Possible Causes for renal involvement Alagille Syndrome Renal involvement occurs in 40% of JAG1-mutation-positive individuals. [ncbi.nlm.nih.gov] Renal involvement has been reported though not formally described. The objective of this study was to systematically characterize the renal involvement in ALGS. [ncbi.nlm.nih.gov] Renal involvement is less common but can take various forms including renovascular disease, renal agenesis or hypoplasia, cystic renal disease, mesangiolipidosis, tubulointerstitial [ncbi.nlm.nih.gov] Henoch-Schönlein Purpura involvement (4.767, P .067). [ncbi.nlm.nih.gov] This meta-analysis identified risk factors associated with renal involvement in childhood HSP. METHODS: PubMed, Embase, and Web of Science were searched. [ncbi.nlm.nih.gov] […] were the significant risk factors for renal involvement. [ncbi.nlm.nih.gov] Purpura AIM: Henoch-Schönlein purpura (HSP), a primary vasculitis, characterized by purpura, abdominal pain, arthritis and renal involvement, is predominantly a disease of childhood [ncbi.nlm.nih.gov] renal involvement (see ‘discussion with Nephrology’ under ‘Follow-Up’ below) Neurological involvement Discharge Advice Prognosis A first episode of HSP, in the absence of [rch.org.au] There is no consensus on prevention or treatment of renal involvement. [patient.info] Renal Vasculitis Renal involvement. [tidsskriftet.no] Renal involvement is present in the majority of patients with ANCA-associated vasculitis (AAV) and the consequences of a missed or delayed diagnosis of renal vasculitis are [ncbi.nlm.nih.gov] Renal involvement ranges between 71% and 88% in patients with GPA and MPA, 2 whereas in EGPA it occurs in up to 25% of cases. 3 Severe renal involvement is an uncommon finding [emjreviews.com] Renal Arteritis […] with renal artery involvement. [jrheum.org] Renal involvement. [tidsskriftet.no] […] in TA patients with renal artery involvement. [acrabstracts.org] Lupus Nephritis These results indicate that IL-35 is a potential biomarker of renal involvement in LN patients. [ncbi.nlm.nih.gov] Arthritis was the dominant clinical manifestation seen in 85.5%, whereas renal involvement was seen in 66.1% of patients. [ncbi.nlm.nih.gov] Abstract Renal involvement in Systemic Lupus Erythematous (SLE) patients is one of the leading causes of morbidity and a significant contributor to mortality. [ncbi.nlm.nih.gov] Microscopic Polyangiitis CONCLUSIONS: Survival rates do not relate to ESRF in MPA patients with mainly renal involvement. [ncbi.nlm.nih.gov] MPA patients with renal involvement. [bmcnephrol.biomedcentral.com] involvements, BVAS 13.5 and FFS 1 at diagnosis were independent predictors of relapse of MPA. [ncbi.nlm.nih.gov] Granulomatosis with Polyangiitis involvement M31.31 …… with renal involvement M31.4 Aortic arch syndrome [Takayasu] M31.5 Giant cell arteritis with polymyalgia rheumatica M31.6 Other giant cell arteritis [icd10data.com] Wegener's granulomatosis with renal involvement Wegener's granulomatosis without renal involvement Wegeners granulomatosis wo renal involvement Clinical Information A multisystemic [icd9data.com] Our data confirms that ENT involvement is not only one of the key clinical features of GPA, but also could point out a milder GPA subset with lower renal involvement and lower [ncbi.nlm.nih.gov] Systemic Vasculitis Of the 41 patients with proven renal involvement that were still alive at the time of the last check-up, 12 continued to require treatment for renal impairment. [ncbi.nlm.nih.gov] Renal involvement. [tidsskriftet.no] Objective signs of renal involvement were found in 39 (59 %) at the first consultation and in 42 (64 %) over the course of the disease. [ncbi.nlm.nih.gov] Scleroderma with Renal Involvement Renal involvement is relatively common in patients with RA. [bmcmedicine.biomedcentral.com] Prognosis of Renal Involvement Prognostic Factors of Renal Involvement in Systemic Sclerosis (SSc). [sclero.org] Lack of activation of renal functional reserve predicts the risk of significant renal involvement in systemic sclerosis. Ann. Rheum. Dis. 70, 1963–1967 (2011). 