Case presentation. This paper presents the case of a 7-year old child presenting with super-refractory status epilepticus and multifocal seizures. [revistas.unal.edu.co]

• Epilepsy

  […] https://doi.org/10.15446/cr.v4n1.61288 Febrile Infection-Related Epilepsy Syndrome (FIRES), a possible cause of super-refractory status epilepticus. Case report. Keywords: Epilepsy; Refractory Epilepsy; Child, Polytherapy; Fever.+. [revistas.unal.edu.co]

  […] and Ragged Red Fibers Myoclonic Epilepsy Associated with Ragged Red Fibers Myoclonic Epilepsy Associated with Ragged-Red Fibers Myoclonic Epilepsy with Ragged Red Fibers Myoclonic Epilepsy with Ragged-Red Fibers Myoclonus with Epilepsy with Ragged Red [finto.fi]

• Inflammation

  Acute encephalopathy with inflammation-mediated status epilepticus. Neurology. 2011;10(1):99-108. http://doi.org/cmck7r. 10.Illingworth MA, Hanrahan D, Anderson CE, O’Kane K, Anderson J, Casey M, et al. [revistas.unal.edu.co]

• Encephalopathy

  Epileptic encephalopathies (including severe epilepsy syndromes). Epilepsia. 2012;53(Suppl 4):114-26. http://doi.org/f37p2r. [revistas.unal.edu.co]

• Seizure

  Initially, isolated seizures, which quickly evolve to SE, may be observed (4). [revistas.unal.edu.co]

The presence of antibodies and an excessive inflammatory response could justify the use of immunotherapy as a treatment for FIRES (3,16). [revistas.unal.edu.co]

Prognosis A third of patients die, usually, 4-8 months after the acute phase or suffer from refractory epilepsy and intellectual disability (3,4,21,31); only a few survive the episode without any neurological sequelae (21,31,32,38,39). [revistas.unal.edu.co]

The presence of prolonged SE can be related to mitochondrial disorders etiologies and affect the reserve of energy and, therefore, neuronal function (11,16). [revistas.unal.edu.co]