Normal Hearing: Causes & Reasons

Possible Causes for Normal Hearing

hearing, later called Romano-Ward syndrome. [en.wikipedia.org]

Long QT syndrome Drawing of a normal ECG tracing ( sinus rhythm ) with waves, segments, and intervals labeled. The QT interval is marked by the blue line at bottom. [en.wikipedia.org]

Specialty Cardiology Symptoms Fainting, hearing loss [1] Complications Sudden death [1] Causes Genetic, certain medications, low blood potassium, low blood calcium, heart [en.wikipedia.org]

Patterson Pseudoleprechaunism Syndrome

Symptoms INHERITANCE: Isolated cases GROWTH: [Weight]; Normal birth weight HEAD AND NECK: [Ears]; Disproportionately large ears; Normal hearing; [Nose]; Disproportionately [findzebra.com]

[…] than 30 dB by screening audiometry at 1.0 Hz 1; hearing not determined or evaluated as normal 2; hearing thresholds 20-49 dB in audiometry or less than 50 dB by screening [library.down-syndrome.org]

1985), for instance, reported that children and young adults with Down syndrome and abnormal tympanograms performed less well in intelligence tests compared to those with normal [library.down-syndrome.org]

Cerebellar Ataxia - Neuropathy - Vestibular Areflexia Syndrome

The hearing may be normal. It leads to imbalance and visual problems. Patients with this condition are severely handicapped. [lmhofmeyr.co.za]

Audiogram demonstrated normal hearing for age. Caloric tests confirmed severe bilateral impairment of the lateral semicircular canal function. [docplayer.net]

Usher syndrome type 2 is characterized by congenital, bilateral, sensorineural hearing loss predominantly in the higher frequencies that ranges from mild to severe; normal [refsumdisease.org]

Presbycusis

[…] brainstem specimens from 13 subjects having normal hearing or presbycusis was undertaken. [ncbi.nlm.nih.gov]

RESULTS: A relationship was not observed between age and the spiral ganglion cell population in the normal hearing group. [ncbi.nlm.nih.gov]

Five additional normal hearing individuals, ranging from 9 to 50 years of age, were also studied. [ncbi.nlm.nih.gov]

Congenital Deafness

The results were compared with standard of normal-hearing children with the same hearing age. [ncbi.nlm.nih.gov]

We examined 16 congenitally deaf adolescents, aged between 16 and 19 years, and 16 normally hearing subjects, matched for gender and age. [ncbi.nlm.nih.gov]

Abstract Functional hemispheric specialization in recognizing faces expressing emotions was investigated in 18 normal hearing and 18 congenitally deaf children aged 13-14 [ncbi.nlm.nih.gov]

Acute Sensorineural Hearing Loss by Acute Acoustic Trauma

Normal hearing limits = 0 to 25 dB Mild Loss = 26 to 40 dB Moderate Loss = 41 to 60 dB Severe Loss = 61 to 80 dB Profound Loss = 81 + dB WHAT IS THE CAUSE OF SUDDEN SENSORINEURAL [californiaearinstitute.com]

[…] loss can expect to suffer losses in compensation due to underemployment -Adults with untreated hearing loss have higher unemployment rates than their normal-hearing peers [flukehearing.com]

Although they didn’t mention it in this study, it seems reasonable that if your hearing doesn’t come back to normal or near normal levels, you should get and wear a hearing [hearinglosshelp.com]

Microtia

Because it usually doesn’t affect the inner ear, children with unilateral (one-side) microtia usually have normal hearing in the other ear. [rainbowkids.com]

This is usually sufficient hearing for normal or nearly normal speech and language development to occur. [ear.co.nz]

Children with single sided (unilateral) atresia and microtia usually have normal hearing ear on the other side. [ear.co.nz]

Acoustic Trauma

The present report applied this model to the effects observed after acute acoustic trauma in normal-hearing guinea pigs and in guinea pigs with idiopathic threshold losses [ncbi.nlm.nih.gov]

A study of the audiometric results of 102 ex-army men with AcT and 25 controls with normal hearing included a detailed questionnaire to relate the patients' functional complaints [ncbi.nlm.nih.gov]

PATIENTS: Seventy one active duty soldiers in the same age with normal hearing INTERVENTIONS: Forty one soldiers suffered assault-rifle-induced acute acoustic traumas with [ncbi.nlm.nih.gov]

Sensorineural Hearing Impairment

OBJECTIVE: To assess the static and dynamic balance performance of students with normal hearing and with sensorineural hearing loss. [ncbi.nlm.nih.gov]

The noisiness ratings were, on average, higher for hearing-impaired subjects than for normally hearing subjects. [doi.org]

Most children with genetic sensorineural hearing loss have two parents with normal hearing, as most genes for sensorineural hearing loss are recessive. [luriechildrens.org]

