Nevus Flammeus: Causes & Reasons

Possible Causes for Nevus Flammeus

Occasionally diffuse choroidal hemangioma can occur in both eyes, particularly when the nevus flammeus involves both sides of the face. [sturge-weber.org]

The diffuse choroidal hemangioma, usually part of the Sturge-Weber syndrome, is generally identified ipsilaterally to a facial nevus flammeus. [medtextfree.wordpress.com]

External examination was positive for a left facial nevus flammeus. Indirect ophthalmoscopy of the OD fundus was unremarkable. [eandv.biomedcentral.com]

Cutis Marmorata Telangiectatica Congenita

We discuss an entirely unique case of Phacomatosis pigmentovascularis with nevus of Ota, extensive Mongolian spot, nevus flammeus, nevus anemicus and cutis marmorata telangiectatica [ncbi.nlm.nih.gov]

flammeus, hemangioma, nevus anemicus, café-au-lait spots, melanocytic nevus, aplasia cutis and acral cyanosis.[6] It has a marbled bluish to deep-purple appearance. [wikidoc.org]

Two cases of cutis marmorata telangiectatica congenita are described in association with nevus flammeus and congenital glaucoma. [ncbi.nlm.nih.gov]

Proliferating Angioendotheliomatosis

flammeus and an epidermal nevus Type II: nevus flammeus with aberrant mongolian spots Type III: nevus flammeus with nevus spilus Type IV: nevus flammeus, ectopic mongolian [slideplayer.com]

flammeus and nevus pigmentosus et verrucosus Nevus flammeus, mongolian spots, ± nevus anemicus Nevus flammeus, nevus spilus, ± nevus anemicus Nevus flammeus, mongolian spots [vdoc.pub]

[…] anemicus Nevus flammeus (Capillary malformation, Port-wine stain) Nevus flammeus nuchae (Stork bite) Nevus lipomatosus superficialis (Nevus lipomatosis of Hoffman and Zurhelle [doctors-hospitals-medical-cape-town-south-africa.blaauwberg.net]

Infantile Choroidocerebral Calcification Syndrome

All types of phakomatosis pigmentovascularis have nevus flammeus as a component. [synapse.koreamed.org]

flammeus Glaucoma Focal white matter lesions Spastic diplegia Arrhythmia Edema Folate deficiency Intellectual disability, moderate Hyperphenylalaninemia Excessive salivation [mendelian.co]

[…] stature Doll-like facies Nonprogressive encephalopathy Abnormal CNS myelination Generalized seizures Focal white matter lesions Lower limb asymmetry Abnormal myelination Nevus [mendelian.co]

Congenital Non-Neoplastic Nevus

NEVUS FLAMMEUS nevus flammeus A large reddish-purple nevus of the face or neck, usually not elevated above the skin. [medical-dictionary.thefreedictionary.com]

[…] stain (also known as nevus flammeus) Hemangiomas (raised lesions) Superficial hemangioma (also known as capillary nevus hemangioma) Deep hemangioma (also known as cavernous [aafp.org]

[nevus flammeus, port-wine stain] The above policy is based on the following references: American Academy of Dermatology (AAD). [aetna.com]

Klippel-Trenaunay-Weber Syndrome

A case of Klippel-Trenaunay-Weber Syndrome (KTWS) in a 2.5-year-old girl with congenital hemihypertrophy, nevus flammeus and liver hemangioma is presented. [ncbi.nlm.nih.gov]

At this stage, the condition appears almost like a nevus flammeus. Over time, more massive vascularization and enlargement of the limb will develop. [medicinenet.com]

Angiokeratoma Circumscriptum

In some cases, the lesions initially present as multiple reddish macules, clinically resembling nevus flammeus. [escholarship.org]

flammeus. [journals.lww.com]

flammeus, cavernous hemangioma Idiopathic solitary or multiple angiokeratomas Essential features Benign vascular lesion Characterized by superficial vascular ectasia and [pathologyoutlines.com]

Upper Limb Hypertrophy

Figure 1 : Bilateral facial nevus flammeus. The right upper limb shows a soft tissue hypertrophy and nevus flammeus. [latunisiemedicale.com]

It is typically of the nevus flammeus type, but cavernous hemangiomas or lymphangiomas may also occur. [reference.medscape.com]

