Edit concept Question Editor Create issue ticket

Congenital Microgastria


Presentation

  • In this report, we present a novel method of foregut reconstruction in an infant with congenital microgastria and a paraesophageal hiatal hernia.[ncbi.nlm.nih.gov]
  • We present 2 patients with congenital microgastria who underwent repair with a Hunt-Lawrence pouch.[indiana.pure.elsevier.com]
Coarse Rales
  • He had tachypnea with supracostal and intercostal retraction, bilateral coarse rales, and expiratory wheezing; moreover, his skin was pale. He also had mild micrognathia, upper left limb hypoplasia ( Figure 1 ), and flat abdomen.[comprped.com]
Rales
  • He had tachypnea with supracostal and intercostal retraction, bilateral coarse rales, and expiratory wheezing; moreover, his skin was pale. He also had mild micrognathia, upper left limb hypoplasia ( Figure 1 ), and flat abdomen.[comprped.com]
Tachypnea
  • He had tachypnea with supracostal and intercostal retraction, bilateral coarse rales, and expiratory wheezing; moreover, his skin was pale. He also had mild micrognathia, upper left limb hypoplasia ( Figure 1 ), and flat abdomen.[comprped.com]
Persistent Vomiting
  • Despite inability to eat anything but pureed foods for the first 13 years and despite persistent vomiting during that time, she has reached normal adult size and has three healthy children.[pediatrics.aappublications.org]
  • Because of persistent vomiting and recurrent pneumonia, which are the major problems in congenital microgastria, most patients require surgical intervention.[comprped.com]
Early Satiety
  • She continued to have signs of early satiety which prevented weight gain. Night-time tube feedings were instituted to supplement her p.o. intake, She has no signs of GE reflux or dumping syndrome.[vdocuments.site]
Projectile Vomiting
  • After discharge from hospital, he had projectile vomiting, cyanosis, and cough during feeding. On admission at six weeks of age, he was malnourished and dehydrated.[comprped.com]
Ejection Murmur
  • At birth, dysmorphic ears, frontal hypertrophy. and a loud systolic ejection murmur were evident. Sonographic examination of the chest and abdomen showed a persistent atriovedtricular canal, a midline liver, asplenia. and an annular pancreas.[kundoc.com]
Trismus
  • TY - JOUR T1 - Congenital microgastria with Pierre Robin sequence and partial trismus.[unboundmedicine.com]
  • A female with congenital microgastria, Pierre Robin sequence and partial trismus is described. This is a previously undescribed association and the etiology of the association is discussed.[ncbi.nlm.nih.gov]
  • […] augmentation in isolated congenital microgastria. ( 14577093 ) Menon P....Nagi B. 2003 12 Congenital microgastria presenting as stridor. ( 12811434 ) Waasdorp C.E....Sullivan C. 2003 13 Congenital microgastria with Pierre Robin sequence and partial trismus[malacards.org]
Decrease in Height
  • Although his feeding problems have decreased, his height and weight are below normal ( 10th percentile). The embryology, clinical presentation, diagnostic procedures, associated anomalies, and management are discussed.[ncbi.nlm.nih.gov]
Prominent Occiput
  • […] lesionsNilPenaShokeirsequenceAbsent stomach bubble Scalp oedema, pulmonary hypoplasia,polyhydramnios, contractures, CNSlesionsFamily history,consanguinityTrisomy 18 Absent stomach bubble Cardiac anomalies, choroids plexuscysts, increased nuchal fold,polyhydramnios, prominent[vdocuments.site]
Pierre Robin Syndrome
  • Links Aggregator Full Text Authors, ,,, Source MeSH Female Humans Infant, Newborn Pierre Robin Syndrome Stomach Trismus Pub Type(s) Case Reports Letter Language eng PubMed ID 11045595 Citation Giurgea, I, et al.[unboundmedicine.com]
Hunger
  • Of interest is the fact that most of this retarded patient's verbal development is associated with food and he appears to experience hunger at appropriate times.[vdocuments.site]

Workup

  • The workup showed congenital microgastria. The infant's diagnostic and treatment course is described.[ncbi.nlm.nih.gov]
  • The workup showed congenital microgastria. The infant’s diagnostic and treatment course is described. Copyright o 1994 by W. B. Saunders Company INDEX WORDS: Congenital microgastria.[kundoc.com]
  • If further prenatal workup results are consistent with microgastria, a thorough evaluation will be required when the infant is born.[dokumen.tips]
  • Many tests are available to assist in the workup of congenital tracheal malformations. The initial otolaryngologic evaluation should include a fiberoptic nasopharyngolaryngoscopy to rule out any supraglottic or glottic abnormalities.[emedicine.medscape.com]

