Rupture of aneurysm of sinus of Valsalva into the right atrium mimicking tricuspid valve endocarditis is a rare presentation. We review a case of spontaneous rupture of aneurysm of sinus of Valsalva into the right atrium presenting as a murmur. [ncbi.nlm.nih.gov]

Clinical complications from SVA are often the initial presentation of SVA. [emedicine.com]

When present, it is usually in either the right (65–85%) or in the noncoronary (10–30%) sinus, rarely in the left ( 5%) sinus. [en.wikipedia.org]

In this report, we present our experience with 53 patients throughout 15 years and propose a classification system purely depending on the algorithm to be followed according to the clinical presentation. 2 Materials and methods Between February 1985 and [doi.org]

• Developmental Delay

  delay and mild mixed aminoaciduria. [ncbi.nlm.nih.gov]

• Suggestibility

  Transthoracic echocardiogram showed a mobile mass that appeared to be attached to the tricuspid valve leaflet with moderate tricuspid regurgitation suggestive of tricuspid valve endocarditis. [ncbi.nlm.nih.gov]

  However, some reports [ 5, 6 ] have suggested that involvement of the interventricular septum is more common among Indian and African populations. [doi.org]

  CT coronary angiography axial, coronal and sagittal images showed a contrast filled out-pouching arising from the left coronary sinus suggestive of aneurysm. [elynsgroup.com]

Unruptured SOV aneurysms Overall, unruptured aneurysms are asymptomatic and are incidentally detected during imaging workup of heart murmurs or abnormal cardiomediastinal silhouette on radiograph ( 16 ). [ncbi.nlm.nih.gov]

The patient had a successful postsurgical recovery and was discharged home with anticoagulation treatment. [ncbi.nlm.nih.gov]

Treatment Therapy for Aneurysm of sinus Valsalva includes controlling blood pressure by use of medicines, such as beta-blockers. However, the long-term treatment is surgical repair. [medigest.uk]

Please consult your own licensed physician regarding diagnosis and treatment of any medical condition! Please see also our disclaimer. This site complies with the HONcode standard for health information: verify here. Database updated 2019-02-19. [diseasesdatabase.com]

Prognosis in patients with a ruptured aneurysm who have not undergone surgical repair may be poor, with survival beyond 1 year uncommon. [chdbabies.com]

Treatment and prognosis Surgical repair with a Bentall procedure could be performed. [radiopaedia.org]

Urgent surgical repair for ruptures aneurysms Many recommend surgical repair of non-ruptures aneurysms as well Complications Rupture (see above) Myocardial infarction Heart block Right ventricular outflow tract obstruction Cardiac tamponade Sudden death Prognosis [learningradiology.com]

[…] echocardiography (TEE) provides conclusive information regarding the origin and size of the aneurysm and presence of thrombotic material and allows precise identification of structural anomalies and shunt locations for perioperative assessment. [1], [4], [5] Prognosis [annals.in]

Following successful surgical repair of a ruptured aneurysm, the prognosis is excellent with 10-year survival rates of 90%–95% ( 45, 46 ). [ncbi.nlm.nih.gov]

An anatomic etiology of symptoms may be suspected with heart auscultation (murmur), and diagnosis is made by a routine echocardiogram or, if the patient is suspected of having coronary disease as the etiology of symptoms, an angiogram. [hqmeded-ecg.blogspot.com]

Root replacement or Ross procedure maybe used if severe local septic etiology. Complications Rupture into RV RA LV IVS/PA leads to formation intracardiac fistulae or tamponade. [pie.med.utoronto.ca]

For etiology, SOV aneurysms are commonly congenital and represent 0.1% to 3.5% of congenital heart defects ( 6, 7 ). [ncbi.nlm.nih.gov]

The etiology of the aneurysm seems atherosclerotic as suggested by age of the patient, atherosclerotic changes visualized on computed tomography imaging of the aorta and histopathology of the surgically excised aneurysm. [annalspc.com]

Cardiac tamponade may occur if the rupture involves the pericardial space. [1] Epidemiology Frequency United States SVA was present in 0.09% of cadavers in a large autopsy series and ranged to 0.14-0.23% in a Western surgical series. [4] Two-dimensional [emedicine.com]

Chest trauma, vasculitic diseases, and iatrogenic injury during aortic valve replacement have all been reported as causes of acquired SOVA.[ 1, 6-8 ] Epidemiology Although the true prevalence of SOVAs is unknown, the estimated rate is approximately 0.09% [onlinelibrary.wiley.com]

Associated conditions include: Syphilis Trauma Endocarditis Atherosclerosis Marfans (diffuse dilatation) Uncommon – Ehlers Danlos (other connective tissue disorders), Takayasu arteritis (other vasculitides), post AV replacement Pathophysiology Congenital [pie.med.utoronto.ca]

[…] intracardiac shunting caused by rupture of the SVA into the right side of the heart. [1] Approximately 65-85% of SVAs originate from the right sinus of Valsalva, while SVAs originating from noncoronary (10-30%) and left sinuses ( 5%) are exceedingly rare. [2] Pathophysiology [emedicine.com]

Pathophysiology Aneurysmal dilatation of the sinuses of Valsalva occurs when the aortic media is defective, allowing separation of the media from the aortic annulus fibrosus. [chdbabies.com]

Deterrence/Prevention Because the genetic mutation that causes the sinus of Valsalva aneurysm is presumed to be spontaneous, no preventive measures are available. [chdbabies.com]

Children’s heart conditions can’t be prevented, but a lot can be done to improve and often completely repair their hearts at any age. [nemours.org]

Such a consideration may prevent some instances of congenital aneurysms from being missed simply because they have not been reported. [pediatrics.aappublications.org]

This encourages early surgical intervention, which helps prevent the development of worse symptoms and more extensive disease leading to more complicated and less satisfying repairs. [doi.org]

They provide a space to prevent blocking of the coronary artery orifices from the open aortic leaflets. [ncbi.nlm.nih.gov]