Severe to Profound Sensorineural Hearing Loss Causes & Reasons

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Severe to Profound Sensorineural Hearing Loss Symptom Checker: Possible causes include Sensorineural Hearing Impairment. Check the full list of possible causes and conditions now! Talk to our Chatbot to narrow down your search.

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Possible Causes

Sensorineural Hearing Impairment

In cases of severe or profound sensorineural hearing loss, cochlear implants may be recommended. [nexgenhearing.com]

Sensorineural hearing loss is classified in different degrees including, mild, moderate, severe and profound. [everydayhearing.com]

A more severe or profound sensorineural hearing loss can be treated with hearing implants. [hear-it.org]

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Autosomal Recessive Deafness 42

sensorineural hearing loss. [dizziness-and-balance.com]

Click here to view The seven 35delG homozygote and heterozygote patients had severe to profound sensorineural hearing loss (SNHL). [ejo.eg.net]

Affected members in these families were described with congenital or prelingual, severe-to-profound sensorineural hearing loss (Table 2 ). [karger.com]

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Acute Sensorineural Hearing Loss by Acute Acoustic Trauma

HEALOS aims to enroll approximately 255 patients with severe to profound idiopathic sudden sensorineural hearing loss. [clinicalleader.com]

Hearing Loss. ( 30772961 ) Levy E...Ronen O 2019 21 Prognostic factors regarding the hearing outcome in severe to profound sudden sensorineural hearing loss treated by tympanotomy [malacards.org]

ASSENT aims to enroll approximately 300 patients with severe to profound idiopathic sudden sensorineural hearing loss. [clinicalleader.com]

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Congenital Deafness

sensorineural hearing loss. [dizziness-and-balance.com]

Usher syndrome type I is characterized by congenital severe-to-profound sensorineural hearing loss and vestibular dysfunction. [nature.com]

[…] interval, torsade de pointe arrhythmias (turning of the points, in reference to the apparent alternating positive and negative QRS complexes), sudden syncopal episodes, and severe-to-profound [dizziness-and-balance.com]

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Deafness

[…] cochlear implantation for severe to profound sensorineural hearing loss in one ear and normal cochlear function in the contralateral ear (single-sided deafness [SSD]). [ncbi.nlm.nih.gov]

Since then, this procedure has become the standard of care for patients with severe-to-profound sensorineural hearing loss. Successful outcomes are dependent ... [centerwatch.com]

GJB2 gene mutations mainly resulted in flat-type, profound-to-severe sensorineural hearing loss (SNHL). [ncbi.nlm.nih.gov]

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Vestibulocochlear Nerve Disease

Sensorineural hearing loss is classified in different degrees including, mild, moderate, severe and profound. [everydayhearing.com]

Audiograms revealed severe-to-profound sensorineural hearing loss on the left and severe sensorineural hearing loss on the right. [ajnr.org]

Sensorineural hearing loss results in difficulty hearing soft sounds and can lead to impaired communication. [everydayhearing.com]

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Cochlear Disorder

Mutation Cochlear implantation is widely accepted for the treatment of severe to profound sensorineural hearing loss since its approval in 1990 by the Food and Drug Administration [atlasofscience.org]

Can every patient with severe to profound sensorineural hearing loss benefit from a cochlear implant? [umm.edu]

Although considered a preservation procedure, it should not be performed in an only hearing ear as up to 45% of patients develop a severe to profound sensorineural hearing [michiganear.com]

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Pendred Syndrome

Pendred syndrome is characterized by severe to profound sensorineural hearing loss, vestibular aqueduct dilation, and thyroid goiter. [medschool.lsuhsc.edu]

Pendred Syndrome is characterized by a congenital (pre-birth) non-progressive, severe-to-profound sensorineural hearing loss which is frequently coupled with a late childhood [californiaearinstitute.com]

In most people with Pendred syndrome, severe to profound hearing loss caused by changes in the inner ear (sensorineural hearing loss) is evident at birth. [ghr.nlm.nih.gov]

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Sudden Hearing Loss

Severe or profound ipsilateral-sensorineural hearing loss was recognized on audiometry. [ncbi.nlm.nih.gov]

[…] and profound idiopathic sudden sensorineural hearing loss (ISSNHL). [ncbi.nlm.nih.gov]

고도 및 심도 돌발성 난청에 대한 고실내 스테로이드 주입술과 경구 스테로이드 병합치료의 효과 The Effects of Combined Intratympanic and Oral Steroid Treatment for Severe to Profound Sudden Sensorineural Hearing Loss [kci.go.kr]

