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Erythema Palmaris Hereditarium

Erythema Palmare Hereditarium


Presentation

  • The first and second cases are twin boys presenting with erythema mainly on the thenar and hypothenar eminences and on the phalanges that appeared 8 months after birth.[onlinelibrary.wiley.com]
  • This report presents a patient with erythema palmare hereditarium. SN - 1662-6567 UR - 'Red_Palms'_'Lane's_Disease'__ L2 - DB - PRIME DP - Unbound Medicine ER -[unboundmedicine.com]
  • Erythema usually presents at birth and remains stable throughout life. Histology shows dilated vessels in the entire dermis with inflammatory infiltrate.[malacards.org]
  • Dermatologist c/o InMedica - Centro Medico Polispecialistico Largo XII Ottobre 62 cell 335.655.97.70 - office 010 5701818 www.lucianoschiazza.it Erythema palmare hereditarium is a benign, permanent condition that usually presents at birth.[lucianoschiazza.it]
  • […] pseudoainhum formation can be ruled out due to the presence of autoamputation of digits in the present case [Figure 3].[jdrntruhs.org]
Gagging
  • Synonym(s): erythema palmare hereditarium Lane dissector Lane elevator Lane forceps Lane mouth gag Lane needle Lane plates - flattened, narrow, metal plates used to hold the fragments of a fractured bone in apposition.[medical-dictionary.thefreedictionary.com]
Kayser-Fleischer Ring
  • […] thrombocytopenic purpura) 287.39 Kaschin-Beck disease (endemic polyarthritis) - see Disease, Kaschin-Beck Kast's syndrome (dyschondroplasia with hemangiomas) 756.4 Katatonia- see Catatonia Katayama disease or fever 120.2 Kathisophobia 781.0 Kawasaki disease 446.1 Kayser-Fleischer[theodora.com]
Erythema
  • TY - JOUR T1 - Erythema Palmare Hereditarium ('Red Palms', 'Lane's Disease').[unboundmedicine.com]
  • OMIM : 58 Erythema palmare hereditarium is a benign condition that was first described by Lane (1929). Erythema usually presents at birth and remains stable throughout life.[malacards.org]
  • Versione Italiana ERYTHEMA PALMARE HEREDITARIUM (Lane’s red palms) Luciano Schiazza M.D.[lucianoschiazza.it]
  • The third case is a girl with congenital palmar erythema and two other capillary malformations. The fourth case is a 58-year-old woman with palmar erythema that appeared after pregnancy.[onlinelibrary.wiley.com]
  • Synonym(s): Lane kink Lane bone-holding clamp Lane bone-holding forceps Lane catheter Lane clamp Lane disease - asymptomatic symmetrical palmar erythema.[medical-dictionary.thefreedictionary.com]
Palmar Erythema
  • The third case is a girl with congenital palmar erythema and two other capillary malformations. The fourth case is a 58-year-old woman with palmar erythema that appeared after pregnancy.[onlinelibrary.wiley.com]
  • Synonym(s): Lane kink Lane bone-holding clamp Lane bone-holding forceps Lane catheter Lane clamp Lane disease - asymptomatic symmetrical palmar erythema.[medical-dictionary.thefreedictionary.com]
  • Primary palmar erythema Primary palmar erythema is classified as: Hereditary Pregnancy-related (30% of pregnant women will develop palmar erythema ) Unknown cause ( idiopathic ) Secondary palmar erythema Causes of secondary palmar erythema include: Liver[dermnetnz.org]
  • Secondary palmar erythema Palmar erythema is a symptom of many different conditions. Its appearance is often the first sign of an underlying medical concern. For example, palmar erythema is associated with several forms of liver disease.[healthline.com]
Freckles
  • Periodontitis Premature loss of primary teeth Plantar hyperkeratosis Abnormality of the fingernails Cryptorchidism Hyperparathyroidism Hypercalcemia Keratoconjunctivitis sicca Blepharitis Eczematoid dermatitis Overbite Telangiectasia of the skin Cellulitis Freckling[mendelian.co]
  • Eosinophilic Folliculitis); (Infantile/Childhood Eosinophilic Pustulosis of the Scalp); (HIV- Associated Eosinophilic Folliculitis); (HIV-Related Eosinophilic Folliculitis); (Sterile Eosinophilic Pustulosis); (Eosinophilic Pustular Dermatosis) Ephelides (Freckles[catdir.loc.gov]
  • […] circumscribed area of change in normal skin color without elevation or depression of the surface relative to the surrounding skin • they are generally less than one centimeter in diameter • they are flat and cannot be palpated • an example of this would be a freckle[quizlet.com]
Fracture
  • Synonym(s): erythema palmare hereditarium Lane dissector Lane elevator Lane forceps Lane mouth gag Lane needle Lane plates - flattened, narrow, metal plates used to hold the fragments of a fractured bone in apposition.[medical-dictionary.thefreedictionary.com]
Osteophyte
  • […] intestine) 560.9 organ or site, congenital NEC - see Anomaly, specified type NEC, by site ureter (pelvic junction) 593.3 congenital 753.20 vein(s) 459.2 caval 459.2 peripheral 459.2 Kinnier Wilson's disease (hepatolenticular degeneration) 275.1 Kissing osteophytes[theodora.com]
Hunger
  • 721.7 Kundrat's disease (lymphosarcoma) 200.1 Kunekune - see Dermatophytosis Kunkel syndrome (lupoid hepatitis) 571.49 Kupffer cell sarcoma (M9124/3) 155.0 Kuru 046.0 Kussmaul's coma (diabetic) 250.3 disease (polyarteritis nodosa) 446.0 respiration (air hunger[theodora.com]
Catatonia
  • 759.3 Kasabach-Merritt syndrome (capillary hemangioma associated with thrombocytopenic purpura) 287.39 Kaschin-Beck disease (endemic polyarthritis) - see Disease, Kaschin-Beck Kast's syndrome (dyschondroplasia with hemangiomas) 756.4 Katatonia- see Catatonia[theodora.com]

