Edit concept Question Editor Create issue ticket

Angiomatosis

Angiomatoses


Presentation

  • In this report, we present a patient with DDA with an underlying mass lesion of the breast, which proved to be an adjacent fat necrosis.[ncbi.nlm.nih.gov]
Intermittent Claudication
  • We report a 63-year-old woman who presented with multiple erythematous-violaceous plaques with central deep skin ulcers on thighs, lower abdomen, and perianal area, associated with intermittent claudication, low-grade fever, and weight loss.[ncbi.nlm.nih.gov]
Pelvic Mass
  • A 26-year-old P2 L2 had two cesarean sections for recurrent obstructed labor due to a large pelvic mass.[ncbi.nlm.nih.gov]
Photophobia
  • A 46-year-old Caucasian man reported frequent episodes of eye redness and pain, conjunctivitis, xerophthalmia, photophobia, and progressive worsening of visual acuity. Slitlamp examination revealed interstitial keratitis.[ncbi.nlm.nih.gov]
Ecthyma
  • Initially, the clinical picture along with positive cultures for Klebsiella pneumoniae suggested a multifocal ecthyma gangrenosum; nevertheless, a skin biopsy showed a diffuse dermal proliferation of endothelial cells interstitially arranged between collagen[ncbi.nlm.nih.gov]
Macrocephaly
  • He had normal neurodevelopment, but progressive macrocephaly (figure, B). Linear brain ultrasonography showed extensive venous angiomatosis in the prominent subarachnoid space (figure, C and D).[ncbi.nlm.nih.gov]
Spinal Cord Syndrome
  • It is stressed the importance of clinical suspicion of cutaneo-meningospinal angiomatosis based on a spinal cord syndrome in the presence of a vascular skin nevus of the same metameric level.[ncbi.nlm.nih.gov]
Behavior Problem
  • It is commonly complicated by glaucoma and neurological disturbances including seizures, hemiparesis, transient stroke-like deficits, and behavioral problems.[ncbi.nlm.nih.gov]
Communicating Hydrocephalus
  • MRI revealed cortical sulcal widening, prominent leptomeningeal vessels in an enlarged subarachnoid space (figure, E and F), and communicating hydrocephalus (figure, F).[ncbi.nlm.nih.gov]
Cesarean Section
  • A 26-year-old P2 L2 had two cesarean sections for recurrent obstructed labor due to a large pelvic mass.[ncbi.nlm.nih.gov]

Workup

  • When an ocular lesion is discovered, a systemic workup should also be considered for possible renal cell carcinoma and pheochromocytoma, as well as for central nervous system lesions.[aao.org]
  • The diagnostic workup involves clinical assessment, imaging and histology.[nzma.org.nz]
  • A workup to exclude calciphylaxis involving the breasts or a hypercoagulable state is advisable in patients with reduced kidney function, end-stage kidney failure, or a history of thromboembolic events.[karger.com]
Mediastinal Mass
  • Although very rare, mediastinal nodal angiomatosis is an entity radiologists should be aware of to be a differential diagnosis for a hypervascular mediastinal mass lesion.[ncbi.nlm.nih.gov]
Left Pleural Effusion
  • A roentgenogram of the chest showed that the patient had left pleural effusion and a left paraspinal mass, computed tomography disclosed a low-density fusiform lesion over the left paraspinal region, and magnetic resonance imaging confirmed a large posterior[ncbi.nlm.nih.gov]

Treatment

  • Aminobisphosphonate therapy represents an elective treatment for bone angiomatosis syndromes, but further studies are necessary to understand the molecular basis of these disorders and of their pharmacological treatment.[ncbi.nlm.nih.gov]

Prognosis

  • It displays some similarity to Gorham-Stout disease (GSD), but has a much better local prognosis, despite the larger number of cysts. These 2 conditions also differ in terms of their location, visceral involvement, and response to treatment.[ncbi.nlm.nih.gov]
  • The treatment method adopted is based on the location of the lesion Prognosis is generally excellent when the lesions are small.[dovemed.com]
  • With early detection and treatment the prognosis is significantly improved.[ninds.nih.gov]
  • Prognosis depends on the size and location of the tumour, untreated angiomatosis may lead to blindness and/ or permanent brain damage. Death may occur, with complications in the kidney or brain. Angioma Hemangioma List of cutaneous conditions[en.wikipedia.org]
  • […] pleural effusions Abdomen ascites abdominal adenopathy soft-tissue masses low-attenuating lesions in the liver /- spleen 5,6 lesions often show enhancement with contrast Musculoskeletal osteomyelitis causing osteolytic bony lesions 4,7 Treatment and prognosis[radiopaedia.org]