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High Myopia-Sensorineural Deafness Syndrome

sensorineural hearing loss. [dizziness-and-balance.com]

Usher syndrome type I is characterized by congenital severe-to-profound sensorineural hearing loss and vestibular dysfunction. [nature.com]

Recessive Usher Syndrome Congenital sensorineural hearing loss Type 1 Severe to profound hearing loss Abnormal vestibular function Delayed walking and sitting Type 2 mild [en.wikibooks.org]

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Autosomal Recessive Deafness 44

They are used in both adults and children with severe to profound sensorineural hearing loss (SNHL) where hearing aids provide insufficient amplification for the understanding [nzma.org.nz]

Severity ranges from mild to profound. The prevalence of bilateral sensorineural hearing loss is 1 in 500 newborns and 3.5 per 1000 adolescents. [egl-eurofins.com]

profound All AIFM1 DFNX5 Prelingual Progressive auditory neuropathy Low frequency COL4A6 DFNX6 Prelingual Progressive sensorineural / severe to profound All Nonsyndromic Hearing [ncbi.nlm.nih.gov]

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Autosomal Dominant Deafness 9

sensorineural hearing loss. [dizziness-and-balance.com]

Usher syndrome type I is characterized by congenital severe-to-profound sensorineural hearing loss and vestibular dysfunction. [nature.com]

United Arab Emirates Houseman et al. (2001) analyzed five subjects with severe-profound prelingual non-syndromic sensorineural hearing loss from a consanguineous family from [cags.org.ae]

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Ménière Disease

In some individuals ‘end stage’ Ménière’s disease (stage 3) can result in a severe to profound hearing loss. [menieres.org.uk]

A surgical labyrinthectomy is done only if preexisting hearing loss is profound. Unfortunately, there is no known way to prevent the natural progression of hearing loss. [msdmanuals.com]

Bilateral Ménière’s disease is reported in 17% to 50% of affected individuals and can be a cause of bilateral profound sensorineural hearing loss. [menieres.org.uk]

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Hemosiderosis

Cochlear implantation may be a viable option for patients with severe to profound sensorineural hearing loss due to SH-CNS. [ncbi.nlm.nih.gov]

For the other case, hearing performance was very low. He showed only disyllabic word identification abilities in a closed set (40%). [ncbi.nlm.nih.gov]

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Autosomal Recessive Deafness 88

A form of non-syndromic deafness characterized by prelingual onset of severe to profound mixed conductive and sensorineural hearing loss. [ghr.nlm.nih.gov]

sensorineural hearing loss. [dizziness-and-balance.com]

[…] deafness characterized by moderate to severe or profound hearing loss which is progressive in some individuals but not in others. [genecards.org]

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Labyrinthine Concussion

Our case illustrates a patient who was involved in motor vehicle accident sustaining bilateral severe to profound sensorineural hearing loss but subsequently recovered fully [researchgate.net]

In some of these cases, labyrinthine concussions can result in severe to profound hearing loss requiring cochlear implantation. [journals.lww.com]

CASE HISTORY The patient is an 80-year-old woman with a history of moderate to severe sensorineural hearing loss in both ears prior to falling backwards and striking her head [journals.lww.com]

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Autosomal Dominant Deafness 28

A mtDNA mutation, in which a G instead of an A is found at position 1555 (called A1555G), causes severe to profound sensorineural hearing loss. [iccons.co.in]

Usher syndrome type I is characterized by congenital severe-to-profound sensorineural hearing loss and abnormal vestibular dysfunction. [consilieregenetica.org]

Severity ranges from mild to profound. The prevalence of bilateral sensorineural hearing loss is 1 in 500 newborns and 3.5 per 1000 adolescents. [egl-eurofins.com]

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Arachnoid Cyst

Chudley-McCullough syndrome is an autosomal recessive disorder associated with severe-to-profound sensorineural hearing loss and partial agenesis of the corpus callosum. [emedicine.com]

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Chronic Otitis Externa

An audiogram demonstrated new, severe to profound, sensorineural hearing loss. The patient was admitted and re-commenced on intravenous antibiotics. [ncbi.nlm.nih.gov]

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Usher Syndrome

Forty-seven children with bilateral severe to profound sensorineural hearing loss were evaluated. [ncbi.nlm.nih.gov]