OCT 2002; 28 (10) : 913-920 Hofer-T Meyerson phenomenon within a nevus flammeus - The different eczematous reactions within port-wine stains DERMATOLOGY-. 2002; 205 (2) : [malattierare.regione.veneto.it]

Phakomatosis Pigmentokeratotica

In 1966, Toda described coexisting nevus flammeus and nevus spilus as type III. [bioline.org.br]

Classification of phakomatosis pigmentovascularis Type Vascular feature I Nevus flammeus II III IV Nevus flammeus±anemic nevus Nevus flammeus±anemic nevus Nevus flammeus±anemic [docksci.com]

Evidence of twin spotting with pigmentary nevus (nevus of Ota) along with adjoining vascular nevus (nevus flammeus, port-wine stain). Figure 4. [mdedge.com]

Sturge-Weber Syndrome

All types of phakomatosis pigmentovascularis have nevus flammeus as a component. [synapse.koreamed.org]

In 37% (all CONCLUSION: Bone marrow signal abnormality and enhancement is common ipsilateral to the nevus flammeus in SWS. [ncbi.nlm.nih.gov]

Sturge-Weber syndrome is a nonhereditary congenital neurocutaneous syndrome characterized by leptomeningeal angiomatosis, facial nevus flammeus, and diffuse choroidal hemangioma [ncbi.nlm.nih.gov]

Congenital Phlebectasia

Three patients (cases 9, 10, and 19) had an associated nevus flammeus. [kundoc.com]

Common anomalies include varicosities, nevus flammeus, ulceration, macrocephaly, and hypoplasia and hypertrophy of soft tissue and bone. [dermatologyoasis.net]

Cutaneous lesions described in patients with CMTC include nevus flammeus, hemangioma, nevus anemicus, café-au-lait spots, melanocytic nevus, aplasia cutis and acral cyanosis [en.wikipedia.org]

Cutis Marmorata

flammeus, hemangioma, nevus anemicus, café-au-lait spots, melanocytic nevus, aplasia cutis and acral cyanosis.[6] It has a marbled bluish to deep-purple appearance. [wikidoc.org]

nevus flammeus or whether they are an exaggerated confluence of the vascular changes found elsewhere. [healio.com]

On the face, an infantile hemangioma and distribution of nevus flammeus over the frontal bone denoted Sturge-Weber syndrome (B). [mdedge.com]

Cobb Syndrome

A 23-year-old Korean female showed spiral cord angiomas and segmentally distributed nevus flammeus of corresponding dermatomes (Th5-Th2). [ncbi.nlm.nih.gov]

If possible, surgical removal of the angioma, see below nevus flammeus lateralis, cooperation with neurologists and neurosurgeons. Treatment of the flammeus nevus. [altmeyers.org]

A 23-year-old Korean female showed spinal cord angiomas and segmentally distributed nevus flammeus of corresponding dermatomes (Th 5 –Th 11 ). [doi.org]

Non-Involuting Congenital Hemangioma

On the face, an infantile hemangioma and distribution of nevus flammeus over the frontal bone denoted Sturge-Weber syndrome (B). [mdedge.com]

Medial congenital macula (synonyms: Nevus flammeus neonatorum, nevus simplex, “salmon patch” or “fading capillary stain”) Extremely common in Caucasian babies, it clinically [ijpd.in]

Flammeus 248 7.18.3.2.2 Nevus Flammeus Neonatorum (Nevus Teleangiectaticus Medialis) 248 7.18.3.2.2.1 Indication for Therapy 248 7.18.3.2.2.2 Techniques 249 7.18.4 Venous [deutscher-apotheker-verlag.de]

Beckwith-Wiedemann Syndrome

Similar differences were observed for the occurrence of nevus flammeus (48.4%, 50.5%, 22.6%, and 34.5%, respectively, P =0.016) ( Figure 1k ). [nature.com]

Features characteristic of the BWS phenotype include both physical attributes, such as macroglossia, abdominal wall defects, gigantism, nevus flammeus, visceromegaly, and [ncbi.nlm.nih.gov]

These features include macrosomia, hemihypertrophy, macroglossia, facial nevus flammeus, earlobe creases and pits, omphalocele, and organomegaly. [ncbi.nlm.nih.gov]

