Presentation
A rationalisation of the 1350 boxes used throughout the book gives a simpler and clearer presentation of the various categories. [books.google.com]
A 66-year-old man with bronchiectasis presented with shortness of breath to the emergency department of our institution, a district hospital in the UK. His medications included long-term supplemental oxygen therapy and prophylactic azithromycin. [ncbi.nlm.nih.gov]
The vast majority of individuals with CF present as clear cut cases. [cfmedicine.com]
Case Presentation Our patient first presented at age 57 with chronic productive cough, shortness of breath, fever, weight loss and occasional wheezing. He is a non-smoker and has a daughter. [article.sapub.org]
Large airway rhonchi are present in 44% (low-pitched snore-like sounds) [ 1 ]. Wheeze may be present in 34%. Clubbing is found infrequently. All causes of bronchiectasis should be considered and assessed as appropriate. [patient.info]
Entire Body System
- Collapse
She suggested that duration of cough and pulmonary symptoms was commonly of three months duration or less in children with reversible bronchiectasis and pulmonary collapse which reexpanded. [hawaii.edu]
Other important respiratory complications include allergic bronchopulmonary aspergillosis, pneumothorax (which carries a bad prognosis because of associated severe lung disease), massive haemoptysis, and lung or lobar collapse. [erswhitebook.org]
X-Ray chest was suggestive of (R) sided collapse consolidation with cystic bronchiectasis (Picture 1-Röntgen of lungs). [tmg.org.rs]
The affected airways are inflamed and easily collapse. There is an impairment of airflow and drainage of secretions, leading to the accumulation of a large amount of mucus in the lungs. [patient.info]
"Recruiting collapsed lung through collateral channels with positive end-expiratory pressure". Scandinavian Journal of Respiratory Diseases. 60 (5): 260–6. PMID 392747. ^ Groth, S.; Stafanger, G.; Dirksen, H.; Andersen, J. B.; Falk, M.; Kelstrup, M. [en.wikipedia.org]
- Military Personnel
Prebronchographic roentgen manifestations observed among military personnel AJR 1944;51:537-47. 7. Ochsner A. Bronchiectasis. Disappearing pulmonary lesion. NY State J Med 1975;75:1683-9. [ PUBMED ] 8. Kinney WM. Bronchiectasis. A neglected disease. [thoracicmedicine.org]
Cardiovascular
- Hypertension
What is chronic pulmonary hypertension and how do we evaluate it? Chronic pulmonary hypertension is an increase in the blood pressure of the blood vessels of the lungs. [ssa.gov]
Another more unusual gastrointestinal complication is biliary cirrhosis leading to portal hypertension. As patients survive longer, systemic complications become more prominent. [erswhitebook.org]
Specialists in Asthma, Allergies, Pulmonary Hypertension, Sarcoidosis, Interstitial Lung diseases, Dyspnea evaluation, Lung Cancer, Occupational lung diseases, other Pulmonary disorders, Sleep disorders and Critical care medicine. [orlandolungdoctors.com]
Pancreatic insufficiency Malabsorption Chronic idiopathic pancreatitis Meconium ileus Distal ileal obstruction syndrome Biliary disease Biliary Disease: In 2-5% of patients Develop focal biliary cirrhosis Due to thickened bile Present with symptomatic portal hypertension [radiology.vcu.edu]
[…] cholestasis à jaundice, focal biliary cirrhosis Elevations in alk phos Lobular hepatomegaly Commonly see asymptomatic liver disease on autopsy In a minority of patients, liver disease is progressive with periportal fibrosis, cirrhosis, symptomatic portal hypertension [pedclerk.bsd.uchicago.edu]
Skin
- Ulcer
Bronchiectasis in a 33 year old man with ulcerative colitis. Ann Aller Asthma Immunol 1999;83:505-9. [ PUBMED ] 46. Eaton TE, Lambie N, Wells AU. Bronchiectasis following colectomy for Crohn's disease. [thoracicmedicine.org]
Workup
An extensive workup was negative including liver function tests, viral hepatitis panel, Alpha 1 antitrypsin (stool, blood), abdominal ultrasound and upper GI endoscopy. [tmg.org.rs]
There are multiple case reports of complete resolution of bronchiectasis, after removal of the foreign body via fibro-optic bronchoscopy. [92], [93], [94] Other diagnostic workup is outlined in [Table - 3]. [thoracicmedicine.org]
Colonoscopy
- Colitis
Bronchiectasis in a 33 year old man with ulcerative colitis. Ann Aller Asthma Immunol 1999;83:505-9. [ PUBMED ] 46. Eaton TE, Lambie N, Wells AU. Bronchiectasis following colectomy for Crohn's disease. [thoracicmedicine.org]
Treatment
[…] and decreased to levels similar to stable patients after antibiotic treatment; Aginine was increased in all groups, with a further increase after antibiotic treatment; -DWI tracked respiratory exacerbation and effectiveness of treatment; a good correlation [research.unipd.it]
Despite prior optimal treatment according to recommended practice guidelines [7], her lung function declined significantly in the two months prior to treatment. [elynsgroup.com]
Newer treatments are likely to be even more expensive. The emerging issue of the costs of genotype-specific treatments will be discussed in detail later. [erswhitebook.org]
