3,463 Possible Causes for Postlingual Progressive Sensorineural Deafness

  • Muckle Wells Syndrome

    Sensorineural hearing loss in MWS often rapidly progresses from mild high-tone deficits to complete deafness [ 10 , 11 ].[ped-rheum.biomedcentral.com] Progressive, high frequency, sensorineural deafness due at least in part to chronic inflammation of the cochlea begins in childhood (generally after the age of 10 years) resulting[orpha.net] Audiogram – high frequency hearing loss initially, progressing to bilateral sensorineural deafness.[dermnetnz.org]

  • Refsum Disease

    Clinically, it manifests by severe sensorineural deafness, atypical retinitis pigmentosa, mental and growth retardation, facial dysmorphism, hepatomegaly ( 4 ), peripheral[ajnr.org] Other findings that may occur in the following 10 to 15 years in decreasing order of frequency are anosmia, neuropathy, deafness, ataxia, and ichthyosis [Skjeldal & Stokke[refsumdisease.org] […] multisystemic metabolic disease, characterized by anosmia, early-onset retinitis pigmentosa and possible neurological manifestations, including neuropathy, and cerebellar ataxia, deafness[orpha.net]

  • Richards-Rundle Syndrome

    sensorineural hearing loss.[cags.org.ae] […] spinocerebellar ataxia, sensorineural hearing loss, and hypergonadotropic hypogonadism associated with additional neurological manifestations (such as peripheral muscle wasting[malacards.org] Orpha Number: 1399 Disease definition Richards-Rundle syndrome is an extremely rare neurodegenerative disorder characterized by progressive spinocerebellar ataxia , sensorineural[rarediseases.info.nih.gov]

  • Meniere's Disease

    […] ear characterized by recurrent episodes of vertigo, which is progressive sensorineural hearing loss.[medical-dictionary.thefreedictionary.com] Hearing loss: fluctuating, unilateral hearing impairment during the vertigo attacks in the form of a sensorineural hearing loss.[ims.uniklinik-freiburg.de] ). [35] In 1972, the academy defined criteria for diagnosing Ménière's disease as: [35] Fluctuating, progressive, sensorineural deafness.[en.wikipedia.org]

  • CINCA Syndrome

    The sensorineural hearing loss occurs in 75%, and tends to be progressive leading to deafness in 20% of cases.[en.wikipedia.org] Several transient episodes of sensorineural deafness resulted in a permanent but mild hearing deficiency but a hearing aid is currently not required.[jrheum.org] […] bilateral perceptive sensorineural deafness 20% Eye problems: affected in at least 80% incidence of eye problems increases with age average age of onset 4.5 years uveitis[dermnetnz.org]

  • Oculomotor Apraxia

    Ataxia - Hypogonadism; Cerebellar Ataxia - Ectodermal Dysplasia; Cerebellar Ataxia - Areflexia - Pes Cavus - Optic Atrophy - Sensorineural Hearing Loss; Brain Tumor Ataxia[diseaseinfosearch.org] Deafness generally progresses rapidly during a 1- to 3-month period.[pubs.sciepub.com] deafness.[ojrd.biomedcentral.com]

  • Roaf's Syndrome

    Sudden hearing loss (Sensorineural) is often associated with it. [4] They often appear late in the progression of the disease but are associated with a poor prognosis.[en.wikipedia.org] Progressive optic atrophy may result in decreased visual acuity or color vision. Intracranial hypertension with papilledema may be present.[en.wikipedia.org] […] with painless decrease of vision with the possibility of floaters or visual field defects. [4] Optic nerve involvement in Behçet's disease is rare, typically presenting as progressive[en.wikipedia.org]

  • Periodontitis

    The National Institutes of Deafness and Communication Disorders (NIDCD) report more than 100 possible etiologies, including infectious diseases, trauma (such as a head injury[audiology.org] CP generally involves chronic inflammation of tissues that support the teeth, destruction of periodontal ligaments, and progressive loss of alveolar bone around the teeth.[audiology.org] Although no one knows the exact cause of a given case of sudden sensorineural hearing loss (SSNHL), the potential etiologies of SSNHL are vast.[audiology.org]

  • Deafness

    Nerve deafness; Hearing loss - sensorineural; Acquired hearing loss; SNHL; Noise-induced hearing loss; NIHL; Presbycusis Sensorineural deafness is a type of hearing loss.[mountsinai.org] There are two principal kinds of deafness, conductive deafness and sensorineural deafness.[infoplease.com] Sensorineural hearing loss Sensorineural hearing loss occurs due to damage to the inner ear (the cochlea).[betterhealth.vic.gov.au]

  • Cholestasis

    Extrahepatic features have been reported including persistent short stature, watery diarrhea, pancreatitis and sensorineural deafness.[orpha.net] LT does not prevent extrahepatic progression of the disease, and does not lead to catch-up growth.[orpha.net]

Further symptoms