Transient Neonatal Pustular Melanosis

flammeus Nevus flammeus, often referred to as the port-wine stain, is a vascular malformation composed of mature ectatic capillaries. [ijdvl.com]

flammeus, macrocephaly, ulceration, hypoplasia, and or hyptertrophy of soft tissue/bone) [studyblue.com]

FIGURE 41-11 ▪ Nevus flammeus (port-wine stain). [plasticsurgerykey.com]

Congenital Hemihypertrophy

Nevus flammeus Diffuse phlebectasia Sturge-Weber Syndriome Klippel-Trenaunay Snydrome Ataxia teleangiectatica M. [posterng.netkey.at]

Signs and symptoms of Beckwith-Wiedemann syndrome include: Large size for a newborn Red birth mark on forehead or eyelids (nevus flammeus) Creases in ear lobes Large tongue [medlineplus.gov]

Sturge-Weber Syndrome: A neurocutaneous syndrome characterized by the presence of vascular tumors of the face (facial hemangioma capillary (nevus flammeus) usually called [accessanesthesiology.mhmedical.com]

Ring Chromosome 7

We report on a boy with ring chromosome 7 who had severe mental retardation, growth failure, microcephaly, cleft lip and palate, café-au-lait spots, nevus flammeus, and genital [ncbi.nlm.nih.gov]

flammeus, dark pigmented nevi, café-au-lait spots), microcephaly and facial dysmorphism (incl. facial asymmetry, small ears, abnormal palpebral fissures, ptosis, epicanthic [orpha.net]

Upward slanting space between eyelids * Broad nasal root * Cleft lip * Cleft palate * Deep palmar creases * Deep plantar creases * Café au lait spots * Pigmented nevi * Nevus [checkorphan.org]

Zosteriform Lentiginosis

Flammeus (39 %) ( Capillary Malformation, Port-wine Stain,) Dermatofibroma (39 %) ( Benign Fibrous Histiocytoma, Dermal Dendrocytoma, Fibrous Dermatofibroma, Fibrous Histiocytoma [gulfdoctor.net]

When nevus spilus is present withWhen nevus spilus is present with a nevus flammeus =a nevus flammeus = phakomatosisphakomatosis pigmentovascularispigmentovascularis phakomatosisphakomatosis [slideshare.net]

Usually do not cross the midline. 3 Nevus Spilus Syndromes Phakomatosis pigmentovascularis - nevus spilus is present with a nevus flammeus. [powershow.com]

Angioma Serpiginosum

Angiokeratosis Naeviformis—A Form of Nevus Telangiectaticus Lateralis (Naevus Flammeus), Dermatologica 130:17, 1965.Crossref 26. [deepdyve.com]

Familial nevus flammeus associated with early onset cherry angiomas Int J Dermatol. 2008;47:1284–6 16. Namazi MR, Maghsoodi M. [journals.lww.com]

Angiokeratosis Naeviformis—A Form of Nevus Telangiectaticus Lateralis (Naevus Flammeus), Dermatologica 130:17-39, 1965.Crossref 25. [deepdyve.com]

Congenital Macroglossia

Other features of BWS include ear pits or creases, nevus flammeus ( port-wine stain ) on the nasal bridge or neck, abdominal wall hernias or anomalies, and hemi-hypertrohpy [nicklauschildrens.org]

Signs and symptoms of Beckwith-Wiedemann syndrome include: Large size for a newborn Red birth mark on forehead or eyelids (nevus flammeus) Creases in ear lobes Large tongue [medlineplus.gov]

flammeus or other vascular malformations, visceromegaly involving abdominal organs, fetal adrenocortical cytomegaly (pathognomonic), renal abnormalities, positive family [orpha.net]

Congenital Alopecia

Herein we report a case of isolated congenital atrichia with nevus flammeus. [idoj.in]

Congenital atrichia associated with nevus flammeus: A rare association. Indian Dermatol Online J [serial online] 2014 [cited 2019 May 13];5:475-7. [idoj.in]

Alopecia areata universalis sparing nevus flammeus. Dermatology 2005;210:227-8. [Figure 1] [dermsinica.org]

Autosomal-Recessive Robinow Syndrome

flammeus ; Pectus excavatum ; Posteriorly rotated ears ; Proptosis ; Radial deviation of finger ; Renal duplication ; Retrognathia ; Rib fusion ; Right ventricular outlet [mousephenotype.org]

