We present a case of prenatally diagnosed DSM and propose a parameter to predict poor fetal outcome. Detailed ultrasonography at 26 weeks of our patient showed an intracranial cyst in the left posterior fossa. [ncbi.nlm.nih.gov]

Purpose: Dural sinus malformations (DSMs) are rare pediatric vascular lesions that have variable presentations and outcomes. We present three cases of midline DSMs and discuss the treatment strategy employed for each lesion. [experts.umn.edu]

and Management; Carotid Cavernous Fistulas: Epidemiology, Clinical Presentation, and Management. [books.google.de]

The treatment strategy and possible link between the complex disease entities presented in this infant are discussed. Despite these attemps, the lesion continued to grow compressing the posterior fossa structures. [biomedsearch.com]

Patients usually present between the ages of 20 and 79 years. [nature.com]

• Congestive Heart Failure

  Congestive heart failure and anuria at birth prompted emergency intervention. [ncbi.nlm.nih.gov]

  Congenital DAVF at the torcula Herophili is a very rare lesion and is associated with a guarded prognosis because of the danger of high-output congestive heart failure. [nature.com]

  Chest x-ray showed cardiomegaly and cardiac ultrasound examination demonstrated congestive heart failure. To improve his symptoms, endovascular treatment was performed on Day 0. [jstage.jst.go.jp]

• Regurgitation

  Because sonography showed cardiomegaly, tricuspid regurgitation, and enlarged neck veins, indicating cardiac failure in utero, caesarean section was performed under spinal anesthesia at GA 38 weeks 6 days. [ajnr.org]

  Associated signs may include heart failure with tachycardia, ventricular extrasystoles, and tricuspid regurgitation. Vein of Galen malformations are rare congenital connections occurring between intracranial vessels. [mrineonatalbrain.com]

• Heart Failure

  Congestive heart failure and anuria at birth prompted emergency intervention. [ncbi.nlm.nih.gov]

  Chest x-ray showed cardiomegaly and cardiac ultrasound examination demonstrated congestive heart failure. To improve his symptoms, endovascular treatment was performed on Day 0. [jstage.jst.go.jp]

  Early diagnosis and treatment of DSM is crucial in order to avoid irreversible brain injuries or heart failure. Here, we report an unusual case of extensive DSM that showed good clinical and angiographic results after endovascular embolization. [sparrho.com]

  Because of progressive heart failure, the patient underwent four sessions of endovascular treatment on postnatal days 4, 10, 12, and 17. [ajnr.org]

• Mitral Valve Prolapse

  Cardiovascular manifestations include MITRAL VALVE PROLAPSE, dilation of the AORTA, and aortic dissection. Other features include lens displacement (ectopia lentis), disproportioned long limbs and enlarged DURA MATER (dural ectasia). [bioportfolio.com]

• Pulsating Exophthalmos

  Ocular manifestations include pulsating exophthalmos, orbital congestion, and oculomotor disorders. DAVMS situated primarily in the inferior petrosal sinus is unusual. [nature.com]

  The indirect form typically occurs spontaneously and is only rarely secondary to trauma. 24 Patients typically present with ocular symptoms – pulsating exophthalmos, orbital bruit, chemosis – resulting from anterior venous drainage. [jaocr.org]

• Ectopia Lentis

  Other features include lens displacement (ectopia lentis), disproportioned long limbs and enlarged DURA MATER (dural ectasia). [bioportfolio.com]

• Low Set Ears

  It is accompanied by signs of mild cranio‐facial dysmorphism: hypertelorism, flattened nose, low set ears, retromicrognathia, increased anteroposterior cranial diameter. Bilobed right lung. Karyotype: 46XX. Not other genetic studies. [obgyn.onlinelibrary.wiley.com]

• Suggestibility

  However, MRI revealed no abnormal findings suggestive of a vascular malformation. [stroke.ahajournals.org]

  Our findings suggest that DWI is a valuable adjunct to the standard T1- and T2-weighted fetal MRI sequences. [ncbi.nlm.nih.gov]

  Eur J Paediatr Neurol. 12(1):41-5, 2008 Laurichesse Delmas H et al: Prenatal diagnosis of thrombosis of the dural sinuses: report of six cases, review of the literature and suggested management. [app.statdx.com]

  Postnatal enlargement of the dural sinus has not been described before suggesting a delay in the maturation of the dural sinus which normally would occur antenatally. [biomedsearch.com]

• Scalp Mass

  Case Reports Case 1 History and Examination A 15-day-old baby girl had a persistent scalp mass, which on ultrasound was shown to be a midline highflow vascular lesion beneath the posterior fontanelle. [thejns.org]

• Anuria

  Congestive heart failure and anuria at birth prompted emergency intervention. [ncbi.nlm.nih.gov]

Isolated coccygeal dimples do not require further workup or treatment. FIGURE 9 Benign coccygeal dimple within the gluteal cleft and overlying the tip of the coccyx. [pediatrics.aappublications.org]

Subsequent workup led to an angiogram, where sagittal sinus thrombosis with extensive trans-cerebral and trans-osseous emissary vein collateral channels was seen. In retrospect, these findings were present on the patient’s earlier contrast MRI. [neuroangio.org]

• Pneumoperitoneum

  […] care unit. 3009074 - Congenital anomalies--retrospective and contemporary treatment. 17158594 - Congenital disorder of glycosylation type ia presenting with hydrops fetalis. 11669044 - Symptomatic congenital syphilis presenting at birth. 24529674 - Pneumoperitoneum [biomedsearch.com]

