Symptoma

Erythroderma Desquamativum

Leiner Disease

It is our ambition to present a complete survey of all medical phenomena named for a person, with a biography of that person. Disclaimer: Whonamedit? does not give medical advice. [whonamedit.com]

The documents contained in this web site are presented for information purposes only. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment. [orpha.net]

This is especially present on the scalp and other oily parts of the body, such as the face and back. On the scalp, seborrheic dermatitis includes red skin, scaly patches, and recurring dandruff. It is also known as “cradle cap.” [diseaseinfosearch.org]

Synonym: ichthyosiform erythroderma, ichthyosis spinosa, keratoma malignum. (05 Mar 2000) ichthyosiform erythroderma, congenital Designation for several severe forms of ichthyosis, present at birth, that are characterised by hyperkeratotic scaling. [kmle.co.kr]

  • Recurrent Infection

    Severe, diffuse seborrheic dermatitis, recurrent infections (usually gram-negative), severe diarrhea, and muscle wasting; onset in infancy. Familial form exists. [insidesurgery.com]

    [erythro G. derma, skin] bullous congenital… … Medical dictionary Leiner disease — a disorder of infancy characterized principally by generalized seborrhealike dermatitis and erythroderma, intractable, severe diarrhea, recurrent infections, and failure [medicine.academic.ru]

    The individual will feel as if they are getting sick all the time or may have recurrent infections. The protein that is lacking usually helps fight inflammation (swelling) and infection of the body. [diseaseinfosearch.org]

    Complement factor I deficiency in a family with recurrent infections. Immunopharmacology. 1997 Dec. 38(1-2):207-13. [Medline]. Lutz HU. [emedicine.medscape.com]

  • Severe Pain

    A condition caused by continuous infusion therapy and resulting in a tingling sensation of the palms and soles, progressing to severe pain and tenderness with erythema and edema. [definithing.com]

  • Failure to Thrive

    […] of Infancy 53 Classifications: MalaCards based summary : Erythroderma Desquamativa of Leiner, is also known as generalized erythroderma, diarrhea, and failure to thrive. [malacards.org]

    From Wikidata Jump to navigation Jump to search disease Erythroderma desquamativum Generalized erythroderma, diarrhea, and failure to thrive Erythroderma desquamativa of Leiner Erythroderma Desquamativum of Infancy Leiner disease Leiner-Moussous Desquamative [wikidata.org]

    Synonyms Generalized erythroderma, diarrhea, and failure to thrive Erythroderma Desquamativum of Infancy Leiner-Moussous Desquamative Erythroderma Overview No overview is available at this time. Please check back for future updates. [rarediseases.org]

  • Chronic Diarrhea

    Additional symptoms include chronic diarrhea and the failure to gain weight at the expected rate (failure to thrive). The exact cause of erythroderma desquamativa of Leiner is unknown. [hekimce.com]

  • Skin Patch

    Other symptoms also include scaling on the trunk and limbs, red patches of skin on parts of the body that bend, fevers, reduced blood protein levels, thick red skin patches, peeling of the skin, itching, corneal ulcers. wasting of the lymph nodes, underdeveloped [en.wikipedia.org]

    Longstanding erythroderma may result in pigmentary changes (brown and/or white skin patches). How is erythroderma diagnosed? Blood count may show anaemia, white cell count abnormalities, and eosinophilia. [dermnetnz.org]

  • Scaly Rash

    The condition usually starts off as a scaly rash on the scalp, face or napkin area. Very rapidly it spreads to other parts of the body. The affected area is bright red and may look swollen. Infants appear uncomfortable but do not itch. [dermnetnz.org]

  • Chancre

    — Gonorrhoea with chancres and warts ; small blisters on orifice of urethra and inner surface of prepuce, forming chancre-like ulcers... ‏ الصفحة 450 - A young man came to me with a bubo in the left groin. [books.google.com]

Diagnosis - Erythroderma desquamativa of Leiner The routine diagnostic workup should include a CBC, sedimentation rate, urinalysis, urine culture, chemistry panel, thyroid profile, sweat test, stool for quantitative fat, chest x-ray, and an EKG. [checkorphan.org]

Initial diagnostic workup is included in Table 2. Figure 5 Algorithm for diagnosis of the erythrodermic infant. [dovepress.com]

  • Neisseria Gonorrhoeae

    These patients are at high risk for recurrent infection with Neisseria gonorrhoeae or Neisseria meningitidis. Severe pyogenic infections and sepsis occur in children and neonates who have a deficiency of a MAC component. [emedicine.medscape.com]

An easy method of treatment of erythroderma desquamativum Archives Francaises de Pediatrie 17: 516-518 1960 (PDF emailed within 1 workday: 29.90) Accession: 048229865 Download citation: RIS BibTeX Text PMID: 13743967 Treatment of Moussous' erythroderma [eurekamag.com]

He had been disappointed in that he had not obtained relief from the treatment used. His bones ached, his tongue was loaded, and his breath smelled badly. [books.google.com]

What treatment is available? Initially affected babies may need to be hospitalised to manage fluid and heat loss. Bland emollients may be used to treat the rash. Providing adequate nutrition is also an essential part of treatment. [dermnetnz.org]

Treatment The treatment is dependent on the cause. Topical steroids are the primary category of medications used to treat exfoliative dermatitis (ED). [dict.eudic.net]