Etiology

  • The etiology of these conditions, often associated with either localized or systemic diseases, is poorly understood.[ncbi.nlm.nih.gov]
  • […] histiocytes are frequently present Purplish grey bacterial colonies may be seen Epidemiology May affect adults and children Most commonly affects immunocompromised individuals Sites Can occur in any cutaneous site Rarely occurs in mucosa or internal organs Etiology[pathologyoutlines.com]
  • This report further discusses DDA with a review of the literature, including its classification, epidemiology, pathophysiology, etiology, histopathology, differential diagnosis, and current therapeutic approaches.[mdedge.com]
  • (Etiology) The exact cause of Angiomatosis occurrence is unknown.[dovemed.com]
  • […] n de un nuevo caso en paciente no fumadora. ( 27617469 ) Delgado-Marquez A.M....Lopez-Gomez S. 2016 31 Bacillary angiomatosis with bone invasion. ( 28099606 ) Diniz L.M....Lucas E.A. 2016 32 Diffuse Dermal Angiomatosis of the Breast With an Apparent Etiology[malacards.org]

Epidemiology

  • Comment Classification and Epidemiology Diffuse dermal angiomatosis is a rare acquired, cutaneous, reactive, vascular disorder first described by Krell et al 1 in 1994.[mdedge.com]
  • […] especially those with HIV) Essential features Lobular proliferation of capillaries with ectatic vessels lined by prominent endothelial cells Neutrophils, lymphocytes and histiocytes are frequently present Purplish grey bacterial colonies may be seen Epidemiology[pathologyoutlines.com]
  • An epidemiological and clinical study.[scielo.br]
Sex distribution
Age distribution

Pathophysiology

  • Pathophysiology The pathophysiology is not fully understood, but occlusion of blood vessel lumens appears to be common to all variants of the disease.[dermatologyadvisor.com]
  • This report further discusses DDA with a review of the literature, including its classification, epidemiology, pathophysiology, etiology, histopathology, differential diagnosis, and current therapeutic approaches.[mdedge.com]
  • Pathophysiology of Sturge-Weber syndrome. J Child Neurol. 18(8): 509—516. ; PMid:13677575 18. Demougeot C, Garnier P, Mossiat C. 2001.[med-expert.com.ua]
  • Comi Presentation, diagnosis, pathophysiology and treatment of the neurological features of Sturge–Weber Syndrome [11] O. Fernandez Concepción, A. Gómez García, N. Sardiñaz Hernandez Síndrome de Sturge Weber.[elsevier.es]

Prevention

  • CONCLUSION: In a case of angiomatosis with an associated pulmonary lobar vascular malformation, lobectomy can be safely performed to prevent life-threatening bleeding.[ncbi.nlm.nih.gov]
  • In certain cases, early detection and treatment of these lesions may prevent their disastrous effects.[ophth.wisc.edu]
  • Current medical research has not established a way of preventing Angiomatosis occurrence. What is the Prognosis of Angiomatosis? (Outcomes/Resolutions) Angiomatoses are benign, but symptomatic; hence, they may require some form of treatment.[dovemed.com]
  • Centers for Disease Control and Prevention, Atlanta, GA 30333 Jane E. Koehler, M.D. University of California, San Francisco, San Francisco, CA 94143-0654 Citing Articles (11)[nejm.org]

Ask Question

5000 Characters left Format the text using: # Heading, **bold**, _italic_. HTML code is not allowed.
By publishing this question you agree to the TOS and Privacy policy.
• Use a precise title for your question.
• Ask a specific question and provide age, sex, symptoms, type and duration of treatment.
• Respect your own and other people's privacy, never post full names or contact information.
• Inappropriate questions will be deleted.
• In urgent cases contact a physician, visit a hospital or call an emergency service!