Workup

  • Many melanin granules in basal cells HID syndrome, CIE Sepsis workup none Meleda type Mal de Meleda, MDM, Meleda Disease, Keratosis Palmoplantaris Transgradiens of Siemens 757.4 Inhabitants of the island of Mljet off the Dalmation Coast SLURP-1, Ly-6[dermatologyadvisor.com]
Ketonuria
  • Kerato-uveitis (see also Iridocyclitis) 364.3 Keraunoparalysis 994.0 Kerion (celsi) 110.0 Kernicterus of newborn (not due to isoimmunization) 774.7 due to isoimmunization (conditions classifiable to 773.0-773.2) 773.4 Ketoacidosis 276.2 diabetic 250.1 Ketonuria[theodora.com]

Treatment

  • MEDICAL INTRO BOOKS ON OLD MEDICAL TREATMENTS AND REMEDIES THE PRACTICAL HOME PHYSICIAN AND ENCYCLOPEDIA OF MEDICINE The biggy of the late 1800's. Clearly shows the massive inroads in medical science and the treatment of disease.[doctortreatments.com]
  • Treatment Treatment regimes are based on surgical techniques, medications and ancillary treatments designed to decrease painful keratosis. Surgical debridement or paring of keratosis is effective, but only temporary.[faoj.org]
  • […] of severe Atopic eczema Trial(TREAT) A randomized controlled trial protocol assessing the effectiveness, safety and cost‐effectiveness of methotrexate vs. ciclosporin in the treatment of severe atopic eczema in children: the TREatment of severe Atopic[maruho.co.jp]
  • What is the treatment of palmar erythema ? No treatment is indicated for primary palmar erythema. If the cause of the palmar erythema is thought to be secondary to a drug, then it may be advisable to stop it.[dermnetnz.org]
  • In such instances, the dentist has a more important role in diagnosing, treatment planning and preservation of the periodontal tissues and, at the same time, referring for the treatment of the skin lesions.[e-ijd.org]

