It is present in 0.5 to 2 % of live births (1). [merckmanuals.com]

• Fever

  People with infective endocarditis may develop fever. If aortic stenosis or aortic regurgitation develops, the person may tire easily, and have shortness of breath, fainting, awareness of heartbeats (palpitations), and chest pain. [merckmanuals.com]

• Pain

  If aortic stenosis or aortic regurgitation develops, the person may tire easily, and have shortness of breath, fainting, awareness of heartbeats (palpitations), and chest pain. [merckmanuals.com]

• Fatigue

  Symptoms depend on the type of complication and can include fever in infective endocarditis or dyspnea, fatigue, syncope, palpitations, and exercise intolerance due to valvular regurgitation or stenosis. [merckmanuals.com]

• Asymptomatic

  Circulation 119(6):880–890, 2009. doi: 10.1161/CIRCULATIONAHA.108.795401 Children with bicuspid aortic valve may be asymptomatic if there is little or no valve dysfunction. [merckmanuals.com]

• Dyspnea

  Symptoms depend on the type of complication and can include fever in infective endocarditis or dyspnea, fatigue, syncope, palpitations, and exercise intolerance due to valvular regurgitation or stenosis. [merckmanuals.com]

• Regurgitation

  If aortic stenosis or aortic regurgitation develops, the person may tire easily, and have shortness of breath, fainting, awareness of heartbeats (palpitations), and chest pain. [merckmanuals.com]

• Palpitations

  If aortic stenosis or aortic regurgitation develops, the person may tire easily, and have shortness of breath, fainting, awareness of heartbeats (palpitations), and chest pain. [merckmanuals.com]

• Ejection Murmur

  Examination reveals an early systolic click, a systolic ejection murmur and, if aortic regurgitation is present, a diastolic decrescendo murmur. Echocardiography Diagnosis is by physical examination findings and echocardiography. [merckmanuals.com]

• Chest Pain

  If aortic stenosis or aortic regurgitation develops, the person may tire easily, and have shortness of breath, fainting, awareness of heartbeats (palpitations), and chest pain. [merckmanuals.com]

• Heart Murmur

  Doctors suspect a bicuspid aortic valve if they hear a heart murmur or a clicking sound during an examination with a stethoscope. Echocardiography is then done to confirm the diagnosis. [merckmanuals.com]

Balloon dilation or surgical repair Treatment of bicuspid aortic valve is indicated if severe valve dysfunction develops and if symptoms occur. Treatment consists of balloon dilation or surgical repair of stenotic valves. [merckmanuals.com]

Tadros TM, Klein MD, Shapira OM: Ascending aortic dilatation associated with bicuspid aortic valve: pathophysiology, molecular biology, and clinical implications. [merckmanuals.com]