Because of improved treatment and life expectancy, about 54% of patients in the US with CF are adults. Resources In This Article Cystic Fibrosis (CF) Cystic Fibrosis [msdmanuals.com]
Prognosis
Complications The complications of bronchiectasis include: Recurrent infection Life-threatening haemoptysis Lung abscess Pneumothorax Poor growth and development Prognosis The long-term prognosis is entirely dependent on the underlying cause. [teachmepaediatrics.com]
Oral supplements, enteral feeds w/ gastrostomy to increase caloric intake Routine vaccinations, including annual influenza vaccine Regular monitoring: pulmonary function tests, CXRs, bone density, glucose, and respiratory cultures for P. aeruginosa Prognosis [pedclerk.bsd.uchicago.edu]
Other important respiratory complications include allergic bronchopulmonary aspergillosis, pneumothorax (which carries a bad prognosis because of associated severe lung disease), massive haemoptysis, and lung or lobar collapse. [erswhitebook.org]
Make an Appointment Our Specialties Our Promise To You Our promise to all of our patients is that you will fully understand your condition, prognosis and treatment plans. [orlandolungdoctors.com]
This case report also shows that despite the longstanding nature of the disease the sequelae of CF can be ameliorated, including the improvement in FEV1 and weight which will improve prognosis in CF [8,9]. [elynsgroup.com]
Etiology
A ciliary defect is thought to be the etiology but has not been consistently demonstrated (15). [hawaii.edu]
Am J Respir Cell Mol Biol. 2009; 41(5): 620. 4 Bronchiectasis in a diverse US population: effects of ethnicity on etiology and sputum culture. McShane PJ, Naureckas ET, and Strek ME. [floridamd.com]
Although BE is commonly due to cystic fibrosis (CF) in developed countries, non-CF etiologies are also common in developing countries [ 1, 2, 3 ]. [karger.com]
However, the etiology for the cystic fibrosis was uncertain. He was well until age 16, when adynamia, chronic cough, and dyspnea during exercise ensued. His pulmonary symptoms worsened, and the cough became productive. [tmg.org.rs]
Table 1, summarized the possible etiological factors associated with bronchiectasis [9]. Table 1. [article.sapub.org]
Epidemiology
Epidemiology, airway defense mechanisms, pathogenesis, imaging and genetic causes of bronchiectasis are discussed. Allergic bronchopulmonary aspergillosis is addressed, as well as non-tuberculous mycobacteria as a cause of bronchiectasis. [books.google.com]
Use this guideline to: Review the epidemiology and risk of rupture of an AAA at various aortic diameters. Ask your learners what the differential diagnosis is of each a pulsatile abdominal mass and a ruptured aortic aneurysm. [annals.org]
Epidemiology In the UK, the estimated prevalence of non-CF bronchiectasis is 172/million children aged Pathophysiology There are several aetiologies of non-CF bronchiectasis, which are categorised below. [teachmepaediatrics.com]
Changing epidemiology and clinical issues arising in an ageing cystic fibrosis population. Ther Adv Respir Dis. 2011;5(2):105-19. [ Links ] 8. Burgel PR, Bellis G, Olesen HV., Viviani L, Zolin A, Blasi F, et al. [scielo.isciii.es]
Konstan MW, Morgan WJ, Butler SM, Pasta DJ, Craib ML, Silva SJ, Stokes DC, Wohl ME, Wagener JS, Regelmann WE, Johnson CA; Scientific Advisory Group and the Investigators and Coordinators of the Epidemiologic Study of Cystic Fibrosis. [tmg.org.rs]
Pathophysiology
In the absence of CFTR function, this downregulation is relieved, and sodium reabsorption increases, contributing to reduction in fluid volume and probably to the airway pathophysiology. [pedsinreview.aappublications.org]
In this article, we will discuss the pathophysiology, clinical features, management and complications of bronchietasis. [teachmepaediatrics.com]
Pathophysiology and management of pulmonary infections in cystic fibrosis. [article.sapub.org]
Bronchiectasis is a chronic lung disease whose pathophysiology is poorly understood. It has traditionally been considered "permanent and irreversible" (1). [hawaii.edu]
Prevention
Rapidly find the answers you need with separate sections on diseases and disorders, differential diagnosis, clinical algorithms, laboratory results, and clinical preventive services, plus an at-a-glance format that uses cross-references, outlines, bullets [books.google.com]
Goals of CF include: a) preventing and controlling lung infections b) loosening and removing thick, sticky mucus c) preventing or treating blockages in the intestines d) providing enough nutrition e) preventing dehydration Treatment of CF -depends on [quizlet.com]
Antibiotics are used for the treatment of acute exacerbations and prevention of exacerbations. Sputum cultures should be obtained prior to antibiotic therapy, and will help with antibiotic choices. [floridamd.com]
His recurrent pneumonias were prevented and his productive cough decreased, going from 6 to 7 teaspoons of daily sputum production to just 2 teaspoons. [jtd.amegroups.com]