Presentation
One was a 15-month-old boy presenting with respiratory distress. He had a right aortic arch and his left pulmonary artery originated from the innominate artery. The other was a 1-month-old girl presenting with congestive heart failure. [ncbi.nlm.nih.gov]
The time is definitely right for a comprehensive presentation of these new diagnostic modalities and the way in which they will influence the field of congenital heart management. * First and only volume on the market presenting all the pre- and post-operative [books.google.com]
Entire Body System
- Pathologist
All clinicians and scientists interested in birth defects, including pediatricians, geneticists, genetic counselors, obstetricians, and pediatric pathologists, will find this book to be an invaluable source of information. [books.google.com]
Department of Radiodiagnosis, Government Medical College and Associated Group of Hospitals, Kota - 324 001, Rajasthan India DOI : 10.4103/1115-1474.134615 The aberrant right subclavian artery (ARSA) is an anatomical abnormality encountered by anatomists and pathologists [wajradiology.org]
- Fever
Dysphagia due to an aberrant right subclavian artery is termed dysphagia lusoria, although this is a rare complication. [2] [3] In addition to dysphagia, aberrant right subclavian artery may cause stridor, dyspnoea, chest pain, or fever. [1] An aberrant [en.wikipedia.org]
Case 2 A 24-year-old man presented to our hospital with complaints of intermittent hemoptysis, left sided chest pain and intermittent high-grade fever for two weeks. He had history of long standing chest problems. [ijccm.org]
- Recurrent Respiratory Infection
Usually, patients with a double aortic arch are severely symptomatic in infancy, with stridor, dyspnea, cough, and recurrent respiratory infections. [musculoskeletalkey.com]
Respiratoric
- Stridor
Vascular rings diagnosed in patients less than 6 months of age are often associated with symptoms of airway obstruction, such as stridor (noisy breathing). [cincinnatichildrens.org]
Usually, patients with a double aortic arch are severely symptomatic in infancy, with stridor, dyspnea, cough, and recurrent respiratory infections. [musculoskeletalkey.com]
It may compress the trachea, leading to stridor, cough and dyspnea. This compression decreases with age and these patients will outgrow it. [radiologyassistant.nl]
Dysphagia due to an aberrant right subclavian artery is termed dysphagia lusoria, although this is a rare complication. [2] [3] In addition to dysphagia, aberrant right subclavian artery may cause stridor, dyspnoea, chest pain, or fever. [1] An aberrant [en.wikipedia.org]
She had no respiratory symptoms such as stridor or wheezing, and there were no signs or symptoms of congestive heart failure. [scmr.org]
- Respiratory Distress
One was a 15-month-old boy presenting with respiratory distress. He had a right aortic arch and his left pulmonary artery originated from the innominate artery. The other was a 1-month-old girl presenting with congestive heart failure. [ncbi.nlm.nih.gov]
Infants feed poorly because of severe respiratory distress and may prefer to assume an opisthotonic posture. Life-threatening episodes of apnea with cyanosis may occur. [musculoskeletalkey.com]
distress and therefore the patients should be followed carefully by their Paediatricians and Respiratory Physicians. [ijponline.biomedcentral.com]
◦ Increased respiratory distress a/w intercurrent respiratory infections. ◦ Swallowing difficulty. ◦ Occasionally, in patients with associated intracardiac anomalies ,the respiratory symptoms may be mistakenly be attributed to cardiac disease. 21. [slideshare.net]
- Dyspnea
This real vascular ring many times produces syptoms of dysphagia and dyspnea with frequent respiratory track infections. [fetalultrasound.com]
3] [6] Clinical presentation [ edit ] Symptoms include hemoptysis, and/or massive hemorrhage which result from the formation of a fistula between the trachea and the brachiocephalic artery. [1] The primary threat is respiratory compromise leading to dyspnea [en.wikipedia.org]
Usually, patients with a double aortic arch are severely symptomatic in infancy, with stridor, dyspnea, cough, and recurrent respiratory infections. [musculoskeletalkey.com]
It may compress the trachea, leading to stridor, cough and dyspnea. This compression decreases with age and these patients will outgrow it. [radiologyassistant.nl]
In infants, prior to the appearance of a mass, the presenting signs may be those of a vascular ring, namely, stridor, dyspnea, or repeated lower respiratory infections. In the adult, the most likely symptom from a vascular ring is dysphagia. [quizlet.com]
