We present 7 patients in 2 families with 13 episodes of spontaneous pneumothorax. Neither congenital defect, alpha1-antitrypsin deficiency nor the described A2B40 HLA haplotype could be found in our patients. [ncbi.nlm.nih.gov]

Among them, spontaneous pneumothorax is the most common presentation of pulmonary involvement with BHDS. [qjmed.oxfordjournals.org]

Excluding pulmonary embolism at the bedside without diagnostic imaging: management of patients with suspected pulmonary embolism presenting to the emergency department by using a simple clinical model and D-dimer. Ann Intern Med. ‎ [books.google.de]

Fibrofolliculomas are present in more than 80% of patients with BHD syndrome and typically appear after the age of 20 years. [hkmj.org]

Workup Laboratory Studies Arterial blood gas - In patients with severe underlying lung disease and in those with persistent respiratory distress despite treatment Hypoxemia occurs with increased alveolar-arterial oxygen tension gradient. [ernights.blogspot.com]

Currently, there is no curative treatment for BHD syndrome. For patients who develop spontaneous pneumothorax, VATS bullectomy combined with pleurodesis seems to be a more effective choice of treatment. [jtd.amegroups.com]

Seite 223 - American Thoracic Society/Centers for Disease Control and Prevention/Infectious Diseases Society of America: treatment of tuberculosis. Am J Respir Crit Care Med 2003;167:603-662. ‎ [books.google.de]

[…] to determine treatment. [chop.edu]

Your long-term outlook depends on the size of the pneumothorax, as well as the cause and treatment required. In general, a small pneumothorax that doesn’t cause significant symptoms can resolve with observation or minimal treatment. [healthline.com]

Bilateral bullectomy through thoracoscopic surgery has been a mainstay of definitive treatment in patients with SBSP ( 3, 6, 7 ). [ispub.com]

If the air leak in the lungs is occurring in one specific location, that area may be removed in a procedure called a pleurectomy.16 Prognosis for pneumothorax The prognosis for primary spontaneous pneumothorax is fair to good. [superpharmacy.com.au]

Treatment and prognosis Treatment depends on a number of factors: size of the pneumothorax symptoms background lung disease/respiratory reserve Estimating the size of pneumothorax is somewhat controversial with no international consensus. [radiopaedia.org]

Prognosis Up to 50% of patients who suffer from a pneumothorax will have another or a recurring pneumothorax. However, there are no long-term complications after successful treatment. [physio-pedia.com]

Prognosis in MVP syndrome is better than for MVP in Marfan syndrome, with significantly lower risk for mitral regurgitation. [nature.com]

To our knowledge, these are the first genetic data to support etiology of neonatal spontaneous familial pneumothorax. [ncbi.nlm.nih.gov]

The etiology of apical subpleural blebs is unknown but could be related to more negative pleural pressure at the apices which may cause a traction-effect on the adjacent lung. This pressure difference is more marked in taller patients. [advancedradteaching.com]

Most recent data: incidence 2.6 cases per 100,000 Primary vs Secondary SPtx Etiology of SPtx is, bascially, due to connective tissue alterations that predispose to leakage of air from the airways into the pleural space. [pedemmorsels.com]

From the clinical and etiological standpoint the pneumothorax is classified as: primary spontaneous pneumothorax if occurring without obvious reason or apparent lung disease, secondary spontaneous pneumothorax if due to a well known underlying lung or [mrmjournal.biomedcentral.com]

They are organised into groups, and further divided into clinical, etiological or histopathological sub-types. [orpha.net]

Epidemiology pathogenesis pneumothorax Pneumothorax is defined as the presence of air in the pleural space. [err.ersjournals.com]

There are many causes of pneumothorax which makes it impossible to generalize the epidemiology. [radiopaedia.org]

Epidemiology of pneumothorax in England. Thorax. Aug 2000;55(8):666-671. Bense L, Eklund G, Wiman LG. Smoking and the increased risk of contracting spontaneous pneumothorax. Chest. Dec 1987;92(6):1009-1012. [superpharmacy.com.au]

Epidemiology The incidence of primary spontaneous pneumothorax (PSP) is 24/100,000 a year in men and 9.9/100,000 a year in women in England and Wales [ 4 ]. [patient.info]

This suggests a possible pathophysiologic relationship between SCA1 and familial occurrence of spontaneous pneumothorax. [ncbi.nlm.nih.gov]

An overview of relevant and updated information on epidemiology, pathophysiology and cause(s) of spontaneous (primary and secondary) pneumothorax is described. [err.ersjournals.com]

An overview of relevant and updated information on epidemiology, pathophysiology, and management of spontaneous (primary and secondary), catamenial, and traumatic (iatrogenic and noniatrogenic) pneumothorax is given. 2008 S. [karger.com]

Pathophysiology: In PSP, subpleural bullae are found in 76-100% of patients during video-assisted thoracoscopic surgery and in virtually all patients during thoracotomy. [razianesth.freeservers.com]

Otherwise, his father and two elder sisters also had relapsed primary SP in spite of recurrent prevention therapies. This transmission pattern of the disease phenotype suggested an autosomal dominant inheritance. [ncbi.nlm.nih.gov]

Seite 223 - American Thoracic Society/Centers for Disease Control and Prevention/Infectious Diseases Society of America: treatment of tuberculosis. Am J Respir Crit Care Med 2003;167:603-662. ‎ [books.google.de]

In our study, both patients were treated with thoracoscopic surgery and apical pleurectomy was performed to prevent recurrence without complications. [ispub.com]

This prevents your lung from expanding properly when you try to breathe in, causing shortness of breath and chest pain. [northshore.org]