Patients usually present between the ages of 20 and 79 years. [nature.com]

On the other hand, in IDAVF, the sinus usually presents with a normal or slightly enlarged dural sinus with high-velocity flow through the AV shunt. [journals.lww.com]

Six patients (75.0%) had a favourable outcome and 2(25.0%) with unfavourable outcome one of which presented with brain damage. Clinical Presentation The most frequent clinical presentation was macrocrania 76.7.0%. [ncbi.nlm.nih.gov]

Purpose: Dural sinus malformations (DSMs) are rare pediatric vascular lesions that have variable presentations and outcomes. We present three cases of midline DSMs and discuss the treatment strategy employed for each lesion. [experts.umn.edu]

• Mitral Valve Prolapse

  Cardiovascular manifestations include MITRAL VALVE PROLAPSE, dilation of the AORTA, and aortic dissection. Other features include lens displacement (ectopia lentis), disproportioned long limbs and enlarged DURA MATER (dural ectasia). [bioportfolio.com]

• Pulsating Exophthalmos

  Ocular manifestations include pulsating exophthalmos, orbital congestion, and oculomotor disorders. DAVMS situated primarily in the inferior petrosal sinus is unusual. [nature.com]

  The indirect form typically occurs spontaneously and is only rarely secondary to trauma. 24 Patients typically present with ocular symptoms – pulsating exophthalmos, orbital bruit, chemosis – resulting from anterior venous drainage. [jaocr.org]

• Scalp Mass

  Case Reports Case 1 History and Examination A 15-day-old baby girl had a persistent scalp mass, which on ultrasound was shown to be a midline highflow vascular lesion beneath the posterior fontanelle. [thejns.org]

• Anuria

  Congestive heart failure and anuria at birth prompted emergency intervention. [ncbi.nlm.nih.gov]

• Global Developmental Delay

  At 42 months’ follow-up, this patient had global developmental delay and was dependent on a gastrostomy feeding tube. The tDSM showed radiological evidence of a decrease in size but not full involution. [thejns.org]

Isolated coccygeal dimples do not require further workup or treatment. FIGURE 9 Benign coccygeal dimple within the gluteal cleft and overlying the tip of the coccyx. [pediatrics.aappublications.org]

Subsequent workup led to an angiogram, where sagittal sinus thrombosis with extensive trans-cerebral and trans-osseous emissary vein collateral channels was seen. In retrospect, these findings were present on the patient’s earlier contrast MRI. [neuroangio.org]

• Pneumoperitoneum

  […] care unit. 3009074 - Congenital anomalies--retrospective and contemporary treatment. 17158594 - Congenital disorder of glycosylation type ia presenting with hydrops fetalis. 11669044 - Symptomatic congenital syphilis presenting at birth. 24529674 - Pneumoperitoneum [biomedsearch.com]

[…] following surgical treatment in combination with embolization has been reported in neonates.7,8 Endovascular embolization in combination with symptomatic treatment remains the primary therapeutic method. [journals.lww.com]

The treatment options must be adjusted to each situation. [ncbi.nlm.nih.gov]

[…] inform treatment decisions and prenatal counseling in these rare disorders. [thejns.org]

The aim of treatment is to preserve the cerebral venous drainage and occlusion of mural AV shunts. [radiopaedia.org]

We present three cases of midline DSMs and discuss the treatment strategy employed for each lesion. A review of the literature was completed to summarize current literature and treatment practices. [experts.umn.edu]

Treatment and prognosis Dural sinus malformations involving the jugular bulb carry excellent prognosis with occlusion of AVF and thrombosis of sigmoid sinus distal to the superior petrosal sinus. [radiopaedia.org]

Although normal cranial circumference is reportedly an essential factor for a favorable prognosis, the patient in this report with a cranial circumference at + 2.0 SD (35.6 cm) had a favorable prognosis. [ncbi.nlm.nih.gov]

In previous studies,2,3 poor prognosis was reported when DSMs involved immature, large, or central dural sinuses with turbulent and slow flow and impairment of the deep and superficial veins. [journals.lww.com]

