infiltration, which reflects remote damage and muscle loss; and crudely assess muscle volume for
[practicalneurology.com]
atrophy or hypertrophy.
[practicalneurology.com]
Muscle atrophy and fatty replacement is seen in chronic cases and can be graded using the Goutallier classification, or assessed with the tangent sign or scapular ratio 6,9
[radiopaedia.org]
Rotator Cuff Tears and Muscle Atrophy This phenomenon can occur and involves the rotator cuff muscles shrinking and being replaced by fat.
[regenexx.com]
While there was a slight trend in that direction, no patient had serious fatty atrophy at follow-up.
[regenexx.com]
fatty replacement, increased endomysial fibrosis, marked variability of fiber size, fiber splitting, and many fibers with multiple internal nuclei.
[orpha.net]
Pathological changes are particularly severe in the gastrocnemius muscle. Atrophy of both type 1 and type 2 fibers can be observed with ATPase staining.
[orpha.net]
Diagnostic methods Diagnosis is based on clinical manifestations, family history and biopsy findings which reveal severe muscle fiber-type grouping and atrophy, extensive
[orpha.net]
The skeletal muscles and the tongue showed neurogenic muscular atrophy with fatty replacement.
[ncbi.nlm.nih.gov]
[…] brightening) as well as atrophy and early fatty replacement indicating that the denervation has been present for some time (i.e. weeks to months). 6 public playlists includes
[radiopaedia.org]
There is also prominent fatty replacement and atrophy in the lateral head of the gastrocnemius muscle ( asterisk ).
[link.springer.com]
Note typical denervation changes to muscle supplied by both the superficial and deep branches of the nerve (i.e. anterior compartment of the leg) characterized by edema (T2
[radiopaedia.org]
An axial T2-weighted image demonstrates bilateral ischiofemoral narrowing and quadratus femoris muscle atrophy with fatty replacement (arrows), greater on the left.
[radsource.us]
The cause of fatty replacement is uncertain, however, muscle atrophy, with replacement by intra-muscular fat, is the end-stage of many of the disease processes that produce
[radsource.us]
QFM atrophy with fatty replacement is best evaluated with axial T1-weighted images. 6 Figure 6: Normal anatomy on an axial proton density image.
[radsource.us]
A muscle biopsy would demonstrate variation in muscle fiber size, atrophic fibers, fatty replacement, and rimmed vacuole formation on light microscopy.
[ncbi.nlm.nih.gov]
Brain MRI would demonstrate cerebellar atrophy, usually more pronounced in the vermis than the hemispheres.
[ncbi.nlm.nih.gov]
Creatine kinase was marginally raised and an MRI of his legs showed a distinctive pattern of fatty replacement of muscle.
[eprints.soton.ac.uk]
It also helps avoiding end-stage muscles with extensive fibrosis or fatty replacement that will likely have a low diagnostic yield.
[sites.google.com]
Muscle biopsy revealed non-selective fibre atrophy and numerous eosinophilic inclusions surrounded by asophilic granules.
[eprints.soton.ac.uk]
atrophy Waddling gait Infantile muscular hypotonia Fatty replacement of skeletal muscle Seizures Global developmental delay Pachygyria Congenital onset Mitral valve prolapse
[mendelian.co]
Scoliosis Rare Symptoms - Less than 30% cases Pica Cerebellar hypoplasia Cerebellar cyst High palate Kyphoscoliosis Myopathy Delayed gross motor development Strabismus Skeletal muscle
[mendelian.co]
[…] edema, extensive necrosis, atrophy, fatty replacement, fascial edema, minimal or absent inflammation T1 hyperintensity especially in posterior thigh; STIR signal is increased
[journals.seedmedicalpublishers.com]
[…] edema, atrophy, and fatty replacement compared with those with polymyositis (PM) and dermatomyositis (DM), unlike the fascial edema is more common and widespread in dermatomyositis
[journals.seedmedicalpublishers.com]
50,000) and persistent despite statins discontinuation EMG Myogenic pattern (usually with spontaneous activity in the form of fibrillations and positive sharp waves) MRI Muscle
[journals.seedmedicalpublishers.com]
Nonresponding cases may show further worsening of T2 SI within the nerves and innervated muscles, along with fatty replacement and atrophy of the muscles on sequential MR
[ajnr.org]
Results of muscle computed tomography revealed proximal dominant muscle atrophy with fatty tissue replacement.
[mafiadoc.com]
A muscle biopsy specimen was obtained from the left rectus femoris and showed marked fiber size variation, scattered regenerating fibers, and fibers with centrally placed
[mafiadoc.com]
In a chronic setting, the muscle will be atrophied with fatty replacement. On the left T1- and T2-weighted images of the thigh muscles.
[radiologyassistant.nl]
This is the chronic phase where there is volume loss and fatty replacement of the muscle.
[radiologyassistant.nl]
There is atrophy of the thigh musculature and gluteal muscles due to disuse.
