Presentation
Such malformations can present antenatally but their early natural history and anatomy is poorly defined. [ncbi.nlm.nih.gov]
We present a case of prenatally diagnosed DSM that regressed before birth and drastically developed postnatally. [epostersonline.com]
Patients usually present between the ages of 20 and 79 years. [nature.com]
Abstract A rare case of dural sinus malformation with dural arteriovenous fistula in an infant is presented. Presenting symptom was progressive macrocrania without hydrocephalus. [journals.sagepub.com]
Entire Body System
- Epilepsy
Epilepsy develops in ~80% of patients, in majority within the first 5 years (11). Bilateral involvement, as in our patient, and involvement of more than half of a single hemisphere are poor prognostic factors (9). [frontiersin.org]
The remaining patient with a less favorable outcome had concomitant SWS and medically intractable epilepsy, making it difficult to determine the extent to which their tDSM contributed to their neurological status. [thejns.org]
[…] pseudoresponse and nonenhancing tumor … G Morana, A Piccardo, ML Garrè, P Nozza, A Consales, A Rossi Journal of clinical oncology: official journal of the American Society of …, 2013 15 2013 Anti–Glutamic Acid Decarboxylase Limbic Encephalitis Without Epilepsy [scholar.google.com]
The selective intracarotid administration of sodium amytal (Wada) test is a tool for assessment of language dominance and memory in a select group of patients for preoperative epilepsy surgery planning. [content.iospress.com]
Neurologic manifestations are usually the consequences of cerebral venous hypertension and include focal neurologic deficits, hydrocephalus, acquired Chiari malformations (hydrovenous disorders), macrocrania, epilepsy, and hemorrhage (12–14). [ajnr.org]
- Collapse
There is certainly a developmental propensity for these to form in most people — Dorcas Padget felt that sinuses form at intersection of dural covers due to the resistance of the channel to pressure-related collapse. [neuroangio.org]
[…] diagnosis] R13.10 - R13.19 Dysphagia R42 Dizziness and giddiness R43.0 - R43.9 Disturbances of smell and taste R47.02 - R47.9 Speech disturbances, not elsewhere classified R51 Headache [sudden explosive headache, unilateral headache] R55 Syncope and collapse [aetna.com]
- Sepsis
Other neonatal conditions associated with SVT are dehydration, bacterial sepsis, meningitis, and various prothrombotic disorders. [radiologykey.com]
- Pseudotumor
DESIGN/METHODS: We performed a PubMed search to identify studies of sinus stenting using the keywords “cerebral venous thrombosis“ or “pseudotumor cerebri” or “idiopathic intracranial hypertension” or “cerebral arteriovenous malformations” or “dural sinus [neurology.org]
Urogenital
- Cesarean Section
Case presentation : A boy with a prenatal diagnosis of DSM was born by cesarean section at a gestational period of 36 weeks. Birth weight was 2741g and head circumference was 38cm. [jstage.jst.go.jp]
A female neonate was delivered by cesarean section at 31 weeks of gestation. Her birth weight was 1538 g and Apgar scores were 6 at both 1 and 5 min. [altmetric.com]
Case presentation A 3300 g infant was born at 38 weeks' gestation to a Gravida 2, Para 2 mother by cesarean section because of difficult extraction due to macrocephaly. [nature.com]
Case Report A 31-year-old woman, healthy, gravida 3, para 1 (one previous cesarean section for fetal distress in labor), was referred for fetal echocardiography at 21.2 weeks’ gestation (w.g.) for suspicious cardiomegaly at the routine obstetric scan. [mdpi.com]
Workup
Isolated coccygeal dimples do not require further workup or treatment. FIGURE 9 Benign coccygeal dimple within the gluteal cleft and overlying the tip of the coccyx. [pediatrics.aappublications.org]
Subsequent workup led to an angiogram, where sagittal sinus thrombosis with extensive trans-cerebral and trans-osseous emissary vein collateral channels was seen. In retrospect, these findings were present on the patient’s earlier contrast MRI. [neuroangio.org]
Treatment
Staged Endovascular treatment in order to prevent further brain injury three times. •The dilated posterior sinus compressed his cerebellum and brain stem at 5 months. The compression was palliated after the 3rd intervention. [epostersonline.com]
Follow-up MRI at 1 month suggested latent venous hypertension and prompted endovascular treatment. [ncbi.nlm.nih.gov]
We present three cases of midline DSMs and discuss the treatment strategy employed for each lesion. A review of the literature was completed to summarize current literature and treatment practices. [experts.umn.edu]
[…] following surgical treatment in combination with embolization has been reported in neonates.7,8 Endovascular embolization in combination with symptomatic treatment remains the primary therapeutic method. [journals.lww.com]
Modalities or Observation of Arteriovenous Malformations; Selection of Treatment Modalities or Observation of Dural Arteriovenous Malformations; Surgical Treatment of Cranial Arteriovenous Malformations and Dural Arteriovenous Fistulas; Anesthesia Considerations [books.google.de]
