Presentation
In this report, we present a novel method of foregut reconstruction in an infant with congenital microgastria and a paraesophageal hiatal hernia. [experts.umich.edu]
Most infants present in the early days of life with vomiting, severe malnutrition and/or aspiration pneumonia. The present report offers two additional patients with congenital microgastria, who presented at birth and 10 months respectively. [vdocuments.site]
Most cases of microgastria present during infancy. This is a report of a four year old child, eldest in litreature presenting with isolated microgastria. Child presented with vomiting, failure to thrive. [ijsurgery.com]
Entire Body System
- Hunting
Keywords : Microgastria; Gastroesophageal reflux; Hunt-Lawrence pouch. [scielo.br]
Use of the Hunt-Lawrence pouch in congenital microgastria - A report of 2 cases. [indiana.pure.elsevier.com]
Hunt-Lawrence jejunal pouch. Note antiperistaltic ana- stomosis at pouch outlet. MICROGASTRIA AND DUMPING SYNDROME 749 Fig. 3. Case 1. [vdocuments.site]
In the present report we describe the case of a 6-year-old girl with isolated CM who presented with dumping syndrome successfully treated by a Hunt-Lawrence pouch. [thieme-connect.com]
- Weight Gain
Initially weight gain was slow but constant. At 13 months weight gain ceased and he developed bilious vomiting. The dumping syndrome appeared when the patient was begun on solid food. [vdocuments.site]
Weight gain was immediate in both patients and has been sustained for 6 months and 8 years respectively. Symptoms of the dumping syndrome were relieved and the pouch delays filling of the jejunum. [ncbi.nlm.nih.gov]
One year later, there has been progressive weight gain, the megaesophagus and gastroesophageal reflux have lessened significantly, pneumonia has not recurred, and the tracheobronchitis and esophagitis have resolved. [scholars.duke.edu]
Including the present case, all five patients treated with HuntLawrence reconstruction are alive and well; however, their growth and weight gain have been moderately to severely retarded. [kundoc.com]
The patient had good weight gain and growth with supplemental nocturnal feedings, in addition to ad libitum daytime oral feedings. [journals.lww.com]
Respiratoric
- Rales
He had tachypnea with supracostal and intercostal retraction, bilateral coarse rales, and expiratory wheezing; moreover, his skin was pale. He also had mild micrognathia, upper left limb hypoplasia ( Figure 1 ), and flat abdomen. [comprped.com]
- Tachypnea
He had tachypnea with supracostal and intercostal retraction, bilateral coarse rales, and expiratory wheezing; moreover, his skin was pale. He also had mild micrognathia, upper left limb hypoplasia ( Figure 1 ), and flat abdomen. [comprped.com]
- Coarse Rales
He had tachypnea with supracostal and intercostal retraction, bilateral coarse rales, and expiratory wheezing; moreover, his skin was pale. He also had mild micrognathia, upper left limb hypoplasia ( Figure 1 ), and flat abdomen. [comprped.com]
Gastrointestinal
- Projectile Vomiting
After discharge from hospital, he had projectile vomiting, cyanosis, and cough during feeding. On admission at six weeks of age, he was malnourished and dehydrated. [comprped.com]
- Abdominal Distension
Case report A 3-month-old female infant with a history of recurrent nonbilious vomiting and abdominal distension since birth was admitted. [journals.lww.com]
Jaw & Teeth
- Trismus
TY - JOUR T1 - Congenital microgastria with Pierre Robin sequence and partial trismus. [unboundmedicine.com]
[…] augmentation in isolated congenital microgastria. ( 14577093 ) Menon P....Nagi B. 2003 12 Congenital microgastria presenting as stridor. ( 12811434 ) Waasdorp C.E....Sullivan C. 2003 13 Congenital microgastria with Pierre Robin sequence and partial trismus [malacards.org]
Congenital microgastria with Pierre Robin sequence and partial trismus. Clin Dysmorphol. 2000; 9 (4) : 307 -8 [ PubMed ] 8. Herman TE, Siegel MJ. Imaging casebook. Asplenia syndrome with congenital microgastria and malrotation. [comprped.com]
Cardiovascular
- Ejection Murmur
At birth, dysmorphic ears, frontal hypertrophy. and a loud systolic ejection murmur were evident. Sonographic examination of the chest and abdomen showed a persistent atriovedtricular canal, a midline liver, asplenia. and an annular pancreas. [kundoc.com]
Face, Head & Neck
- Prominent Occiput
[…] lesionsNilPenaShokeirsequenceAbsent stomach bubble Scalp oedema, pulmonary hypoplasia,polyhydramnios, contractures, CNSlesionsFamily history,consanguinityTrisomy 18 Absent stomach bubble Cardiac anomalies, choroids plexuscysts, increased nuchal fold,polyhydramnios, prominent [vdocuments.site]
Psychiatrical
- Hunger
Of interest is the fact that most of this retarded patient's verbal development is associated with food and he appears to experience hunger at appropriate times. [vdocuments.site]
Urogenital
- Cesarean Section
She was delivered by cesarean section, weighed 2,000 g (-3.1 SD, p0) and measured 43 cm in height (-3.3 SD, p0), corrected for gestational age. [revistagastroenterologiamexico.org]