In addition, antenatal diagnosis and thrombosis of pouch also have good prognosis, possibly because the clot may spontaneously obliterate the fistulas [1, 2]. [karger.com]

Dural sinus malformations, which are characterized by massively dilated dural sinuses, are one of the etiologies of an intracranial fetal cystic mass. [ncbi.nlm.nih.gov]

Objective To review tDSMs reported in the literature of multiple specialties for features that support a common etiology, and to identify key prognostic factors, with an emphasis on tDSM trajectory highlighted in part I. [jnis.bmj.com]

Introduction: Dural sinus malformations, which are characterized by massively dilated dural sinuses, are one of the etiologies of an intracranial fetal cystic mass. [tandfonline.com]

Torcular dural sinus malformations (tDSMs) are described as slow flow dural arteriovenous fistulae with frequently poor outcomes in the neuroangiographic literature, but other etiologies have been proposed in the obstetric literature, where outcomes have [bioportfolio.com]

Articles in this issue include: Arteriovenous Malformations: Epidemiology and Clinical Presentation; Dural Arteriovenous Fistulas: Epidemiology and Clinical Presentation; Historical Perspective of Treatments of Arteriovenous Malformations and Dural Arteriovenous [books.google.de]

Epidemiology [ edit ] 10-15% of intracranial AV malformations are DAVFs. [4] There is a higher preponderance in females (61-66%), and typically patients are in their fourth or fifth generation of life. [en.wikipedia.org]

Moreover, the epidemiology and clinical findings particular to children with AVMs can be ascribed to the distinct angioarchitecture of pediatric AVMs. However, the natural history and treatment of pediatric AVMs is relatively unknown. [content.iospress.com]

The Strengthening the Reporting of Observational Studies in Epidemiology (STROBE) statement: guidelines for reporting observational studies. PLoS Med. 2007;4(10):e296. [thejns.org]

Favourable clinical evolution 17/29(58.6%) Favourable clinical evolution with morphological exclusion Unfavourable clinical evolution 10/17(58.8%) 12/29(41.4%) Unfavourable clinical evolution with death 11/12(90.9%) No follow-up 1/30(3.3%) Discussion Epidemiology [ncbi.nlm.nih.gov]

Owing to its rarity, the pathophysiology of DSM has not been fully elucidated. We report a case of prenatally diagnosed DSM with an unusual clinical course. [ncbi.nlm.nih.gov]

Such a prenatal and postnatal morphological change and clinical course have not been reported previously, and will be useful in elucidating the pathophysiology of this rare but important clinical entity. [epostersonline.com]

Seite 697 - Physiological and pathophysiological roles of excitatory amino acids during central nervous system development. ‎ [books.google.de]

الصفحة 697 - Physiological and pathophysiological roles of excitatory amino acids during central nervous system development. ‏ [books.google.com]

DSM (tDSM), generalizable statements about etiology and prognosis are difficult because neurosurgeons/neuroradiologists and obstetrical imagers have focused on different patient age groups, have reported different outcomes, and have offered differing pathophysiologic [jnis.bmj.com]

Conclusion: Early diagnosis and treatment, if necessary, of DSMs are critical to prevent cardiac failure or parenchymal injury from chronic venous hypertension. [experts.umn.edu]

In addition, medical treatment with heparin, diuretics, and/or inotropic agents help to prevent dural sinus thrombosis and hyperdynamic cardiac failure. [journals.lww.com]

Staged Endovascular treatment in order to prevent further brain injury three times. •The dilated posterior sinus compressed his cerebellum and brain stem at 5 months. The compression was palliated after the 3rd intervention. [epostersonline.com]

Type III dural fistulas need to be treated to prevent hemorrhage. Treatment can be as simple as clipping the draining vein at the site of the dural sinus. [en.wikipedia.org]

Although thrombosis plays an important role in the involution of the tDSM, systemic anticoagulation may be utilized to prevent rapid progression of a thrombus posttreatment or during the natural history to prevent deleterious effects from occlusive dural [thejns.org]