Create issue ticket

14 Possible Causes for Progressive Bilateral Postlingual Sensorineural Hearing Loss

  • Isolated Congenital Sclerocornea

    It is a congenital hereditary endothelial dystrophy (CHED) joined with progressive, postlingual sensorineural hearing loss.[emedicine.medscape.com] […] corneal edema and occurs with severe corneal clouding, blurred vision, visual loss, and nystagmus.[emedicine.medscape.com] […] when persistent and total corneal opacification fails to resolve after bilaterally elevated IOP normalizes. [5] Harboyan syndrome Harboyan syndrome manifests with diffuse bilateral[emedicine.medscape.com]

  • Salti-Salem Syndrome

    Sensorineural hearing loss (SNHL). Moderate bilateral SNHL was noted in 62% of reports.[ncbi.nlm.nih.gov] When present, deafness is invariably postlingual, usually starting in adolescence [ Woodhouse & Sakati 1983, Al-Semari & Bohlega 2007, Schneider & Bhatia 2008, Ben-Omran et[ncbi.nlm.nih.gov] […] although extrapyramidal features were not mentioned in the original report of Woodhouse and Sakati [1983], subsequent follow up in the originally reported families revealed progressive[ncbi.nlm.nih.gov]

  • Autosomal Recessive Congenital Cataract 5

    It is a congenital hereditary endothelial dystrophy (CHED) joined with progressive, postlingual sensorineural hearing loss.[emedicine.medscape.com] […] corneal edema and occurs with severe corneal clouding, blurred vision, visual loss, and nystagmus.[emedicine.medscape.com] […] when persistent and total corneal opacification fails to resolve after bilaterally elevated IOP normalizes. [5] Harboyan syndrome Harboyan syndrome manifests with diffuse bilateral[emedicine.medscape.com]

  • Corneal Opacity

    It is a congenital hereditary endothelial dystrophy (CHED) joined with progressive, postlingual sensorineural hearing loss.[emedicine.medscape.com] […] corneal edema and occurs with severe corneal clouding, blurred vision, visual loss, and nystagmus.[emedicine.medscape.com] […] when persistent and total corneal opacification fails to resolve after bilaterally elevated IOP normalizes. [5] Harboyan syndrome Harboyan syndrome manifests with diffuse bilateral[emedicine.medscape.com]

  • Autosomal Dominant Keratitis

    It is a congenital hereditary endothelial dystrophy (CHED) joined with progressive, postlingual sensorineural hearing loss.[emedicine.medscape.com] […] corneal edema and occurs with severe corneal clouding, blurred vision, visual loss, and nystagmus.[emedicine.medscape.com] […] when persistent and total corneal opacification fails to resolve after bilaterally elevated IOP normalizes. [5] Harboyan syndrome Harboyan syndrome manifests with diffuse bilateral[emedicine.medscape.com]

  • Sanjad-Sakati Syndrome

    It is a congenital hereditary endothelial dystrophy (CHED) joined with progressive, postlingual sensorineural hearing loss.[emedicine.medscape.com] […] corneal edema and occurs with severe corneal clouding, blurred vision, visual loss, and nystagmus.[emedicine.medscape.com] […] when persistent and total corneal opacification fails to resolve after bilaterally elevated IOP normalizes. [5] Harboyan syndrome Harboyan syndrome manifests with diffuse bilateral[emedicine.medscape.com]

  • Extrapyramidal Disorder

    Sensorineural hearing loss (SNHL). Moderate bilateral SNHL was noted in 62% of reports.[ncbi.nlm.nih.gov] When present, deafness is invariably postlingual, usually starting in adolescence [ Woodhouse & Sakati 1983, Al-Semari & Bohlega 2007, Schneider & Bhatia 2008, Ben-Omran et[ncbi.nlm.nih.gov] […] although extrapyramidal features were not mentioned in the original report of Woodhouse and Sakati [1983], subsequent follow up in the originally reported families revealed progressive[ncbi.nlm.nih.gov]

  • Woodhouse Sakati Syndrome

    Sensorineural hearing loss (SNHL). Moderate bilateral SNHL was noted in 62% of reports.[ncbi.nlm.nih.gov] When present, deafness is invariably postlingual, usually starting in adolescence [ Woodhouse & Sakati 1983, Al-Semari & Bohlega 2007, Schneider & Bhatia 2008, Ben-Omran et[ncbi.nlm.nih.gov] […] although extrapyramidal features were not mentioned in the original report of Woodhouse and Sakati [1983], subsequent follow up in the originally reported families revealed progressive[ncbi.nlm.nih.gov]

  • Congenital Cornea Plana

    It is a congenital hereditary endothelial dystrophy (CHED) joined with progressive, postlingual sensorineural hearing loss.[emedicine.medscape.com] […] corneal edema and occurs with severe corneal clouding, blurred vision, visual loss, and nystagmus.[emedicine.medscape.com] […] when persistent and total corneal opacification fails to resolve after bilaterally elevated IOP normalizes. [5] Harboyan syndrome Harboyan syndrome manifests with diffuse bilateral[emedicine.medscape.com]

  • Neurodegeneration with Brain Iron Accumulation

    Sensorineural hearing loss (SNHL). Moderate bilateral SNHL was noted in 62% of reports.[ncbi.nlm.nih.gov] When present, deafness is invariably postlingual, usually starting in adolescence [ Woodhouse & Sakati 1983, Al-Semari & Bohlega 2007, Schneider & Bhatia 2008, Ben-Omran et[ncbi.nlm.nih.gov] […] although extrapyramidal features were not mentioned in the original report of Woodhouse and Sakati [1983], subsequent follow up in the originally reported families revealed progressive[ncbi.nlm.nih.gov]

Further symptoms