Intravenous immunoglobulin in the treatment of autoimmune neuromuscular diseases: present status and practical therapeutic guidelines. Muscle Nerve. 1999; 22 1479-1497 39 Donaghy M, Mills K R, Boniface S J, Simmons J, Wright I, Gregson N, Jacobs J. [thieme-connect.com]

• Weakness

  Lower motor neuron syndromes defined by patterns of weakness, nerve conduction abnormalities, and high titers of antiglycolipid antibodies. Ann Neurol. 1990; 27 316-326 PD Dr. [thieme-connect.com]

  Demyelination and axonal loss in multifocal motor neuropathy: distribution and relation to weakness. Brain 2003;126(Pt 1):186–198. PubMed View Article Kuijf ML, van Doorn PA, Tio-Gillen AP, Geleijns K, Ang CW, Hooijkaas H, Hop WC, Jacobs BC. [springermedizin.de]

• Polyradiculoneuropathy

  Treatment of chronic immune-mediated neuropathies: chronic inflammatory demyelinating polyradiculoneuropathy, multifocal motor neuropathy, and the Lewis-Sumner syndrome. Semin Neurol 2010;30(4):443–456. PubMed View Article Nobile-Orazio E. [springermedizin.de]

  Multifocal motor neuropathy and chronic inflammatory demyelinating polyradiculoneuropathy. [thieme-connect.com]

• Myokymia

  Motor neuropathy with proximal multifocal persistent conduction block, fasciculations and myokymia. Evolution to tetraplegia. Eur Neurol 1986;25(6):416–423. [springermedizin.de]

• Polyneuropathy

  IgM antibody-related polyneuropathies: B-cell depletion chemotherapy using Rituximab. Neurology. 1999; 52 1701-1704 62 Scheglmann K, Rentz E. [thieme-connect.com]

In some patients, however, disease progression may be observed despite of regular IVIG treatment. As long-lasting IVIG treatment is expensive, combination with cyclophosphamide may be performed to reduce the IVIG dosage. [thieme-connect.com]

Follow-up study and response to treatment in 23 patients with Lewis-Sumner syndrome. Brain 2004;127(Pt 9):2010–2017. [springermedizin.de]

Multifocal motor neuropathy: update on clinical characteristics, pathophysiological concepts and therapeutic options. Eur Neurol 2010;63(4):193–204. PubMed View Article Nobile-Orazio E, Cappellari A, Priori A. [springermedizin.de]