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Congenital Renal Artery Stenosis

Congenital Renovascular Hypoplasia


Presentation

  • […] if the condition was present at the time of inpatient admission.[icd.codes]
  • On Admission POA Help "Present On Admission" is defined as present at the time the order for inpatient admission occurs — conditions that develop during an outpatient encounter, including emergency department, observation, or outpatient surgery, are[icd10data.com]
  • · Presents new chapters on pathogenesis and pathophysiology of diabetic nephropathy and genetic basis of glomerular and structural kidney disorders.. · Provides expanded coverage of the pathophysiology and management of chronic kidney disease.[books.google.com]
  • All children were confirmed to have RAS after presentation with hypertension at a median age of 10 (3.5-16.2) years. Angioplasty was performed in 7 children, of which 6 achieved control of their blood pressure on reduced medications.[ncbi.nlm.nih.gov]
  • The neonate presented at birth with malignant hypertension, hematuria, proteinuria, and normal GFR. Initial course was complicated by salt wasting, retinal arteriolar narrowing and labile blood pressure.[nature.com]
Venous Insufficiency
  • Aortic arch syndrome (Medical Encyclopedia) Arterial embolism (Medical Encyclopedia) Arteriogram (Medical Encyclopedia) Cerebral angiography (Medical Encyclopedia) Duplex ultrasound (Medical Encyclopedia) Venous insufficiency (Medical Encyclopedia) Venous[icdlist.com]
Ectopia Lentis
  • Page 896 - Genetic linkage of the Marfan syndrome, ectopia lentis, and congenital contractural arachnodactyly to the fibrillin genes on chromosomes 15 and 5. N Engl J Med 1992;326:905-909. ‎[books.google.com]

Workup

Colitis
  • 757 GASTROINTESTINAL TRACT 769 Differential Diagnosis of Colonic Polyps 799 Anatomy and Function 804 Gastrointestinal Disorders 812 Attenuation Values of Fluid 822 Staging of Colorectal Cancer 830 Gastric Ulcer 851 between Crohn Disease and Ulcerative Colitis[books.google.com]

Treatment

  • · Delivers balanced and accurate cutting-edge management and treatment guidelines. · Features over 70 international experts in all who offer fresh perspectives and a global view of kidney disease.[books.google.com]
  • Other treatments include medicines and surgery.[icdlist.com]
  • Access up-to-date diagnostic and treatment information on more than 700 common medical conditions with Ferri’s Clinical Advisor 2017, which boasts the popular "5 books in 1" format![books.google.com]
  • Wettasinghe M, Pussepitiya K, Samarasinghe B, Wickramasinghe N Surgical Treatment of Abdominal Aortic Aneurysm with Congenital Solitary Pelvic Kidney and Superior Mesenteric Artery Stenosis.[medicbind.com]
  • Optimal medical therapy remains the preferred first-line treatment.[scai.org]

Prognosis

  • […] decompression or excision of cysts do not improve renal function There is no higher incidence of renal cell carcinoma in these patients 50% of the children of affected adults will have the disease When the disease affects children, it has a very poor prognosis[clevelandurology.net]
  • Diagnosis, therapy and prognosis in patients with chronic heart failure (in German) Wagdi Ph. Praxisorentierte Diagnose, Behandlung und Prognosestellung bei Patienten mit chronischer Herzinsuffizienz. DMW 1999; 124: 291-295.[philippwagdi.ch]

Etiology

  • Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology.[icd10coded.com]
  • Etiology Majority are caused by fibromuscular dysplasia (FMD), a noninflammatory vascular disease of unknown etiology. Primarily affects females and affects up to 4 in 100 adults The renal vasculature is the most common arterial bed affected.[unboundmedicine.com]
  • "Fibromuscular Dysplasia: Practice Essentials, Background, Pathophysiology" . 2018-09-19. a b c "Renal Artery Stenosis: Background, Pathophysiology, Etiology" . 2018-12-14. Steyerberg, Ewout (2008-12-16).[en.wikipedia.org]

Epidemiology

  • […] first section of this topic is shown below -- Basics Description Narrowing of 1 or both renal arteries and/or their more distal branches, resulting in decreased perfusion, increased renin release, increased vascular resistance, and systemic hypertension Epidemiology[unboundmedicine.com]
  • Epidemiology of pyridoxine dependent and pyridoxine responsive seizures in the UK . P Baxter. Arch Dis Child 1999; 81 :431–3. Indirect measurements of sweat electrolyte concentration in the laboratory diagnosis of cystic fibrosis .[adc.bmj.com]
  • Working group for Clinical Epidemiology Wagdi Ph, Bertel O: Ursachen der Notfallhospitalisationen bei chronischer Herzinsuffizienz Xth Symposium for invasive and interventional Cardiology , Havana, Cuba, April 28th 2003. Ph. Wagdi.[philippwagdi.ch]
Sex distribution
Age distribution

Pathophysiology

  • · Presents new chapters on pathogenesis and pathophysiology of diabetic nephropathy and genetic basis of glomerular and structural kidney disorders.. · Provides expanded coverage of the pathophysiology and management of chronic kidney disease.[books.google.com]
  • "Fibromuscular Dysplasia: Practice Essentials, Background, Pathophysiology" . 2018-09-19. a b c "Renal Artery Stenosis: Background, Pathophysiology, Etiology" . 2018-12-14. Steyerberg, Ewout (2008-12-16).[en.wikipedia.org]
  • Pathophysiology Arterial narrowing leads to diminished perfusion of the affected kidney, leading to signals in the juxtaglomerular apparatus, which lead to renin release and results in increased vascular resistance and blood pressure (BP).[unboundmedicine.com]

Prevention

  • Centers for Disease Control and Prevention Intersex (Medical Encyclopedia) [ Read More ] Kidney Diseases Also called: Renal disease You have two kidneys, each about the size of your fist.[icdlist.com]
  • Such recognition could prevent the unnecessary treatment of these patients with an angiotensin-converting enzyme inhibitor or nephrectomy. FULL TEXT[annals.org]
  • Treatment & Prevention Treatments that can improve blood flow to the kidneys and reduce blood pressure include: Surgical removal or by-pass of the narrowing in the renal artery.[vascularcures.org]
  • "Our findings clearly show that renal artery stenting does not confer any benefit for the prevention of clinical events when added to a comprehensive, multi-factorial medical therapy."[sciencedaily.com]
  • Hypertension is a usual consequence of RAS, unless cardiac disease prevents it from developing.[edrep.org]

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