Treatment

  • Various forms of surgical treatment have been used to provide improved enteral nutrition in individuals with more severe dysplasia 4-5,9-10 Treatment of congenital microgastria must be individualized.[kundoc.com]
  • The infant's diagnostic and treatment course is described.[ncbi.nlm.nih.gov]
  • The authors reviewed the literature and recommend the gastric augmentation for the treatment for microgastria. Keywords : Microgastria; Gastroesophageal reflux; Hunt-Lawrence pouch.[scielo.br]
  • […] megaduodenum: case report and review of literature. ( 22468061 ) Vasas P....Akle C.A. 2011 3 Congenital microgastria: a rare cause of failure to visualise the fetal stomach. ( 21744366 ) Shepherd P....Chitty L.S. 2011 4 Gastric dissociation for the treatment[malacards.org]
  • Significant updates on bariatric surgery, Barrett's esophagus, endoscopic ultrasound, endosonography, treatment of liver disease, and much more keep you current on the latest advances.[books.google.com]

Prognosis

  • Diagnosis - Microgastria limb reduction defect These home medical tests may be relevant to Congenital microgastria limb reduction defect: * Cold & Flu: Home Testing: o Home Fever Tests o Home Ear Infection Tests o Home Flu Tests Prognosis - Microgastria[checkorphan.org]
  • […] congenital abnormalities and analyze 42 (including our own) reported cases, including our 2 cases, of hypothalamic hamartoma or hypothalamic hamartoblastoma with multiple congenital abnormalities, to understand the timing of their occurrence and clarify the prognosis[biomedsearch.com]

Etiology

  • This is a previously undescribed association and the etiology of the association is discussed.[ncbi.nlm.nih.gov]
  • This is a previously undescribed association and the etiology of the association is discussed. SN - 0962-8827 UR - L2 - DB - PRIME DP - Unbound Medicine ER -[unboundmedicine.com]
  • Evidence for a humoral etiology of the dumping syndrome . Surg Forum 1961; 12: 316-317 19 Hattori K, Bvulani B, Numanoglu A, Cox SG, Millar AJ. Total Esophageal gastric dissociation for the failed antireflux procedure in a child with microgastria .[thieme-connect.com]
  • Congenital malformations, deformations and chromosomal abnormalities Other congenital malformations of the digestive system Mode of Inheritance Isolated cases Gene Map Locus Not Mapped Microgastria-limb reduction defect is a rare disorder of unknown etiology[cags.org.ae]

Epidemiology

  • Feldkamp ML, Botto LD, Amar E et al. (2011) Cloacal exstrophy: an epidemiologic study from the International Clearinghouse for Birth Defects Surveillance and Research.[els.net]
  • The ICD is the international standard diagnostic classification for all general epidemiological, many health management purposes and clinical use.[embryology.med.unsw.edu.au]
Sex distribution
Age distribution

Pathophysiology

  • The association of complete laryngotracheoesophageal cleft with left lung agenesis: pathophysiological clues provided by an experiment of nature. J Pediatr Surg 1998;33:1546-9 4. Kroes E, Festen C.[koreascience.or.kr]
  • Postprandial hypoglycemia in children after gastric surgery: clinical characterization and pathophysiology . Horm Res Paediatr 2016; 85 (02) 140-146 18 Johnson LP, Jesseph JE. Evidence for a humoral etiology of the dumping syndrome .[thieme-connect.com]

Prevention

  • […] immune defect from absence of the spleen, the mortality among patients with asplenia is high. 3 Intestinal malrotation and malfixation are present in essentially all patients with asplenia syndrome. 1, 4 A prophylactic Ladd procedure is recommended to prevent[nature.com]
  • Hunt-Lawrence pouch has been used to enlarge gastric reservoir capacity.5,9-10 CONGENITAL 1593 MICROGASTRIA Construction of a gastric pouch not only lessens the frequency of feedings and improves nutritional intake, but also facilitates drainage and prevents[kundoc.com]
  • She continued to have signs of early satiety which prevented weight gain. Night-time tube feedings were instituted to supplement her p.o. intake, She has no signs of GE reflux or dumping syndrome.[vdocuments.site]
  • In our patient, malnutrition was prevented by early supplemental jejunal feedings. Several surgical procedures have been undertaken to permit increased nutritional intake and/or increased gastric capacity.[journals.lww.com]

Ask Question

5000 Characters left Format the text using: # Heading, **bold**, _italic_. HTML code is not allowed.
By publishing this question you agree to the TOS and Privacy policy.
• Use a precise title for your question.
• Ask a specific question and provide age, sex, symptoms, type and duration of treatment.
• Respect your own and other people's privacy, never post full names or contact information.
• Inappropriate questions will be deleted.
• In urgent cases contact a physician, visit a hospital or call an emergency service!