22. [nature.com] Renal Sarcoidosis Conclusions Several small series have suggested that renal involvement (as defined by either histologic changes in the kidney or a decline in renal function in the absence [ard.bmj.com] Radiographic evidence of renal involvement by sarcoidosis is usually demonstrated as nephrocalcinosis or nephrolithiasis. [ncbi.nlm.nih.gov] Eye and renal involvement are rarely found together, and may be confused with Wegener's granulomatosis or polyarteritis. [ncbi.nlm.nih.gov] Hypocomplementemic Vasculitis We emphasize the fact that renal involvement can occur with this disease and that the renal involvement is of the immune-mediate type and cannot be considered as benign as [ncbi.nlm.nih.gov] Ramirez G, Saba SR, Espinoza L: Hypocomplementemic vasculitis and renal involvement. Nephron 1987;45:147–150. [karger.com] Renal involvement is described as usually mild, but dialysis may be required [ 10 ]. [omicsonline.org] Renal Amyloidosis Renal involvement leading to chronic renal disease and renal failure is a common sign. [orpha.net] Those with amyloid in previous generations presented with renal involvement, frequently developed complications due to gastrointestinal amyloid, and died before age 60. [ncbi.nlm.nih.gov] Homepage Rare diseases Search Search for a rare disease Hereditary amyloidosis with primary renal involvement Disease definition A group of rare renal diseases, characterized [orpha.net] Nephritis Renal involvement is relatively uncommon and may precede other complaints. Tubulointestitial nephritis (TIN) is the most common renal involvement in SS. [ncbi.nlm.nih.gov] We describe a case of IgG4-TIN with isolated renal involvement in an elderly male patient with poor response to corticosteroid therapy. [ncbi.nlm.nih.gov] involvement from those without renal involvement. [ncbi.nlm.nih.gov] Vasculitis Two hundred and forty-five patients with ANCA-AAV and biopsy-proven renal involvement diagnosed between 2000 and 2104 were recruited in 12 nephrology services. [ncbi.nlm.nih.gov] involvement from those without renal involvement. [ncbi.nlm.nih.gov] We aimed to know the impact on renal survival and identify the prognostic factors of this treatment in Chinese AAV patients with severe renal involvement. [ncbi.nlm.nih.gov] Nail-Patella Syndrome Renal involvement occurs in 30-60% of patients and presents with proteinuria and/or microscopic hematuria, edema, hypertension. [ncbi.nlm.nih.gov] While glomerulonephritis occurs in 30% of patients with nail-patella syndrome, there was no evidence of renal involvement. [ncbi.nlm.nih.gov] We report three cases of NPS with different degrees of renal involvement and present a review of the literature on this rare hereditary condition. [ncbi.nlm.nih.gov] AApoAIV Amyloidosis Renal involvement is commonly seen in AA, AL, and several other hereditary and acquired amyloidoses. [intechopen.com] Renal involvement is commonly seen in AL, AH, AA, ALECT2, and several other hereditary and acquired amyloidoses [ 1, 2, 3, 4 ], main features are summarized in Table 1. [intechopen.com] […] of renal tubules involved. [jasn.asnjournals.org] Renal Tuberculosis The remaining 5 LAM-positive patients had disseminated TB without renal involvement. Of the 23 LAM-negative patients, 3 had disseminated TB without renal involvement. [ncbi.nlm.nih.gov] Renal involvement by TB infection is underdiagnosed in most health care centers. [ncbi.nlm.nih.gov] Renal involvement in tuberculosis occurs through haemogeneous spread from a primary focus and is usually a bilateral disease. The most common primary site are the lungs. [ncbi.nlm.nih.gov] Pauci-Immune Glomerulonephritis Renal involvement is a frequent feature in patients with APS. [ncbi.nlm.nih.gov] These subjects had significantly higher renal involvement, less extra-renal manifestations and lower BVAS. [ncbi.nlm.nih.gov] Renal involvement in patients with temporal arteritis is not common and the presence of glomerulonephritis is rare [Jennette and Falk 1994]. [ncbi.nlm.nih.gov] Interstitial Nephritis Tubulointerstitial nephritis (TIN) is the most common type of renal involvement in pSS. However, clinically significant renal involvement is uncommon. [ncbi.nlm.nih.gov] These pathological features were compatible with SS with renal involvement. [ncbi.nlm.nih.gov] Renal involvement frequently ensues and usually results in acute tubular necrosis with associated interstitial