Presentation
[…] if the condition was present at the time of inpatient admission. [icd.codes]
Case history and necropsy findings of a 5-month-old infant with a unique heart defect with features of truncus arteriosus communis and aortopulmonary defect in combination with severe tricuspid stenosis are presented. [ncbi.nlm.nih.gov]
The clinical presentation of aortopulmonary septal defects is dependent on the size of the defect and on the associated lesions. The presentation is usually similar to that of other patients with left-to-right shunts. [radiopaedia.org]
We present a case of a minor infant with symptomatology of congestive heart failure; during stay in intensive care unit presents multiple co-morbidities. [go.gale.com]
Entire Body System
- Atrial Septal Defect
Q21 Congenital malformations of cardiac septa Excludes1 acquired cardiac septal defect ( I51.0 ) Q21.0 Ventricular septal defect Inclusion term(s): Roger's disease Q21.1 Atrial septal defect Inclusion term(s): Coronary sinus defect Patent or persistent [icd10coded.com]
Simple defects are those that do not require surgical repair, occur with no other defects, or those that require minor stright-forward repair ( ductus arteriosus, atrial septal defect ). [en.wikipedia.org]
Herein, for the first time in the medical literature, we present percutaneous closure of an isolated ostium secundum atrial septal defect in this syndrome. [elsevier.pt]
[…] closure (approximate) ICD-10-CM Siblings (same level / similar specificity) of Q21.4: Q21.0 - Ventricular septal defect Q21.1 - Atrial septal defect Q21.2 - Atrioventricular septal defect Q21.3 - Tetralogy of Fallot Q21.8 - Other congenital malformations [emedcodes.com]
- Congestive Heart Failure
Complications pulmonary hypertension Eisenmenger phenomenon congestive heart failure [radiopaedia.org]
We present a case of a minor infant with symptomatology of congestive heart failure; during stay in intensive care unit presents multiple co-morbidities. [go.gale.com]
This causes high blood pressure in the lungs (a condition called pulmonary hypertension) and congestive heart failure. The bigger the defect, the more blood that is able to enter the pulmonary artery. [mountsinai.org]
Commonly, the defect is large and a large left-to-right shunt is present, resulting in congestive heart failure and pulmonary vascular obstructive disease. Cyanosis is usually absent unless severe pulmonary vascular disease has developed. [tgkdc.dergisi.org]
- Asymptomatic
We report on a patient with a small aortopulmonary window, who presented with an asymptomatic murmur and in whom catheter closure was successfully performed with an Amplatzer Duct Occluder. [ncbi.nlm.nih.gov]
In isolation, these defects may be asymptomatic, or they may produce symptoms which can range from mild to severe, biological tissues may be used to construct artificial passages. [wikivisually.com]
Surgical closure is indicated in all patients with an APW, except for asymptomatic patients with small defects. In most patients, closure should be undertaken at the time of diagnosis because of the risk for pulmonary vascular disease. [tgkdc.dergisi.org]
The remaining patients are asymptomatic without treatment after a mean follow-up period of 69 months. Conclusions. [revespcardiol.org]
- Pulmonary Valve Stenosis
Intracardiac associated anomalies were as follows: ventricular septal defects (7 cases), tetralogy of Fallot (2 cases), aortic valve stenosis (2 cases), atrial septal defect (3 cases), patent ductus arteriosus (3 cases), pulmonary valve stenosis (1 case [ncbi.nlm.nih.gov]
[…] and tricuspid valves Q22.0 Pulmonary valve atresia Q22.1 Congenital pulmonary valve stenosis Q22.2 Congenital pulmonary valve insufficiency Q22.3 Other congenital malformations of pulmonary valve Q22.4 Congenital tricuspid stenosis Q22.5 Ebstein's anomaly [icd10data.com]
[…] and tricuspid valves Q22.0 Pulmonary valve atresia Q22.1 Congenital pulmonary valve stenosis Q22.2 Congenital pulmonary valve insufficiency Congenital pulmonary valve regurgitation Q22.3 Other congenital malformations of pulmonary valve Congenital malformation [apps.who.int]
It is reported to be associated with cardiovascular disorders including atrial septal defect, anomalous pulmonary venous return, aortopulmonary window, pulmonary valve stenosis, mitral valve prolapse, tetralogy of Fallot, truncus arteriosus, and patent [elsevier.pt]
- Poor Feeding
feeding and failure to thrive in infancy. [en.wikipedia.org]
Respiratoric
- Tachypnea
Clinical signs and symptoms include cyanosis that is present at birth, poor growth, dyspnea, tachypnea, arrhythmia, cardiomegaly, and heart failure. If it is not surgically repaired, it leads to death. [fpnotebook.com]