Conductive Hearing Loss

AIM: The goal was to compare temporal resolution of children with normal hearing, with those bearing conductive hearing loss and auditory processing disorders. [ncbi.nlm.nih.gov]

In total, measurements were made on 30 subjects who had a unilateral refer near birth (during their first 2 days of life) and bilateral normal hearing at follow-up (about [ncbi.nlm.nih.gov]

This study aimed to measure sound source localization performance in patients with congenital UCHL and contralateral normal hearing who received a new bone conduction implant [ncbi.nlm.nih.gov]

Autosomal Recessive Deafness 44

They stated that no M34T homozygotes had been reported among individuals with normal hearing. [catalog.coriell.org]

Hearing is considered normal if an individual's thresholds are within 15 dB of normal thresholds. Severity of hearing loss is graded as shown in Table 1. Table 1. [ncbi.nlm.nih.gov]

Auditory brainstem responses elicited by chirp stimuli in adults with normal hearing and sensorineural hearing loss. Ear Hear 35, 271-282. 47. [vumc.org]

Autosomal Dominant Deafness 9

His mother also carried the mutation but had normal hearing. Consequently, the mutation was not considered to be the cause of the proband's hearing loss. [ncbi.nlm.nih.gov]

For PTA, the levels of hearing loss are described as follows: ~20 dB is assigned as normal hearing; 21–40 dB as mild hearing impairment; 41–70 dB as moderate hearing impairment [bmcmedgenet.biomedcentral.com]

Hearing is considered normal if an individual's thresholds are within 15 dB of normal thresholds. Severity of hearing loss is graded as shown in Table 1. Table 1. [ncbi.nlm.nih.gov]

Autosomal Recessive Deafness 24

Hearing is considered normal if an individual's thresholds are within 15 dB of normal thresholds. Severity of hearing loss is graded as shown in Table 1. Table 1. [ncbi.nlm.nih.gov]

Individuals IV:10 (affected) and IV:12 (normal hearing sibling) show an identical chromosome 21 haplotype. [bmcmedgenet.biomedcentral.com]

Methods Clinical and genetic evaluations were conducted in a deaf proband and her normal-hearing parents. [scinapse.io]

Autosomal Recessive Deafness 1B

Read this page to find out how parents with normal hearing can have a child with genetic hearing loss. [raisingdeafkids.org]

They stated that no M34T homozygotes had been reported among individuals with normal hearing. [catalog.coriell.org]

In autosomal recessive hearing loss, both parents who typically have normal hearing, carry a recessive gene. [asha.org]

Autosomal Recessive Deafness 22

[…] and Yemenite) individuals with normal hearing. [cags.org.ae]

Identification of all genes involved in hereditary hearing loss will help in our understanding of the basic mechanisms underlying normal hearing, in early diagnosis and therapy [ingentaconnect.com]

In the presence of normal hearing or sensorineural hearing loss, air conduction is better than bone conduction. [aafp.org]

Thickened Earlobes-Conductive Deafness Syndrome

We define "normal hearing" as thresholds no poorer than 20 dB for .5, 1, 2, and 3 kHz. [audiologyonline.com]

In autosomal recessive hearing loss, both parents who typically have normal hearing, carry a recessive gene. [asha.org]

Your ear specialist can often repair this damage through surgery and your hearing returns to normal or near normal again. Sudden Sensorineural Hearing Loss (SSHL). [hearinglosshelp.com]

Other Acquired Abnormality of Ear Ossicles

Female carriers have normal hearing or only mild hearing loss. Vestibular function is impaired in affected males, however normal in females. [radiopaedia.org]

When everything is working normally, the hearing is normal. [seanpalaciosmd.com]

In the presence of normal hearing or sensorineural hearing loss, air conduction is better than bone conduction. [aafp.org]

Cochlear Disorder

Cochlear implants are still not a replacement for normal hearing, but they are more effective than normal hearing aids for a severe to profoundly deaf individual. [icommunicatetherapy.com]

Characteristics of ANSD patients with normal tonal hearing Figure 6. ASSR and ABR response of an ANSD child with normal hearing Figure 7. [medichub.ro]

An implant does not restore normal hearing. [nidcd.nih.gov]

Usher Syndrome Type 1J

People with type III are born with normal hearing and near-normal balance but develop vision problems and then hearing loss. There is no cure. [medlineplus.gov]

A person with Usher syndrome type 3 is born with normal hearing and close to normal balance, however hearing gradually deteriorates with age. [usherkidsuk.com]

Individuals with the disease will learn to speak normally before their hearing declines. [myriad.com]

Usher Syndrome Type 1

There was also great variation in performance on ToM, however the majority of individuals performed similar to the control group with normal hearing and vision. [diva-portal.org]

