Symptoma

Congenital Mesoblastic Nephroma

Classic Congenital Mesoblastic Nephroma

In this report, the clinical presentation and the pathological features of congenital mesoblastic nephroma are also reviewed from available literature. [ncbi.nlm.nih.gov]

  • Fishing

    FISH analysis using a chromosome 11-centromere probe detected trisomy or tetrasomy 11 in all three tumors with the ETV6-NTRK3 fusion signal. [ncbi.nlm.nih.gov]

  • Sore Throat

    There was no history of fever, increased frequency of urine, sore throat, pyoderma, swelling of body or abdomen or periorbital puffiness, skin rash, or drug intake. No antenatal USG was available. [indianjnephrol.org]

  • Hypertrophic Pyloric Stenosis

    Coincidental findings were congenital hypertrophic pyloric stenosis (CHPS) and nephrocalcinotic hypercalcemia that reverted after nephrectomy. As of the day of writing, this multiple association has not been reported. [ncbi.nlm.nih.gov]

  • Urticaria

    Histaminuria in urticaria pigmentosa. Arch Oermatol 1961;83:127-38. 5. Dale HH, Laidlow PP. The physiological action of beta• iminazolylethylamine. J Physiol 1910;41:318-44. POLYHYDRAMNIOS AND HYPERCALCEMIA ASSOCIATED WITH 6. Holinka CF, Gurpide E. [kundoc.com]

  • Placental Disorder

    Various fetal or placental disorders cause Ballantyne's (mirror) syndrome. For the first time, we report a maternal manifestation of Ballantyne's syndrome occurring concomitantly with the development of fetal congenital mesoblastic nephroma (CMN). [ncbi.nlm.nih.gov]

  • Hyperreninemia

    In the present article, we report, for the first time, a prenatal diagnosis of a congenital mesoblastic nephroma in combination with a post-partum hyperreninemia with hypertension. [ncbi.nlm.nih.gov]

    Polyhydramnios, with or without hydrops fetalis, and/or preterm labor are associated with CMN. [7] Some CMNs are associated with paraneoplastic syndromes such as hypertension (due to hyperreninemia) and hypercalcemia (due to prostaglandin secretion from [jfcmonline.com]

    Hyperreninemia and congenital mesoblastic nephroma: case report and review of the literature. Urology 2000;55:775. 6. Ko SM, Kim MJ, Im YJ, Park KI, Lee MJ. [synapse.koreamed.org]

    Usually, the treatment of this type of tumor is surgical, either with nephrectomy or total nephrouretectomy which, besides reducing the possibility of recurrence, will serve as treatment for the hypertension secondary to hyperreninemia(3,6). [docksci.com]

The risk of treatment-related mortality (both surgery- and chemotherapy-related) is relatively high in the first weeks of life, indicating that these young patients deserve special attention with respect to timing and type of treatment. 2017 Wiley Periodicals [ncbi.nlm.nih.gov]

CONCLUSIONS: Low frecuency of this tumor limit the experience on diagnostic and treatment. Standard treatment is nephroureterectomy radical with free margins. Adjuvant therapy should be considered in recurrent disease although exists few studies. [biomedsearch.com]

Univariate analysis showed that early gestational week at diagnosis was the only feature significantly associated with poor prognosis. [ncbi.nlm.nih.gov]

The clinical course of this patient may suggest an etiology of Ballantyne's syndrome. [ncbi.nlm.nih.gov]

Metastasis to lung, liver, brain, and heart have been reported. [14], [15], [16], [17], [18] Cystic nephroma, also known as MCN, is a rare nongenetic lesion of unknown etiology. [jiaps.com]

Fievet L, Faure A, Coze S, Harper L, Panait N, et al. (2014) Fetal megacystis: etiologies, management, and outcome according to the trimester. Urology 84: 185-190. [transbiomedicine.com]

Others have concluded that the morphology and epidemiology of mixed epithelial and stromal tumor indicate that it is unrelated to congenital mesoblastic nephroma. [ncbi.nlm.nih.gov]

Definition / general Congenital myofibroblastic tumor that resembles infantile fibromatosis / leiomyoma (classic) or fibrosarcoma (cellular) Also called fetal mesenchymal / leiomyomatous hamartoma First described in 1967 ( Pediatrics 1967;40:272 ) Epidemiology [pathologyoutlines.com]

The epidemiology of neonatal tumors. Report of an international working group. Pediatr Surg Int 2003; 19:509-19. 4. Watkinson. Hypertension in the newborn baby. Arch Dis Chil Fetal Neonatal 2002; 86:78-81. 5. Willert JR, Feusner J, Beckwith JB. [jfcmonline.com]

RENAL CELL CARCINOMA EPIDEMIOLOGY RENAL CELL CARCINOMA: THE 2012 ISUP VANCOUVER CLASSIFICATION David Grignon MD, Indiana University, Indianapolis, IN RENAL CELL CARCINOMA EPIDEMIOLOGY Siegel et al. [docplayer.net]

Epidemiological features of Wilms tumor: results of the national wilms tumor study. J Natl Cancer Inst 1982 ;68:429 -436. Beckwith JB. [fetalultrasound.com]

We present a case involving a premature infant with congenital mesoblastic nephroma with discussion of embryology, pathophysiology, diagnostic, management, and prognostic implications for the neonate and family. [ncbi.nlm.nih.gov]

It brings together the pathophysiology of disease with detailed clinical guidance on diagnosis and management for the full range of childhood cancers, including aspects important in optimal supportive care. [books.google.ro]

Nathan and Oski’s is the only comprehensive product on the market that relates pathophysiology in such depth to hematologic and oncologic diseases affecting children. [books.google.es]

The main treatment of this pathology if diagnosed during pregnancy remains the prevention of preterm labor, and after birth the removal of the kidney. [ncbi.nlm.nih.gov]

Slickers JE, Olshan AF, Siega-Riz AM, Honein MA, Aylsworth AS; National Birth Defects Prevention Study (2008) Maternal body mass index and lifestyle exposures and the risk of bilateral renal agenesis or hypoplasia: the National Birth Defects Prevention [transbiomedicine.com]