Presentation
Intravenous immunoglobulin in the treatment of autoimmune neuromuscular diseases: present status and practical therapeutic guidelines. Muscle Nerve. 1999; 22 1479-1497 39 Donaghy M, Mills K R, Boniface S J, Simmons J, Wright I, Gregson N, Jacobs J. [thieme-connect.com]
Entire Body System
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Weakness
Lower motor neuron syndromes defined by patterns of weakness, nerve conduction abnormalities, and high titers of antiglycolipid antibodies. Ann Neurol. 1990; 27 316-326 PD Dr. [thieme-connect.com]
Demyelination and axonal loss in multifocal motor neuropathy: distribution and relation to weakness. Brain 2003;126(Pt 1):186–198. PubMed View Article Kuijf ML, van Doorn PA, Tio-Gillen AP, Geleijns K, Ang CW, Hooijkaas H, Hop WC, Jacobs BC. [springermedizin.de]
Neurologic
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Polyradiculoneuropathy
Treatment of chronic immune-mediated neuropathies: chronic inflammatory demyelinating polyradiculoneuropathy, multifocal motor neuropathy, and the Lewis-Sumner syndrome. Semin Neurol 2010;30(4):443–456. PubMed View Article Nobile-Orazio E. [springermedizin.de]
Multifocal motor neuropathy and chronic inflammatory demyelinating polyradiculoneuropathy. [thieme-connect.com]
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Myokymia
Motor neuropathy with proximal multifocal persistent conduction block, fasciculations and myokymia. Evolution to tetraplegia. Eur Neurol 1986;25(6):416–423. [springermedizin.de]
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Limb Weakness
A syndrome of asymmetric limb weakness with motor conduction block. Neurology. 1990; 40 118-127 30 Report from an Ad Hoc Subcommittee of the American Academy of Neurology AIDS Task Force. [thieme-connect.com]
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Polyneuropathy
IgM antibody-related polyneuropathies: B-cell depletion chemotherapy using Rituximab. Neurology. 1999; 52 1701-1704 62 Scheglmann K, Rentz E. [thieme-connect.com]
Treatment
In some patients, however, disease progression may be observed despite of regular IVIG treatment. As long-lasting IVIG treatment is expensive, combination with cyclophosphamide may be performed to reduce the IVIG dosage. [thieme-connect.com]
Follow-up study and response to treatment in 23 patients with Lewis-Sumner syndrome. Brain 2004;127(Pt 9):2010–2017. [springermedizin.de]
Pathophysiology
Multifocal motor neuropathy: update on clinical characteristics, pathophysiological concepts and therapeutic options. Eur Neurol 2010;63(4):193–204. PubMed View Article Nobile-Orazio E, Cappellari A, Priori A. [springermedizin.de]