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Atrophodermia Vermiculata

Atrophoderma Vermiculatum


Presentation

  • Atrophodermia vermiculata presents with erythematous follicular papules on the cheeks in childhood and, with time, the lesions develop into pit-like depressions. Skin lesion Cicatricial alopecia Ulerythema List of cutaneous conditions[en.wikipedia.org]
  • Two patients, a father and a daughter, with atrophoderma vermiculatum are presented. Pedigree of a family with atrophoderma vermiculatum.[sayarujoyujy.cf]
  • Two patients, a father and a daughter, with atrophoderma vermiculatum are presented.[medigoo.com]
  • Classification of these conditions often presents many nosological challenges, since underlying etiologies and pathogenetics are often not known.[howlingpixel.com]
Asymptomatic
  • Erythema and pinhead follicular plugs developing mainly on the cheeks are soon followed by asymptomatic, sharply demarcated, pit-like or net-like impressions. The forehead, chin, helices and air lobes may also be affected.[dermis.net]
  • Erythema and pinhead follicular plugs developing mainly on the cheeks are soon followed by asymptomatic, sharply demarcated, pit-like or net-like impressions. Symptoms - Atrophodermia vermiculata Not supplied.[checkorphan.org]
Hodgkin's Disease
  • ’s disease NHL, MF, MM, and carcinomatosis Sarcoidosis, especially over the lower extremities Others: leprosy, nutritional deficiency, AIDS, human T-cell lymphocytic virus, LE, etc. 8 Pityriasis Rotunda Perfectly circular scaly patches on the torso and[slideplayer.com]
Cyanosis
  • Atrophoderma vermiculatum also is a key feature of Rombo syndrome, an autosomal dominant disorder characterized by AV, milia, hypotrichosis, trichoepitheliomas, basal cell carcinomas, and peripheral vasodilation with cyanosis.[medigoo.com]
  • Rombo syndrome is a very rare genetic disorder characterized mainly by atrophoderma vermiculatum of the face, : 580 multiple milia, telangiectases, acral erythema, peripheral vasodilation with cyanosis and a propensity to develop basal cell carcinomas[sayarujoyujy.cf]
  • […] producing cribiform or honeycomb surface Worm-eaten(vermiculate) appearance Cause is undertermined Skin covering the ridges is even with normal skin 63 Keratosis Follicularis Spinulosa Decalvans(Siemens-1 Syndrome) Rombo syndrome Atrophodermia vermiculata, cyanosis[slideplayer.com]
  • Patients typically have a history of intrauterine growth retardation, low birth weight, feeble cry, weak suck and failure to thrive and present with inspiratory stridor, recurrent episodes of dyspnea or apnea, cyanosis and absent deep tendon reflexes.[mendelian.co]
Keratosis
  • Treatment of keratosis pilaris atrophicans with the pulsed tunable dye laser. J Cutan Laser Ther. 2000; 2 :151–156. [ PubMed ] [ Google Scholar ] Golusin Z, Jovanović M, Poljacki M. Atrophic pilar keratosis of the face: case report.[ncbi.nlm.nih.gov]
  • […] by keratosis pilaris and atrophy of the skin.[revistasrd.ro]
Papule
  • Atrophodermia vermiculata presents with erythematous follicular papules on the cheeks in childhood and, with time, the lesions develop into pit-like depressions. Skin lesion Cicatricial alopecia Ulerythema List of cutaneous conditions[en.wikipedia.org]
  • Eight months later the patient showed tiny, atrophic depressions and follicular plugs with reticulate teleangectases in the same area of the right cheek (with disappearance of the tiny papules). A clinical diagnosis of AV was done.[unboundmedicine.com]
  • Multiple inflammatory symmetric papules on the cheeks, presumably centered around hair follicles, may precede the atrophic lesions. These papules then go on to develop pitted, atrophic, and depressed scars in a reticulated or honeycomb pattern . .[dermaamin.com]
  • Multiple inflammatory symmetric papules on the cheeks, presumably centered around hair follicles, may precede the atrophic lesions. These papules then go on to develop pitted, atrophic, and depressed scars in a reticulated or honeycomb pattern..[dermaamin.com]
Skin Lesion
  • Skin lesion Cicatricial alopecia Ulerythema List of cutaneous conditions[en.wikipedia.org]
  • See also Skin lesion Cicatricial alopecia Ulerythema List of cutaneous conditions[wikidoc.org]
  • lesion Cicatricial alopecia Ulerythema List of cutaneous conditions References James, William; Berger, Timothy; Elston, Dirk (2005).[popflock.com]
  • Clinically, the diagnosis of any particular skin condition is made by gathering pertinent information regarding the presenting skin lesion(s), including the location (such as arms, head, legs), symptoms (pruritus, pain), duration (acute or chronic), arrangement[howlingpixel.com]
Follicular Plugging
  • The degree of inflammation, the presence of milia, and the extent of follicular plugs are variable. As seen in our patient, AV tends to be symmetric, but unilateral involvement has been reported.[medigoo.com]
  • Atrophodermia vermiculata is characterized by erythema and follicular plugs on the cheeks, developing into painless reticular impressions.[ncbi.nlm.nih.gov]
  • Erythema and pinhead follicular plugs developing mainly on the cheeks are soon followed by asymptomatic, sharply demarcated, pit-like or net-like impressions. The forehead, chin, helices and air lobes may also be affected.[dermis.net]

Workup

  • Subsequent workup, with particular attention to his history and presentation, led to his diagnosis.[stanfordchildrens.org]
Hepatocellular Carcinoma
  • carcinoma Ulcerative colitis Prolonged prothrombin time Vitamin D deficiency Vitamin E deficiency Cholangiocarcinoma Hyperammonemia Systemic lupus erythematosus Proximal muscle weakness in lower limbs Decreased number of peripheral myelinated nerve fibers[mendelian.co]