Prognosis

  • Hyde, James Nevins Montgomery, Frank Hugh Diseases of the skin Anatomy and physiology of skin General symptomatology General etiology General pathology General diagnosis General prognosis General therapeutics Classification Disorders of the glands Disorders[momicoh.pastperfectonline.com]
  • PE has been reported to occur in 60% of patients with rheumatoid arthritis and is associated with a favorable prognosis. Up to 18% of patients with thyrotoxicosis and 4.1% of patients with diabetes mellitus can have PE.[drwarrenrheymann.com]
  • Prognosis and T r ea t me nt. — The condition is irremediable as to permanent relief, but treatment can do much to keep the malady i n abeyance.[doctortreatments.com]
  • […] palmoplantar keratodermas (PPKs) are a group of heterogeneous skin disorders classified based upon their mode of inheritance, age of onset, morphology and distribution of palmoplantar thickening, presence of skin lesions elsewhere, histopathology, and prognosis[jdrntruhs.org]
  • Dental treatment done for this patient included oral prophylaxis, extraction of teeth with poor prognosis followed by replacement with removable prosthesis [Figure 5].[e-ijd.org]

Etiology

  • The etiology of PLS is multifactorial with genetic, immunological, and microbial factors playing a role in etiopathogenesis.[hindawi.com]
  • It is not improbable that there are several distinct varieties, as indicated by the unusual types referred to, and that the etiologic factors are somewhat varied.[doctortreatments.com]
  • Hyde, James Nevins Montgomery, Frank Hugh Diseases of the skin Anatomy and physiology of skin General symptomatology General etiology General pathology General diagnosis General prognosis General therapeutics Classification Disorders of the glands Disorders[momicoh.pastperfectonline.com]
  • The underlying cause for PLS is not well understood, but is thought to be a genetically transmitted trait, suggesting a multigenic etiology for PLS. [3] Recent studies have suggested a greater incidence of mutations of the cathepsin-C gene located on[e-ijd.org]

Epidemiology

  • ., et al. (1998).Mutations in keratin K9 in kindreds with epidermolyticpalmoplantar keratoderma and epidemiology in NorthernIreland. The Journal of Investigative Dermatology, 111,12071209.Da Rosa Santos, O. L. R., Amorim, J.[dokumen.tips]
  • Disorder Synonyms PPK Column* ICD-9 Selected Epidemiologic Features Genetic Cause Syndromic Associations Distinguishing features Age of onset (for disorder manifistation) Erythema Transgrediens Other Epidermal Features** Systemic Features*** Relevant[dermatologyadvisor.com]
Sex distribution
Age distribution

Prevention

  • Your skin Holds body fluids in, preventing dehydration Keeps harmful microbes out, preventing infections Helps you feel things like heat, cold, and pain Keeps your body temperature even Makes vitamin D when the sun shines on it Anything that irritates[icdlist.com]
  • CASE REPORT Year : 2011 Volume : 56 Issue : 6 Page : 740-743 Papillon-lefevre syndrome: A combined approach from the dermatologist and dentist - A clinical presentation Department of Pedodontics with Preventive Dentistry, Panineeya Dental College, Hyderabad[e-ijd.org]
  • Prevention includes the use of sun screen agents and the avoidance of drugs (for example tetracyclines) known to cause photosensitivity reactions. Usually a discreet slightly raised, red or pink lesion located on a sun exposed surface.[kmle.co.kr]
  • […] the disease, its usual involvement of all extremities, the absence of inflammatory symptoms, the frequent association of hyperidrosis of the parts, and the common history of its existence since birth and of hereditary tendency will gen erally serve to prevent[doctortreatments.com]
  • Theoretically, retinoids may help in prevention against some of the malignancies in these patients. Knowledge about the disease-causing gene in punctate PPK and its function might provide insights into possible skin-cancer risk.[the-medical-dictionary.com]

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