[…] common: Marfan syndrome (upward and outward) Homocystinuria (downward and inwards) Weill–Marchesani syndrome Sulfite oxidase deficiency HyperlysinemiaLess common: Ehlers–Danlos syndrome Crouzon disease Refsum syndrome Kniest syndrome Mandibulofacial dysostosis [en.wikipedia.org]

Other systemic diseases associated with ectopia lentis: Weill-Marchesani syndrome Sulfite oxidase deficiency Hyperlysinemia Ehlers-Danlos syndrome Sturge-Weber syndrome Mandibulofacial dysostosis Wildervanck syndrome Conradi syndrome Pfaundler syndrome [retinavitreous.com]

Rare Systemic Associations  Ehlers-Danlos syndrome  Crouzon disease  Refsum syndrome  Kniest syndrome  Mandibulofacial dysostosis  Sturge-Weber syndrome 19. [es.slideshare.net]

[…] cases occurs in the inferior or nasal direction. [12] [13] Other systemic diseases associated with ectopia lentis [5] [6] : Weill-Marchesani syndrome Sulfite oxidase deficiency Hyperlysinemia Ehlers-Danlos syndrome Sturge-Weber syndrome Mandibulofacial dysostosis [eyewiki.aao.org]

The other cousin had an atrial septal defect, mitral valve prolapse, and only mild myopia. Their intelligence is normal. [ncbi.nlm.nih.gov]

Sodium hyaluronate (Healon GV) enhanced stability of the crystalline lens during aspiration and maintenance of the anterior chamber during passage of the needles through the ciliary sulcus. [ncbi.nlm.nih.gov]

Vajpayee Intralenticular bimanual irrigation: aspiration for subluxated lens in Marfan's syndrome [33] I. Anteby, M. Isaac, D. BenEzra Hereditary subluxated lenses: visual performances and long-term follow-up after surgery [34] M. Halpert, D. [elsevier.es]

[…] cutting or aspiration. [springerplus.springeropen.com]

A study of five cases of EL in Saudi Arabia suggested better visual outcomes compared to eyes with acquired EL managed by lens aspiration. [10] In Oman, ten out of twenty eyes with subluxated lens managed by pars plana scleral lensectomy and scleral-fixated [meajo.org]

Congenital contractural arachnodactyly (CCA) was described by Beals and Hecht as an autosomal dominant disorder distinct from Marfan syndrome and comprising joint contractures, arachnodactyly, scoliosis, and a distinct "crumpled ear" deformity. [ncbi.nlm.nih.gov]

If the eye is not dilated, look for iridodonesis (abnormal tremor of the iris), phacodonesis (abnormal movement of the lens), deep anterior chamber depth or vitreous herniation into the anterior chamber. [mrcophth.com]

Trembling of the iris (iridodonesis) Trembling of the lens (phacodonesis) Aphakic crescent Mild conjunctival redness Vitreous humour degeneration Prolapse of the vitreous into the anterior chamber Increase or decrease of anterior chamber depth Removal [premilife.com]

L21) See corectopia ; iridodonesis ; pupillary block. Fig. [medical-dictionary.thefreedictionary.com]

Megalocornea, With Ectopia Lentis And With Or Without Secondary Glaucoma Synonyms - Classification developmental, eye, genetic Phenotypes Autosomal recessive inheritance ; Deep anterior chamber ; Ectopia lentis ; Glaucoma ; High palate ; Hypermetropia ; Iridodonesis [mousephenotype.org]

It can be recognized by trembling of the iris (iridodonesis) or lens (phacodonesis) and the presence of an aphakic crescent (an area of the pupil where the lens is absent). [en.wikipedia.org]

Subluxation is one of the causes of monocular diplopia. If the luxation is complete the eye becomes markedly hyperopic and is unable to accommodate. [medical-dictionary.thefreedictionary.com]

While most clinicians immediately think of neurological problems when diplopia is mentioned, monocular diplopia is always attributed to some type of media issue, such as a cataract, corneal opacity or subluxated lens. [reviewofoptometry.com]

Patients may also complain of monocular diplopia and are at risk of developing amblyopia, glaucoma, and retinal detachment. Ectopia lentis can be inherited as an isolated condition, usually autosomal dominant (simple ectopia lentis). [visualdx.com]

Presentation  Common presenting symptoms include the following:  Decreased distance visual acuity (secondary to astigmatism or lenticular myopia)  Poor near vision (loss of accommodative power)  Monocular diplopia  Red painful eye 22. [es.slideshare.net]