inflammation. [ncbi.nlm.nih.gov] Hereditary Amyloidosis with Primary Renal Involement The clinical phenotype of hereditary renal amyloid is non-specific and is readily misdiagnosed as acquired AL amyloidosis. [ncbi.nlm.nih.gov] Renal involvement in systemic amyloidosis. [academic.oup.com] Renal involvement from amyloidosis in pathological specimens is quite common. However, renal function compromise is rare. [radiopaedia.org] Familial Interstitial Nephritis In contrast with previous reports, microscopic/macroscopic hematuria was not a consistent marker for renal involvement. [ncbi.nlm.nih.gov] Winn Keywords Nephritis, Interstitial, Genetics Abstract Chronic tubulo-interstitial nephritis (TIN) leads to progressive decline in renal function, involving patho-physiological [epubs.rcsi.ie] This is because this type of involvement usually does not lead to renal dysfunction. [bjn.org.br] Light Chain Disease It can affect multiple organ systems. renal manifestations of light chain deposition disease - renal involvement is a constant feature, resulting in proteinuria with or without [radiopaedia.org] Renal involvement is constant and often the main clinical and laboratory feature. [omicsonline.org] Induction treatment of light chain deposition disease with bortezomib: rapid hematological response with persistence of renal involvement. [emedicine.medscape.com] Cryoglobulinemic Vasculitis The patients had no or mild renal involvement at entry and the ANCA was negative as tested by immunoflourescence and ELISA. [ncbi.nlm.nih.gov] Renal involvement was associated with an increased mortality, and was the most common cause of death; these data were obtained before effective antiviral treatment was available [ncbi.nlm.nih.gov] involvement is severe. [ncbi.nlm.nih.gov] Polyarteritis Nodosa The spectrum of disease ranges from involving a single organ to polyvisceral failure. [ncbi.nlm.nih.gov] When applying the Chapel Hill nomenclature, PAN is a rare but severe disease with a high incidence of renal involvement and frequent relapses. [ncbi.nlm.nih.gov] Weight loss was present in 20 (74%), fever in 14 (51.9%), renal involvement in 16 (59.3%), cutaneous in nine (33.3%), peripheral gangrene in eight (29.6%), gastrointestinal [ncbi.nlm.nih.gov] Rapidly Progressive Glomerulonephritis involvement and a positive ANCA serology. [ncbi.nlm.nih.gov] Severe renal involvement was reversible with early appropriate treatment. [ncbi.nlm.nih.gov] The reason why the effectiveness of plasmapheresis therapy cannot be clearly demonstrated in renal involvement in these diseases is that it does not appear to be possible [ncbi.nlm.nih.gov] Necrotizing Arteritis involvement in dysproteinemias 314 The hyperuricemic nephropathies 327 Therapy of renal disorders in liver disease 334 The management of renal insufficiency 495 Management [books.google.com] One case of cPAN developed renal involvement. [acrabstracts.org] This was caused by a densely fibrotic mass involving the main renal artery. Microscopy revealed a necrotizing arteritis with no other arteries involved. [ncbi.nlm.nih.gov] Urticarial Vasculitis Isolated microhaematuria can be the only sign of subclinical renal involvement: its role should not be underestimated and a renal biopsy should be considered. [ncbi.nlm.nih.gov] This case shows for the first time that HUVS can induce severe renal involvement responsible for ESRD and that HUVS can relapse after renal transplantation. [ncbi.nlm.nih.gov] Abstract We present a patient with previously diagnosed hypocomplementemic urticarial vasculitis syndrome, with skin, lung, and renal involvement, who presented with congestive [ncbi.nlm.nih.gov] Churg-Strauss Syndrome Renal involvement may be seen in up to 50% of cases. [ncbi.nlm.nih.gov] Renal Disease Traditionally, renal involvement in CSS has been reported as being mild. [jasn.asnjournals.org] CONCLUSIONS: ANCA(-) CSS patients showed less frequent renal involvement. [ncbi.nlm.nih.gov] Cryoglobulinemia involvement. [uninet.edu] Glucocorticoid and immunosuppressants were good choices for relieving renal involvement. [ncbi.nlm.nih.gov] All 13 patients who died had renal involvement, with renal insufficiency in 10 patients, and none had a complete response to therapy. [jamanetwork.com]