- Tracheal Deviation
The tracheal deviation to the left is seen through the translucent D Ao. Compare with Figure 36.10A. C: Cranial view shows trachea (green) and esophagus (E) compressed between Div and LCA and pulmonary artery (blue). [quizlet.com]
Gastrointestinal
- Dysphagia
Dysphagia due to an aberrant right subclavian artery is termed dysphagia lusoria, although this is a rare complication. [2] [3] In addition to dysphagia, aberrant right subclavian artery may cause stridor, dyspnoea, chest pain, or fever. [1] An aberrant [en.wikipedia.org]
It is important to recognize such variations on cross-sectional imaging modalities. [9] Our patient complains was respiratory difficulty and mild dysphagia. [wajradiology.org]
Abstract Dysphagia lusoria is the term which for years has been applied to symptomatic esophageal compression by an arteria lusoria. An arteria lusoria is an anomalous form of the right subclavian artery (figure 1). [annals.org]
In combination with an aberrant right subclavian artery it can cause a dysphagia lusoria. History and etymology The name stems from the similarity of this variant with that of a normal bovine arch. [radiopaedia.org]
Autenrieth, -. (1807-08) Zusatz zu der Abhandlung: De Dysphagia lusoria. Arch. Physiol. 8:264-268. Autenrieth, -. und -. Pfleiderer. (1807) Disseratatio inauguralis. De Dysphagia lusoria. Arch. Physiol. 7:145-188. [anatomyatlases.org]
- Choking
Choking or swallowing difficulties are more common in older children as the predominant symptoms. Occasionally, a vascular ring is discovered incidentally during evaluation of a seemingly unrelated problem. [cincinnatichildrens.org]
Symptoms- ◦ Stridor,Pneumonia,bronchitis ◦ Reflex apnoea or choking on eating. ◦ Posture of Hyperextension of neck in infant. ◦ Increased respiratory distress a/w intercurrent respiratory infections. ◦ Swallowing difficulty. ◦ Occasionally, in patients [slideshare.net]
Less commonly and usually in toddlers or older children, the presentation will be swallowing difficulty or choking on food. [quizlet.com]
Cardiovascular
- Heart Disease
Now, in full color, this leading reference offers you everything you need to treat and manage pediatric heart conditions. A comprehensive and exhaustive reference of fundamental and clinical aspects of heart disease in infancy and childhood. [books.google.com]
Usually, associated congenital heart disease is not present, but it may occur in as many as 22% of patients. Cyanotic congenital heart disease, including tetralogy of Fallot and transposition of the great arteries, predominates. [musculoskeletalkey.com]
In the United States there are now more than one million adults who have survived their congenital heart disease. [radiologyassistant.nl]
Other factors that make vascular disease more likely include Family history of vascular or heart diseases Pregnancy Illness or injury Long periods of sitting or standing still Any condition that affects the heart and blood vessels, such as diabetes or [icdlist.com]
- Vascular Disease
You are more likely to have vascular disease as you get older. [icdlist.com]
Associated vascular disease and hypertension were common. There was no mortality and few complications. Axillo-axillary bypass grafting is considered the operation of choice for patients with subclavian steal syndrome. ( Arch Surg 114:394-399, 1979) [jamanetwork.com]
Account for 15% to 20% of all congenital cardiovascular diseases. Result from errors in the embryologic development of the branchial arches, including errors of involution or migration, or abnormal persistence of vascular structures. Strong associations [slideshare.net]
This should be carried out as early as possible to avoid the development of pulmonary vascular disease. [quizlet.com]
Treatment
Emphasizes the treatment of corrected congenital heart disease for coverage of the clinical management of cardiac problems in the adolescent and young adult. [books.google.com]
Other treatments include medicines and surgery. [icdlist.com]
Even were it not for medical-legal liability, the importance of prompt recognition and correct treatment of injuries that we ourselves cause is obvious, as is the need for preventive measures to be clearly identified and adopted. [books.google.it]
Aortopexy for the treatment of tracheomalacia in children: review of the literature. [ijponline.biomedcentral.com]
Other treatments of tracheomalacia, particularly tracheal stenting, were associated with a higher rate of failure, severe morbidity and mortality. [scinapse.io]
Prognosis