Treatment

  • A) Patient before treatment: grouped, pitlike atrophic scars over the cheek, B) Improved cosmetic appearance of the skin after systemic treatment with isotretinoin.[ncbi.nlm.nih.gov]
  • Treatment: Management of atrophoderma vermiculatum is challenging. Atrophoderma vermiculatum is mainly a cosmetic problem.[medigoo.com]
  • Unfortunately, there was no improvement and the treatment was discontinued. At the age of 12 years, the patient underwent a rectus transposition procedure to correct his strabismus.[docksci.com]

Prognosis

  • Prognosis - Atrophodermia vermiculata Not supplied. Treatment - Atrophodermia vermiculata Not supplied. Resources - Atrophodermia vermiculata[checkorphan.org]
  • PMID: 9218894 Prognosis Marqueling AL, Gilliam AE, Prendiville J, Zvulunov A, Antaya RJ, Sugarman J, Pang ML, Lee P, Eichenfield L, Metz B, Goldberg GN, Phillips RJ, Frieden IJ Arch Dermatol 2006 Dec;142(12):1611-6. doi: 10.1001/archderm.142.12.1611.[ncbi.nlm.nih.gov]
  • Atrophoderma vermiculata information including symptoms, diagnosis, misdiagnosis, treatment, causes, patient stories, videos, forums, prevention, and prognosis.[sayarujoyujy.cf]
  • The prognosis is good, with many instances of spontaneous regression. Primarily a cosmetic problem, therapy for this condition is aimed at reassurance, genetic counseling, and dermabrasion where appropriate.[medigoo.com]
  • Prognosis Usually slowly progressive; spontaneous regression has been reported. Management Dermabrasion, cryotherapy, UV light radiation, topicals, CO2 and 585 nm pulsed dye lasers.[medical-dictionary.thefreedictionary.com]

Etiology

  • Our ability to treat acne and rosacea ef fectively has outpaced the vastly expanded understanding of their etiologies. Acne today is not only an eminently treatable disease; in some cases, for exam is actually curable.[books.google.ro]
  • Classification of these conditions often presents many nosological challenges, since underlying etiologies and pathogenetics are often not known.[howlingpixel.com]
  • Etiology J Eur Acad Dermatol Venereol 2003 Jan;17(1):70-2. PMID: 12602976 Diagnosis Schaller J, Rytina E, Rütten A, Hendricks C, Ha T, Requena L J Cutan Pathol 2010 Sep;37(9):1002-9. Epub 2010 Feb 18 doi: 10.1111/j.1600-0560.2010.01527.x.[ncbi.nlm.nih.gov]
  • Etiology — traumatic injury of nerves, and also toxic or infectious polyneuritis, myelosyringosis, tabes, rheumatism, gout, leprosy. Clinically damage of skin of extremities, preferential fingers is noted.[bigmed.info]

Epidemiology

  • Neurology and Neurosurgery Czech and Slovak Ophthalmology Czech and Slovak Psychiatry Czech Geriatric Review Czech Gynaecology Czech Rheumatology Czech Dental Journal Czech Urology Czech-Slovak Dermatology Czecho-Slovak Pathology Czech-Slovak Pediatrics Epidemiology[prolekare.cz]
  • Epidemiology Frequency United States The exact incidence of idiopathic atrophoderma of Pasini and Pierini is not known. The small number of cases reported may reflect its asymptomatic nature rather than its true incidence.[emedicine.medscape.com]
Sex distribution
Age distribution

Pathophysiology

  • .- Etiology, Pathophysiology, and Nosology of Acne.- Prevalence.- A Precis of Pathogenesis.- Anatomy of Follicles.- Epidermal Lipids.- Sebaceous Glands.- Anatomy of Sebaceous Glands.- Physiology of Sebaceous Glands.- Micro-organisms.- Cocci.- Yeasts.-[hoepli.it]
  • Pathophysiology The cause of atrophoderma of Pasini and Pierini is not known. The pathophysiologic events that cause the discrete lesions seen clinically, as well as the timing of their appearance, are also unknown.[emedicine.medscape.com]
  • Palm-plantar hyperkeratosis, photophobia, corneal abnormalities and atopies can be associated. 1 Men are more seriously affected by the disease. 1 The pathophysiology of the destruction of the pilar follicle is not well known yet.[scielo.br]

Prevention

  • Topical comedolytic agents such as retinoids prescribed at the incipient stage might then prevent the evolution of the full-fledged disorder. This therapeutic maneuver could prevent the dreaded sequel of scarring.[books.google.ro]
  • Prevention - Atrophodermia vermiculata Not supplied. Diagnosis - Atrophodermia vermiculata Not supplied. Prognosis - Atrophodermia vermiculata Not supplied. Treatment - Atrophodermia vermiculata Not supplied. Resources - Atrophodermia vermiculata[checkorphan.org]
  • Atrophoderma vermiculata information including symptoms, diagnosis, misdiagnosis, treatment, causes, patient stories, videos, forums, prevention, and prognosis.[sayarujoyujy.cf]
  • Your skin Holds body fluids in, preventing dehydration Keeps harmful microbes out, preventing infections Helps you feel things like heat, cold, and pain Keeps your body temperature even Makes vitamin D when the sun shines on it Anything that irritates[icdlist.com]
  • Specialty Editor Board Robert A Schwartz, MD, MPH Professor and Head of Dermatology, Professor of Pathology, Pediatrics, Medicine, and Preventive Medicine and Community Health, Rutgers New Jersey Medical School; Visiting Professor, Rutgers University[emedicine.medscape.com]

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