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202 Possible Causes for Onset of Deafness in Early Childhood

  • Perrault Syndrome Type 2

    SNHL is bilateral and ranges from profound with prelingual ( congenital ) onset to moderate with early-childhood onset.[ncbi.nlm.nih.gov] Of note, the variable age of onset and degree of deafness do not depend on the sex of the affected individual.[ncbi.nlm.nih.gov]

  • Deafness - Opticoacoustic Nerve Atrophy - Dementia Syndrome

    Definition An X-linked recessive disorder characterized by postlingual sensorineural deafness with onset in early childhood, dystonia, spasticity, dysphagia, mental deterioration[uniprot.org] Acronym MTS Synonyms DDS DFN-1 Dystonia-deafness syndrome Jensen syndrome Opticoacoustic nerve atrophy with dementia X-linked progressive deafness type 1 Keywords Disclaimer[uniprot.org]

  • Unilateral Deafness with Delayed Endolymphatic Hydrops

    The most common cause of hearing loss preceding DEH is juvenile-onset unilateral profound deafness (early childhood unilateral profound sensorineural hearing loss of unknown[ncbi.nlm.nih.gov] In both types of DEH, the most common diagnosis of precedent deafness was deafness of unknown cause with onset in early childhood: 43.9% in both types of DEH.[dizziness-and-balance.com] The time that elapses between the occurrence of hearing loss and the onset of DEH can range from 1 to 74 years.[ncbi.nlm.nih.gov]

  • Usher Syndrome Type I

    People with Usher type 1 develop profound deafness from birth and in early childhood symptoms of RP become evident.[retina-international.org] People with Usher type 1 develop profound deafness from birth and early childhood symptoms of RP.[fightingblindness.ie] The deafness is generally so early in onset and so severe that hearing aids may not be of value, (although cochlear implants may be beneficial), and patients fail to develop[retina-international.org]

  • Usher Syndrome Type 1J

    People with Usher type 1 develop profound deafness from birth and early childhood symptoms of RP.[fightingblindness.ie] The deafness is generally so early in onset and so severe that hearing aids may not be of value, (although cochlear implants may be beneficial), and patients fail to develop[fightingblindness.ie]

  • Usher Syndrome Type 3B

    People with Usher type 1 develop profound deafness from birth and early childhood symptoms of RP.[fightingblindness.ie] The deafness is generally so early in onset and so severe that hearing aids may not be of value, (although cochlear implants may be beneficial), and patients fail to develop[fightingblindness.ie]

  • Usher Syndrome, Type 3

    People with Usher type 1 develop profound deafness from birth and early childhood symptoms of RP.[fightingblindness.ie] The deafness is generally so early in onset and so severe that hearing aids may not be of value, (although cochlear implants may be beneficial), and patients fail to develop[fightingblindness.ie]

  • Usher Syndrome Type 2

    People with Usher type 1 develop profound deafness from birth and early childhood symptoms of RP.[fightingblindness.ie] The deafness is generally so early in onset and so severe that hearing aids may not be of value, (although cochlear implants may be beneficial), and patients fail to develop[fightingblindness.ie]

  • Usher Syndrome

    People with Usher type 1 develop profound deafness from birth and early childhood symptoms of RP.[fightingblindness.ie] The deafness is generally so early in onset and so severe that hearing aids may not be of value, (although cochlear implants may be beneficial), and patients fail to develop[fightingblindness.ie]

  • Brown-Vialetto-Van Laere Syndrome

    Format Definition An autosomal recessive progressive neurologic disorder characterized by early childhood onset of sensorineural deafness, bulbar dysfunction, and severe diffuse[uniprot.org] Confusing it is possible to have presentations without the deafness, in which case the presentation has the phenotype of childhood bulbar motor neuron disease ( Fazio-Londe[ganfyd.org] childhood-onset nystagmus Early childhood-onset sensory (gait) ataxia Childhood onset sensorineural deafness Weakness and atrophy of the upper limbs (first distally then[ncbi.nlm.nih.gov]

Further symptoms