Midface retrusion Decreased size of midface Midface deficiency Underdevelopment of midface [ more ] 0011800 Missing ribs Absent ribs Decreased rib number [ more ] 0000921 Nevus [rarediseases.info.nih.gov]

/ naevus flammeus / port-wine stain - Carpal bones fusion / synostosis - Cleft lip and palate - Death in infancy - Downslanted palpebral fissures / anti-mongoloid slanting [csbg.cnb.csic.es]

Zinc-Responsive Necrolytic Acral Erythema

flammeus 653 200 Postinflammatory hyperpigmentation and other disorders of hyperpigmentation 658 201 Pregnancy dermatoses 662 202 Pretibial myxedema 668 203 Prurigo nodularis [books.google.com]

635 194 Pityriasis rosea 638 195 Polycystic ovary syndrome 640 196 Polymorphic light eruption 643 197 Porokeratoses 646 198 Porphyria cutanea tarda 650 199 Port wine stain nevus [books.google.com]

Autosomal Recessive Congenital Cataract 5

 Characterstic lesions:- * Cutaneous facial nevus flammeus ( in distribution of branches of trigeminal nerve ) * Ipsilateral diffuse cavernous hemangioma choroid * Ipsilateral [fr.slideshare.net]

Flammeus Simplex- Severe Intellectual Disability Syndrome AR 100 5 of 5 MIP Cataract Multiple Types AD 100 29 of 29 MIR184 Edict Syndrome AD na na MIR204 Retinal Dystrophy [igenomix.es]

flammeus/port wine stain * zone of dilated telangiectatic cutaneous capillaries * usually unilateral  CNS Manifestations: * Ipsilateral leptomeningeal hemangiomatosis * [fr.slideshare.net]

Vulvar Hemangioma

Familial nevus flammeus associated with early onset cherry angiomas has been noted. 7 The histology of cherry angiomas is well defined. [clinicaladvisor.com]

[nevus flammeus, port-wine stain] The above policy is based on the following references: American Academy of Dermatology (AAD). [aetna.com]

Familial nevus flammeus associated with early-onset cherry angiomas. Int J Dermatol. 2008;47:1284-1286. 8. Nakashima T, Jinnin M, Etoh T, et al. [clinicaladvisor.com]

Genee-Wiedemann Syndrome

flammeus (11424137) large congenital arteriovenous malformations (AVM) (17162526) Increased tumour risk hemihypertrophy nephromegaly (9544890) aberrant H19 and not KCNQ1OT1 [humpath.com]

In addition, some children with BWS have other findings including nevus flammeus, prominent occiput, midface hypoplasia, hemihypertrophy, genitourinary anomalies (enlarged [jcnonweb.com]

A recognizable facial gestalt is common and may include prominent eyes with infraorbital creases, facial nevus flammeus, midfacial hypoplasia, macroglossia, full lower face [medigoo.com]

Progressive Familial Intrahepatic Cholestasis Type 5

CONDRODISTROFIE CONGENITE CONDRODISTROFIA MIOTONICA RFG090 DISTROFIE MIOTONICHE CONDROGENESI IMPERFETTA RNG050 CONDRODISTROFIE CONGENITE CONGENITAL CATARACT-MICROCEPHALY-NEVUS [malattierare.regione.veneto.it]

FLAMMEUS SIMPLEX-SEVERE INTELLECTUAL DISABILITY SYNDROME RNG100 ALTRE ANOMALIE CONGENITE MULTIPLE CON RITARDO MENTALE CONGIUNTIVITE LIGNEA RF0290 CONGIUNTIVITE LIGNEA CONNESSIONI [malattierare.regione.veneto.it]

Angiokeratoma of Mibelli

flammeus, cavernous hemangioma Idiopathic solitary or multiple angiokeratomas Essential features Benign vascular lesion Characterized by superficial vascular ectasia and [pathologyoutlines.com]

[…] associated with Anderson-Fabry disease (X-linked recessive lysosomal storage disease) Angiokeratoma circumscriptum: least common type, usually congenital, associated with nevus [pathologyoutlines.com]

Bier Spots

flammeus and nevus anemicus.22 Happle R. [scielo.br]

[…] first used by Happle in 1990, to explain the occurrence of vascular twin nevi, i.e., the close spatial proximity between two functionally different vascular birthmarks: nevus [scielo.br]