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Dural Sinus Malformation

Malformation of Dural Sinus


Presentation

  • We present a case of prenatally diagnosed DSM and propose a parameter to predict poor fetal outcome. Detailed ultrasonography at 26 weeks of our patient showed an intracranial cyst in the left posterior fossa.[ncbi.nlm.nih.gov]
  • Purpose: Dural sinus malformations (DSMs) are rare pediatric vascular lesions that have variable presentations and outcomes. We present three cases of midline DSMs and discuss the treatment strategy employed for each lesion.[experts.umn.edu]
  • , and Management; Carotid Cavernous Fistulas: Epidemiology, Clinical Presentation, and Management.[books.google.de]
Mitral Valve Prolapse
  • Cardiovascular manifestations include MITRAL VALVE PROLAPSE, dilation of the AORTA, and aortic dissection. Other features include lens displacement (ectopia lentis), disproportioned long limbs and enlarged DURA MATER (dural ectasia).[bioportfolio.com]
Myopathy
  • الصفحة 701 - Mitochondrial myopathy, encephalopathy, lactic acidosis, and stroke-like episodes: a distinctive clinical syndrome. Ann Neurol 1984;16:481-488. ‏ الصفحة 680 - The vascular system of the cerebral cortex. Adv Anat Embryol Cell Biol... ‏[books.google.com]
  • Seite 701 - Mitochondrial myopathy, encephalopathy, lactic acidosis, and stroke-like episodes: a distinctive clinical syndrome. Ann Neurol 1984;16:481-488. ‎ Seite 680 - The vascular system of the cerebral cortex. Adv Anat Embryol Cell Biol... ‎[books.google.de]
Ectopia Lentis
  • Other features include lens displacement (ectopia lentis), disproportioned long limbs and enlarged DURA MATER (dural ectasia).[bioportfolio.com]
Hydrops Fetalis
  • Documents : 23356634 - Cytomegalovirus infection in infants admitted to a neonatal intensive care unit. 3009074 - Congenital anomalies--retrospective and contemporary treatment. 17158594 - Congenital disorder of glycosylation type ia presenting with hydrops[biomedsearch.com]
Indecisiveness
  • الصفحة 32 - The actions of the -feet indicate more clearly, perhaps, than those of any other part of the body (with the possible exception of the face) a man's feeling of happiness, sorrow, indecision, embarrassment, determination, pride, or joy of living[books.google.com]
  • Seite 32 - The actions of the -feet indicate more clearly, perhaps, than those of any other part of the body (with the possible exception of the face) a man's feeling of happiness, sorrow, indecision, embarrassment, determination, pride, or joy of living[books.google.de]
Anuria
  • Congestive heart failure and anuria at birth prompted emergency intervention.[ncbi.nlm.nih.gov]

Workup

  • Isolated coccygeal dimples do not require further workup or treatment. FIGURE 9 Benign coccygeal dimple within the gluteal cleft and overlying the tip of the coccyx.[pediatrics.aappublications.org]
  • Subsequent workup led to an angiogram, where sagittal sinus thrombosis with extensive trans-cerebral and trans-osseous emissary vein collateral channels was seen. In retrospect, these findings were present on the patient’s earlier contrast MRI.[neuroangio.org]
Pneumoperitoneum
  • […] care unit. 3009074 - Congenital anomalies--retrospective and contemporary treatment. 17158594 - Congenital disorder of glycosylation type ia presenting with hydrops fetalis. 11669044 - Symptomatic congenital syphilis presenting at birth. 24529674 - Pneumoperitoneum[biomedsearch.com]

Treatment

  • We present three cases of midline DSMs and discuss the treatment strategy employed for each lesion. A review of the literature was completed to summarize current literature and treatment practices.[experts.umn.edu]
  • Follow-up MRI at 1 month suggested latent venous hypertension and prompted endovascular treatment.[ncbi.nlm.nih.gov]
  • Modalities or Observation of Arteriovenous Malformations; Selection of Treatment Modalities or Observation of Dural Arteriovenous Malformations; Surgical Treatment of Cranial Arteriovenous Malformations and Dural Arteriovenous Fistulas; Anesthesia Considerations[books.google.de]

