DFNA71 is characterized by bilateral mild to moderate hearing loss before age 20 years, which gradually progresses to severe to profound hearing loss.
[ghr.nlm.nih.gov]
[…] developmental delay and Progressive hearing impairment that can help you solving undiagnosed cases.
[mendelian.co]
Cerebellar ataxia, areflexia, pes cavus, optic atrophy and sensorinural hearing loss C1832466 OMIM100150HP:0001730 HP:0000408 Progressive sensorineural hearing impairment1
[mseqdr.org]