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Double Outlet Left Ventricle

DOLV


Presentation

Pathologist
  • Angiography has often been considered indispensable, and diagnosis has often been left to the surgeon or pathologist. 5 DOLV may thus have been underdiagnosed.[circ.ahajournals.org]
Pleural Effusion
  • The patient initially did well postoperatively but, despite vigorous diuretic therapy, developed large bilateral pleural effusions necessitating frequent aspiration. He died unexpectedly one month after the operation.[ncbi.nlm.nih.gov]
  • He had one mediastinal chest drain in situ and had significant bleeding (10 ml/kg/hr), 4 hours postoperative ultrasound showed large right pleural effusion and a right pleural drain was inserted immediately, this drained 150 ml of blood.[apicareonline.com]

Workup

Right Pleural Effusion
  • He had one mediastinal chest drain in situ and had significant bleeding (10 ml/kg/hr), 4 hours postoperative ultrasound showed large right pleural effusion and a right pleural drain was inserted immediately, this drained 150 ml of blood.[apicareonline.com]
Pleural Effusion
  • The patient initially did well postoperatively but, despite vigorous diuretic therapy, developed large bilateral pleural effusions necessitating frequent aspiration. He died unexpectedly one month after the operation.[ncbi.nlm.nih.gov]
  • He had one mediastinal chest drain in situ and had significant bleeding (10 ml/kg/hr), 4 hours postoperative ultrasound showed large right pleural effusion and a right pleural drain was inserted immediately, this drained 150 ml of blood.[apicareonline.com]

Treatment

  • To our knowledge, this represents the second instance of surgical treatment of double-outlet left ventricle [I,D,D] reported in the literature.[ncbi.nlm.nih.gov]
  • Many children with congenital heart defects don't need treatment, but others do. Treatment can include medicines, catheter procedures, surgery, and heart transplants.[icdlist.com]
  • Management and treatment Biventricular repair is the usual treatment for DOLV and is usually accomplished by an intraventricular baffle procedure, by the Rastelli procedure or by a variant of the Lecompte operation.[orpha.net]

Prognosis

  • Prognosis DOLV is associated with high mortality, generally due to heart failure, myocardial infarction or aortic thrombosis. With surgery, the five-year survival rate is estimated at 70-75%.[orpha.net]
  • The prognosis after this operation for single ventricle patients is better than for other treatments, and improvements of surgical technique continue to be made.[chla.congenital.org]
  • Factors that determine the type and number of operations the baby needs include: The type of DORV The severity of the defect The presence of other problems in the heart The child's overall condition Outlook (Prognosis) How well the baby does depends on[ufhealth.org]

Etiology

  • Etiology The etiopathology is not clearly understood.[orpha.net]
  • Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology.[icd10coded.com]

Epidemiology

  • Summary Epidemiology Prevalence is unknown. The birth prevalence is estimated at less than 1/ 200,000 live births.[orpha.net]
  • Epidemiology [ edit ] DORV affects between 1% and 3% of people born with congenital heart defects. [1] Chromosomal abnormalities were reported in about 40% of reported cases in the medical literature. [1] References [ edit ] a b Obler D, Juraszek AL,[en.wikipedia.org]
  • Search term: Taussig-Bing malformation Taussig-Bing malformation International Classification of Diseases The International Classification of Diseases (ICD) World Health Organization's classification used worldwide as the standard diagnostic tool for epidemiology[embryology.med.unsw.edu.au]
Sex distribution
Age distribution

Pathophysiology

  • (Click picture to show/hide bloodflows) Pathophysiology The hemodynamics involved with double outlet right ventricle are dependent on the anatomy of the great vessels and associated defects.[vhlab.umn.edu]
  • Anatomy and pathophysiology [ edit ] DORV occurs in multiple forms, with variability of great artery position and size, as well as of ventricular septal defect (VSD) location. It can occur with or without transposition of the great arteries.[en.wikipedia.org]

Prevention

  • This prevents infections around the heart. Antibiotics may also be needed after surgery. Call your health care provider if your child seems to tire easily, has trouble breathing, or has bluish skin or lips.[medlineplus.gov]
  • This prevents infections around the heart. Antibiotics may also be needed after surgery. When to Contact a Medical Professional Call your health care provider if your child seems to tire easily, has trouble breathing, or has bluish skin or lips.[ufhealth.org]
  • Table 19-1 Double Outlet Right Ventricle: Clinical Classification The aorta is either to the right of and anterior to the pulmonary trunk or side-by-side with the aorta to the right. 9 Each great artery arises above a conus that prevents fibrous continuity[clinicalgate.com]

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