Objective: We present a case of primary renal epithelioid angiomyolipoma, its association with tuberous sclerosis and review the literature. [scielo.isciii.es]

Well circumscribed cutaneous mass Gross description Usually solitary Most lesions are completely encapsulated Nerve of origin may be present at the periphery - does not penetrate substance of tumor Large tumors have an eccentric position in relation to [pathologyoutlines.com]

• Aggressive Behavior

  Nevertheless, the epithelioid variant has been described recently, a rare entity with aggressive behavior, difficult histological characterization and poor prognosis. Palabras clave : Epithelioid angiomyolipoma; Kidney; Tuberous sclerosis. [scielo.isciii.es]

Surgical excision is the treatment of choice Local recurrence is uncommon Delayed facial nerve palsy can occur after surgical removal of vestibular schwannoma (Neurosurgery 2016;78:251) Clinical images Contributed by Mark R. [pathologyoutlines.com]

Results: The presence of this epithelial variant is rare and must be taken into account because of its malignant potential and, thus, with different prognosis and follow up, compared to classical angiomyolipoma. [scielo.isciii.es]

[…] cellular areas (Antoni A) with nuclear palisading (Verocay bodies) and a hypocellular component (Antoni B) Terminology Neurilemoma (acceptable) ICD coding ICD-10: D36.10 - benign neoplasm of peripheral nerves and autonomic nervous system, unspecified Epidemiology [pathologyoutlines.com]

[…] mediastinum and retroperitoneum Other areas include posterior spinal roots, bone, gastrointestinal tract, pancreas, liver, thyroid, adrenal glands and lymph nodes Rare sites include penis and vulva (Urol Ann 2017;9:301, World J Surg Oncol 2015;13:139) Pathophysiology [pathologyoutlines.com]