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158 Possible Causes for Progressive Mild Sensorineural Hearing Loss

  • Meniere's Disease

    (Suh et al, 2018) In most cases, a progressive hearing loss occurs in the affected ear(s).[dizziness-and-balance.com] Even if one does become bilateral, usually the second ear is affected only to a mild extent -- perhaps a little tinnitus or fullness.[dizziness-and-balance.com] A low-frequency sensorineural pattern is commonly found initially, but as time goes on, it usually changes into either a flat loss or a peaked pattern (click here for more[dizziness-and-balance.com]

  • Congenital Deafness

    […] to profound All SMPX DFNX4 Postlingual Progressive sensorineural / mild to profound All AIFM1 DFNX5 Prelingual Progressive auditory neuropathy Low frequency COL4A6 DFNX6[ncbi.nlm.nih.gov] loss ranges from mild to profound hearing loss.[wvdhhr.org] Prelingual Progressive sensorineural / severe to profound All Nonsyndromic Hearing Loss and Deafness, Mitochondrial The majority of pathogenic variants in mitochondrial genes[ncbi.nlm.nih.gov]

  • Deafness

    […] to profound All SMPX DFNX4 Postlingual Progressive sensorineural / mild to profound All AIFM1 DFNX5 Prelingual Progressive auditory neuropathy Low frequency COL4A6 DFNX6[ncbi.nlm.nih.gov] Prelingual Progressive sensorineural / severe to profound All Nonsyndromic Hearing Loss and Deafness, Mitochondrial The majority of pathogenic variants in mitochondrial genes[ncbi.nlm.nih.gov] Locus Onset Type / Degree Frequencies PRPS1 DFNX1 Postlingual Progressive sensorineural / severe to profound All POU3F4 DFNX2 Prelingual Progressive, mixed / variable, but progresses[ncbi.nlm.nih.gov]

  • Autosomal Recessive Optic Atrophy Type 7

    […] visual impairment, optic disc pallor and central scotoma, variably associated with dyschromatopsia, auditory neuropathy (e.g. mild progressive sensorineural hearing loss)[orpha.net] Both siblings demonstrated a very mild but progressive sensorineural hearing loss, with no evidence of a conductive loss, and normal cochlear function, as judged by normal[molvis.org] […] rare disease Autosomal recessive optic atrophy, OPA7 type Disease definition A rare, syndromic, hereditary optic neuropathy disorder characterized by early-onset, severe, progressive[orpha.net]

  • Isolated Congenital Sclerocornea

    It is sensorineural, slowly progressive, with typical deficits in the 20–50 db range (mild to moderate) at ages 10–25 yrs, and mainly affects the higher frequencies (Figure[ojrd.biomedcentral.com] Although symptomatic hearing loss is not reported in early childhood, it might probably be detected in the first years of life if sought [ 24 ].[ojrd.biomedcentral.com]

  • Cryopyrin-Associated Periodic Syndrome

    The progressive nerve damage leads to sensorineural hearing loss that becomes evident during adolescence.[ivami.com] Hearing loss caused by progressive nerve damage (sensorineural deafness) typically becomes apparent during the teenage years.[ghr.nlm.nih.gov] Sensorineural hearing loss in MWS often rapidly progresses from mild high-tone deficits to complete deafness [ 10, 11 ].[ped-rheum.biomedcentral.com]

  • Autosomal Dominant Prognathism

    Most patients develop mild-to-moderate slowly progressive bilateral sensorineural hearing loss.[findzebra.com] It is progressive and leads to blindness, usually by the 2nd decade of life.[findzebra.com]

  • Sensorineural Hearing Impairment

    Sensorineural hearing loss in MWS often rapidly progresses from mild high-tone deficits to complete deafness [ 10, 11 ].[ped-rheum.biomedcentral.com] Sensorineural hearing loss in MWS often rapidly progresses from mild high-tone deficits to complete deafness [ 10 , 11 ].[ped-rheum.biomedcentral.com]

  • Ptosis

    Cerebellar ataxia, sensorineural hearing loss, and increased protein content of the cerebrospinal fluid have also been reported.[journals.lww.com] […] to bilateral ptosis. [51,52] Other examples are the Kearns–Sayre syndrome, in which patients manifest with progressive external ophthalmoplegia, retinitis pigmentosa, and[journals.lww.com] CPEO encompasses a heterogeneous and wide-ranging group of disorders including the above-mentioned CPEO syndrome in which patients might show mild clinical features restricted[journals.lww.com]

  • Autosomal Recessive Deafness 23

    loss is bilateral and stable with prelingual onset Mitochondrial variants often cause sensorineural hearing loss that varies in severity and onset m.7445 A G variant Palmar[arupconsult.com] […] to profound All SMPX DFNX4 Postlingual Progressive sensorineural / mild to profound All AIFM1 DFNX5 Prelingual Progressive auditory neuropathy Low frequency COL4A6 DFNX6[ncbi.nlm.nih.gov] hearing loss Normal vestibular function USH2A, VLGR1, WHRN Type 3 Progressive hearing Loss Progressive vestibular dysfunction CLRN1i PDZD7 Pendred syndrome Autosomal recessive[bcidaho.com]

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