People with type III are born with normal hearing and near-normal balance but develop vision problems and then hearing loss. There is no cure. [medlineplus.gov]

Individuals with the disease will learn to speak normally before their hearing declines. [myriad.com]

Usher Syndrome Type 3B

Unlike the other forms of Usher syndrome, type III is usually associated with normal hearing at birth. [ncbi.nlm.nih.gov]

Children with Usher's syndrome type 3 (USH3) have normal hearing and normal or mildly impaired balance. Hearing deteriorates with time. [patient.info]

Speech can develop normally because of the late onset of the hearing deficit. [disorders.eyes.arizona.edu]

Sudden Hearing Loss

Over the next 2 weeks, hearing sensitivity recovered to within normal limits. [ncbi.nlm.nih.gov]

normally hearing ear is reported. [ncbi.nlm.nih.gov]

[…] of the normal hearing ear. [en.wikipedia.org]

Usher Syndrome Type 1D

Her sister (with normal hearing) was also heterozygous for the c.5131G>A (p.Val1711Ile) variant of the CDH23 gene but not the c.2884C>T (p.Arg962Cys) variant of the PCDH15 [pesquisa.bvsalud.org]

People with type III are born with normal hearing and near-normal balance but develop vision problems and then hearing loss. There is no cure. [medlineplus.gov]

A person with Usher syndrome type 3 is born with normal hearing and close to normal balance, however hearing gradually deteriorates with age. [usherkidsuk.com]

Stapedectomy

The control group included 13 volunteers aged 18-50 years with normal hearing and normal otoscopic findings. [ncbi.nlm.nih.gov]

If the hearing nerve (cochlear nerve) is functioning normally, restoration of normal ossiclular movement will result in hearing improvement. What is a stapedectomy? [entillinois.com]

The stapes bone can be replaced with an implant to restore normal hearing with an outpatient surgical procedure called stapedectomy. [nwentsurgerycenter.com]

Autosomal Recessive Deafness 42

In one family, a normal hearing maternal aunt was a carrier for 35delG. In another family, a normal hearing sib was not a carrier. [ejo.eg.net]

IV:3, who is homozygous for the wild-type allele, also has normal hearing. [jmg.bmj.com]

hearing, the ratio of members with deafness to siblings with normal hearing, the sex ratio, and the transmission of deafness by affected males. [nejm.org]

Isolated Congenital Auditory Ossicle Malformation

Four of 17 patients presented normal hearing whereas others presented audiometric anomalies (Table 1). Figure 4. [em-consulte.com]

Patients with unilateral microtia and congential aural atresia usually have normal hearing on the opposite ear. Hearing status on the affected side should be recorded. [drtbalu.co.in]

Pure tone audiometry and speech testing showed total deafness of the right side, but normal hearing thresholds in the left side. [kjronline.org]

Familial Progressive Vestibulocochlear Dysfunction

Children with Usher's syndrome type 3 (USH3) have normal hearing and normal or mildly impaired balance. Hearing deteriorates with time. [patient.info]

Under the age of 35 years, almost all the affected family members had normal hearing, whereas above the age of 55 years, the hearing loss was at least moderate, and vestibular [neus-keel-oor.be]

A person with Usher syndrome type 3 is born with normal hearing and close to normal balance, however hearing gradually deteriorates with age. [usherkidsaustralia.com]

Usher Syndrome

Type III consists of normal hearing at birth with progressive loss in childhood or early teens and night vision problems (retinitis pigmentosa) often begins in the teen years [nationaldb.org]

Intelligence is usually normal, though some educational intervention may be necessary due to issues with hearing and vision loss. Life expectancy is normal. [ushersyndrome.wordpress.com]

Born with normal hearing Hearing problems develop in teenage years Near normal balance Deafness by late adulthood Retinitis pigmentosa begins around puberty Blindness by mid-adulthood [entcolumbia.org]

Autosomal Dominant Deafness 64

Hearing is considered normal if an individual’s thresholds are within 15 dB of normal thresholds. Severity of hearing loss is graded as shown in Table 1. Table 1. [consilieregenetica.org]

The KCNQ4 c.887G > A mutation was also not detected in the normal hearing controls. [link.springer.com]

IV:3, who is homozygous for the wild-type allele, also has normal hearing. [jmg.bmj.com]

Superior Semicircular Canal Dehiscence

We retrospectively compared the prevalence of SSCD in the ears classified as conductive hearing loss (CHL), mixed hearing loss (MHL), and normal hearing status using submillimetric [journals.lww.com]

The threshold for eliciting vestibular-evoked myogenic potentials from affected ears was (mean +/- SD) 81 +/- 9 dB normal hearing level. [ncbi.nlm.nih.gov]

Audiometric examination indicated normal hearing in the right ear; low-frequency hearing loss was detected in the left ear. [ejo.eg.net]