Prognosis

  • Although normal cranial circumference is reportedly an essential factor for a favorable prognosis, the patient in this report with a cranial circumference at 2.0 SD (35.6 cm) had a favorable prognosis.[ncbi.nlm.nih.gov]
  • Treatment and prognosis DSMs involving the jugular bulb carry excellent prognosis with occlusion of AVF and thrombosis of sigmoid sinus distal to the superior petrosal sinus. Prognosis of DSMs of torcular and adjacent sinuses is less favourable.[radiopaedia.org]
  • Dural sinus malformation (DSM) is a relatively rare pediatric arteriovenous (AV) shunt disease, and is defined as a large dural sinus lake accompanying dural AV shunts with a poor prognosis.[epostersonline.com]

Etiology

  • Dural sinus malformations, which are characterized by massively dilated dural sinuses, are one of the etiologies of an intracranial fetal cystic mass.[ncbi.nlm.nih.gov]
  • Objective To review tDSMs reported in the literature of multiple specialties for features that support a common etiology, and to identify key prognostic factors, with an emphasis on tDSM trajectory highlighted in part I.[jnis.bmj.com]
  • Torcular dural sinus malformations (tDSMs) are described as slow flow dural arteriovenous fistulae with frequently poor outcomes in the neuroangiographic literature, but other etiologies have been proposed in the obstetric literature, where outcomes have[bioportfolio.com]
  • (Fig. 11) Conventional angiography may help elucidate the etiology and be utilized for embolization with coils or glue.[jaocr.org]

Epidemiology

  • Articles in this issue include: Arteriovenous Malformations: Epidemiology and Clinical Presentation; Dural Arteriovenous Fistulas: Epidemiology and Clinical Presentation; Historical Perspective of Treatments of Arteriovenous Malformations and Dural Arteriovenous[books.google.de]
  • Epidemiology [ edit ] 10-15% of intracranial AV malformations are DAVFs. [4] There is a higher preponderance in females (61-66%), and typically patients are in their fourth or fifth generation of life.[en.wikipedia.org]
  • Moreover, the epidemiology and clinical findings particular to children with AVMs can be ascribed to the distinct angioarchitecture of pediatric AVMs. However, the natural history and treatment of pediatric AVMs is relatively unknown.[content.iospress.com]
Sex distribution
Age distribution

Pathophysiology

  • Owing to its rarity, the pathophysiology of DSM has not been fully elucidated. We report a case of prenatally diagnosed DSM with an unusual clinical course.[ncbi.nlm.nih.gov]
  • Such a prenatal and postnatal morphological change and clinical course have not been reported previously, and will be useful in elucidating the pathophysiology of this rare but important clinical entity.[epostersonline.com]
  • الصفحة 697 - Physiological and pathophysiological roles of excitatory amino acids during central nervous system development. ‏[books.google.com]
  • Seite 697 - Physiological and pathophysiological roles of excitatory amino acids during central nervous system development. ‎[books.google.de]
  • DSM (tDSM), generalizable statements about etiology and prognosis are difficult because neurosurgeons/neuroradiologists and obstetrical imagers have focused on different patient age groups, have reported different outcomes, and have offered differing pathophysiologic[jnis.bmj.com]

Prevention

  • Conclusion: Early diagnosis and treatment, if necessary, of DSMs are critical to prevent cardiac failure or parenchymal injury from chronic venous hypertension.[experts.umn.edu]
  • Staged Endovascular treatment in order to prevent further brain injury three times. •The dilated posterior sinus compressed his cerebellum and brain stem at 5 months. The compression was palliated after the 3rd intervention.[epostersonline.com]
  • Conclusion Early diagnosis and treatment, if necessary, of DSMs are critical to prevent cardiac failure or parenchymal injury from chronic venous hypertension.[link.springer.com]
  • Type III dural fistulas need to be treated to prevent hemorrhage. Treatment can be as simple as clipping the draining vein at the site of the dural sinus.[en.wikipedia.org]
  • Consequently the clinical goals that we have set are early diagnosis and early treatment, whether it be preventive or curative, in an effort to prevent or cure the disorder’s natural history which, we suppose, begins at birth 2 , 3 .[mrineonatalbrain.com]

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