Prognosis
Although normal cranial circumference is reportedly an essential factor for a favorable prognosis, the patient in this report with a cranial circumference at + 2.0 SD (35.6 cm) had a favorable prognosis. [ncbi.nlm.nih.gov]
Treatment and prognosis Dural sinus malformations involving the jugular bulb carry excellent prognosis with occlusion of AVF and thrombosis of sigmoid sinus distal to the superior petrosal sinus. [radiopaedia.org]
Dural sinus malformation (DSM) is a relatively rare pediatric arteriovenous (AV) shunt disease, and is defined as a large dural sinus lake accompanying dural AV shunts with a poor prognosis. [epostersonline.com]
In previous studies,2,3 poor prognosis was reported when DSMs involved immature, large, or central dural sinuses with turbulent and slow flow and impairment of the deep and superficial veins. [journals.lww.com]
Etiology
Dural sinus malformations, which are characterized by massively dilated dural sinuses, are one of the etiologies of an intracranial fetal cystic mass. [ncbi.nlm.nih.gov]
Introduction: Dural sinus malformations, which are characterized by massively dilated dural sinuses, are one of the etiologies of an intracranial fetal cystic mass. [tandfonline.com]
Objective To review tDSMs reported in the literature of multiple specialties for features that support a common etiology, and to identify key prognostic factors, with an emphasis on tDSM trajectory highlighted in part I. [jnis.bmj.com]
Torcular dural sinus malformations (tDSMs) are described as slow flow dural arteriovenous fistulae with frequently poor outcomes in the neuroangiographic literature, but other etiologies have been proposed in the obstetric literature, where outcomes have [bioportfolio.com]
Epidemiology
Articles in this issue include: Arteriovenous Malformations: Epidemiology and Clinical Presentation; Dural Arteriovenous Fistulas: Epidemiology and Clinical Presentation; Historical Perspective of Treatments of Arteriovenous Malformations and Dural Arteriovenous [books.google.de]
Epidemiology [ edit ] 10-15% of intracranial AV malformations are DAVFs. [4] There is a higher preponderance in females (61-66%), and typically patients are in their fourth or fifth generation of life. [en.wikipedia.org]
Moreover, the epidemiology and clinical findings particular to children with AVMs can be ascribed to the distinct angioarchitecture of pediatric AVMs. However, the natural history and treatment of pediatric AVMs is relatively unknown. [content.iospress.com]
The Strengthening the Reporting of Observational Studies in Epidemiology (STROBE) statement: guidelines for reporting observational studies. PLoS Med. 2007;4(10):e296. [thejns.org]
Favourable clinical evolution 17/29(58.6%) Favourable clinical evolution with morphological exclusion Unfavourable clinical evolution 10/17(58.8%) 12/29(41.4%) Unfavourable clinical evolution with death 11/12(90.9%) No follow-up 1/30(3.3%) Discussion Epidemiology [ncbi.nlm.nih.gov]
Pathophysiology
Such a prenatal and postnatal morphological change and clinical course have not been reported previously, and will be useful in elucidating the pathophysiology of this rare but important clinical entity. [epostersonline.com]
Owing to its rarity, the pathophysiology of DSM has not been fully elucidated. We report a case of prenatally diagnosed DSM with an unusual clinical course. [ncbi.nlm.nih.gov]
Seite 697 - Physiological and pathophysiological roles of excitatory amino acids during central nervous system development. [books.google.de]
الصفحة 697 - Physiological and pathophysiological roles of excitatory amino acids during central nervous system development. [books.google.com]
DSM (tDSM), generalizable statements about etiology and prognosis are difficult because neurosurgeons/neuroradiologists and obstetrical imagers have focused on different patient age groups, have reported different outcomes, and have offered differing pathophysiologic [jnis.bmj.com]
Prevention
Staged Endovascular treatment in order to prevent further brain injury three times. •The dilated posterior sinus compressed his cerebellum and brain stem at 5 months. The compression was palliated after the 3rd intervention. [epostersonline.com]
Conclusion: Early diagnosis and treatment, if necessary, of DSMs are critical to prevent cardiac failure or parenchymal injury from chronic venous hypertension. [experts.umn.edu]
In addition, medical treatment with heparin, diuretics, and/or inotropic agents help to prevent dural sinus thrombosis and hyperdynamic cardiac failure. [journals.lww.com]
Type III dural fistulas need to be treated to prevent hemorrhage. Treatment can be as simple as clipping the draining vein at the site of the dural sinus. [en.wikipedia.org]
Working towards safe and affordable prevention strategies and comprehensive care and support for people with memory problems and their families Brain Plasticity Laboratory Studying the brain's ability to reorganize and form new connections in either desirable [med.umn.edu]