Individuals with Type 1 Usher Syndrome typically have a congenital severe-to-profound sensorineural hearing loss and severe vestibular (balance) problems. [californiaearinstitute.com]

All children with severe to profound, preverbal sensorineural hearing loss should be screened for Usher syndrome by ophthalmologic examination including electroretinogram. [ncbi.nlm.nih.gov]

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Autosomal Recessive Deafness 76

Click here to view The seven 35delG homozygote and heterozygote patients had severe to profound sensorineural hearing loss (SNHL). [ejo.eg.net]

Prevalence of GBJ2 mutations in patients with severe to profound congenital non-syndromic sensorineural hearing loss in Bulgarian population. [degruyter.com]

Severity ranges from mild to profound. The prevalence of bilateral sensorineural hearing loss is 1 in 500 newborns and 3.5 per 1000 adolescents. [egl-eurofins.com]

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Otosclerosis

PATIENTS: 6 patients (7 ears), 5 patients with severe to profound sensorineural hearing loss; 1 patient with mild to profound sensorineural hearing loss, with radiologic evidence [ncbi.nlm.nih.gov]

sensorineural hearing loss. [ncbi.nlm.nih.gov]

In about 50% of cases, stapes gusher will result in profound sensorineural hearing loss. [audiologyonline.com]

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Temporal Bone Fracture

Severe-to-profound sensorineural hearing loss most commonly occurs in patients who have transverse fractures with otic capsule involvement. [emedicine.medscape.com]

Cochlear and vestibular structures are usually destroyed, producing a profound sensorineural hearing loss and severe ablative vertigo. [emedicine.medscape.com]

Sensorineural hearing loss can also occur with intralabyrinthine bleeding without evidence of temporal bone fracture. [emedicine.medscape.com]

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Autosomal Recessive Deafness 22

sensorineural hearing loss. [dizziness-and-balance.com]

Recessive Usher Syndrome Congenital sensorineural hearing loss Type 1 Severe to profound hearing loss Abnormal vestibular function Delayed walking and sitting Type 2 mild [en.wikibooks.org]

Severity ranges from mild to profound. The prevalence of bilateral sensorineural hearing loss is 1 in 500 newborns and 3.5 per 1000 adolescents. [egl-eurofins.com]

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Usher Syndrome Type 1J

Individuals with Type 1 Usher Syndrome typically have a congenital severe-to-profound sensorineural hearing loss and severe vestibular (balance) problems. [californiaearinstitute.com]

Diagnostic methods Clinical diagnosis is based on findings of bilateral sensorineural hearing loss (symmetric, congenital and profound for type 1, and moderate to severe with [orpha.net]

Genes involved in Type I Usher syndrome type I is the most severe form of Usher syndrome and is characterized by congenital, profound, sensorineural hearing loss; vestibular [usher-syndrome.org]

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Benign Paroxysmal Positional Vertigo

We describe two patients with intractable BPPV and profound sensorineural hearing loss in the affected ear treated by transmastoid posterior semicircular canal occlusion. [ncbi.nlm.nih.gov]

Some individuals with this disorder have severe and protracted symptoms requiring more than expectant therapy. [ncbi.nlm.nih.gov]

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Microtia

If the hearing loss is severe to profound in both ears, the child may be a candidate for a cochlear implant (beyond the scope of this discussion). [en.wikipedia.org]

[…] for this hearing loss. [en.wikipedia.org]

Sensorineural hearing loss is not correctable by surgery, but properly fitted and adjusted hearing amplification (hearing aids) generally provide excellent rehabilitation [en.wikipedia.org]

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Autosomal Recessive Deafness 24

Affiliated tissues include brain, and related phenotype is profound sensorineural hearing impairment. [malacards.org]

Severity ranges from mild to profound. The prevalence of bilateral sensorineural hearing loss is 1 in 500 newborns and 3.5 per 1000 adolescents. [egl-eurofins.com]

Show info

Autosomal Dominant Deafness 11

sensorineural hearing loss. [dizziness-and-balance.com]

Recessive Usher Syndrome Congenital sensorineural hearing loss Type 1 Severe to profound hearing loss Abnormal vestibular function Delayed walking and sitting Type 2 mild [en.wikibooks.org]

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Tinnitus

[…] to profound sudden idiopathic sensorineural hearing loss after failure of systemic therapy. [doi.org]

(2009) Randomized, double blind, placebo controlled trial on the safety and efficacy of continuous intratympanic dexamethasone delivered via a round window catheter for severe [doi.org]

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