The pathological features are not specific for EHK, but can be seen in other benign and malignant dermatoses, such as pilar cysts, seborrheic keratosis, squamous cell carcinoma, verrucous keratosis, lichenoid amyloidosis, and granuloma annulare. [ommegaonline.org]

The name “epidermolytic hyperkeratosis” was introduced by Frost and Van Scott for the autosomal dominant blistering form of congenital ichthyosis [1]. It presents at birth with generalized erythema, blisters, and erosions. [ommegaonline.org]

It is characterised by blisters, skin fragility and ichthyosis. What does it look like? From birth the skin is noted to be fragile with blisters and peeling. [ichthyosis.org.uk]

Affected babies may have very red skin (erythroderma) and severe blisters. [ghr.nlm.nih.gov]

Epidermolytic Hyperkeratosis definition A form of congenital ichthyosis inherited as an autosomal-dominant trait and characterized by generalized blistering, erythroderma and severe hyperkeratosis.It is manifested at birth by widespread bullae followed [dermis.net]

Within a few weeks from birth, erythroderma and blister formation diminish and hyperkeratoses develop. [genecards.org]