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59 Possible Causes for Postlingual Progressive Sensorineural Deafness

  • Deafness - Opticoacoustic Nerve Atrophy - Dementia Syndrome

    It is a recessive neurodegenerative syndrome characterized by postlingual progressive sensorineural deafness as the first presenting symptom in early childhood, followed by[abcam.com] Defects in TIMM8A are the cause of Mohr-Tranebjaerg syndrome (MTS); also known as dystonia-deafness syndrome (DDS) or X-linked progressive deafness type 1 (DFN-1).[mybiosource.com] […] syndrome;dds, deafness-dystonia-optic atrophy syndrome;ddp, deafness syndrome, progressive, with blindness, dystonia, fractures, and mental deficiency, opticoacoustic nerve[mendelian.co]

  • Y-Linked Deafness 1

    Symptoms via clinical synopsis from OMIM: 54 Head And Neck- Ears: hearing loss, sensorineural, postlingual progressive, moderate to severe tinnitus (less common) Clinical[malacards.org] Mohr-Tranebjaerg Syndrome (DFN-1) Mohr-Tranebjaerg syndrome (DFN-1) is an X-linked recessive syndromic hearing loss characterized by postlingual sensorineural deafness in[american-hearing.org] sensorineural deafness (De Leenheer et al, 2001).[dizziness-and-balance.com]

  • Deafness

    Mohr-Tranebjaerg Syndrome (DFN-1) Mohr-Tranebjaerg syndrome (DFN-1) is an X-linked recessive syndromic hearing loss characterized by postlingual sensorineural deafness in[american-hearing.org] […] childhood, followed by progressive dystonia, spasticity, dysphagia and optic atrophy.[american-hearing.org] Pointe arrhythmias (turning of the points, in reference to the apparent alternating positive and negative QRS complexes), sudden syncopal episodes, and severe to profound sensorineural[american-hearing.org]

  • Mitochondrial Non-Syndromic Sensorineural Deafness

    Affected individuals manifest progressive, postlingual, sensorineural hearing loss involving high frequencies. {ECO:0000269 PubMed:10577941}.[genecards.org] Mohr-Tranebjaerg Syndrome (DFN-1) Mohr-Tranebjaerg syndrome (DFN-1) is an X-linked recessive syndromic hearing loss characterized by postlingual sensorineural deafness in[american-hearing.org] Deafness, sensorineural, mitochondrial (DFNM) [MIM:500008]: A form of non-syndromic deafness with maternal inheritance.[genecards.org]

  • Nonsyndromic Isolated Dilated Cardiomyopathy

    Mutations in this gene are associated with postlingual, progressive, autosomal dominant hearing loss at the deafness, autosomal dominant non-syndromic sensorineural 10 locus[genecards.org]

  • Congenital Deafness

    Mohr-Tranebjaerg Syndrome (DFN-1) Mohr-Tranebjaerg syndrome (DFN-1) is an X-linked recessive syndromic hearing loss characterized by postlingual sensorineural deafness in[american-hearing.org] sensorineural deafness (De Leenheer et al, 2001).[dizziness-and-balance.com] […] childhood, followed by progressive dystonia, spasticity, dysphagia and optic atrophy.[american-hearing.org]

  • Autosomal Dominant Deafness 11

    postlingual sensorineural deafness maps to chromosome 14q12-13.[karger.com] sensorineural deafness (De Leenheer et al, 2001).[dizziness-and-balance.com] […] from microscopic hematuria to proteinuria, progressive renal insufficiency, ESRD XL Deafness-dystonia-optic neuronopathy syndrome (Mohr-Tranebjaerg syndrome) TIMM8A Sensorineural[ncbi.nlm.nih.gov]

  • X-Linked Deafness 6

    , X-linked, 4 (DFNX4) [MIM:300066]: A non-syndromic form of sensorineural, progressive hearing loss with postlingual onset.[genecards.org] sensorineural deafness (De Leenheer et al, 2001).[dizziness-and-balance.com] […] of SNPs for SMPX No data available for Polymorphic Variants from UniProtKB/Swiss-Prot for SMPX Gene - elite association - COSMIC cancer census association via MalaCards Deafness[genecards.org]

  • X-Linked Deafness 4

    , X-linked, 4 (DFNX4) [MIM:300066]: A non-syndromic form of sensorineural, progressive hearing loss with postlingual onset.[genecards.org] Mohr-Tranebjaerg Syndrome (DFN-1) Mohr-Tranebjaerg syndrome (DFN-1) is an X-linked recessive syndromic hearing loss characterized by postlingual sensorineural deafness in[american-hearing.org] sensorineural deafness (De Leenheer et al, 2001).[dizziness-and-balance.com]

  • Nonsyndromic Renal Hypodysplasia Type 1

    Mohr-Tranebjaerg Syndrome (DFN-1) Mohr-Tranebjaerg syndrome (DFN-1) is an X-linked recessive syndromic hearing loss characterized by postlingual sensorineural deafness in[american-hearing.org] sensorineural deafness (De Leenheer et al, 2001).[dizziness-and-balance.com] […] childhood, followed by progressive dystonia, spasticity, dysphagia and optic atrophy.[american-hearing.org]

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