Presentation
A 5-day-old infant was found to have an unusual presentation of a congenital liver cyst. [ncbi.nlm.nih.gov]
In most of the reports presented, the cases were diagnosed and confirmed on ultrasonography. [jiaps.com]
Liver, Gall & Pancreas
- Liver Mass
Fetal ultrasound revealed a pelvic cystic mass measuring 3.4 x 2.9 x 3.7 cm. [acgcasereports.gi.org]
The vast majority is asymptomatic; they are usually discovered incidentally during work-up of abdominal pain, and appear as smooth-walled water-filled liver masses (Figure 7). [clinicaladvisor.com]
Workup
[…] liver can be seen along the portal tracts of the liver at CT and MRI.It is key to make an accurate diagnosis of peribiliary cyst because complications secondary to peribiliary cysts, such as obstructive jaundice, can arise, and may avoid unnecessary workup [slideshare.net]
Treatment
Surgery Surgery is the most common treatment for liver cysts that do not respond to other forms of treatment and which are particularly large. [healthyliving.azcentral.com]
Simple cysts Most patients with simple cysts are asymptomatic and require no treatment. When the cysts become large and cause symptoms, such as pain, treatment is warranted. [emedicine.medscape.com]
In conclusion, laparoscopy allowed final diagnosis and simultaneous treatment of an infant with the rare combination of a liver cyst and a diaphragmatic defect. [ncbi.nlm.nih.gov]
Treatment In most of the cases, no treatment is required; however, the treatment, when necessary, may vary according to the cause. Generally, large and painful hepatic cysts are drained by the doctor. [buzzle.com]
Prognosis
Prognosis Pyogenic liver abscess : advances in diagnostic and interventional radiology over the period of three decades have reduced the mortality rate from 9-80% to 5-30%. [ 27 ] Factors that affect prognosis include presence of shock, acute kidney injury [patient.info]
Prognosis [ edit ] Mortality is indirect and caused by complications. [en.wikipedia.org]
When symptomatic, gallbladder carcinoma is typically extensive with poor prognosis. [clinicaladvisor.com]
Etiology
All conventional diagnostics, including magnetic resonance imaging (MRI), failed to clarify its etiology definitively. Moreover, a phrenic irregularity was suspected at the site of Morgagni. [ncbi.nlm.nih.gov]
[…] cystadenoma. https://twitter.com/GIPathologyURMC/status/859076314862628864 Autosomal dominant polycystic kidney disease involving liver https://twitter.com/JMGardnerMD/status/875715108651094016 https://twitter.com/rositadeolivop1/status/882008688747327488 Etiology [humpath.com]
They grow slowly and most are detected in the 4th and 5th decades of life (3) Their etiology is unknown, although, it is hypothesized that such cysts are produced in aberrant bile ducts by either inflammatory or obstructive processes (4) or by a vascular [fetalultrasound.com]
We discuss the etiology, differential diagnosis, and treatment options for this rare entity. Key words Solitary Liver Biliary Cyst Congenital Newborn This is a preview of subscription content, log in to check access. [link.springer.com]
Epidemiology Frequency: hepatic hemangioma (most common) > focal nodular hyperplasia ( FNH ) > hepatocellular adenoma (rare) Sex: ♀ > ♂ (∼ 6:1) Age: can appear at any age, but mostly affects young women Most often an incidental finding on imaging tests Etiology [amboss.com]
Epidemiology
Giorgio A, Esposito V, Farella N, et al ; Amebic liver abscesses: a new epidemiological trend in a non-endemic area? In Vivo. 2009 Nov-Dec23(6):1027-30. [patient.info]
Benign liver tumors General Epidemiology Frequency: hepatic hemangioma (most common) > focal nodular hyperplasia ( FNH ) > hepatocellular adenoma (rare) Sex: ♀ > ♂ (∼ 6:1) Age: can appear at any age, but mostly affects young women Most often an incidental [amboss.com]
Abu-Wasel, B., et al., Pathophysiology, epidemiology, classification and treatment options for polycystic liver diseases. World J Gastroenterol, 2013. 19(35): p. 5775-86. 4. [rarediseases.org]
After cholangitis occurs, patients typically die within 5–10 years. [3] Epidemiology [ edit ] Caroli disease is typically found in Asia, and diagnosed in persons under the age of 22. Cases have also been found in infants and adults. [en.wikipedia.org]
Caremani M, Vincenti A, Benci A: Echographic epidemiology of non parasitic hepatic cysts. J Clin Ultrasound; 1993; 2: 115-8. 4. Plard L, Guedin P, Le Pennec V, Chiche L : Kystes hépatiques dits « kystes biliaires du foie ». [ispub.com]
Pathophysiology
Temmerman, F., et al., Systematic review: the pathophysiology and management of polycystic liver disease. Aliment Pharmacol Ther, 2011. 34(7): p. 702-13. 8. [rarediseases.org]
Singh V, Bhalla A, Sharma N, et al ; Pathophysiology of jaundice in amoebic liver abscess. Am J Trop Med Hyg. 2008 Apr78(4):556-9. [patient.info]
Prevention
Continued Can Polycystic Liver Disease Be Prevented? There is not much you can do to prevent the growth of liver cysts if you have PLD. [webmd.com]
To prevent surgical complications, clinicians should perform adequate management and use of devices. To prevent postoperative recurrence of cysts, performing complete deroofing is essential. [karger.com]
This approach prevents the fluid from accumulating within the cyst. However, in a small proportion of patients the cyst walls come together again, heal, and the cyst re-accumulates with subsequent recurrence of the symptoms. [laparoscopicspecialist.co.uk]
In cases where the proportion of the cyst wall that can be excised easily is small, omentum should be positioned on a pedicle into the cyst cavity to prevent closure of the roof defect and cyst recurrence. [emedicine.medscape.com]
Screening and prevention of colorectal cancer Source: Finnish Medical Society Duodecim This article is freely available only to users in the UK. [evidence.nhs.uk]