Workup
The workup showed congenital microgastria. The infant's diagnostic and treatment course is described. [ncbi.nlm.nih.gov]
The workup showed congenital microgastria. The infant’s diagnostic and treatment course is described. Copyright o 1994 by W. B. Saunders Company INDEX WORDS: Congenital microgastria. [kundoc.com]
If further prenatal workup results are consistent with microgastria, a thorough evaluation will be required when the infant is born. [dokumen.tips]
Many tests are available to assist in the workup of congenital tracheal malformations. The initial otolaryngologic evaluation should include a fiberoptic nasopharyngolaryngoscopy to rule out any supraglottic or glottic abnormalities. [emedicine.medscape.com]
X-Ray
- Pneumoperitoneum
A plain abdominal radiograph showed pneumoperitoneum. After resuscitation, emergency laparotomy revealed nasogastric tube-related gastric perforation with a very small stomach. The perforation was repaired, and a jejunostomy was created for feeding. [journals.lww.com]
Treatment
Various forms of surgical treatment have been used to provide improved enteral nutrition in individuals with more severe dysplasia 4-5,9-10 Treatment of congenital microgastria must be individualized. [kundoc.com]
The infant's diagnostic and treatment course is described. [ncbi.nlm.nih.gov]
The authors reviewed the literature and recommend the gastric augmentation for the treatment for microgastria. Keywords : Microgastria; Gastroesophageal reflux; Hunt-Lawrence pouch. [scielo.br]
[…] megaduodenum: case report and review of literature. ( 22468061 ) Vasas P....Akle C.A. 2011 3 Congenital microgastria: a rare cause of failure to visualise the fetal stomach. ( 21744366 ) Shepherd P....Chitty L.S. 2011 4 Gastric dissociation for the treatment [malacards.org]
Prognosis
Diagnosis - Microgastria limb reduction defect These home medical tests may be relevant to Congenital microgastria limb reduction defect: * Cold & Flu: Home Testing: o Home Fever Tests o Home Ear Infection Tests o Home Flu Tests Prognosis - Microgastria [checkorphan.org]
[…] congenital abnormalities and analyze 42 (including our own) reported cases, including our 2 cases, of hypothalamic hamartoma or hypothalamic hamartoblastoma with multiple congenital abnormalities, to understand the timing of their occurrence and clarify the prognosis [biomedsearch.com]
Etiology
This is a previously undescribed association and the etiology of the association is discussed. [unboundmedicine.com]
Evidence for a humoral etiology of the dumping syndrome. Surg Forum 1961; 12: 316-317 19 Hattori K, Bvulani B, Numanoglu A, Cox SG, Millar AJ. Total Esophageal gastric dissociation for the failed antireflux procedure in a child with microgastria. [thieme-connect.com]
Congenital malformations, deformations and chromosomal abnormalities Other congenital malformations of the digestive system Mode of Inheritance Isolated cases Gene Map Locus Not Mapped Microgastria-limb reduction defect is a rare disorder of unknown etiology [cags.org.ae]
Epidemiology
Feldkamp ML, Botto LD, Amar E et al. (2011) Cloacal exstrophy: an epidemiologic study from the International Clearinghouse for Birth Defects Surveillance and Research. [els.net]
The ICD is the international standard diagnostic classification for all general epidemiological, many health management purposes and clinical use. [embryology.med.unsw.edu.au]
Pathophysiology
Postprandial hypoglycemia in children after gastric surgery: clinical characterization and pathophysiology. Horm Res Paediatr 2016; 85 (02) 140-146 18 Johnson LP, Jesseph JE. Evidence for a humoral etiology of the dumping syndrome. [thieme-connect.com]
The association of complete laryngotracheoesophageal cleft with left lung agenesis: pathophysiological clues provided by an experiment of nature. J Pediatr Surg 1998;33:1546-9 4. Kroes E, Festen C. [koreascience.or.kr]
Prevention
However, improved technologies that allow routine use of gastric or jejunal slow-drip feedings has been reported to have successful outcomes. 6 This approach prevents gastroesophageal reflux and allows appropriate nutrition for growth. [accesspediatrics.mhmedical.com]
Our database lists the following as having Congenital microgastria limb reduction defect as a symptom of that condition: Other Possible Causes of these Symptoms * Cardiac defects * Cystic kidney dysplasia * Failure to thrive * Renal anomalies Prevention [checkorphan.org]
Centers for Disease Control and Prevention Intersex (Medical Encyclopedia) [ Read More ] Stomach Disorders Also called: Gastric disorders Your stomach is an organ between your esophagus and small intestine. It is where digestion of protein begins. [icdlist.com]
Hunt-Lawrence pouch has been used to enlarge gastric reservoir capacity.5,9-10 CONGENITAL 1593 MICROGASTRIA Construction of a gastric pouch not only lessens the frequency of feedings and improves nutritional intake, but also facilitates drainage and prevents [kundoc.com]