[…] sudden death急死〈頓死〉、突然死 superior vena cava (SVC)上大静脈 supraventricular premature contraction(SVPC)上室期外収縮 supraventricular tachycardia (SVT)上室頻拍 symptom 症状 syncope意識消失、失神 systole[心]収縮[期] systolic function収縮機能 systolic murmur (SM)収縮期雑音 t tachycardia 頻拍(脈) tachypnea [tokyo-med.ac.jp]
Gastrointestinal
- Failure to Thrive
[…] to thrive and respiratory distress. [jbsr.be]
A 5-month boy (weight, 3.5 kilogram) presented to our institute with complaints of failure to thrive, recurrent respiratory tract infections and progressively increasing cyanosis since birth. Oxygen saturation was recorded as 78% on room air. [bjcvs.org]
[…] to thrive in infancy. [en.wikipedia.org]
Cardiovascular
- Heart Disease
Diagnosis and Management of Adult Congenital Heart Disease, by Drs. Gatzoulis, Webb, and Daubeney, is a practical, one-stop resource designed to help you manage the unique challenges of treating long-term adult survivors of congenital heart disease. [books.google.com]
NIH: National Heart, Lung, and Blood Institute Atrial septal defect (Medical Encyclopedia) Bicuspid aortic valve (Medical Encyclopedia) Congenital heart defect corrective surgeries (Medical Encyclopedia) Congenital heart disease (Medical Encyclopedia) [icdlist.com]
Prevention of infective endocarditis: guidelines from the American Heart Association: a guideline from the American Heart Association Rheumatic Fever, Endocarditis, and Kawasaki Disease Committee, Council on Cardiovascular Disease in the Young, and the [emedicine.medscape.com]
Echocardiogram showed dilatation of left heart cavities, patent foramen ovale, small muscular ventricular septal defect and pulmonary hypertension. Angio-CT was performed on a 64-slice CT to better characterize the congenital heart disease. [jbsr.be]
- Hypertension
Echocardiography revealed severe pulmonary hypertension, and chest radiography identified signs of pulmonary hypertension. [appliedradiology.com]
A case report of surgical treatment for test tube baby suffering from congenital ventricular septal defect 試管嬰兒患先天性室間隔缺損外科治療1例 Perioperative management of ventricular septal defect with pulmonary hypertension in infants 嬰幼兒室間隔缺損伴肺動脈高壓圍術期處理 [dict.site]
Hemodynamics were the consequence of a large left-to-right shunt (mean ratio of pulmonary to systemic flow, 3.0) with right ventricular hypertension (mean right ventricular pressure, 86 mm Hg) and increased pulmonary vascular resistance (mean, 7.4 U) [ncbi.nlm.nih.gov]
A special focus has been placed on noninvasive imaging techniques, normative blood pressure standards, suggested approaches to pediatric hypertension, detection and management of lipid abnormalities as recommended by the Expert Panel, pediatric arrhythmias [books.google.com]
Complications pulmonary hypertension Eisenmenger phenomenon congestive heart failure [radiopaedia.org]
- Heart Murmur
Cyanotic heart disease (Medical Encyclopedia) Dextrocardia (Medical Encyclopedia) Echocardiogram -- children (Medical Encyclopedia) Heart murmurs and other sounds (Medical Encyclopedia) Patent ductus arteriosus (Medical Encyclopedia) Ventricular septal [icdlist.com]
murmur associated with failure to thrive and respiratory distress. [jbsr.be]
The patient was a 46-year-old woman with heart murmur which had been discovered in her childhood. She went through two pregnancies and delivered with no manifestation of heart failure. She was admitted to our hospital due to orthopnea. [webview.isho.jp]
- Continuous Murmur
Sell : Patent ductus arteriosus in the absence of a continuous murmur. Circulation 6, 110 (1952). PubMed Google Scholar Daniel, R.: Diskussion in Surgery 42, 120 (1957). Google Scholar Davis Jr., C., E. H. Fell, B. M. Gasul, and R. [link.springer.com]
[…] complete transposition of great arteries完全大血管転位[症] complication 合併症 composite graft人工弁逢着人工血管 concentric hypertrophy求心性心肥大 conduction 伝導 conduit導管 congenital heart disease (CHD) 先天性心疾患 congestive heart failure (CHF)うっ血性心不全 constrictive pericarditis 収縮性心膜炎 continuous [tokyo-med.ac.jp]
Workup
Abbreviations used APW, Aortopulmonary Window; CT, Computed Tomography; RPA, Right Pulmonary Ar-tery; References Love BA, Aortopulmonary Septal Defect: Differential Diagnoses & Workup. Emedicine 2009; March 16. [alliedacademies.org]
Axis
- Right Axis Deviation
Electrocardio-gram showed P pulmonale and features of right ventricu-lar hypertrophy and right axis deviation. 2D-echocardiography revealed severe pulmonary artery hy-pertension with dilated right atrium and ventricle and paradoxical motion of interventricular [alliedacademies.org]
Treatment
details of surgical treatment, potential complications and literature references. [books.google.com]