[radiologyassistant.nl]
Persistent weakness was exacerbated with age, and MR analysis showed marked atrophy of temporal, masseter, and finger flexor muscles with fatty replacement.
[content.iospress.com]
Persistent weakness was exacerbated with age, and MR analysis showed marked atrophy of temporal, masseter, and finger flexor muscles with fatty replacement... 2020: Journal
[read.qxmd.com]
Case report:We report a family with a history of PC accompanied by persistent hand muscle weakness with masticatory muscle involvement.
[content.iospress.com]
RESULTS: In FSHD patients, we detected a specific pattern of muscle fatty replacement and atrophy, particularly in upper girdle muscles.
[ncbi.nlm.nih.gov]
Whole-body muscle MRI revealed severe changes in the lower leg muscles, tibialis anterior and gastrocnemius muscles were highly replaced by fatty tissue.
[ncbi.nlm.nih.gov]
Additionally, fatty degeneration of shoulder girdle and straight back muscles, and atrophy of dorsal upper leg muscles were seen.
[ncbi.nlm.nih.gov]
[…] weakness Rare Symptoms - Less than 30% cases Muscle fiber atrophy Achilles tendon contracture Calf muscle pseudohypertrophy Distal amyotrophy Dilated cardiomyopathy Increased
[mendelian.co]
[…] variability in muscle fiber diameter Falls Frequent falls Fatty replacement of skeletal muscle Increased endomysial connective tissue Hyporeflexia Milia Progressive Waddling
[mendelian.co]
Flexion contracture Difficulty climbing stairs Mildly elevated creatine phosphokinase Muscle fiber splitting Myalgia Autophagic vacuoles Myoglobinuria Pica Pelvic girdle muscle
[mendelian.co]
Histopathological examination showed the following: (1) The muscle fibers were sparse, degenerated, and atrophied and were replaced by fatty-fibers (Figures 3C–F). (2) The
[frontiersin.org]
Lots of nemaline rods in muscle fibers were strongly stained with anti-α-actinin antibody (thin black arrow).
[frontiersin.org]
Later in adult life, there is persistent and progressive muscle weakness and atrophy with fatty replacement.
[mendelian.co]
It also helps avoiding end-stage muscles with extensive fibrosis or fatty replacement that will likely have a low diagnostic yield.
[sites.google.com]
Patients may report muscle weakness, myalgia, and lack of endurance since childhood or adolescence.
[mendelian.co]
Muscle fiber atrophy Proximal muscle weakness in upper limbs Fatty replacement of skeletal muscle Increased endomysial connective tissue Upper limb amyotrophy Hamstring contractures
[mendelian.co]
Wrist flexion contracture Exercise-induced myalgia Pelvic girdle muscle weakness Proximal muscle weakness in lower limbs Lower limb amyotrophy Abnormality of muscle fibers
[mendelian.co]
Flexion contracture of finger Internally nucleated skeletal muscle fibers EMG: myotonic runs Shoulder girdle muscle weakness Pelvic girdle muscle atrophy EMG: axonal abnormality
[mendelian.co]
Atrophy was defined by the presence of any amount of fatty replacement of muscle mass on T1-weighted images (Figs. 1 and 2 ).
[link.springer.com]
Fig. 1 Coronal T1-weighted image demonstrating normal abductor digiti minimi ( ADM ) muscle Fig. 2 Coronal T1-weighted image demonstrating fatty replacement of the abductor
[link.springer.com]
[…] digiti minimi muscle ( ADM ), indicating atrophy Statistical analysis Age and gender distribution, as well as the frequency of plantar fasciitis, calcaneal spur formation
[link.springer.com]
The degree of muscle fatty replacement and atrophy may also be helpful in guiding the surgical management in terms of nerve repair or tendon-transfer procedures. 1, 2, 4,
[ajnr.org]
B, Axial T2-weighted MR image at the level of right mid forearm shows marked atrophy with fatty replacement (arrows) of the muscles.
[omicsonline.org]
These may range from edema-like T2 signal abnormalities in the initial stages of denervation to fatty replacement and atrophy in subacute and chronic stages.
[ajnr.org]
ANSWER Image Gallery: (Summary of Microscopic Findings) The low power view (left) shows fatty replacement of muscle fibers and hypertrophy and atrophy of fibers.
[web.duke.edu]
A muscle biopsy is performed. 544-1. What is the differential diagnosis?
[web.duke.edu]
The imaging in the initial assessment of individual A showed symmetrical atrophy and fatty replacement of the semitendinosus in the proximal lower extremities (left) and the
[nature.com]
Figure 2 Family clinical data. ( A ) Muscle computed tomography of affected lower extremity.
[nature.com]
[…] tibialis anterior, tibialis posterior, extensor hallucis and digitorum longus, and peroneal muscle in the distal (right) lower extremities. ( B ) Pathology of muscle biopsy
[nature.com]