[…] bleeding, seal the mediastinum, fill dead space, cover major vital structures, provide a blood supply and venous drainage, and increase the concentration of antibiotics. [3] [4] Innominate artery ligation has a 10% risk of neurological deficit. [2] Prognosis [en.wikipedia.org]
The location and extent of the dissection has important implications for treatment and prognosis. The DeBakey and Stanford classifications are illustrated in Figure 6-10. [radiologykey.com]
View Article PubMed Google Scholar Kaku B, Shimizu M, Yoshio H, Ino H, Mizuno S, Kanaya H, Ishise S, Mabuchi H: Clinical features and prognosis of japanese patients with anomalous origin of the coronary artery. [cardiothoracicsurgery.biomedcentral.com]
Etiology
This book serves these needs well through a nicely balanced focus on prevention, on the one hand, with its comprehensive review of epidemiology and etiology, and on management, on the other, with its practical comments on diagnosis, treatment and outcome [books.google.it]
Dissection (online cases 13 and 52) Etiology A dissection is a longitudinal split in the media of the aortic wall. In most cases, an intimal tear connects this medial channel with the aortic lumen. [radiologykey.com]
Embryology [Print Section] The etiology of interrupted aortic arches can be thought of in terms similar to those that describe the formation of the other arch anomalies discussed above. [quizlet.com]
McKissock. (1934-35) The etiology of the vascular symptoms of cervical rib. Br. J. Surg. 22:406-414. Blalock, A. (1947) Technique of creation of an artificial ductus arteriosus in the treatment of pulmonary stenosis. J. Thoracic Surgery 16:244-254. [anatomyatlases.org]
Epidemiology
The anomalies are organized by anatomical system and presented in a consistent manner, including details of the clinical presentation, epidemiology, embryology, treatment and prevention for each anomaly. [books.google.com]
This book serves these needs well through a nicely balanced focus on prevention, on the one hand, with its comprehensive review of epidemiology and etiology, and on management, on the other, with its practical comments on diagnosis, treatment and outcome [books.google.it]
Research output : Contribution to journal › Article Epidemiology of invasive fungal diseases in children with solid tumours undergoing autologous haematopoietic stem cell transplantation: a 10-year experience in a tertiary Italian centre Tatarelli, P. [moh-it.pure.elsevier.com]
Pathophysiology
Embryology of coronary arteries and anatomy/pathophysiology of coronary anomalies. A comprehensive update. [jtcvstechniques.org]
[…] the proximal descending aorta, the so-called Diverticulum of Kommerell (which was named for the German Radiologist, Burkhard Friedrich Kommerell (1901–1990), who discovered it in 1936). [5] [6] It is alternatively known as a lusorian artery. [1] [3] Pathophysiology [en.wikipedia.org]
Embryology of coronary arteries and anatomy/pathophysiology of coronary anomalies. A comprehensive update. Int J Cardiol. 2019;281:28–34. [PubMed] [Google Scholar] 4. Bini R.M., Nicolosi L., Alfieri O. [ncbi.nlm.nih.gov]
Ultimately, it is important to understand the pathophysiology of AOCA treatment to manage this condition effectively. [cardiothoracicsurgery.biomedcentral.com]
The pathophysiology of the interruption is thought to be an absolute decrease in left ventricular output to the ascending aorta (owing to the combination of outflow obstruction and VSD) with maintenance of normal cerebral perfusion, resulting in a P.755 [quizlet.com]
Prevention
The anomalies are organized by anatomical system and presented in a consistent manner, including details of the clinical presentation, epidemiology, embryology, treatment and prevention for each anomaly. [books.google.com]
Even were it not for medical-legal liability, the importance of prompt recognition and correct treatment of injuries that we ourselves cause is obvious, as is the need for preventive measures to be clearly identified and adopted. [books.google.it]
Patients can later present with hypovolemic shock which include symptoms of tachycardia, cyanosis, cold and clammy skin, dizziness, confusion, and fatigue. [3] [5] Patients may also develop septicemia. [3] [5] Treatment [ edit ] Prevention [ edit ] To [en.wikipedia.org]
Centers for Disease Control and Prevention Intersex (Medical Encyclopedia) [ Read More ] Vascular Diseases The vascular system is the body's network of blood vessels. [icdlist.com]
Non-visualization This means that there is an absence of a normal artery because it did not form, or it is not seen on an MRI/MRA because blockage prevents the flow of contrast through the vessel. [chw.org]