Many children with congenital heart defects don't need treatment, but others do. Treatment can include medicines, catheter procedures, surgery, and heart transplants. [icdlist.com]
例句 Infracristal ventricular septal defect 嵴下型室間隔缺損 Surgical treatment of ventricular septal defect with pulmonary hypertension in infants 嬰幼兒室間隔缺損並肺動脈高壓的外科治療 Pathologic anatomy and surgical treatment of muscular ventricular septal defect 肌部室間隔缺損類型與外科糾治方法探討 [dict.site]
Surgical reoperation was the treatment of choice traditionally, while associated with increased risk and suffering. [ncbi.nlm.nih.gov]
Importantly, treatment with bosentan has been shown not to reduce systemic arterial blood oxygen saturation over short- [ 42 ] and long-term treatment [ 47 ], demonstrating that it had no negative effect on the overall shunt. [err.ersjournals.com]
Prognosis
Outlook (Prognosis) Surgery to correct aortopulmonary window is successful in most cases. If the defect is treated quickly, the child should not have any lasting effects. [mountsinai.org]
The prognosis reaching the adulthood without surgery is poor. In contrast to our described congenital defect, cases of persistent ductus arteriosus are reported with the survival to age 72 and older. [thieme-connect.com]
In the absence of associated anomalies, the late results of surgical correction are excellent; however, in patients with complex anomalies, the prognosis is largely determined by the presence of these anomalies. [tgkdc.dergisi.org]
The prognosis depends on the presence of other associated congenital heart malformations 3. [scielo.br]
Treatment and prognosis Early surgical or device closure is indicated as soon as the diagnosis is established to prevent congestive heart failure and pulmonary hypertension. Associated cardiovascular defects should also be repaired. [radiopaedia.org]
Etiology
Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology. [icd10coded.com]
While its etiology remains unclear, there is some evidence concerning its embryogenic and genetic origin. 1–3 It is reported to be associated with cardiovascular disorders. [elsevier.pt]
Epidemiology
Epidemiology Frequency United States Aortopulmonary septal defect is a rare defect that comprises about 0.1-0.3% of congenital heart diseases in children. No attempt to assess regional or worldwide variation in incidence has been made. [emedicine.medscape.com]
[…] with potential placement of a local anesthetic infusion catheter under the fascia, to enhance postoperative pain control. j) Multiple muscular VSDs are a challenge to close, achieving a complete closure can be aided by the use of fluorescein dye. [15] Epidemiology [en.wikipedia.org]
Pathophysiology
The Congenital Heart Defects are presented with each chapter devoted to a single malformation, with incidence, morphology, associated anomalies, pathophysiology, diagnosis (including clinical pattern, electrocardiogram, chest X-ray, echocardiogram, cardiac [books.google.com]
The current European Society of Cardiology guidelines provide an anatomical–pathophysiological classification of the congenital left-to-right shunts associated with PAH [ 3 ]. [err.ersjournals.com]
Aortopulmonary septal defect has been described in other mammals including dogs, cats, and horses. [11] Pathophysiology The fetus is unaffected by this defect. [emedicine.medscape.com]
Pathophysiology [ edit ] During ventricular contraction, or systole, some of the blood from the left ventricle leaks into the right ventricle, passes through the lungs and reenters the left ventricle via the pulmonary veins and left atrium. [en.wikipedia.org]
Prevention
What about preventing endocarditis? Most children with an ASD are not at increased risk for developing endocarditis. [heart.org]
To prevent the narrowing of the proximal right pulmonary artery in the distal aortopulmonary septal defect caused by conventional intraluminal prosthetic patch reconstruction, rerouting of the right pulmonary artery using native aortic wall tissue without [ncbi.nlm.nih.gov]
Prevention There is no known way to prevent aortopulmonary window. References Hirsch-Romano JC, Ohye RG, Si M-S, Bove EL. Truncus arteriosus and aortopulmonary window. In: Sellke FW, del Nido PJ, Swanson SJ, eds. [mountsinai.org]
The surgery must be carried out as early as possible in order to prevent the development of the most feared complication, the irreversible pulmonary arterial hypertension. [scielo.br]
Treatment and prognosis Early surgical or device closure is indicated as soon as the diagnosis is established to prevent congestive heart failure and pulmonary hypertension. Associated cardiovascular defects should also be repaired. [radiopaedia.org]