We present three cases of midline DSMs and discuss the treatment strategy employed for each lesion. A review of the literature was completed to summarize current literature and treatment practices. [experts.umn.edu]

Modalities or Observation of Arteriovenous Malformations; Selection of Treatment Modalities or Observation of Dural Arteriovenous Malformations; Surgical Treatment of Cranial Arteriovenous Malformations and Dural Arteriovenous Fistulas; Anesthesia Considerations [books.google.de]

Staged Endovascular treatment in order to prevent further brain injury three times. •The dilated posterior sinus compressed his cerebellum and brain stem at 5 months. The compression was palliated after the 3rd intervention. [epostersonline.com]

The treatment options must be adjusted to each situation. [ncbi.nlm.nih.gov]

Treatment and prognosis DSMs involving the jugular bulb carry excellent prognosis with occlusion of AVF and thrombosis of sigmoid sinus distal to the superior petrosal sinus. Prognosis of DSMs of torcular and adjacent sinuses is less favourable. [radiopaedia.org]

Although normal cranial circumference is reportedly an essential factor for a favorable prognosis, the patient in this report with a cranial circumference at + 2.0 SD (35.6 cm) had a favorable prognosis. [ncbi.nlm.nih.gov]

Malformation involving the central, large dural sinus and torcular has poor prognosis and high mortality while lateral dural sinus malformations have excellent prognosis after endovascular treatment. [jcvs.in]

In this type of DAVF the prognosis depends on the location—midline malformations (those involving the torcula) have a worse prognosis than those located laterally because in the latter cases the normal venous vessels provide the necessary drainage for [ispn.guide]

Dural sinus malformations, which are characterized by massively dilated dural sinuses, are one of the etiologies of an intracranial fetal cystic mass. [ncbi.nlm.nih.gov]

Objective To review tDSMs reported in the literature of multiple specialties for features that support a common etiology, and to identify key prognostic factors, with an emphasis on tDSM trajectory highlighted in part I. [jnis.bmj.com]

Introduction: Dural sinus malformations, which are characterized by massively dilated dural sinuses, are one of the etiologies of an intracranial fetal cystic mass. [tandfonline.com]

Torcular dural sinus malformations (tDSMs) are described as slow flow dural arteriovenous fistulae with frequently poor outcomes in the neuroangiographic literature, but other etiologies have been proposed in the obstetric literature, where outcomes have [bioportfolio.com]

Articles in this issue include: Arteriovenous Malformations: Epidemiology and Clinical Presentation; Dural Arteriovenous Fistulas: Epidemiology and Clinical Presentation; Historical Perspective of Treatments of Arteriovenous Malformations and Dural Arteriovenous [books.google.de]

Epidemiology [ edit ] 10-15% of intracranial AV malformations are DAVFs. [4] There is a higher preponderance in females (61-66%), and typically patients are in their fourth or fifth generation of life. [en.wikipedia.org]

Moreover, the epidemiology and clinical findings particular to children with AVMs can be ascribed to the distinct angioarchitecture of pediatric AVMs. However, the natural history and treatment of pediatric AVMs is relatively unknown. [content.iospress.com]

Favourable clinical evolution 17/29(58.6%) Favourable clinical evolution with morphological exclusion Unfavourable clinical evolution 10/17(58.8%) 12/29(41.4%) Unfavourable clinical evolution with death 11/12(90.9%) No follow-up 1/30(3.3%) Discussion Epidemiology [ncbi.nlm.nih.gov]

Owing to its rarity, the pathophysiology of DSM has not been fully elucidated. We report a case of prenatally diagnosed DSM with an unusual clinical course. [ncbi.nlm.nih.gov]

Such a prenatal and postnatal morphological change and clinical course have not been reported previously, and will be useful in elucidating the pathophysiology of this rare but important clinical entity. [epostersonline.com]

Seite 697 - Physiological and pathophysiological roles of excitatory amino acids during central nervous system development. ‎ [books.google.de]

الصفحة 697 - Physiological and pathophysiological roles of excitatory amino acids during central nervous system development. ‏ [books.google.com]

DSM (tDSM), generalizable statements about etiology and prognosis are difficult because neurosurgeons/neuroradiologists and obstetrical imagers have focused on different patient age groups, have reported different outcomes, and have offered differing pathophysiologic [jnis.bmj.com]

Conclusion: Early diagnosis and treatment, if necessary, of DSMs are critical to prevent cardiac failure or parenchymal injury from chronic venous hypertension. [experts.umn.edu]

Staged Endovascular treatment in order to prevent further brain injury three times. •The dilated posterior sinus compressed his cerebellum and brain stem at 5 months. The compression was palliated after the 3rd intervention. [epostersonline.com]

Type III dural fistulas need to be treated to prevent hemorrhage. Treatment can be as simple as clipping the draining vein at the site of the dural sinus. [en.wikipedia.org]

Consequently the clinical goals that we have set are early diagnosis and early treatment, whether it be preventive or curative, in an effort to prevent or cure the disorder’s natural history which, we suppose, begins at birth 2, 3. [mrineonatalbrain.com]

Working towards safe and affordable prevention strategies and comprehensive care and support for people with memory problems and their families Brain Plasticity Laboratory Studying the brain's ability to reorganize and form new connections in either desirable [med.umn.edu]