Prognosis - Erythroderma desquamativa of Leiner Not supplied. [checkorphan.org]

The prognosis is very good unless proper intensive care and skin care are not provided. The disease is both a familial and a nonfamilial form. [dermaamin.com]

Prognosis of erythroderma depends on the underlying disease process. If the cause can be removed or corrected, prognosis is generally good. [dermnetnz.org]

Wilson HTH: Exfoliative dermatitis: Its etiology and prognosis. Arch Dermatol 1954;69:577–588. [karger.com]

Prognosis and treatment In the study done by Pruszkowski et al, the prognosis was poor with a mortality of 16%. [4] Patients died either due to complications arising from their erythroderma or their underlying disease at a mean age of 7 months. [e-ijd.org]

Other drugs specifically indicated for management of underlying etiology of exfoliative dermatitis may be necessary. [dict.eudic.net]

Anemia * Diarrhea * Failure to thrive * Reddish skin rash * Thickened skin rash * Spreading rash * Peeling rash * Scaling rash * Itching Causes - Erythroderma desquamativa of Leiner o Psychosocial (non-organic) –Insufficient caloric intake –Most common etiology [checkorphan.org]

Article Fr MEDLINE ID: mdl-26830925 Crohn Disease/complications, Edema/etiology, Vulvar Diseases/etiology, Adrenal Cortex Hormones/therapeutic use, Anus Diseases/etiology, Crohn Disease/drug therapy, Crohn Disease/pathology, Drug Combinations, Drug Substitution [pesquisa.bvsalud.org]

Erythroderma (from the Greek. erythros red and derma - skin) - a collective term that refers to a group of skin diseases of different etiology and pathogenesis. [medicalency.com]

Archives Francaises de Pediatrie 8(3): 337-338, 1951 Etiological role of Staphylococcus aureus in erythroderma desquamativum in infants (Leiner-Moussous disease); the presence of Staphylococcus aureus in the breast milk. [eurekamag.com]

[…] skin diseases, skin appendage diseases, pigmentary diseases, genetic diseases, nutritional and metabolic disorders, tumors, sexually transmitted diseases, AIDS, traditional medicine, integrated Chinese and Western medicine, evidence-based medicine, epidemiology [journalseek.net]

EPIDEMIOLOGY Erythroderma is a rare condition. The annual incidence has been estimated to be approximately 1 per 100,000 in the adult population [ 1 ]. [uptodate.com]

This report defines the prevalence of genital colonization in a large population of women, characterizes the women with S. aureus, and describes epidemiologic features of genital carriage. ‎ Página 50 - Lautenschlager S, Eichmann A. [books.google.es]

License: CC BY-SA 3.0 Definition and Epidemiology of Seborrhoeic Dermatitis Seborrhoeic dermatitis is a chronic papulosquamous dermatosis characterised by scaling and poorly defined erythematous patches. [lecturio.com]

EPIDEMIOLOGY • Bimodal Age Incidence 0-3 Months of life 4th – 7th Decade of life • Common in HIV/AIDS & PARKINSONISM • Men Women • 03 – 05 % Prevalence 6. [slideshare.net]

History The classification of exfoliative dermatitis into Wilson-Brocq (chronic relapsing), Hebra or pityriasis rubra (progressive), and Savill (self-limited) types may have had historical value, but it currently lacks pathophysiologic or clinical utility [dict.eudic.net]

Erythrodermic psoriasis: pathophysiology and current treatment perspectives - Dove Medical Press 2 years ago dovepress.com Abstract: Erythrodermic psoriasis (EP) is a rare and severe variant of psoriasis vulgaris, with an estimated prevalence of 1%–2.25% [wikinow.co]

Psoriasis pathophysiology: Current conceps of pathogenesis. Ann Rheum Dis. 2005; 64(Supple. 2)30-6. Rosenbach M, Hsu S, Korman N. Treatment of erythrodermic psoriasis: from the medical board of the National Psoriasis Foundation. [revistamedicahjca.med.ec]

Pathophysiology of Seborrhoeic Dermatitis The exact pathophysiology behind seborrhoeic dermatitis remains unknown with a number of theories propounded. Here, we discuss the most popular ones. [lecturio.com]

Pathophysiology The complement cascade consists of 3 separate pathways that converge in a final common pathway. [emedicine.medscape.com]

Hospitalization for the diseased person is suggested because of the controlled environment because it may prevent nutritional deficiencies and skin infections. [en.wikipedia.org]

[…] tubular acidosis –Chronic urinary tract infections –Chronic renal insufficiency * Syndromes –Down syndrome –Turner syndrome –Russell-Silver dwarfism –Fetal alcohol syndrome * Anatomic –Cleft lip/palate –Malrotation –Pyloric stenosis * Lead poisoning Prevention [checkorphan.org]

Propoxyphene-containing products may be taken with food to reduce or prevent... [mottchildren.org]

Thus, the role of new and innovative investigations related to skin care, skin health, various cutaneous diseases and their preventive or treatment strategies and the need for inaugurating this new journal is self-evident. [wjgnet.com]

(PDQ ): Prevention - Health Professional Information [NCI] Endometrial Cancer Prevention (PDQ ): Prevention - Patient Information [NCI] Endometrial Cancer Screening (PDQ ): Screening - Health Professional Information [NCI] Endometrial Cancer Screening [healthmedicinet.com]